Mouse MitoCarta3.0: 1140 mitochondrial genes

The MitoCarta3.0 mouse inventory is a collection of 1140 nuclear and mtDNA genes encoding proteins with strong support of mitochondrial localization. This table provides a summary of evidence supporting mitochondrial localization, the protein distribution across 14 tissues, as well as annotation of biological pathways (based on manual literature review) and sub-compartment (based on annotator's "best guess" integrating sequence features, experimental data, literature, and pathway context; note all subunits of protein complexes are assigned the same compartment). The genes are ordered by strength of mitochondrial evidence. More complete information is available for download in file Mouse.MitoCarta3.0.xls. See also MitoCarta3.0 home for a description of the project and MitoCarta3.0 documentation for information on the columns below.

SymbolDescriptionSynonymsMaestro scoreEvidenceSub-compartmentMitoPathwaysTissues
Cyc1cytochrome ­c-12610002H19Rik, AA408921, Cyct1, Q9D0M3, gene:6644544literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
Metabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Electron carriers > Cytochromes;
OXPHOS > OXPHOS subunits
all 14
Pdha1pyruvate ­dehydrogenase ­E1 ­alpha ­1Pdha, Pdha-1, P35486, gene:1859742literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Atp5dATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­delta ­subunit0610008F14Rik, 1500000I11Rik, AA960090, AI876556, AU020773, Atp5f1d, C85518, Q9D3D9, gene:6604342literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Isca2iron-sulfur ­cluster ­assembly ­20710001C05Rik, 5730594E03Rik, Hbld, Hbld1, Q9DCB8, gene:7431642APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
Pdhbpyruvate ­dehydrogenase ­(lipoamide) ­beta2610103L06Rik, AL024199, C81408, Q9D051, gene:6826342literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Uqcrc1ubiquinol-cytochrome ­c ­reductase ­core ­protein ­11110032G10Rik, Q9CZ13, gene:2227342literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
OXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits
all 14
Coq9coenzyme ­Q92310005O14Rik, C78387, Q8K1Z0, gene:6791442APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismall 14
Mrpl12mitochondrial ­ribosomal ­protein ­L120610034O11Rik, 1500031N16Rik, L12mt, MRP-, MRP-L12, Rpm, Rpml12, Q9DB15, gene:5628242literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > Transcription;
Mitochondrial central dogma > Translation > Mitochondrial ribosome
all 14
Mrps35mitochondrial ­ribosomal ­protein ­S35MDSO, MDSO23, MRP, MRP-, MRP-S28, MRPS28, Q8BJZ4, gene:23253642literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Cox5acytochrome ­c ­oxidase ­subunit ­5AAA959768, CcO, CcOX, P12787, gene:1285842literature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Uqcrfs1ubiquinol-cytochrome ­c ­reductase, ­Rieske ­iron-sulfur ­polypeptide ­14430402G14Rik, AI875505, Q9CR68, gene:6669441literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Coq7demethyl-Q ­7clk-, clk-1, P97478, gene:1285041literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismall 14
Sdhasuccinate ­dehydrogenase ­complex, ­subunit ­A, ­flavoprotein ­(Fp)1500032O14Rik, 2310034D06Rik, 4921513A11, C81073, F, FP, SDH, SDH2, SDHF, Q8K2B3, gene:6694541literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex II > CII subunits;
Metabolism > Carbohydrate metabolism > TCA cycle;
OXPHOS > OXPHOS subunits
all 14
Sdhbsuccinate ­dehydrogenase ­complex, ­subunit ­B, ­iron ­sulfur ­(Ip)0710008N11Rik, Q9CQA3, gene:6768041literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex II > CII subunits;
Metabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Atp5a1ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­alpha ­subunit ­1AI035633, AL022851, AL023067, At, Atp5f1a, Atpm, D18Ertd206, D18Ertd206e, Mom, Mom2, Q03265, gene:1194641literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Sdhaf4succinate ­dehydrogenase ­complex ­assembly ­factor ­41110058L19Rik, 1700001E18Rik, C6orf57, Q8BTE0, gene:6800241targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MSMatrixOXPHOS > Complex II > CII assembly factors;
OXPHOS > OXPHOS assembly factors
adipose, testis
Pmpcbpeptidase ­(mitochondrial ­processing) ­beta3110004O18Rik, MPP, MPP11, MPPB, MPPP52, Q9CXT8, gene:7307841literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases
all 14
Sdhdsuccinate ­dehydrogenase ­complex, ­subunit ­D, ­integral ­membrane ­protein3110001M13Rik, AVLL5809, C78570, PRO19626, Q9CXV1, gene:6692541literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex II > CII subunits;
Metabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Metals and cofactors > Heme-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Uqcrc2ubiquinol ­cytochrome ­c ­reductase ­core ­protein ­21500004O06Rik, Q9DB77, gene:6700340literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
OXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits
all 14
Coq5coenzyme ­Q5 ­methyltransferase1810014G04Rik, D5Ertd33, D5Ertd33e, Q9CXI0, gene:5206440APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismall 14
Ogdhoxoglutarate ­(alpha-ketoglutarate) ­dehydrogenase ­(lipoamide)2210403E04Rik, 2210412K19Rik, AA409584, d1401, mKIAA4192, Q60597, gene:1829340literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Uqcrqubiquinol-cytochrome ­c ­reductase, ­complex ­III ­subunit ­VII1100001F06Rik, 1500040F11Rik, 5830407L17Rik, 9.5kDa, AA959903, QP-, QP-C, Qp, Qpc, Uqcrb, c1502, Q9CQ69, gene:2227240literature, APEX_IMS, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits
all 14
Mdh2malate ­dehydrogenase ­2, ­NAD ­(mitochondrial)MDH, Mdh-2, Mo, Mor, Mor-1, Mor1, P08249, gene:1744839literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Carbohydrate metabolism > TCA cycle
all 14
Dbtdihydrolipoamide ­branched ­chain ­transacylase ­E2BCKAD-E2, D3Wsu60, D3Wsu60e, P53395, gene:1317138literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex
all 14
Dlatdihydrolipoamide ­S-acetyltransferase ­(E2 ­component ­of ­pyruvate ­dehydrogenase ­complex)6332404G05Rik, DLTA, PDC-E, PDC-E2, Q8BMF4, gene:23533938literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Lrpprcleucine-rich ­PPR-motif ­containing3110001K13Rik, C76645, Gp130, Lrp, Lrp130, Lsfc, Q6PB66, gene:7241638literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial central dogma > Translation
all 14
Mrpl53mitochondrial ­ribosomal ­protein ­L531110007K17Rik, Q9D1H8, gene:6849938literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Dlstdihydrolipoamide ­S-succinyltransferase ­(E2 ­component ­of ­2-oxo-glutarate ­complex)1600017E01Rik, 4632413C10Rik, 4930529O08Rik, DLTS, Q9D2G2, gene:7892038literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Amino acid metabolism > Lysine metabolism
all 14
Pdhxpyruvate ­dehydrogenase ­complex, ­component ­XAI481367, E3bp, Pdx, Pdx1, Q8BKZ9, gene:2740238literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Gfm1G ­elongation ­factor, ­mitochondrial ­1AW545374, D3Wsu133, D3Wsu133e, Gfm, Q8K0D5, gene:2803037literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorsall 14
Grpel1GrpE-like ­1, ­mitochondrialAA408748, mt-GrpE, mt-GrpE#1, mt-Grpel1, Q99LP6, gene:1771337literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Import motor;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis
all 14
Mpc2mitochondrial ­pyruvate ­carrier ­20610006C01Rik, 2010002I07Rik, 2610205H19Rik, AA108335, Brp, Brp44, ESTM4, ESTM43, Q9D023, gene:7045637literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Pyruvate metabolism;
Metabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport
all 14
Uqcr10ubiquinol-cytochrome ­c ­reductase, ­complex ­III ­subunit ­X1110020P15Rik, AA960494, Ucrc, Q8R1I1, gene:6615237literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits
all 14
Coq3coenzyme ­Q3 ­methyltransferase4732433J24, C77934, Q8BMS4, gene:23002737APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Atp5eATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­epsilon ­subunit2410043G19Rik, ATPE, AV000645, Atp5f1e, P56382, gene:6712637literature, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Slc25a3solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­phosphate ­carrier), ­member ­35730556H19Rik, PTP, Ph, Phc, Q8VEM8, gene:1867437literature, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Copper metabolism;
Signaling > Calcium homeostasis > Calcium cycle;
Small molecule transport > SLC25A family
all 14
Mrpl34mitochondrial ­ribosomal ­protein ­L340610007O17Rik, D8Bwg1484e, Q99N91, gene:9406537literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrps15mitochondrial ­ribosomal ­protein ­S151500003E24Rik, 2410002B11Rik, Mprs15, Q9DC71, gene:6640737literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Sdhcsuccinate ­dehydrogenase ­complex, ­subunit ­C, ­integral ­membrane ­protein0610010E03Rik, AI316496, AU019277, Q9CZB0, gene:6605236literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MIMOXPHOS > Complex II > CII subunits;
Metabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Metals and cofactors > Heme-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Atp5bATP ­synthase, ­H+ ­transporting ­mitochondrial ­F1 ­complex, ­beta ­subunitAtp5f1b, P56480, gene:1194736literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Mrps23mitochondrial ­ribosomal ­protein ­S23D11Bwg1153e, MRP-S23, Rpm, Rpms23, S23mt, Q8VE22, gene:6465636literature, APEX_matrix, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Etfaelectron ­transferring ­flavoprotein, ­alpha ­polypeptide2010200I21Rik, D9Ertd394, D9Ertd394e, Q99LC5, gene:11084236literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Electron carriers > Q-linked reactions, other
all 14
Fh1fumarate ­hydratase ­1Fh, Fh-1, fuma, P97807, gene:1419436literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Mrps27mitochondrial ­ribosomal ­protein ­S272610028H14Rik, Q8BK72, gene:21850636literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Isca1iron-sulfur ­cluster ­assembly ­11810010A06Rik, Hbld, Hbld2, Q9D924, gene:6904636APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Idh3aisocitrate ­dehydrogenase ­3 ­(NAD+) ­alpha1110003P10Rik, 1500012E04Rik, AA407078, AI316514, Q9D6R2, gene:6783436APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Ndufs1NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S15830412M15Rik, 9930026A05Rik, Q91VD9, gene:22719735literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits
all 14
AuhAU ­RNA ­binding ­protein/enoyl-coenzyme ­A ­hydrataseC77140, W91705, Q9JLZ3, gene:1199235literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolism;
Metabolism > Amino acid metabolism > BCAA metabolism
all 14
Afg3l2AFG3-like ­AAA ­ATPase ­22310036I02Rik, AW260507, Emv6, Emv66, par, Q8JZQ2, gene:6959735literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Pmpcapeptidase ­(mitochondrial ­processing) ­alpha1200002L24Rik, 4933435E07Rik, Alp, Alpha-MPP, IN, P-55, Q9DC61, gene:6686535literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases
all 14
Cox11cytochrome ­c ­oxidase ­assembly ­protein ­11, ­copper ­chaperone2010004I09Rik, Q6P8I6, gene:6980235literature, APEX_IMS, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, spinalcord, skeletalmuscle, largeintestine, placenta
Sucla2succinate-Coenzyme ­A ­ligase, ­ADP-forming, ­beta ­subunit4930547K18Rik, A-SCS, SCS-betaA, Q9Z2I9, gene:2091635literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Carbohydrate metabolism > Itaconate metabolism;
Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing
all 14
Lars2leucyl-tRNA ­synthetase, ­mitochondrialAI035546, Kiaa0028, LEURS, Q8VDC0, gene:10243635literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesall 14
Atp5oATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­O ­subunitATPO, Atp5po, D12Wsu28, D12Wsu28e, OSCP, Q9DB20, gene:2808034literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Mrpl46mitochondrial ­ribosomal ­protein ­L463110052F15Rik, C15orf4, C80107, LIEC, LIECG2, P2E, P2ECSL, Q9EQI8, gene:6730834literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
Cox15cytochrome ­c ­oxidase ­assembly ­protein ­152900026G05Rik, Q8BJ03, gene:22613934literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Heme synthesis and processing;
OXPHOS > OXPHOS assembly factors
cerebrum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Higd2aHIG1 ­domain ­family, ­member ­2A2010110M21Rik, AA690237, Q9CQJ1, gene:6704434APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > OXPHOS assembly factors;
OXPHOS > Respirasome assembly
all 14
Uqcrhubiquinol-cytochrome ­c ­reductase ­hinge ­protein2210416J04Rik, 2310021J10Rik, 2610041P16Rik, P99028, gene:6657634literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits
all 14
Etfdhelectron ­transferring ­flavoprotein, ­dehydrogenase0610010I20Rik, AV001013, Q921G7, gene:6684134literature, APEX_matrix, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Electron carriers > Q-linked reactions, other
all 14
Timm10translocase ­of ­inner ­mitochondrial ­membrane ­10Tim1, Tim13, Timm1, Timm13a, P62073, gene:3005934literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting
cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Echs1enoyl ­Coenzyme ­A ­hydratase, ­short ­chain, ­1, ­mitochondrialC80529, SCEH, Q8BH95, gene:9374734literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism
all 14
Hadhahydroxyacyl-CoA ­dehydrogenase ­trifunctional ­multienzyme ­complex ­subunit ­alphaC77020, Mt, Mtpa, TP-alpha, Q8BMS1, gene:9721233literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Amino acid metabolism > BCAA metabolism
all 14
Bckdhabranched ­chain ­ketoacid ­dehydrogenase ­E1, ­alpha ­polypeptideQ3U3J1, gene:1203933literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex
cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Suclg1succinate-CoA ­ligase, ­GDP-forming, ­alpha ­subunit1500000I01Rik, Suc, Sucla1, Q9WUM5, gene:5645133targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Carbohydrate metabolism > Itaconate metabolism;
Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing
all 14
Cscitrate ­synthase2610511A05Rik, 9030605P22Rik, Ahl4, BB234005, C, Cis, ah, Q9CZU6, gene:1297433literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Cox6a1cytochrome ­c ­oxidase ­subunit ­6A1VIaL, P43024, gene:1286133literature, targetP signal+, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Acadsacyl-Coenzyme ­A ­dehydrogenase, ­short ­chainAI196007, Bcd-1, Bcd1, Hdlq, Hdlq8, SC, SCAD, Q07417, gene:1140933literature, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Ndufv2NADH:ubiquinone ­oxidoreductase ­core ­subunit ­V22900010C23Rik, Q9D6J6, gene:7290032literature, APEX_matrix, targetP signal+, Rickettsial homolog, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Iars2isoleucine-tRNA ­synthetase ­2, ­mitochondrial2010002H18Rik, C79125, Q8BIJ6, gene:38131432APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesall 14
Coq6coenzyme ­Q6 ­monooxygenase5930427M12Rik, AW742344, Q8R1S0, gene:21770732literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Atp5kATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1F0 ­complex, ­subunit ­E2610008D24Rik, Atp5i, Atp5me, Lfm, Lfm1, Q06185, gene:1195832literature, APEX_IMS, yeast mito homolog++, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits;
Mitochondrial dynamics and surveillance > Cristae formation
all 14
Idh3bisocitrate ­dehydrogenase ­3 ­(NAD+) ­betaC78231, Q91VA7, gene:17071832literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Ndufa6NADH:ubiquinone ­oxidoreductase ­subunit ­A614kD, 14kDa, 2700038D15Rik, B230217P19Rik, Q9CQZ5, gene:6713032literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Letm1leucine ­zipper-EF-hand ­containing ­transmembrane ­protein ­1Q9Z2I0, gene:5638432literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MIMSignaling > Calcium homeostasis > Calcium cycleall 14
Atpaf2ATP ­synthase ­mitochondrial ­F1 ­complex ­assembly ­factor ­2ATP, ATP12, ATP12p, Q91YY4, gene:24678232literature, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMatrixOXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Rtn4ip1reticulon ­4 ­interacting ­protein ­1D10Ertd690, D10Ertd690e, N, NIMP, Q924D0, gene:17072832literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++Matrixnoneall 14
Mrpl43mitochondrial ­ribosomal ­protein ­L434930442D21Rik, bMRP, bMRP36a, Q5RL20, gene:9406731literature, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Abhd11abhydrolase ­domain ­containing ­111110054D16Rik, A630008N09Rik, Wbscr, Wbscr21, Q8K4F5, gene:6875831literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Timm50translocase ­of ­inner ­mitochondrial ­membrane ­502810403L02Rik, AU015082, TIM5, TIM50L, Q9D880, gene:6652531literature, APEX_IMS, targetP signal+, yeast mito homolog++, mito protein domain, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathwayall 14
Mrpl28mitochondrial ­ribosomal ­protein ­L281110015G04Rik, L28mt, MAA, MAAT1, MRP-L28, p1, p15, Q9D1B9, gene:6861131literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sdhaf2succinate ­dehydrogenase ­complex ­assembly ­factor ­20610038F07Rik, AA407634, AW049997, Q8C6I2, gene:6607231GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixOXPHOS > Complex II > CII assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ndufb8NADH:ubiquinone ­oxidoreductase ­subunit ­B82900010I05Rik, AI987932, CI-ASHI, Q9D6J5, gene:6726431literature, APEX_IMS, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Dlddihydrolipoamide ­dehydrogenaseO08749, gene:1338231literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism;
Metabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex;
Metabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Amino acid metabolism > Glycine cleavage system
all 14
Ndufs2NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S2CI-49kD, Q91WD5, gene:22664631literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Ndufv1NADH:ubiquinone ­oxidoreductase ­core ­subunit ­V1CI-51kD, Q91YT0, gene:1799531literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Opa1OPA1, ­mitochondrial ­dynamin ­like ­GTPase1200011N24Rik, AI225888, AI847218, l, lilr3, mKIAA0567, P58281, gene:7414331literature, APEX_IMS, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Cristae formation
all 14
Immtinner ­membrane ­protein, ­mitochondrial1700082C19Rik, D830041H16Rik, HM, HMP, Mico, Micos60, P8, P87, P87/8, P87/89, P89, mit, Q8CAQ8, gene:7661431literature, targetP signal, yeast mito homolog, mito protein domain+, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Apoolapolipoprotein ­O-like6720473G16Rik, 9430083G14Rik, E130106L15Rik, Mico, Micos27, Q78IK4, gene:6811731literature, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Lonp1lon ­peptidase ­1, ­mitochondrial1200017E13Rik, LON, Pr, Prss15, Q8CGK3, gene:7414231literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Letmd1LETM1 ­domain ­containing ­11110019O13Rik, AI593524, BB130465, BB235638, HCCR, HCCR-, HCCR-2, HCCR1, MCC-32, Mccr, Q924L1, gene:6861431GFP, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MembraneSmall molecule transportcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Pdk4pyruvate ­dehydrogenase ­kinase, ­isoenzyme ­4AV005916, O70571, gene:2727331literature, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, testis
Mtif2mitochondrial ­translational ­initiation ­factor ­22310038D14Rik, 2410112O06Rik, IF-2(Mt), IF-2m, IF-2mt, IF2(mt), Q91YJ5, gene:7678431literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Translation factorsall 14
Ndufs8NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S8BC021616, CI-23kD, TYKY, Q8K3J1, gene:22588730literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Ndufs7NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S71010001M04Rik, CI-20kD, Q9DC70, gene:7540630literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Mrrfmitochondrial ­ribosome ­recycling ­factor2400002D02Rik, MRFF, MTRRF, RRF, Q9D6S7, gene:6787130literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorsall 14
Mrpl2mitochondrial ­ribosomal ­protein ­L2CGI-2, CGI-22, L2mt, MRP-, MRP-L14, MRP-L2, Rpm, Rpml14, Q9D773, gene:2739830literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomespinalcord, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
Gfm2G ­elongation ­factor, ­mitochondrial ­26530419G12Rik, A930009M04Rik, EF-G2mt, EFG2, MST02, MST027, RRF2mt, Q8R2Q4, gene:32080630literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorsall 14
Timm9translocase ­of ­inner ­mitochondrial ­membrane ­92810011L15Rik, Tim1, Tim10a, Timm1, Timm10, Q9WV98, gene:3005630literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting
all 14
Pitrm1pitrilysin ­metallepetidase ­12310012C15Rik, AA410010, MP-, MP-1, MP1, Ntu, Ntup1, P, PreP, mKIAA1104, Q8K411, gene:6961730literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Acadmacyl-Coenzyme ­A ­dehydrogenase, ­medium ­chainAU018656, MCA, MCAD, P45952, gene:1136430literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Supv3l1suppressor ­of ­var1, ­3-like ­1 ­(S. ­cerevisiae)6330443E10Rik, Q80YD1, gene:33835930literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrpl1mitochondrial ­ribosomal ­protein ­L12410002L03Rik, 5830418D04Rik, AI462572, L1mt, Q99N96, gene:9406130literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Aco2aconitase ­2, ­mitochondrialAc, Aco, Aco-2, Aco3, D10Wsu183, D10Wsu183e, Q99KI0, gene:1142930literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
Coq10acoenzyme ­Q10AGm1, E9Q3H6, gene:21058230targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach
Samm50SAMM50 ­sorting ­and ­assembly ­machinery ­component1110030L07Rik, Q8BGH2, gene:6865330literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, induction, coexpression++, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
all 14
Mrps2mitochondrial ­ribosomal ­protein ­S21500019M10Rik, Q924T2, gene:11845130literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Surf1surfeit ­gene ­10610010F23Rik, Surf, Surf-1, P09925, gene:2093030literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl44mitochondrial ­ribosomal ­protein ­L441810030E18Rik, 5730593H20Rik, AI463302, Q9CY73, gene:6916330literature, APEX_matrix, targetP signal+, yeast mito homolog++, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
PhbprohibitinBap32, P67778, gene:1867330literature, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Guf1GUF1 ­homolog, ­GTPase4631409J12, AA407526, EF-4, Q8C3X4, gene:23127930APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MatrixMitochondrial central dogma > Translationcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Polrmtpolymerase ­(RNA) ­mitochondrial ­(DNA ­directed)1110018N15Rik, 4932416K13, Q8BKF1, gene:21615129literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression++, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtRNA metabolism > Transcription
cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Ghitmgrowth ­hormone ­inducible ­transmembrane ­protein1010001P14Rik, C77840, MICS1, PTD01, PTD010, Tmbim, Tmbim5, Q91VC9, gene:6609229literature, APEX_IMS, targetP signal+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MSMIMMitochondrial dynamics and surveillance > Apoptosisall 14
Timm13translocase ­of ­inner ­mitochondrial ­membrane ­13D10Ertd378, D10Ertd378e, Tim, Tim9, Timm, Timm9, P62075, gene:3005529literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting
all 14
Cpt2carnitine ­palmitoyltransferase ­2AI323697, CP, CPTII, P52825, gene:1289629literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle
all 14
Mrpl10mitochondrial ­ribosomal ­protein ­L100610040E02Rik, C78440, L10mt, MRP, MRP-L8, Rp, Rpml8, Q3TBW2, gene:10773229literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mto1mitochondrial ­tRNA ­translation ­optimization ­12310039H01Rik, 5730419A02Rik, Q923Z3, gene:6829129literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism
cerebellum, spinalcord, stomach, placenta
Prdx3peroxiredoxin ­3A, AW822249, Aop1, D0Toh, D0Tohi1, Ef2, Ef2l, Mer, Mer5, Prx3, SP, SP22, TDXM, P20108, gene:1175729literature, APEX_IMS, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismall 14
Cox7a2cytochrome ­c ­oxidase ­subunit ­7A2COX, COX7AL, Cox7, Cox7a3, CoxVIIa-L, P48771, gene:1286629literature, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Atp5jATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­FAtp5pf, CF6, P97450, gene:1195729literature, APEX_IMS, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Iba57IBA57 ­homolog, ­iron-sulfur ­cluster ­assembly4930543L23Rik, A230051G13Rik, C1orf69, Q8CAK1, gene:21679229APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesiscerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl40mitochondrial ­ribosomal ­protein ­L40Nl, Nlvcf, Q9Z2Q5, gene:1810029literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hibch3-hydroxyisobutyryl-Coenzyme ­A ­hydrolase2610509I15Rik, HIBYL-C, HIBYL-COA-H, Q8QZS1, gene:22709529literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Ndufs6NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S6BC059730, IP, IP13, P52503, gene:40778529literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Oxct13-oxoacid ­CoA ­transferase ­12610008O03Rik, Oxct, Oxct2a, Sco, Scot-s, Q9D0K2, gene:6704129literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Gatd3aglutamine ­amidotransferase ­like ­class ­1 ­domain ­containing ­3AC21orf33, D10Jhu81e, ES1, Q9D172, gene:2829529APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++Matrixnoneall 14
Ndufb9NADH:ubiquinone ­oxidoreductase ­subunit ­B91190008J14Rik, CI-B22, Q9CQJ8, gene:6621829literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Cox6ccytochrome ­c ­oxidase ­subunit ­6CQ9CPQ1, gene:1286429literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Sod2superoxide ­dismutase ­2, ­mitochondrialMn, MnSOD, Sod, Sod-2, P09671, gene:2065629literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismall 14
Ndufb5NADH:ubiquinone ­oxidoreductase ­subunit ­B50610007D05Rik, AU015782, CI-SGDH, SGDH, Q9CQH3, gene:6604629literature, APEX_IMS, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Hadhhydroxyacyl-Coenzyme ­A ­dehydrogenaseAA409008, AU019341, AW742602, HCDH, Hadhsc, Sch, Schad, Q61425, gene:1510728literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > Lysine metabolism
all 14
FechferrochelataseAI894116, Fc, Fcl, fch, Q544X6, gene:1415128literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
Liaslipoic ­acid ­synthetase2900022L22Rik, 4933425M12Rik, 7a5e, 7a5ex, C77512, LS, lip-syn, mL, Q99M04, gene:7946428literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertion;
Metabolism > Metals and cofactors > Fe-S-containing proteins
brainstem, skeletalmuscle, adipose, largeintestine, placenta
Nfs1nitrogen ­fixation ­gene ­1 ­(S. ­cerevisiae)AA987187, m-Nf, m-Nfs1, m-Nfsl, Q9Z1J3, gene:1804128literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
Fdx1ferredoxin ­1ADRE, P46656, gene:1414828literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
Metabolism > Vitamin metabolism > Vitamin D metabolism
all 14
Mrm1mitochondrial ­rRNA ­methyltransferase ­1A530065E19Rik, Q99J25, gene:21703828APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
spinalcord, placenta, testis
Mrps18amitochondrial ­ribosomal ­protein ­S18A1110004O20Rik, C79712, Q99N85, gene:6856528literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Malsu1mitochondrial ­assembly ­of ­ribosomal ­large ­subunit ­12410003K15Rik, Matsu1, Q9CWV0, gene:7559328literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblycerebrum, cerebellum, liver, smallintestine, largeintestine, placenta
Gatbglutamyl-tRNA(Gln) ­amidotransferase, ­subunit ­B9430026F02Rik, Pet11, Pet112, Pet112l, Q99JT1, gene:22948728literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, skeletalmuscle, adipose, stomach, testis
Yars2tyrosyl-tRNA ­synthetase ­2 ­(mitochondrial)2210023C10Rik, tyrRS, Q8BYL4, gene:7012028literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesbrainstem, spinalcord, kidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
FxnfrataxinFA, FARR, Fr, Frda, X25, O35943, gene:1429728literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesisall 14
Idh3gisocitrate ­dehydrogenase ­3 ­(NAD+), ­gammaP70404, gene:1592928literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Mrps28mitochondrial ­ribosomal ­protein ­S281500012D08Rik, AW061224, Q9CY16, gene:6623028literature, targetP signal+, mito protein domain+, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Timm44translocase ­of ­inner ­mitochondrial ­membrane ­440710005E20Rik, D8Ertd118, D8Ertd118e, Mimt4, Mimt44, Tim4, Tim44, O35857, gene:2185628literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motorall 14
Clpxcaseinolytic ­mitochondrial ­matrix ­peptidase ­chaperone ­subunitAU014732, E330029I21, Q9JHS4, gene:27016628literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Mrpl3mitochondrial ­ribosomal ­protein ­L32010320L16Rik, 5930422H18Rik, AA407889, L3mt, dc, dcr, Q99N95, gene:9406228literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Mecrmitochondrial ­trans-2-enoyl-CoA ­reductaseAI195831, NRBF-1, Nrb, Nrbf1, Q9DCS3, gene:2692228literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisall 14
Slc25a20solute ­carrier ­family ­25 ­(mitochondrial ­carnitine/acylcarnitine ­translocase), ­member ­201110007P09Rik, C78826, CAC, Cact, mCA, mCAC, Q9Z2Z6, gene:5727928literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle;
Small molecule transport > SLC25A family
all 14
Slc25a4solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­adenine ­nucleotide ­translocator), ­member ­4AU019225, An, Ant1, mANC1, P48962, gene:1173928literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Small molecule transport > SLC25A family
all 14
Mtch2mitochondrial ­carrier ­22310034D24Rik, 4930539J07Rik, HSPC0, HSPC032, Q791V5, gene:5642828literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression+, MS/MS++MOMSmall molecule transport > SLC25A family;
Mitochondrial dynamics and surveillance > Fusion
all 14
Pdk2pyruvate ­dehydrogenase ­kinase, ­isoenzyme ­2Q9JK42, gene:1860428literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Cox6b1cytochrome ­c ­oxidase, ­subunit ­6B12010000G05Rik, COX VIb-1, Cox6b, P56391, gene:11032328literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Vdac1voltage-dependent ­anion ­channel ­1AL033343, Vda, Vdac5, mVDAC1, mVDAC5, Q60932, gene:2233328literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MOMSignaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Mitochondrial dynamics and surveillance > Organelle contact sites;
Small molecule transport
all 14
Mrpl4mitochondrial ­ribosomal ­protein ­L41110017G11Rik, Q9DCU6, gene:6616328literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Mrps14mitochondrial ­ribosomal ­protein ­S141810032L21Rik, AL022847, Rpm, Rpms14, Q9CR88, gene:6465928literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hspa9heat ­shock ­protein ­974kDa, C, Csa, GRP, Grp75, Hs, Hsc7, Hsc74, Hsp, Hsp74, Hsp74a, Hspa9a, Mortalin, Mot-2, Mot2, Mthsp70, PBP, Pbp74, mo, mot-, mthsp, P38647, gene:1552628APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesisall 14
Ndufa9NADH:ubiquinone ­oxidoreductase ­subunit ­A91010001N11Rik, Q9DC69, gene:6610827literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Ndufa2NADH:ubiquinone ­oxidoreductase ­subunit ­A2AV000592, B8, C1-B8, CI-B8, Q9CQ75, gene:1799127literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Iscuiron-sulfur ­cluster ­assembly ­enzyme2310020H20Rik, AA407971, ISCU2, Ni, Nifu, Nifun, Q9D7P6, gene:6638327literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
C1qbpcomplement ­component ­1, ­q ­subcomponent ­binding ­proteinAA407365, AA986492, D11Wsu182, D11Wsu182e, HAB, HABP1, P3, P32, gC1qBP, Q8R5L1, gene:1226127literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixSignaling > Immune responseall 14
Afg1lAFG1 ­like ­ATPaseCG8520, Lac, Lace1, Q3V384, gene:21595127APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, spinalcord, heart, adipose, smallintestine, largeintestine, stomach, placenta
Micos10mitochondrial ­contact ­site ­and ­cristae ­organizing ­system ­subunit ­102310028O11Rik, Mi, Minos1, Q7TNS2, gene:43377127literature, APEX_IMS, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Cox17cytochrome ­c ­oxidase ­assembly ­protein ­17, ­copper ­chaperoneAI037035, COX1, P56394, gene:1285627literature, APEX_IMS, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++IMSOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors
heart, adipose, smallintestine, placenta, testis
Uqcc1ubiquinol-cytochrome ­c ­reductase ­complex ­assembly ­factor ­12310079L17Rik, 2410003P15Rik, 3110038N19Rik, Bfz, Bfzb, Bfzp, Cbp, Cbp3, Uqcc, Q9CWU6, gene:5604627literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl33mitochondrial ­ribosomal ­protein ­L330610009M10Rik, L33mt, MRP-L33, Q9CQP0, gene:6684527literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, stomach, placenta, testis
Acadlacyl-Coenzyme ­A ­dehydrogenase, ­long-chainAA960361, AU018452, C79855, LC, LCAD, P51174, gene:1136327literature, targetP signal+, mito protein domain+, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Ndufs4NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S46720411N02Rik, C1-18k, Q9CXZ1, gene:1799327literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Phb2prohibitin ­2AU044498, BAP, Bap37, Bcap, Bcap37, R, REA, O35129, gene:1203427literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Bckdhbbranched ­chain ­ketoacid ­dehydrogenase ­E1, ­beta ­polypeptideBCKDE1B, BCKDH E1-beta, Q6P3A8, gene:1204027literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrps12mitochondrial ­ribosomal ­protein ­S12AI327385, Rpm, Rpms12, rp, rps12, O35680, gene:2403027literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mcatmalonyl ­CoA:ACP ­acyltransferase ­(mitochondrial)AI225907, BC025519, Q8R3F5, gene:22372227literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisspinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl24mitochondrial ­ribosomal ­protein ­L242010005E08Rik, 2810470K06Rik, 6720473G22Rik, AA407670, Q9CQ06, gene:6770727literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl13mitochondrial ­ribosomal ­protein ­L131110002D09Rik, Q9D1P0, gene:6853727literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Pccapropionyl-Coenzyme ­A ­carboxylase, ­alpha ­polypeptideC79630, Q91ZA3, gene:11082127literature, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Vitamin metabolism > Biotin utilizing proteins
all 14
Mrpl17mitochondrial ­ribosomal ­protein ­L17MRP-, MRP-L26, Rpm, Rpml26, Q9D8P4, gene:2739727literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Aifm1apoptosis-inducing ­factor, ­mitochondrion-associated ­1A, AIF, AIFsh2, Hq, Pdcd, Pdcd8, Q9Z0X1, gene:2692627literature, APEX_IMS, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > MIA40;
OXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors;
Mitochondrial dynamics and surveillance > Apoptosis
all 14
Cox4i1cytochrome ­c ­oxidase ­subunit ­4I1AL024441, CO, COX, COX IV-1, COXIV, Cox4, Cox4a, IV-1, P19783, gene:1285727literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Ndufaf4NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­41110007M04Rik, 3000003G13Rik, AW214064, Q9D1H6, gene:6849327APEX_matrix, GFP, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
Slc25a35solute ­carrier ­family ­25, ­member ­351810012H11Rik, Q5SWT3, gene:7199827APEX_matrix, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMSmall molecule transport > SLC25A familycerebrum, cerebellum, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dap3death ­associated ­protein ­34921514D13Rik, DAP, DAP-3, MRP-S29, S29mt, Q9ER88, gene:6511127literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Atp5c1ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F1 ­complex, ­gamma ­polypeptide ­11700094F02Rik, Atp5f1c, Q91VR2, gene:1194927literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Slc25a11solute ­carrier ­family ­25 ­(mitochondrial ­carrier ­oxoglutarate ­carrier), ­member ­112310022P18Rik, 2ox, 2oxoc, Q9CR62, gene:6786327literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport > SLC25A family
all 14
Timm8btranslocase ­of ­inner ­mitochondrial ­membrane ­8BTim8, Tim8b, P62077, gene:3005727literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sdhaf1succinate ­dehydrogenase ­complex ­assembly ­factor ­10610010E21Rik, AI430885, AW490662, Lyr, Lyrm8, Q3U276, gene:6833226literature, targetP signal+, yeast mito homolog, mito protein domain+, induction, coexpression+, MS/MSMatrixOXPHOS > Complex II > CII assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrpl15mitochondrial ­ribosomal ­protein ­L15HSPC1, HSPC145, MRP, MRP-L7, Rp, Rpml7, Q9CPR5, gene:2739526literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Alas1aminolevulinic ­acid ­synthase ­1A, ALAS, ALAS-N, Al, Alas-1, Alas-h, Q8VC19, gene:1165526literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Heme synthesis and processingliver, heart, adipose, largeintestine, placenta
Cmc2COX ­assembly ­mitochondrial ­protein ­21110046L09Rik, 2310061C15Rik, DC13, Q8K199, gene:6653126APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+IMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, spinalcord, liver, heart, adipose, largeintestine, stomach, placenta, testis
Pptc7PTC7 ­protein ­phosphatase ­homolog9130017A15Rik, AA672638, AI848390, TA-PP2C, Q6NVE9, gene:32071726APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixSignalingcerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, largeintestine, placenta, testis
Bckdkbranched ­chain ­ketoacid ­dehydrogenase ­kinaseAI327402, BCKD-ki, O55028, gene:1204126literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex
cerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Txn2thioredoxin ­22510006J11Rik, AI788873, Trx, Trx2, P97493, gene:5655126literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MatrixMetabolism > Vitamin metabolism > Vitamin C metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism
all 14
Suclg2succinate-Coenzyme ­A ­ligase, ­GDP-forming, ­beta ­subunitAF171077, AW556404, D6Wsu120, D6Wsu120e, G-SCS, GTPSCS, SCS-betaG, Q9Z2I8, gene:2091726literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle;
Metabolism > Carbohydrate metabolism > Itaconate metabolism;
Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing
all 14
Mfn1mitofusin ­12310002F04Rik, 6330416C07Rik, D3Ertd265, D3Ertd265e, HR, HR2, mKIAA4032, Q811U4, gene:6741426literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Organelle contact sites
cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Ndufb6NADH:ubiquinone ­oxidoreductase ­subunit ­B6CI-B17, Gm137, Q3UIU2, gene:23007526literature, APEX_IMS, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Ndufa5NADH:ubiquinone ­oxidoreductase ­subunit ­A52900002J19Rik, CI-13kD-B, Q9CPP6, gene:6820226literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Mtx2metaxin ­21500012G02Rik, O88441, gene:5337526literature, mito protein domain+, induction, coexpression++, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
all 14
Ogdhloxoglutarate ­dehydrogenase-likeE9Q7L0, gene:23901726APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Acat1acetyl-Coenzyme ­A ­acetyltransferase ­16330585C21Rik, Ac, Acat, Q8QZT1, gene:11044626literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism
all 14
Echdc3enoyl ­Coenzyme ­A ­hydratase ­domain ­containing ­32310005D12Rik, AI662097, Q9D7J9, gene:6785626targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++Matrixnonespinalcord, kidney, liver, heart, adipose, largeintestine, stomach, placenta, testis
Mrpl21mitochondrial ­ribosomal ­protein ­L21BC028768, L21mt, MRP-L21, Q9D1N9, gene:35324226literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Nfu1NFU1 ­iron-sulfur ­cluster ­scaffold0610006G17Rik, CGI-3, CGI-33, Hi, Hirip5, Q9QZ23, gene:5674826APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
Mrpl55mitochondrial ­ribosomal ­protein ­L552810038N09Rik, L55mt, MRP-L55, Q9CZ83, gene:6721226literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Taco1translational ­activator ­of ­mitochondrially ­encoded ­cytochrome ­c ­oxidase ­I2310066I18Rik, Ccdc44, Q8K0Z7, gene:7020726literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factors;
OXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
Sdhaf3succinate ­dehydrogenase ­complex ­assembly ­factor ­30610005M07Rik, 4933430A16Rik, Ac, Acn9, Q8BQU3, gene:7123826targetP signal, yeast mito homolog++, mito protein domain+, coexpression+, MS/MSMatrixOXPHOS > Complex II > CII assembly factors;
OXPHOS > OXPHOS assembly factors
adipose, testis
Mrpl11mitochondrial ­ribosomal ­protein ­L112410001P07Rik, L11mt, Q9CQF0, gene:6641926literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Echdc2enoyl ­Coenzyme ­A ­hydratase ­domain ­containing ­21300017C12Rik, 2610009M20Rik, D4Ertd765e, Q3TLP5, gene:5243026targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++Matrixnoneall 14
Cox5bcytochrome ­c ­oxidase ­subunit ­5BQ9D881, gene:1285926literature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Acadsbacyl-Coenzyme ­A ­dehydrogenase, ­short/branched ­chain1300003O09Rik, 2-MEBCAD, BB066609, SBCAD, Q9DBL1, gene:6688525literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism
all 14
Eral1Era ­(G-protein)-like ­1 ­(E. ­coli)2610524P08Rik, 9130407C09Rik, AU019798, Era, M-ERA, MER, MERA, MERA-S, MERA-W, Q9CZU4, gene:5783725APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
none
Abcb10ATP-binding ­cassette, ­sub-family ­B ­(MDR/TAP), ­member ­10ABC-m, Abc-me, Abcb12, Q9JI39, gene:5619925literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MIMMetabolism > Metals and cofactors > Heme synthesis and processing;
Small molecule transport > ABC transporters
cerebellum, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Bcs1lBCS1-like ­(yeast)9130022O19Rik, Q9CZP5, gene:6682125literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS+MIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hsdl2hydroxysteroid ­dehydrogenase ­like ­22610207I16Rik, Q2TPA8, gene:7247925APEX_matrix, GFP, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS++Matrixnoneall 14
Cmc1COX ­assembly ­mitochondrial ­protein ­12010110K16Rik, 2010312P05Rik, AI596001, Q9CPZ8, gene:6789925APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+IMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Me3malic ­enzyme ­3, ­NADP(+)-dependent, ­mitochondrial1700020C08Rik, B230207H15Rik, Q8BMF3, gene:10926425literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hspd1heat ­shock ­protein ­1 ­(chaperonin)60kDa, CPN60, HSP-60, HSP-65, Hsp, Hsp60, P63038, gene:1551025literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Lyrm7LYR ­motif ­containing ­71700024C24Rik, 9330147L21Rik, Q9DA03, gene:7553025literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MatrixOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
TsfmTs ­translation ­elongation ­factor, ­mitochondrial2310050B20Rik, 9430024O13Rik, EF-T, EF-TS, EF-Tsm, EF-Tsmt, Q9CZR8, gene:6639925literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorscerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ethe1ethylmalonic ­encephalopathy ­10610025L15Rik, Hsco, Q9DCM0, gene:6607125literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixMetabolism > Sulfur metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Aldh4a1aldehyde ­dehydrogenase ­4 ­family, ­member ­A1A930035F14Rik, ALD, Ahd, Ahd-, Ahd-1, Ahd1, Aldh4, Aldh5a1, E330022C09, P5cd, P5cdh, P5cdhl, P5cdhs, Ssd, Ssdh1, Q8CHT0, gene:21264725literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolism;
Metabolism > Amino acid metabolism > Glyoxylate metabolism
all 14
Vdac2voltage-dependent ­anion ­channel ­2Vda, Vdac6, mVDAC2, mVDAC6, Q60930, gene:2233425literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MOMSmall molecule transportall 14
Coa6cytochrome ­c ­oxidase ­assembly ­factor ­61810063B05Rik, AI447995, Q8BGD8, gene:6789225APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
Coq4coenzyme ­Q4D2Ertd97, D2Ertd97e, Q8BGB8, gene:22768325literature, targetP signal+, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, brainstem, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Ivdisovaleryl ­coenzyme ­A ­dehydrogenase1300016K07Rik, 6720455E18Rik, AI463340, Q9JHI5, gene:5635725literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Acadvlacyl-Coenzyme ­A ­dehydrogenase, ­very ­long ­chainVL, vlcad, P50544, gene:1137025literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Slc25a1solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­citrate ­transporter), ­member ­11300019P08Rik, 2610100G11Rik, AI194714, Ctp, Dgs, Dgsj, Slc2, Slc20a3, Q8JZU2, gene:1335825literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > TCA-associated;
Metabolism > Lipid metabolism;
Small molecule transport > SLC25A family
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a42solute ­carrier ­family ­25, ­member ­422900084M01Rik, Q8R0Y8, gene:7309525literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme A metabolism;
Small molecule transport > SLC25A family
all 14
Abcb8ATP-binding ­cassette, ­sub-family ­B ­(MDR/TAP), ­member ­84833412N02Rik, AA409895, MITOSUR, Q9CXJ4, gene:7461025literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMSmall molecule transport > ABC transportersall 14
Ndufs5NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S5AI256693, Q99LY9, gene:59513625literature, APEX_IMS, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Mrps7mitchondrial ­ribosomal ­protein ­S7MRP, MRP-S7, Rp, Rpms7, S7mt, Q80X85, gene:5052925literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome
all 14
Mccc1methylcrotonoyl-Coenzyme ­A ­carboxylase ­1 ­(alpha)1810045E08Rik, 2310058B18Rik, MCC, MCCalpha, Mcca, R75106, Q99MR8, gene:7203925literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Vitamin metabolism > Biotin utilizing proteins
all 14
Mrpl49mitochondrial ­ribosomal ­protein ­L49L49mt, MRP-L49, No, Nof1, Q9CQ40, gene:1812025literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Ndufaf5NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­52310003L22Rik, A2APY7, gene:6948725literature, APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
cerebellum, brainstem, skeletalmuscle, largeintestine, stomach, placenta
Mrps9mitochondrial ­ribosomal ­protein ­S92310002A08Rik, AW322516, Mrp-S9, S9mt, mg637, Q9D7N3, gene:6952725literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome
all 14
Ndufb10NADH:ubiquinone ­oxidoreductase ­subunit ­B100610011B04Rik, 22kD, 22kDa, PDSW, Q9DCS9, gene:6834224literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Dnaja3DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­A31200003J13Rik, 1810053A11Rik, C81173, Tid-, Tid-1, Tid1l, Q99M87, gene:8394524literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Mrpl19mitochondrial ­ribosomal ­protein ­L199030416F12Rik, 9130412E02Rik, D6Ertd157, D6Ertd157e, MRP-, MRP-L15, RL, RLX1, Rpm, Rpml15, Q9D338, gene:5628424literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mipepmitochondrial ­intermediate ­peptidase5730405E07Rik, MIP, A6H611, gene:7047824literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases
cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tomm40ltranslocase ­of ­outer ­mitochondrial ­membrane ­40-likeQ9CZR3, gene:64137624targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression+, MS/MSMOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, testis
Adhfe1alcohol ­dehydrogenase, ­iron ­containing, ­16330565B14Rik, AI043035, Adh8, HOT, Q8R0N6, gene:7618724targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolismkidney, liver, heart, adipose, stomach, placenta
Coq8acoenzyme ­Q8A4632432J16Rik, AI462003, Adck, Adck3, Cabc, Cabc1, mKIAA0451, Q60936, gene:6742624literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismall 14
Bdh13-hydroxybutyrate ­dehydrogenase, ­type ­12310032J20Rik, AI327223, Bdh, Q80XN0, gene:7191124literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Ketone metabolismall 14
Tomm7translocase ­of ­outer ­mitochondrial ­membrane ­71110020J08Rik, AW047273, TOM, Tom7, Q9D173, gene:6616924literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
cerebrum, cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
Hccsholocytochrome ­c ­synthetaseP53702, gene:1515924literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSIMSMetabolism > Metals and cofactors > Heme synthesis and processing;
OXPHOS > OXPHOS subunits;
OXPHOS > Cytochrome C
cerebrum, spinalcord, heart, adipose, smallintestine, largeintestine, placenta, testis
Mrpl16mitochondrial ­ribosomal ­protein ­L162310039D06Rik, Q99N93, gene:9406324literature, targetP signal, yeast mito homolog++, mito protein domain, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Prodhproline ­dehydrogenaseP, Pr, Pro-1, Pro1, Ym24d07, Q9WU79, gene:1912524literature, targetP signal, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Proline metabolism;
Metabolism > Electron carriers > Q-linked reactions, other
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl30mitochondrial ­ribosomal ­protein ­L302310001L22Rik, L30mt, MRP-, MRP-L28, MRP-L30, Rpm, Rpml28, Q9D7N6, gene:10773424literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Ndufa10NADH:ubiquinone ­oxidoreductase ­subunit ­A102900053E13Rik, Q99LC3, gene:6727324literature, targetP signal+, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Mars2methionine-tRNA ­synthetase ­2 ­(mitochondrial)C730026E21Rik, MetRS, Q499X9, gene:21267924literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Clppcaseinolytic ­mitochondrial ­matrix ­peptidase ­proteolytic ­subunitAU019820, D17Wsu160, D17Wsu160e, O88696, gene:5389524literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Ak3adenylate ­kinase ­3AA407498, AI506714, AK-, AK-3, Ak3l, Ak3l1, Akl3l, Q9WTP7, gene:5624824literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingall 14
Spg7SPG7, ­paraplegin ­matrix ­AAA ­peptidase ­subunitAI452278, AU015315, Cm, Cmar, PGN, pa, Q3ULF4, gene:23484723literature, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MSMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sco1SCO1 ­cytochrome ­c ­oxidase ­assembly ­protein2610001C07Rik, D11Bwg1310e, Q5SUC9, gene:5289223literature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Atpif1ATPase ­inhibitory ­factor ­1ATP5IF1, Atpi, IF(1), If, If1, O35143, gene:1198323literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MatrixOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Chchd3coiled-coil-helix-coiled-coil-helix ­domain ­containing ­30610041L09Rik, 1700039J09Rik, AW558177, Mico, Micos19, Q9CRB9, gene:6607523literature, APEX_IMS, APEX_matrix, GFP, Rickettsial homolog, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
all 14
Acad12acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­129330129D05Rik, D3Z7X0, gene:33835023targetP signal+, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hibadh3-hydroxyisobutyrate ­dehydrogenase6430402H10Rik, AI265272, Q99L13, gene:5887523literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Gatcglutamyl-tRNA(Gln) ­amidotransferase, ­subunit ­C2010003O18Rik, Q8CBY0, gene:38428123literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, spinalcord, kidney, largeintestine, testis
Cox8bcytochrome ­c ­oxidase ­subunit ­8BCOX8, Cox8h, CoxVIII-H, P48772, gene:1286923literature, targetP signal, mito protein domain+, induction, coexpression+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
skeletalmuscle
ClpbClpB ­caseinolytic ­peptidase ­BAL118244, Skd, Skd3, Q60649, gene:2048023APEX_IMS, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++IMSProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tmem126atransmembrane ­protein ­126A1810020E01Rik, Q9D8Y1, gene:6627123literature, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
Aldh6a1aldehyde ­dehydrogenase ­family ­6, ­subfamily ­A11110038I05Rik, Mmsd, Mmsdh, Q9EQ20, gene:10477623literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > BCAA metabolismall 14
Mrps18cmitochondrial ­ribosomal ­protein ­S18C1110037D14Rik, Q8R2L5, gene:6873523literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pdk1pyruvate ­dehydrogenase ­kinase, ­isoenzyme ­1B830012B01, D530020C15Rik, Q8BFP9, gene:22802623literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismall 14
Ppifpeptidylprolyl ­isomerase ­F ­(cyclophilin ­F)AW457192, CyP-, CyP-D, CyP-F, Cyp, CypD, PPIase, Q99KR7, gene:10567523literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS++MatrixSignaling > Calcium homeostasis > Mitochondrial permeability transition poreall 14
Lyrm4LYR ­motif ­containing ­4BC034664, Gm903, Q8K215, gene:38084023literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesisall 14
Ech1enoyl ­coenzyme ­A ­hydratase ­1, ­peroxisomalAA617331, O35459, gene:5179823APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolismall 14
Acaa2acetyl-Coenzyme ­A ­acyltransferase ­2 ­(mitochondrial ­3-oxoacyl-Coenzyme ­A ­thiolase)0610011L04Rik, AI255831, AI265397, D18Ertd240, D18Ertd240e, Q8BWT1, gene:5253823literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > Lysine metabolism
all 14
Ndufa7NADH:ubiquinone ­oxidoreductase ­subunit ­A714.5kD, 14.5kDa, 2400007M02Rik, CI-B14.5a, Q9Z1P6, gene:6641623literature, APEX_matrix, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Mrpl35mitochondrial ­ribosomal ­protein ­L351110066C01Rik, Q9CQL6, gene:6622323literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomelargeintestine, testis
Pccbpropionyl ­Coenzyme ­A ­carboxylase, ­beta ­polypeptide1300012P06Rik, AI314687, R74805, Q99MN9, gene:6690423literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation
all 14
Coq2coenzyme ­Q2 ­4-hydroxybenzoate ­polyprenyltransferase2310002F18Rik, PHB:PPT, Q66JT7, gene:7188323literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismnone
Mrpl20mitochondrial ­ribosomal ­protein ­L202610008D01Rik, 4930425I20Rik, Q9CQL4, gene:6644823literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Timm17atranslocase ­of ­inner ­mitochondrial ­membrane ­17a17kD, Tim17a, mTim1, mTim17a, Q9Z0V8, gene:2185423literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathwayall 14
Timm22translocase ­of ­inner ­mitochondrial ­membrane ­22Tim22, Q9CQ85, gene:5632223literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathwayall 14
Mrpl54mitochondrial ­ribosomal ­protein ­L540610008M19Rik, D10Sut1, D10Sut1e, Q9CPW3, gene:6604723literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tomm22translocase ­of ­outer ­mitochondrial ­membrane ­222310047D01, Tom2, Tom22, Q9CPQ3, gene:22369622literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOMall 14
Cratcarnitine ­acetyltransferaseAW107812, CA, CARAT, P47934, gene:1290822literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Mrps5mitochondrial ­ribosomal ­protein ­S51620401I16Rik, AI850294, Q99N87, gene:7772122literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dhtkd1dehydrogenase ­E1 ­and ­transketolase ­domain ­containing ­1C330018I04Rik, A2ATU0, gene:20969222APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MSMatrixMetabolism > Amino acid metabolism > Lysine metabolismcerebrum, kidney, liver, adipose, placenta, testis
Tmem70transmembrane ­protein ­701110020A09Rik, 2210416J16Rik, Q921N7, gene:7039722literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Alkbh7alkB ­homolog ­72310045B01Rik, 2510008E23Rik, Abh, Abh7, Spa, Spata11, Q9D6Z0, gene:6640022APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MSMatrixnonecerebellum, brainstem, largeintestine, testis
Mrps22mitochondrial ­ribosomal ­protein ­S223100002P07Rik, Rpm, Rpms22, Q9CXW2, gene:6465522literature, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Uqcrbubiquinol-cytochrome ­c ­reductase ­binding ­protein2210415M14Rik, QP-, QP-C, QPC, UQBC, UQBP, UQPC, Q9CQB4, gene:6753022literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits
all 14
Cox7ccytochrome ­c ­oxidase ­subunit ­7CCOX, COXVIIc, Cox7c1, P17665, gene:1286722literature, APEX_IMS, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Ndufaf1NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­12410001M24Rik, CGI-6, CGI-65, CIA, CIA30, Q9CWX2, gene:6970222literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
cerebellum, brainstem, spinalcord, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Acad8acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­82310016C19Rik, AI786953, Q9D7B6, gene:6694822literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Wars2tryptophanyl ­tRNA ­synthetase ­2 ­(mitochondrial)5730427B17Rik, 9430020O07Rik, AI413375, T, TrpRS, Q9CYK1, gene:7056022literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, kidney, skeletalmuscle, adipose, largeintestine, placenta, testis
Mrps34mitochondrial ­ribosomal ­protein ­S340610007F04Rik, 5330430D13Rik, AV001970, Tce2, Q9JIK9, gene:7904422literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Ndufv3NADH:ubiquinone ­oxidoreductase ­core ­subunit ­V31500032D16Rik, Q8BK30, gene:7833022literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Ndufb2NADH:ubiquinone ­oxidoreductase ­subunit ­B21810011O01Rik, 8kD, 8kDa, AGGG, AI325567, CI-AGGG, Q9CPU2, gene:6819822literature, targetP signal, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Slc25a12solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­Aralar), ­member ­122610002D09Rik, AI839531, B230107K20Rik, BB129864, Q8BH59, gene:7883022literature, yeast mito homolog+, mito protein domain+, induction, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Amino acid metabolism > Glutamate metabolism;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family
all 14
Slc25a5solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­adenine ­nucleotide ­translocator), ­member ­5An, Ant2, P51881, gene:1174022literature, yeast mito homolog+, mito protein domain+, induction, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Small molecule transport > SLC25A family
all 14
Mrps21mitochondrial ­ribosomal ­protein ­S211810031B19Rik, S21mt, P58059, gene:6629222literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Msrb2methionine ­sulfoxide ­reductase ­B22310050L06Rik, Mrsb, Ms, Msrb, Pilb, Q78J03, gene:7646722APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Sulfur metabolism
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Glrx5glutaredoxin ­5Q80Y14, gene:7304622literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
Chchd10coiled-coil-helix-coiled-coil-helix ­domain ­containing ­101620401E04Rik, AI267078, Ndg, Ndg2, Q7TNL9, gene:10317222literature, targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression++IMSnonenone
Coq10bcoenzyme ­Q10B1500041J02Rik, 1700030I21Rik, 9530077A17Rik, AV002237, AW742641, Q3THF9, gene:6787622GFP, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
Slc25a30solute ­carrier ­family ­25, ­member ­304933433D23Rik, AV025504, AV221431, AW319655, KMCP, KMCP1, Q9CR58, gene:6755421literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Sulfur metabolism;
Small molecule transport > SLC25A family
cerebrum, cerebellum, liver, placenta, testis
Slc25a13solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­adenine ­nucleotide ­translocator), ­member ­13AI785475, Ct, Ctrn, ci, Q9QXX4, gene:5079921literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Amino acid metabolism > Urea cycle;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family
all 14
Slc25a10solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­dicarboxylate ­transporter), ­member ­10Di, Dic, Q9QZD8, gene:2737621literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Small molecule transport > SLC25A family
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox7a1cytochrome ­c ­oxidase ­subunit ­7A1COX, COX7, COX7A, COX7AH, COX7AM, P56392, gene:1286521literature, targetP signal, mito protein domain+, induction, coexpression, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
cerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a19solute ­carrier ­family ­25 ­(mitochondrial ­thiamine ­pyrophosphate ­carrier), ­member ­192900089E13Rik, DN, DNC, MUP, MUP1, TP, TPC, Q9DAM5, gene:6728321literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin B1 metabolism;
Small molecule transport > SLC25A family
cerebellum, spinalcord, adipose, testis
Smdt1single-pass ­membrane ­protein ­with ­aspartate ­rich ­tail ­11500032L24Rik, Emr, Emre, Q9DB10, gene:6902921literature, targetP signal, mito protein domain+, induction, coexpression+, MS/MSMIMSignaling > Calcium homeostasis > Calcium cycle;
Small molecule transport > Calcium uniporter
cerebrum, cerebellum, brainstem, spinalcord, kidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl22mitochondrial ­ribosomal ­protein ­L22E030011D16Rik, HSPC1, HSPC158, L22mt, MRP-, MRP-L22, MRP-L25, Rpm, Rpml25, Q8BU88, gene:21676721literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mrps10mitochondrial ­ribosomal ­protein ­S101110038B19Rik, AW743084, Rpm, Rpms10, G5E8U5, gene:6465721literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Afg3l1AFG3-like ­AAA ­ATPase ­11700047G05Rik, 3110061K15Rik, Q920A7, gene:11489621literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Fdxrferredoxin ­reductaseAR, Q61578, gene:1414921literature, APEX_matrix, targetP signal, yeast mito homolog++, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Vitamin metabolism > Vitamin D metabolism
spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
SlirpSRA ­stem-loop ­interacting ­RNA ­binding ­protein1810035L17Rik, Q9D8T7, gene:38077321literature, APEX_matrix, GFP, targetP signal+, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial central dogma > Translation
all 14
Poldip2polymerase ­(DNA-directed), ­delta ­interacting ­protein ­21300003F06Rik, Pdip38, Q91VA6, gene:6781121literature, APEX_matrix, targetP signal+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoidall 14
Acsf3acyl-CoA ­synthetase ­family ­member ­3BB101783, Q3URE1, gene:25763321APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisall 14
Oxa1loxidase ­assembly ­1-like1810020M02Rik, AI894287, Q8BGA9, gene:6908921literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMIMProtein import, sorting and homeostasis > Protein import and sorting > OXA;
Mitochondrial central dogma > Translation
cerebrum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, placenta, testis
Idh2isocitrate ­dehydrogenase ­2 ­(NADP+), ­mitochondrialE430004F23, ID, IDPm, Idh-, Idh-2, P54071, gene:26995121literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycleall 14
Atp5lATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­G4933437C06Rik, Atp5mg, Q9CPQ8, gene:2742521literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits;
Mitochondrial dynamics and surveillance > Cristae formation
all 14
Bola1bolA-like ­1 ­(E. ­coli)1810037G04Rik, Q9D8S9, gene:6916821GFP, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
cerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Fahd2afumarylacetoacetate ­hydrolase ­domain ­containing ­2A1500003K14Rik, B430104H02Rik, Cgi-105, Fahd2, Q3TC72, gene:6812621APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS++Matrixnoneall 14
Etfrf1electron ­transfer ­flavoprotein ­regulatory ­factor ­14930469P12Rik, AL022899, Gh, Ghiso, Lyr, Lyrm5, Q91V16, gene:6763621mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Electron carriers > Q-linked reactions, othercerebrum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
Ndufc2NADH:ubiquinone ­oxidoreductase ­subunit ­C21810004I06Rik, 2010300P09Rik, G1, R75094, Q9CQ54, gene:6819721literature, APEX_IMS, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Ndufa8NADH:ubiquinone ­oxidoreductase ­subunit ­A80610033L03Rik, AW261656, CI-19kD, CI-PGIV, Q9DCJ5, gene:6837521literature, APEX_IMS, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Mthfd1lmethylenetetrahydrofolate ­dehydrogenase ­(NADP+ ­dependent) ­1-like2410004L15Rik, AI647056, Fthfsdc, Fthfsdc1, Q3V3R1, gene:27068521literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pdk3pyruvate ­dehydrogenase ­kinase, ­isoenzyme ­32610001M10Rik, AI035637, Q922H2, gene:23690021literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox14cytochrome ­c ­oxidase ­assembly ­protein ­142310016M24Rik, AA959804, Q8BH51, gene:6637921literature, GFP, mito protein domain+, induction, coexpression++, MS/MS+MIMMitochondrial central dogma > Translation > Translation factors;
OXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, smallintestine, testis
Gcdhglutaryl-Coenzyme ­A ­dehydrogenase9030411L18, AI266902, D17825, GCD, Q60759, gene:27007621literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolismall 14
Mrpl51mitochondrial ­ribosomal ­protein ­L512610511M02Rik, CDA0, CDA09, HSPC2, HSPC241, Mrp, Mrp64, Q9CPY1, gene:6649321literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Haghhydroxyacyl ­glutathione ­hydrolaseBC019817, Gl, Glo, Glo-2, Glo2, Rs, Rsp29, Q99KB8, gene:1465121literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mtx1metaxin ­1Gca, Gcap6, Mtx, F7C846, gene:1782721literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
all 14
Fars2phenylalanine-tRNA ­synthetase ­2 ­(mitochondrial)Fa, Fars1, pheRS, Q99M01, gene:6995521literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesadipose, largeintestine, stomach, placenta, testis
Cbr4carbonyl ­reductase ­4A730083J17Rik, BC009118, Q91VT4, gene:23430921literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisall 14
Mrpl32mitochondrial ­ribosomal ­protein ­L320610033O15Rik, Q9DCI9, gene:7539821literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
2310061I04RikRIKEN ­cDNA ­2310061I04 ­geneB8JJ69, gene:6966221targetP signal, induction, coexpression++, MS/MS+Matrixnoneall 14
Fdx2ferredoxin ­2B230118G17Rik, Fdx1, Fdx1l, Q9CPW2, gene:6816521APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
mt-Co2cytochrome ­c ­oxidase ­subunit ­IIP00405, gene:1770921literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
mt-Atp6ATP ­synthase ­F0 ­subunit ­6P00848, gene:1770521literature, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Trap1TNF ­receptor-associated ­protein ­12410002K23Rik, HSP, HSP75, Q9CQN1, gene:6801521APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression++, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Gpd2glycerol ­phosphate ­dehydrogenase ­2, ­mitochondrialAA408484, AI448216, AU021455, AW494132, GPDH, Gdm1, Gpd-m, Gpdh-m, TISP38, Q64521, gene:1457121literature, APEX_IMS, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Glycerol phosphate shuttle;
Metabolism > Electron carriers > Q-linked reactions, other
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Abcb7ATP-binding ­cassette, ­sub-family ­B ­(MDR/TAP), ­member ­7AA517758, AU019072, Abc, Abc7, Q61102, gene:1130621literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins;
Small molecule transport > ABC transporters
all 14
Hsd17b10hydroxysteroid ­(17-beta) ­dehydrogenase ­1017bHSD10, Ad, Ads9, ER, ERAB, Hadh, Hadh2, Q99N15, gene:1510821literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Amino acid metabolism > BCAA metabolism
all 14
Glud1glutamate ­dehydrogenase ­1AI118167, Gdh-X, Glu, Glud, Gludl, P26443, gene:1466121literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolism;
Metabolism > Amino acid metabolism > GABA metabolism
all 14
Aldh2aldehyde ­dehydrogenase ­2, ­mitochondrialAHD-M1, ALDH-E2, ALDHI, Ahd, Ahd-, Ahd-5, Ahd5, P47738, gene:1166921literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
TufmTu ­translation ­elongation ­factor, ­mitochondrial2300002G02Rik, C76308, C76389, EF-TuMT, EFTU, Q8BFR5, gene:23387020literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factorsall 14
Stoml2stomatin ­(Epb7.2)-like ­20610038F01Rik, MSLP2, SL, SLP-2, Q99JB2, gene:6659220literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasisall 14
Dhrs4dehydrogenase/reductase ­(SDR ­family) ­member ­4AI043103, AI790593, CR, D14Ucl, D14Ucla2, NDRD, PHCR, PSCD, R, RRD, mouNRDR, Q99LB2, gene:2820020targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin A metabolismall 14
Aldh9a1aldehyde ­dehydrogenase ­9, ­subfamily ­A1AA139417, Abaldh, ESTM4, ESTM40, TMABA-, TMABA-DH, Tmabadh, Q9JLJ2, gene:5675220APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism
brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Nars2asparaginyl-tRNA ­synthetase ­2 ­(mitochondrial)(putative)AI875199, Q8BGV0, gene:24414120GFP, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesspinalcord, adipose, largeintestine, stomach, placenta
Vwa8von ­Willebrand ­factor ­A ­domain ­containing ­81300010F03Rik, 4932416F07Rik, AI957255, Kiaa0564, mKIAA0564, Q8CC88, gene:21918920APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression+, MS/MS++Matrixnoneall 14
Mrps26mitochondrial ­ribosomal ­protein ­S26AI648866, GI00, GI008, MRP-, MRP-S13, MRP-S26, Rpm, Rpms13, Q80ZS3, gene:9904520literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Adck5aarF ­domain ­containing ­kinase ­5A230108P17, Q80V03, gene:26882220targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSunknownnonecerebrum, largeintestine, testis
Cars2cysteinyl-tRNA ­synthetase ­2 ­(mitochondrial)(putative)2310051N18Rik, 2410044A07Rik, D530030H10Rik, cysRS, Q8BYM8, gene:7194120APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox10heme ­A:farnesyltransferase ­cytochrome ­c ­oxidase ­assembly ­factor ­102410004F01Rik, AU042636, Q8CFY5, gene:7038320literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++MIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Heme synthesis and processing;
OXPHOS > OXPHOS assembly factors
none
Ndufb11NADH:ubiquinone ­oxidoreductase ­subunit ­B11CI-ESSS, D5Bwg0566e, D5Bwg0577e, NP15.6, Np, Np15, p15.6, O09111, gene:10413020literature, APEX_IMS, APEX_matrix, targetP signal+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Pdha2pyruvate ­dehydrogenase ­E1 ­alpha ­2Pd, Pdhal, P35487, gene:1859820literature, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ssbp1single-stranded ­DNA ­binding ­protein ­12810480P10Rik, G630031O20Rik, MtSSB, mtDB, mtDBP, Q9CYR0, gene:38176020literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid
all 14
HscbHscB ­iron-sulfur ­cluster ­co-chaperoneAI325508, AW049829, Hsc20, Q8K3A0, gene:10090020APEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesiscerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrpl27mitochondrial ­ribosomal ­protein ­L27A630055F16Rik, D11Moh4, D11Moh47, D18Ertd643, D18Ertd643e, Q99N92, gene:9406420literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Hint2histidine ­triad ­nucleotide ­binding ­protein ­21190005L05Rik, Q9D0S9, gene:6891720APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesisall 14
Etfbelectron ­transferring ­flavoprotein, ­beta ­polypeptide0610009I16Rik, 2810441H06Rik, Q9DCW4, gene:11082620literature, APEX_matrix, yeast mito homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Electron carriers > Q-linked reactions, other
all 14
Slc25a15solute ­carrier ­family ­25 ­(mitochondrial ­carrier ­ornithine ­transporter), ­member ­15D630044L02Rik, Or, Ornt1, Q9WVD5, gene:1840820literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Urea cycle;
Small molecule transport > SLC25A family
spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta
Oxnad1oxidoreductase ­NAD-binding ­domain ­containing ­12410002F01Rik, AW492292, BC019806, Q8VE38, gene:21888520APEX_matrix, GFP, targetP signal, yeast mito homolog, mito protein domain, coexpression++, MS/MS++Matrixnonecerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cyctcytochrome ­c, ­testisT-Cc, P00015, gene:1306720literature, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++IMSMetabolism > Electron carriers > Cytochromes;
OXPHOS > OXPHOS subunits;
OXPHOS > Cytochrome C
all 14
Cycscytochrome ­c, ­somaticP62897, gene:1306320literature, APEX_IMS, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++IMSMetabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Electron carriers > Cytochromes;
OXPHOS > OXPHOS subunits;
OXPHOS > Cytochrome C;
Mitochondrial dynamics and surveillance > Apoptosis
all 14
Mrpl23mitochondrial ­ribosomal ­protein ­L23L23, L23mrp, Rp, Rpl23, Rpl23l, O35972, gene:1993520literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mrpl9mitochondrial ­ribosomal ­protein ­L98030480E20Rik, AA409733, C330013D18Rik, L9mt, Q99N94, gene:7852320literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Chchd1coiled-coil-helix-coiled-coil-helix ­domain ­containing ­11110001O19Rik, 2400010G13Rik, MRP-S37, Q9CQA6, gene:6612120GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpression+, MS/MSMIMMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Atad3aATPase ­family, ­AAA ­domain ­containing ­3A2400004H09Rik, Atad3, Tob, Tob3, mKIAA1273, Q925I1, gene:10888820APEX_IMS, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression, MS/MS++MIMMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial dynamics and surveillance > Organelle contact sites;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
all 14
Mmutmethylmalonyl-Coenzyme ­A ­mutaseD230010K02Rik, Mcm, Mut, P16332, gene:1785020literature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Vitamin metabolism > Vitamin B12 metabolism
all 14
Cisd1CDGSH ­iron ­sulfur ­domain ­1AU043990, AW743335, D10Ertd214, D10Ertd214e, Zcd1, mitoN, mitoNEET, Q91WS0, gene:5263720literature, mito protein domain, induction, coexpression++, MS/MS++MOMMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
Dars2aspartyl-tRNA ­synthetase ­2 ­(mitochondrial)5830468K18Rik, aspRS, Q8BIP0, gene:22653920APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Aldh18a1aldehyde ­dehydrogenase ­18 ­family, ­member ­A12810433K04Rik, AI429789, Py, Pycs, Q9Z110, gene:5645420literature, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolismcerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl50mitochondrial ­ribosomal ­protein ­L50AA408971, AI317351, D4Wsu125, D4Wsu125e, Q8VDT9, gene:2802820literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox8acytochrome ­c ­oxidase ­subunit ­8ACOX, COX8L, Q64445, gene:1286820literature, targetP signal+, mito protein domain+, coexpression+, MS/MSMIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
stomach, placenta, testis
Mrps6mitochondrial ­ribosomal ­protein ­S6AW046321, P58064, gene:12102220literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Hspe1heat ­shock ­protein ­1 ­(chaperonin ­10)10kDa, Hsp, Hsp10, mt-cpn10, Q64433, gene:1552820literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Ppa2pyrophosphatase ­(inorganic) ­21110013G13Rik, Sid63, Sid6306, Q91VM9, gene:7477620literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance;
Mitochondrial central dogma > mtRNA metabolism;
Mitochondrial central dogma > Translation;
Metabolism > Nucleotide metabolism
all 14
Pcxpyruvate ­carboxylaseP, Pc, Pcb, E9QPD7, gene:1856320literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > TCA-associated;
Metabolism > Vitamin metabolism > Biotin utilizing proteins
all 14
Gldcglycine ­decarboxylaseD030049L12Rik, D19Wsu57, D19Wsu57e, b2b2679C, b2b2679Clo, Q91W43, gene:10417420literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Amino acid metabolism > Glycine cleavage system
cerebrum, cerebellum, kidney, liver, adipose, placenta
Tamm41TAM41 ­mitochondrial ­translocator ­assembly ­and ­maintenance ­homolog1500001M20Rik, TAM41, G5E881, gene:6897120GFP, yeast mito homolog++, mito protein domain+, MS/MS++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Atp5g3ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­C3 ­(subunit ­9)6030447M23, Atp5mc3, P56384, gene:22803319literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
none
Mrpl38mitochondrial ­ribosomal ­protein ­L381110036N21Rik, 4733401F03Rik, MRP, MRP-L3, R75240, Rp, Rpml3, Q8K2M0, gene:6044119APEX_matrix, targetP signal+, mito protein domain, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, spinalcord, heart, smallintestine, largeintestine, stomach, placenta, testis
Ndufa12NADH:ubiquinone ­oxidoreductase ­subunit ­A122410011G03Rik, AW112974, CI-B17.2, CIB17.2, Q7TMF3, gene:6641419literature, APEX_matrix, Rickettsial homolog, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Pdfpeptide ­deformylase ­(mitochondrial)2610019N19Rik, S4R2K0, gene:6802319APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > fMet processing;
Protein import, sorting and homeostasis > Protein homeostasis
cerebrum, heart, skeletalmuscle, adipose, largeintestine, placenta, testis
Acad10acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­102410021P16Rik, Q8K370, gene:7198519APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ptges2prostaglandin ­E ­synthase ­20610038H10Rik, C79137, Gbf1, Mpges2, Pges2, Q8BWM0, gene:9697919literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Eicosanoid metabolismall 14
Ccdc58coiled-coil ­domain ­containing ­58A930007B11Rik, AI413631, Q8R3Q6, gene:38104519APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++IMSnoneall 14
Slc25a31solute ­carrier ­family ­25 ­(mitochondrial ­carrier; ­adenine ­nucleotide ­translocator), ­member ­311700034J06Rik, Ant4, Sfec, Q3V132, gene:7333319literature, yeast mito homolog++, mito protein domain+, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Small molecule transport > SLC25A family
all 14
Atp5hATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­D0610009D10Rik, Atp5pd, Q9DCX2, gene:7167919literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Atp5pbATP ­synthase ­peripheral ­stalk-membrane ­subunit ­bAtp5, Atp5f1, C76477, Q9CQQ7, gene:1195019literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Mrpl41mitochondrial ­ribosomal ­protein ­L41MRP-, MRP-L27, Rpm, Rpml27, Q9CQN7, gene:10773319literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Txnrd2thioredoxin ­reductase ­2AA118373, ESTM57301, ESTM573010, TG, TGR, TR, Tr3, Trxr2, Trxrd2, Q9JLT4, gene:2646219literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Detoxification > Selenoproteins
cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mceemethylmalonyl ­CoA ­epimerase1110007A04Rik, Q9D1I5, gene:7372419targetP signal, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation
all 14
Mccc2methylcrotonoyl-Coenzyme ­A ­carboxylase ­2 ­(beta)4930552N12Rik, MCCB, Q3ULD5, gene:7803819literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismall 14
Ptcd2pentatricopeptide ­repeat ­domain ­21190005P08Rik, Q8R3K3, gene:6892719literature, targetP signal, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing
smallintestine, largeintestine, placenta
Ak4adenylate ­kinase ­4AK 4, Ak-, Ak-3, Ak-4, Ak3, Ak3l1, D4Ertd274, D4Ertd274e, Q9WUR9, gene:1163919APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingall 14
Slc25a25solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­phosphate ­carrier), ­member ­251110030N17Rik, MCSC, mKIAA1896, A2ASZ8, gene:22773119literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family
cerebrum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, placenta
Tomm40translocase ­of ­outer ­mitochondrial ­membrane ­40AW539759, Mom35, Tom4, Tom40, Q9QYA2, gene:5333319literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Clyblcitrate ­lyase ­beta ­like0610033J05Rik, 2310014M14Rik, AI256068, Cl, Clb, Q8R4N0, gene:6963419APEX_matrix, targetP signal+, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolismall 14
Mterf2mitochondrial ­transcription ­termination ­factor ­21700007D05Rik, Mterfd, Mterfd3, Q8BKY8, gene:7423819literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoidcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, testis
Dnajc11DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C11E030019A03Rik, Q5U458, gene:23093519GFP, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
all 14
Decr12,4-dienoyl ­CoA ­reductase ­1, ­mitochondrial1200012F07Rik, Dec, Decr, Na, Nadph, Q9CQ62, gene:6746019literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Ndufaf6NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­62310030N02Rik, A2AIL4, gene:7694719literature, targetP signal, mito protein domain, induction, coexpression++, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
adipose, smallintestine, largeintestine, placenta, testis
Ptrh1peptidyl-tRNA ­hydrolase ­1 ­homolog2210013M04Rik, AW046744, Q8BW00, gene:32938419APEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixnonecerebrum, cerebellum, brainstem, largeintestine, placenta
Rmnd1required ­for ­meiotic ­nuclear ­division ­1 ­homolog0610042C05Rik, AA408137, AI462664, AW536662, Q8CI78, gene:6608419literature, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation
cerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
Gcatglycine ­C-acetyltransferase ­(2-amino-3-ketobutyrate-coenzyme ­A ­ligase)AI526977, Kb, Kbl, O88986, gene:2691219literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++unknownMetabolism > Amino acid metabolism > Glycine metabolismbrainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
PyurfPigy ­upstream ­reading ­frame2610022G08Rik, AI847956, Pi, Prey, Q9D1C3, gene:6645919targetP signal+, induction, coexpression++, MS/MSunknownnonecerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
Acsm1acyl-CoA ­synthetase ­medium-chain ­family ­member ­1Acas3, Bucs, Bucs1, Ma, Macs, Q91VA0, gene:11714719literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationspinalcord, kidney, liver, smallintestine
Atad1ATPase ­family, ­AAA ­domain ­containing ­14921525H23Rik, AW107648, Tho, Thorase, Q9D5T0, gene:6797919yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Tmem14ctransmembrane ­protein ­14C1110021D01Rik, AU020193, HSPC1, HSPC194, Q9CQN6, gene:6615419literature, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS+MIMnoneall 14
C030006K11RikRIKEN ­cDNA ­C030006K11 ­gene1110033I13Rik, Q8VE95, gene:22366519APEX_matrix, targetP signal+, coexpression+, MS/MS++Matrixnoneall 14
Nit2nitrilase ­family, ­member ­21190017B19Rik, D16Ertd502, D16Ertd502e, Q9JHW2, gene:5263319yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++unknownMetabolism > Detoxificationcerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a26solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­phosphate ­carrier), ­member ­264930433D19Rik, 4933433F13Rik, AW557176, D6Bwg0781e, Slc25a6, Q5U680, gene:6758219literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A familycerebrum, cerebellum, adipose, largeintestine, placenta, testis
Timm21translocase ­of ­inner ­mitochondrial ­membrane ­211700034H14Rik, 2700002I20Rik, Q8CCM6, gene:6710519APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMMitochondrial central dogma > Translation > Translation factors;
Protein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway;
OXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Ndufa4Ndufa4, ­mitochondrial ­complex ­associatedML, MLRQ, Q62425, gene:1799219literature, targetP signal, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Rexo2RNA ­exonuclease ­21810038D15Rik, AW107347, Rex, Rex2, S, Sfn, Sm, Smfn, Q9D8S4, gene:10444419APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decayall 14
Me2malic ­enzyme ­2, ­NAD(+)-dependent, ­mitochondrialAW120568, D030040L20Rik, NAD-ME, Q99KE1, gene:10702919literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sars2seryl-aminoacyl-tRNA ­synthetase ­22410015F05Rik, D7Ertd353, D7Ertd353e, SerRS, SerRSmt, Q9JJL8, gene:7198419literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesskeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
DnlzDNL-type ­zinc ­finger1110034G11Rik, D2Bwg1335e, HEP1, Q9D113, gene:5283819APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MSMatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonescerebrum, cerebellum, brainstem, heart, adipose, smallintestine, largeintestine, stomach, placenta
Ckmt2creatine ­kinase, ­mitochondrial ­22300008A19Rik, ScCKm, ScCKmit, Q6P8J7, gene:7672219literature, targetP signal, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Creatine metabolismcerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Spryd4SPRY ­domain ­containing ­44633402N23Rik, AA114801, Q91WK1, gene:6670118APEX_matrix, GFP, targetP signal, mito protein domain, coexpression+, MS/MS++Matrixnoneall 14
Bphlbiphenyl ­hydrolase-like ­(serine ­hydrolase, ­breast ­epithelial ­mucin-associated ­antigen)2010012D11Rik, 5730533B08Rik, AI115341, Q8R164, gene:6802118targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
Chchd4coiled-coil-helix-coiled-coil-helix ­domain ­containing ­42410012P20Rik, 2810014D17Rik, AI838740, Q8VEA4, gene:7217018literature, APEX_IMS, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS+IMSProtein import, sorting and homeostasis > Protein import and sorting > MIA40cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl37mitochondrial ­ribosomal ­protein ­L372300004O14Rik, AI132596, MRP, MRP-L2, Rp, Rpml2, Q921S7, gene:5628018literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomekidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a51solute ­carrier ­family ­25, ­member ­519130208E07Rik, D130005A03Rik, Gm138, Mcar, Mcart1, Q5HZI9, gene:23012518GFP, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolism;
Small molecule transport > SLC25A family
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mtarc2mitochondrial ­amidoxime ­reducing ­component ­22810484M10Rik, Mar, Marc2, Mos, Mosc2, mARC1, Q922Q1, gene:6724718literature, targetP signal, mito protein domain+, induction, coexpression, MS/MS++MOMMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins;
Metabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > Amidoxime reducing complex
all 14
Immp1lIMP1 ­inner ­mitochondrial ­membrane ­peptidase-like ­(S. ­cerevisiae)1500034J20Rik, 2610528O17Rik, AU042386, Q9CQU8, gene:6654118literature, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases
testis
Fam210afamily ­with ­sequence ­similarity ­210, ­member ­A4933403F05Rik, AA987140, AV134576, AW491926, Q8BGY7, gene:10865418GFP, targetP signal, induction, coexpression++, MS/MSMIMnoneall 14
Mrps24mitochondrial ­ribosomal ­protein ­S243110030K20Rik, AI414579, MRP-S24, Rpm, Rpms24, S24mt, Q9CQV5, gene:6466018literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Timm17btranslocase ­of ­inner ­mitochondrial ­membrane ­17b17kD, 17kDa, Sfc, Sfc3, mTim17, mTim17b, Q9Z0V7, gene:2185518literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathwayall 14
Hars2histidyl-tRNA ­synthetase ­24631412B19Rik, H, HARSR, HO, HO3, Harsl, Q99KK9, gene:7079118literature, APEX_matrix, GFP, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebellum, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox16cytochrome ­c ­oxidase ­assembly ­protein ­161810020G14Rik, 1810055I05Rik, BB388670, Q9CR63, gene:6627218APEX_IMS, GFP, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
kidney, liver, adipose, largeintestine, placenta, testis
Pdss2prenyl ­(solanesyl) ­diphosphate ­synthase, ­subunit ­25430420P03Rik, Gm60, P, Plmp, kd, mDL, mDLP1, Q33DR3, gene:7136518literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolismsmallintestine, largeintestine
Eci1enoyl-Coenzyme ­A ­delta ­isomerase ­1Dc, Dci, ec, eci, P42125, gene:1317718literature, APEX_matrix, targetP signal+, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Ndufs3NADH:ubiquinone ­oxidoreductase ­core ­subunit ­S30610010M09Rik, CI-30kD, Q9DCT2, gene:6834918literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Hmgcs23-hydroxy-3-methylglutaryl-Coenzyme ­A ­synthase ­21300002P16, mH, mHS, P54869, gene:1536018literature, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolismcerebellum, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
L2hgdhL-2-hydroxyglutarate ­dehydrogenaseBC016226, Q91YP0, gene:21766618literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, testis
Zadh2zinc ­binding ­alcohol ­dehydrogenase, ­domain ­containing ­2C530046K17Rik, PTGR-3, Pth, Pthr3, Q8BGC4, gene:22579118targetP signal, mito protein domain, induction, coexpression+, MS/MS++unknownMetabolism > Lipid metabolism > Eicosanoid metabolismall 14
Aurkaip1aurora ­kinase ­A ­interacting ­protein ­10610033H09Rik, Aip, Akip, MRP-S38, Q9DCJ7, gene:6607718GFP, targetP signal+, yeast mito homolog++, mito protein domain, coexpression+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomenone
Coa5cytochrome ­C ­oxidase ­assembly ­factor ­51700001A24Rik, 6330578E17Rik, Pet19, Pet191, Q99M07, gene:7617818literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
adipose, placenta, testis
H2-Ke6H2-K ­region ­expressed ­gene ­6D17H6S112E, H-2Ke6, Hsd17b8, Ke-6, Ke6, Ri, Ring2, P50171, gene:1497918APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis;
Metabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis
all 14
Micos13mitochondrial ­contact ­site ­and ­cristae ­organizing ­system ­subunit ­132410015M20Rik, Mic13, QI, QIL1, sr104, Q8R404, gene:22490418induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Ndufb7NADH:ubiquinone ­oxidoreductase ­subunit ­B71110002H15Rik, Q9CR61, gene:6691618literature, APEX_IMS, APEX_matrix, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Nipsnap2nipsnap ­homolog ­2AV006093, Gb, Gbas, N, Q7TMG8, gene:1446718literature, APEX_matrix, targetP signal+, induction, coexpression, MS/MS++MatrixMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
all 14
Mrpl47mitochondrial ­ribosomal ­protein ­L474833424P18Rik, CGI-20, CGI-204, Gm9859, L47mt, MRP-L47, MTF/L47, NCM, NCM1, Q8K2Y7, gene:7460018literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome
all 14
Mtres1mitochondrial ­transcription ­rescue ­factor ­11700021F05Rik, Q9CQF4, gene:6785118GFP, targetP signal, induction, coexpression++, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > Transcription;
Mitochondrial central dogma > Translation
all 14
Ndufaf7NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­72410091C18Rik, AL033374, PRO1853, Q9CWG8, gene:7369418APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, brainstem, spinalcord, kidney, adipose, largeintestine, stomach, placenta, testis
Acad9acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­92600017P15Rik, 4732402K02, C630012L17Rik, NPD0, NPD002, Q8JZN5, gene:22921118literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
NagsN-acetylglutamate ­synthase1700120E20Rik, argA, Q8R4H7, gene:21721418literature, targetP signal, yeast mito homolog++, mito protein domain+, MS/MSMatrixMetabolism > Amino acid metabolism > Urea cycleliver
Ldhdlactate ­dehydrogenase ­D4733401P21Rik, D8Bwg1320e, DLD, Q7TNG8, gene:5281518literature, targetP signal+, yeast mito homolog+, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolismkidney, liver, heart, adipose, stomach, placenta, testis
Sardhsarcosine ­dehydrogenaseQ99LB7, gene:19216618literature, targetP signal+, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sprsepiapterin ­reductaseAA409688, Gm10328, Q91XH5, gene:2075118targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++unknownMetabolism > Metals and cofactors > Tetrahydobiopterin synthesiscerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach
NaxeNAD(P)HX ­epimeraseAA087124, AI, AI-BP, AIBP, AP, Apoa1bp, Apoa1ip, ESTM3, ESTM37, Q8K4Z3, gene:24670318APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismall 14
Timm23translocase ­of ­inner ­mitochondrial ­membrane ­23Tim2, Tim23, Q9CXU4, gene:5360018literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathwayall 14
Mpv17MpV17 ­mitochondrial ­inner ­membrane ­proteinTg.Mpv, Tg.Mpv17, P19258, gene:1752718literature, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MIMSmall molecule transportall 14
Mtg1mitochondrial ­ribosome-associated ­GTPase ­1Gm169, Gtpb, Gtpbp7, Q8R2R6, gene:21250818literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblylargeintestine, testis
Ideinsulin ­degrading ­enzyme1300012G03Rik, 4833415K22Rik, AA675336, AI507533, AI507533, gene:1592518literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Trnt1tRNA ­nucleotidyl ­transferase, ­CCA-adding, ­12410043H24Rik, 2610044E04Rik, 9830143O18Rik, AA408384, C76540, CGI-4, CGI-47, mt-Trat, Q8K1J6, gene:7004718literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsspinalcord, adipose, placenta, testis
Mrps25mitochondrial ­ribosomal ­protein ­S252810429N01Rik, Rpm, Rpms25, Q9D125, gene:6465818literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mrpl14mitochondrial ­ribosomal ­protein ­L141110006I11Rik, AI846816, MRP-, MRP-L32, Rpm, Rpml32, Q9D1I6, gene:6846318literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mrps30mitochondrial ­ribosomal ­protein ­S302610020A16Rik, AA968347, PAP, Pdcd, Pdcd9, Q9D0G0, gene:5905418literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrps16mitochondrial ­ribosomal ­protein ­S161500011E11Rik, Mprs16, S16mt, Q9CPX7, gene:6624217literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Prelid2PRELI ­domain ­containing ­21700003A01Rik, C330008K14Rik, Q0VBB0, gene:7761917yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MSIMSnonelargeintestine, stomach
Shmt2serine ­hydroxymethyltransferase ­2 ­(mitochondrial)2700043D08Rik, AA408223, AA986903, SHMT, Q9CZN7, gene:10803717literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Serine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism
cerebrum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Suoxsulfite ­oxidaseSO, Q8R086, gene:21138917APEX_IMS, targetP signal, mito protein domain+, coexpression, MS/MS++IMSMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins;
Metabolism > Sulfur metabolism
cerebrum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ccdc90bcoiled-coil ­domain ­containing ­90B2310015N07Rik, C86558, Q8C3X2, gene:6636517literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, MS/MSMIMnoneall 14
Rmdn1regulator ­of ­microtubule ­dynamics ­1Fam82, Fam82b, RMD-1, Q9DCV4, gene:6630217APEX_IMS, targetP signal+, mito protein domain, induction, coexpression, MS/MSMOMnoneall 14
Acsm5acyl-CoA ­synthetase ­medium-chain ­family ­member ­5C730019D22, C730027J19Rik, Q8BGA8, gene:27242817literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Detoxification > Xenobiotic metabolism
kidney, liver, adipose, smallintestine, largeintestine
Mrpl36mitochondrial ­ribosomal ­protein ­L36AI646041, Q99N90, gene:9406617literature, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomenone
Gstk1glutathione ­S-transferase ­kappa ­10610025I19Rik, AW260476, Dsb, DsbA-L, Q9DCM2, gene:7626317literature, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
Fmc1formation ­of ­mitochondrial ­complex ­V ­assembly ­factor ­11110001J03Rik, Q9CR13, gene:6611717literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixOXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl58mitochondrial ­ribosomal ­protein ­L581110001A02Rik, 1110002E03Rik, Ict, Ict1, MRP-L58, Q8R035, gene:6857217APEX_matrix, GFP, targetP signal+, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome;
Mitochondrial central dogma > Translation > Translation factors
all 14
Cpt1acarnitine ­palmitoyltransferase ­1a, ­liverC730027G07, CP, CPTI, Cpt, Cpt1, P97742, gene:1289417literature, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle
all 14
Ak2adenylate ­kinase ­2Ak-, Ak-2, D4Ertd220, D4Ertd220e, Q9WTP6, gene:1163717literature, APEX_IMS, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++IMSMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingall 14
2810006K23RikRIKEN ­cDNA ­2810006K23 ­geneQ80VP5, gene:7265017literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Translation factorscerebrum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta
Glsglutaminase6330442B14, AI314027, B230365M23Rik, D3Z7P3, gene:1466017literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Glutamate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Them4thioesterase ­superfamily ­member ­42700077M13Rik, 4921507I02Rik, Q3UUI3, gene:7577817literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, MS/MS++MIMMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Pdss1prenyl ­(solanesyl) ­diphosphate ­synthase, ­subunit ­12610203G20Rik, 2700031G06Rik, TPT, TPT 1, Tp, Tprt, mDLP1, mS, mSPS1, Q33DR2, gene:5607517APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Metals and cofactors > Coenzyme Q metabolismskeletalmuscle, largeintestine, placenta, testis
Mtg2mitochondrial ­ribosome ­associated ­GTPase ­21810011P19Rik, 2900056P18Rik, D2Bwg0647e, Gtpb, Gtpbp5, A2AFK4, gene:5285617literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblylargeintestine, placenta
Mrps11mitochondrial ­ribosomal ­protein ­S110710005I03Rik, C79873, MRP-S11, S11mt, Q3U8Y1, gene:6799417literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Mlycdmalonyl-CoA ­decarboxylaseAI324784, Mcd, Q99J39, gene:5669017literature, APEX_matrix, targetP signal, mito protein domain, coexpression++, MS/MSMatrixMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
TcaimT ­cell ­activation ­inhibitor, ­mitochondrialD9Ertd402, D9Ertd402e, Gm1129, TOAG-1, Q66JZ4, gene:38211717literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++Matrixnonenone
Ndufc1NADH:ubiquinone ­oxidoreductase ­subunit ­C12310016K22Rik, KFYI, Q9CQY9, gene:6637717literature, targetP signal+, mito protein domain+, coexpression++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
none
Gsrglutathione ­reductaseAI325518, D8Ertd238, D8Ertd238e, Gr-, Gr-1, Gr1, P47791, gene:1478217literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismspinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Rars2arginyl-tRNA ­synthetase ­2, ­mitochondrial1500002I10Rik, PRO1, PRO1992, Rarsl, Q3U186, gene:10909317literature, APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesall 14
Slc25a24solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­phosphate ­carrier), ­member ­242610016M12Rik, Q8BMD8, gene:22973117literature, APEX_IMS, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family
adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a18solute ­carrier ­family ­25 ­(mitochondrial ­carrier), ­member ­181500015I14Rik, AW125787, Q9DB41, gene:7180317literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a22solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­glutamate), ­member ­221300006L01Rik, AI060884, Gc1, Q9D6M3, gene:6826717literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mpc1mitochondrial ­pyruvate ­carrier ­10610006G08Rik, 3830411I18Rik, Brp, Brp44l, P63030, gene:5595117GFP, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Pyruvate metabolism;
Metabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport
all 14
Timm8a1translocase ­of ­inner ­mitochondrial ­membrane ­8A1DXHXS1274, DXHXS1274E, Ddp, Ddp1, Fci-1, Fci-12, Tim, Tim8a, Timm8a, Q9WVA2, gene:3005817literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting
all 14
Vdac3voltage-dependent ­anion ­channel ­3Q60931, gene:2233517literature, yeast mito homolog+, mito protein domain+, MS/MS++MOMSignaling > Calcium homeostasis > Mitochondrial permeability transition pore;
Small molecule transport
all 14
Akap1A ­kinase ­(PRKA) ­anchor ­protein ­1AKA, AKAP121, AKAP84, Akap, C76494, C81186, DAK, DAKAP1, S-AK, S-AKAP84, O08715, gene:1164017literature, mito protein domain, induction, coexpression++, MS/MS+MOMSignaling > cAMP-PKA signalingcerebellum, skeletalmuscle, testis
Eci2enoyl-Coenzyme ­A ­delta ­isomerase ­2ACBD, Acbd2, DR, Drs1, HCA8, Hca88, Pe, Peci, Q9WUR2, gene:2398617literature, APEX_matrix, targetP signal, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Mrm2mitochondrial ­rRNA ­methyltransferase ­22310037B18Rik, Ftsj, Ftsj2, Q9CPY0, gene:6801717literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
cerebrum
Lipt2lipoyl(octanoyl) ­transferase ­2 ­(putative)2610209A20Rik, Q9D009, gene:6716417yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertioncerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
Nubplnucleotide ­binding ­protein-like2410170E07Rik, Q9CWD8, gene:7682617literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MatrixOXPHOS > Complex I > CI assembly factors;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins;
OXPHOS > OXPHOS assembly factors
spinalcord, adipose, largeintestine, stomach, placenta, testis
Sfxn1sideroflexin ­12810002O05Rik, A930015P12Rik, f, Q99JR1, gene:1405717literature, yeast mito homolog, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Serine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Small molecule transport > Sideroflexins
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc30a9solute ­carrier ­family ­30 ­(zinc ­transporter), ­member ­92310024J23Rik, AL024256, GAC6, GAC63, HUEL, znT-9, Q5IRJ6, gene:10910817APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MSMIMSmall molecule transportcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Gatmglycine ­amidinotransferase ­(L-arginine:glycine ­amidinotransferase)1810003P21Rik, AI314789, AT, Q9D964, gene:6709217literature, targetP signal, mito protein domain+, MS/MS++MatrixMetabolism > Nucleotide metabolism > Creatine metabolismspinalcord, kidney, liver, stomach, placenta, testis
Triap1TP53 ­regulated ­inhibitor ­of ­apoptosis ­11810015M01Rik, AU020874, AU043831, P53csv, Wf-1, Q9D8Z2, gene:6907616literature, yeast mito homolog++, mito protein domain, induction, MS/MS++IMSMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
adipose, stomach, placenta
Cpoxcoproporphyrinogen ­oxidaseC, CPX, Cpo, HCP, ca, cac, nc, nct, P36552, gene:1289216literature, APEX_IMS, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Heme synthesis and processingcerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Xpnpep3X-prolyl ­aminopeptidase ­3, ­mitochondrialAPP3, E430012M05Rik, B7ZMP1, gene:32100316literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases
cerebrum, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pnpla8patatin-like ­phospholipase ­domain ­containing ­81200006O19Rik, AI467579, Ipla2(gamma), Q8K1N1, gene:6745216APEX_matrix, Rickettsial homolog, induction, coexpression++, MS/MS+MIMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, testis
Gadd45gip1growth ­arrest ­and ­DNA-damage-inducible, ­gamma ­interacting ­protein ­12310040G17Rik, AI425883, Cri, Crif1, MRP-L59, Plinp1, Q9CR59, gene:10206016APEX_matrix, GFP, targetP signal+, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Gfergrowth ­factor, ­augmenter ­of ­liver ­regenerationAlr, ER, ERV1, P56213, gene:1169216literature, GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MSIMSProtein import, sorting and homeostasis > Protein import and sorting > MIA40cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ngrnneugrin, ­neurite ­outgrowth ­associatedAW552001, Q99KS2, gene:8348516APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
none
Mrpl57mitochondrial ­ribosomal ­protein ­L572610025P17Rik, AV005697, Mrp, Mrp63, Q9CQF8, gene:6784016literature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Ndufa3NADH:ubiquinone ­oxidoreductase ­subunit ­A31010001M12Rik, 1700022J01Rik, Q9CQ91, gene:6609116literature, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Ptcd3pentatricopeptide ­repeat ­domain ­32610034F17Rik, 2810422B04Rik, AA589622, AU045708, MRP-S39, Q14C51, gene:6995616literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
all 14
Mrpl45mitochondrial ­ribosomal ­protein ­L452600005P05Rik, AU043542, R75241, Q9D0Q7, gene:6703616literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a16solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­Graves ­disease ­autoantigen), ­member ­163110021G18Rik, GDA, GDC, HGT.1, ML, ML7, Q8C0K5, gene:7313216literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A familycerebrum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
Ucp1uncoupling ­protein ­1 ­(mitochondrial, ­proton ­carrier)AI385626, Slc2, Slc25a7, Ucp, P12242, gene:2222716literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A familyadipose
Tars2threonyl-tRNA ­synthetase ­2, ­mitochondrial ­(putative)2610024N01Rik, AI429208, Ta, Tarsl1, thrRS, Q3UQ84, gene:7180716APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Trit1tRNA ­isopentenyltransferase ­12310075G14Rik, AI314189, AI314635, AV099619, IPPT, IPT, MOD, MOD5, Q80UN9, gene:6696616literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
cerebellum
Ndufab1NADH:ubiquinone ­oxidoreductase ­subunit ­AB12210401F17Rik, 2310039H15Rik, 2610003B19Rik, 8kD, 8kDa, 9130423F15Rik, ACP, CI-SDAP, SDAP, Q9CR21, gene:7031616literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS+MIMOXPHOS > Complex I > CI subunits;
Metabolism > Lipid metabolism > Type II fatty acid synthesis;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis;
OXPHOS > OXPHOS subunits
all 14
Cslcitrate ­synthase ­like1700007H16Rik, Q80X68, gene:7183216targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++Matrixnoneall 14
Slc25a39solute ­carrier ­family ­25, ­member ­393010027G13Rik, D11Ertd333, D11Ertd333e, Q9D8K8, gene:6806616literature, yeast mito homolog+, mito protein domain+, induction, coexpressionMIMSmall molecule transport > SLC25A familynone
Prelid3bPRELI ­domain ­containing ­3B2310042G06Rik, AA407013, Sl, Slmo2, Q9CYY7, gene:6639016GFP, yeast mito homolog+, mito protein domain+, induction, coexpressionIMSMetabolism > Lipid metabolism > Phospholipid metabolismnone
Mtch1mitochondrial ­carrier ­12310034O17Rik, AI255158, AU018396, C77849, PSAP, Q791T5, gene:5646216literature, yeast mito homolog+, mito protein domain+, MS/MS++MOMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dele1DAP3 ­binding ­cell ­death ­enhancer ­10610009O20Rik, 2700004E22Rik, DELE1(L), Dele, Kiaa0141, Q9DCV6, gene:6683916targetP signal+, yeast mito homolog, mito protein domain, induction, coexpressionMIMSignalingnone
Acaa1aacetyl-Coenzyme ­A ­acyltransferase ­1AAc, Acaa, Acaa1, D9Ertd25, D9Ertd25e, P, PTL, Q921H8, gene:11386816targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Fatty acid oxidationspinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Acot13acyl-CoA ­thioesterase ­130610006O17Rik, Them2, Q9CQR4, gene:6683416mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolismall 14
Ndufa13NADH:ubiquinone ­oxidoreductase ­subunit ­A132700054G14Rik, AU022060, CDA01, CDA016, CGI-3, CGI-39, CI-B16.6, GRIM-, GRIM-19, Grim, Grim19, F6W8I0, gene:6718416literature, APEX_IMS, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Agxt2alanine-glyoxylate ­aminotransferase ­2AI303810, AI663818, Q3UEG6, gene:26878216literature, targetP signal, yeast mito homolog++, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolism > Glyoxylate metabolismkidney, liver
Selenooselenoprotein ­O1300018J18Rik, S, Selo, Q9DBC0, gene:22377616targetP signal+, yeast mito homolog, mito protein domain+, coexpressionMatrixMetabolism > Detoxification > Selenoproteinsspinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Oxld1oxidoreductase ­like ­domain ­containing ­11810049H13Rik, Q9CR10, gene:6643116targetP signal, yeast mito homolog, mito protein domain+, coexpression+unknownnoneadipose, largeintestine, stomach
Mfn2mitofusin ­2D630023P19Rik, Fz, Fzo, Q80U63, gene:17073116literature, mito protein domain+, induction, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Organelle contact sites
cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
Chdhcholine ­dehydrogenaseAU041472, D630034H06Rik, Q8BJ64, gene:21886516APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Metabolism > Electron carriers > Q-linked reactions, other
spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Msramethionine ­sulfoxide ­reductase ­A2310045J23Rik, 6530413P12Rik, MS, MSR-A, Q9D6Y7, gene:11026516targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Sulfur metabolism
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Nit1nitrilase ­1AI255805, ESTM3, ESTM30, W57327, Q8VDK1, gene:2704516APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox4i2cytochrome ­c ­oxidase ­subunit ­4I2Cox4, Cox4b, CoxIV-2, Q91W29, gene:8468216literature, targetP signal, yeast mito homolog++, mito protein domain+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
cerebrum, spinalcord, heart, adipose, largeintestine, stomach, placenta
Lactblactamase, ­betaLACT-1, Lact1, Mrp, Mrpl56, Q9EP89, gene:8090716literature, APEX_IMS, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++IMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Metabolism > Lipid metabolism > Phospholipid metabolism
all 14
Tstthiosulfate ­sulfurtransferase, ­mitochondrialRhod, rhodanese, P52196, gene:2211716literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Sulfur metabolism
all 14
Coa8cytochrome ­c ­oxidase ­assembly ­factor ­81700081D05Rik, 2810002N01Rik, Ap, Apop-1, Apop1, Apopt1, Q9CQW7, gene:6802016literature, targetP signal+, mito protein domain+, coexpression+MIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
largeintestine, placenta
Prodh2proline ­dehydrogenase ­(oxidase) ­22510028N04Rik, 2510038B11Rik, HYPDH, MmPO, MmPOX, MmPOX1, POX1, Q8VCZ9, gene:5618916targetP signal, yeast mito homolog+, mito protein domain+, MS/MS+MIMMetabolism > Amino acid metabolism > Glyoxylate metabolism;
Metabolism > Electron carriers > Q-linked reactions, other
kidney, liver
Cox7bcytochrome ­c ­oxidase ­subunit ­7B1110004F07Rik, C80563, P56393, gene:6614216literature, targetP signal, mito protein domain+, induction, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
Glrx2glutaredoxin ­2 ­(thioltransferase)1700010P22Rik, AI645710, Grx, Grx2, Q923X4, gene:6936716literature, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S-containing proteins;
Metabolism > Vitamin metabolism > Vitamin C metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism
cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, largeintestine, placenta, testis
Aldh1b1aldehyde ­dehydrogenase ­1 ­family, ­member ­B12700007F14Rik, Q9CZS1, gene:7253516literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
Ndufb3NADH:ubiquinone ­oxidoreductase ­subunit ­B32700033I16Rik, CI-B12, Q9CQZ6, gene:6649516literature, APEX_IMS, APEX_matrix, mito protein domain+, coexpression+, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Ehhadhenoyl-Coenzyme ­A, ­hydratase/3-hydroxyacyl ­Coenzyme ­A ­dehydrogenase1300002P22Rik, HD, L-P, L-PBE, LBFP, LBP, MF, MFE1, MFP, MFP-1, MFP1, PBFE, Q9DBM2, gene:7414715yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+unknownMetabolism > Lipid metabolismspinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta
Echdc1enoyl ­Coenzyme ­A ­hydratase ­domain ­containing ­11700028A24Rik, AI314462, AI930038, D10Ertd667e, MMCD, Q9D9V3, gene:5266515yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+unknownMetabolism > Lipid metabolismbrainstem, spinalcord, liver, adipose, largeintestine, placenta, testis
TrmutRNA ­5-methylaminomethyl-2-thiouridylate ­methyltransferase1110005N20Rik, 1600025P05Rik, AI314320, Trmt, Trmt1, Q9DAT5, gene:7202615literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsadipose, largeintestine, placenta
Vars2valyl-tRNA ­synthetase ­2, ­mitochondrial1190004I24Rik, V, Vars2l, mKIAA1885, Q3U2A8, gene:6891515APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mettl17methyltransferase ­like ­172310032K15Rik, D14Ertd209, D14Ertd209e, Mett11d1, Q3U2U7, gene:5253515GFP, targetP signal+, yeast mito homolog++, mito protein domain+MatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
none
Aassaminoadipate-semialdehyde ­synthaseLKR, LKR/SDH, LOR, LOR/SDH, Lo, Lorsdh, SDH, Q99K67, gene:3095615APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Aadataminoadipate ­aminotransferaseAI875679, Aadt, KA, KATII, Kat, Kat2, Kyat, Kyat2, mKat-, mKat-2, Q9WVM8, gene:2392315targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolismkidney, liver
Ndufa11NADH:ubiquinone ­oxidoreductase ­subunit ­A112010012C24Rik, AV006275, B14.7, G5E814, gene:6987515literature, APEX_IMS, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Gm4984predicted ­pseudogene ­4984AI428901, EG245347, EG245347, gene:24534715yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > Pyruvate metabolism;
Metabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport
testis
Slc25a21solute ­carrier ­family ­25 ­(mitochondrial ­oxodicarboxylate ­carrier), ­member ­219930033G19Rik, A630030I10, BB158148, Q8BZ09, gene:21759315literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism;
Small molecule transport > SLC25A family
spinalcord, kidney, liver, testis
Slc25a29solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­palmitoylcarnitine ­transporter), ­member ­29C030003J19Rik, CA, CACL, mCA, mCACL, Q8BL03, gene:21466315literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Lysine metabolism;
Small molecule transport > SLC25A family
placenta, testis
Mthfd2methylenetetrahydrofolate ­dehydrogenase ­(NAD+ ­dependent), ­methenyltetrahydrofolate ­cyclohydrolaseAW558851, NMDM, NMDMC, P18155, gene:1776815literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismspinalcord, placenta, testis
Mmabmethylmalonic ­aciduria ­(cobalamin ­deficiency) ­cblB ­type ­homolog ­(human)9130222L19Rik, ATR, Q9D273, gene:7769715APEX_matrix, GFP, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Hsd17b4hydroxysteroid ­(17-beta) ­dehydrogenase ­417-beta-HSD, 17[b]-HS, 17[b]-HSD, DBP, MFE-2, MFP, MFP2, MPF-2, Mfp-, Mfp-2, perMFE, perMFE-2, P51660, gene:1548815Rickettsial homolog, mito protein domain+, induction, coexpressionunknownMetabolism > Lipid metabolismkidney, liver, adipose, largeintestine, stomach, testis
Nntnicotinamide ­nucleotide ­transhydrogenase4930423F13Rik, AI323702, BB168308, Q8C1W8, gene:1811515literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebrum, spinalcord, skeletalmuscle, adipose, placenta
Tmem11transmembrane ­protein ­115730466P16Rik, AA409091, Q8BK08, gene:21682115GFP, targetP signal, mito protein domain+, induction, coexpression, MS/MSMIMMitochondrial dynamics and surveillanceall 14
Mrm3mitochondrial ­rRNA ­methyltransferase ­34833420N02Rik, AI255153, HC90, Rnm, Rnmtl1, Q5ND52, gene:6739015APEX_matrix, GFP, targetP signal, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
none
Ridareactive ­intermediate ­imine ­deaminase ­A ­homologHR1, HR12, HRP, HRP12, Hrs, Hrsp12, P52760, gene:1547315APEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MS+Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox6a2cytochrome ­c ­oxidase ­subunit ­6A2COX, CoxVIaH, V, VIaH, P43023, gene:1286215literature, yeast mito homolog+, mito protein domain+, induction, coexpressionMIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
heart, skeletalmuscle
Sco2SCO2 ­cytochrome ­c ­oxidase ­assembly ­proteinQ8VCL2, gene:10012682415literature, APEX_IMS, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors
all 14
Cox18cytochrome ­c ­oxidase ­assembly ­protein ­18BC038311, Q8VC74, gene:23143015literature, targetP signal+, yeast mito homolog++, mito protein domain, coexpressionMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
none
Gcshglycine ­cleavage ­system ­protein ­H ­(aminomethyl ­carrier)1100001L02Rik, 5730591C18Rik, Q91WK5, gene:6813315literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain+, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertion;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Amino acid metabolism > Glycine cleavage system
spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
Dmgdhdimethylglycine ­dehydrogenase ­precursor1200014D15Rik, AI787269, Q9DBT9, gene:7412915literature, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism
spinalcord, kidney, liver, smallintestine, stomach, placenta
Rdh13retinol ­dehydrogenase ­13 ­(all-trans ­and ­9-cis)8430425D21Rik, Q8CEE7, gene:10884115yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin A metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Lyrm2LYR ­motif ­containing ­22610208E05Rik, Q8R033, gene:10875515APEX_matrix, GFP, targetP signal+, mito protein domain+, coexpression, MS/MSMatrixOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
heart, adipose, largeintestine, placenta
Prdx5peroxiredoxin ­5AOEB1, AOEB166, AOPP, P, PLP, PMP, Pmp20, Prd, Prdx6, PrxV, P99029, gene:5468314literature, APEX_matrix, targetP signal, mito protein domain, induction, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolismall 14
Maip1matrix ­AAA ­peptidase ­interacting ­protein ­19430016H08Rik, AA409999, C78988, Q8BHE8, gene:6811514GFP, targetP signal, induction, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesall 14
Gstz1glutathione ­transferase ­zeta ­1 ­(maleylacetoacetate ­isomerase)GSTZ1-1, MAAI, Q9WVL0, gene:1487414APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismall 14
Twnktwinkle ­mtDNA ­helicaseD19Ertd626, D19Ertd626e, PEO, Pe, Peo1, Tw, Twinl, twin, Q8CIW5, gene:22615314literature, APEX_matrix, targetP signal+, Rickettsial homolog, induction, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid
none
Tefmtranscription ­elongation ­factor, ­mitochondrial1110002N22Rik, Q5SSK3, gene:6855014APEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Transcriptionliver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Coa3cytochrome ­C ­oxidase ­assembly ­factor ­31810033A19Rik, Ccdc56, D11Ertd99, D11Ertd99e, HSPC009, Q9D2R6, gene:5246914APEX_IMS, APEX_matrix, mito protein domain+, coexpression, MS/MS++MIMMitochondrial central dogma > Translation > Translation factors;
OXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
Mcur1mitochondrial ­calcium ­uniporter ­regulator ­16230416A05Rik, AU015498, AV136929, AW554392, C88263, Ccdc90, Ccdc90a, Q9CXD6, gene:7613714APEX_matrix, yeast mito homolog+, mito protein domain+, induction, MS/MSMIMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Pck2phosphoenolpyruvate ­carboxykinase ­2 ­(mitochondrial)1810010O14Rik, 9130022B02Rik, PEPCK-M, Q8BH04, gene:7455114literature, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis;
Metabolism > Carbohydrate metabolism > TCA-associated
cerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hmgcl3-hydroxy-3-methylglutaryl-Coenzyme ­A ­lyaseAW476067, HL, P38060, gene:1535614literature, APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism;
Metabolism > Amino acid metabolism > BCAA metabolism
all 14
Abhd10abhydrolase ­domain ­containing ­10Q6PE15, gene:21301214literature, APEX_IMS, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
BC003965cDNA ­sequence ­BC003965Ccsmst1, Q6RUT7, gene:21448914APEX_IMS, targetP signal+, induction, coexpression, MS/MSIMSnonebrainstem, spinalcord, adipose, largeintestine, placenta, testis
Acot2acyl-CoA ­thioesterase ­2AA571646, MTE-, MTE-I, Mte1, Q9QYR9, gene:17121014literature, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolismall 14
Alas2aminolevulinic ­acid ­synthase ­2, ­erythroidA, ALAS, ALAS-E, ALASE, Al, Alas-2, P08680, gene:1165614literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpressionMatrixMetabolism > Metals and cofactors > Heme synthesis and processingnone
Acsm3acyl-CoA ­synthetase ­medium-chain ­family ­member ­3S, Sa, Sah, Q3UNX5, gene:2021614literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationkidney, liver, adipose, smallintestine, largeintestine, stomach
Romo1reactive ­oxygen ­species ­modulator ­12010100O12Rik, AI853864, P60603, gene:6706714literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway;
Small molecule transport
cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
Mrpl39mitochondrial ­ribosomal ­protein ­L39C21orf8, MRP, MRP-L5, ORF22, Rp, Rpml5, Q9JKF7, gene:2739314literature, APEX_matrix, targetP signal, Rickettsial homolog, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Rhot2ras ­homolog ­family ­member ­T2Arh, Arht2, Mi, Miro2, Q8JZN7, gene:21495214literature, yeast mito homolog, mito protein domain+, induction, coexpressionMOMSignaling > Calcium homeostasis > EF hand proteins;
Mitochondrial dynamics and surveillance > Trafficking
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Higd1aHIG1 ­domain ­family, ­member ­1A2210020B17Rik, 7420700H20Rik, AI303276, AW049839, HIM, HIMP1, Hig, Hig1, Q9JLR9, gene:5629514literature, APEX_IMS, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors;
OXPHOS > Respirasome assembly
all 14
Tbrg4transforming ­growth ­factor ­beta ­regulated ­gene ­42310042P22Rik, AA120735, AA408001, AI527316, Cp, Cpr2, R74877, Tb-12, Q91YM4, gene:2137914literature, APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
all 14
Apooapolipoprotein ­O0610008C08Rik, 1110019O03Rik, Mico, Micos26, Q9DCZ4, gene:6831614literature, APEX_IMS, targetP signal, mito protein domain+, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexall 14
Pdp1pyruvate ­dehyrogenase ­phosphatase ­catalytic ­subunit ­1Gm1024, Ppm, Ppm2c, Q3UV70, gene:38151114literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dnajc15DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C151110003P16Rik, Dnaj, Dnajd1, Q78YY6, gene:6614814GFP, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motorcerebrum, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
Bcat2branched ­chain ­aminotransferase ­2, ­mitochondrialBcat(m), Bcat-, Bcat-2, Eca4, Eca40, O35855, gene:1203614literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > BCAA metabolismcerebrum, cerebellum, brainstem, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Abcd3ATP-binding ­cassette, ­sub-family ­D ­(ALD), ­member ­3AI313901, AU018866, AW146054, PMP, PMP68, PMP70, Pxm, Pxmp1, P55096, gene:1929914GFP, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpressionMembraneSmall molecule transport > ABC transporterskidney, liver, adipose, placenta, testis
Cps1carbamoyl-phosphate ­synthetase ­14732433M03Rik, C, CPS, D1Ucl, D1Ucla3, Q8C196, gene:22723114literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Urea cyclecerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Atp5mplATP ­synthase ­membrane ­subunit ­6.8PL2010107E04Rik, 9430003J03Rik, AU043134, AV124504, MLQ, Mp68, P56379, gene:7025714induction, coexpression++, MS/MS+MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
Oatornithine ­aminotransferaseAI194874, rh, rhg, P29758, gene:1824214literature, APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolismall 14
Hao2hydroxyacid ­oxidase ­2AI325478, Ha, Hao-2, Hao3, Haox3, Q9NYQ2, gene:5618514yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSunknownMetabolism > Lipid metabolismkidney, largeintestine, testis
Tha1threonine ­aldolase ­11300017K07Rik, GLY, GLY1, Q6XPS7, gene:7177614targetP signal+, mito protein domain+, MS/MS+Matrixnonekidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, testis
Hadhbhydroxyacyl-CoA ­dehydrogenase ­trifunctional ­multienzyme ­complex ­subunit ­beta4930479F15Rik, Mtp, Mtpb, TP-beta, Q99JY0, gene:23108614literature, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Ketone metabolism;
Metabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Amino acid metabolism > Lysine metabolism
all 14
Rdh14retinol ­dehydrogenase ­14 ­(all-trans ­and ­9-cis)3110030G19Rik, AW215439, P, PAN2, Q9ERI6, gene:10501414yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMembraneMetabolism > Vitamin metabolism > Vitamin A metabolismcerebrum, cerebellum, brainstem, spinalcord, smallintestine, largeintestine, stomach, placenta, testis
Fastkd1FAST ­kinase ­domains ­15330408N05Rik, mKIAA1800, Q6DI86, gene:32072014APEX_matrix, targetP signal, induction, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
liver, largeintestine
Car5bcarbonic ­anhydrase ­5b, ­mitochondrial7330410H16Rik, CA, CAVB, Ca5b, CarVb, D730005F19Rik, Q9QZA0, gene:5607814literature, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Urea cyclecerebellum, spinalcord, kidney, adipose, stomach, placenta, testis
Grpel2GrpE-like ­2, ­mitochondrialmt-GrpE, mt-GrpE#2, mt-Grpel2, O88396, gene:1771414literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+MatrixProtein import, sorting and homeostasis > Protein import and sorting > Import motor;
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis
placenta
Mrps17mitochondrial ­ribosomal ­protein ­S171810006P02Rik, Mprs17, Q9CQE3, gene:6625814literature, targetP signal, mito protein domain, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Lipt1lipoyltransferase ­1EG623661, Q8VCM4, gene:62366114GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Lipoate insertionadipose, placenta
Slc25a44solute ­carrier ­family ­25, ­member ­446720482A19, B430110G05Rik, Q8BGF9, gene:22951714yeast mito homolog+, mito protein domain+, induction, MS/MSMIMMetabolism > Amino acid metabolism > BCAA metabolism;
Small molecule transport > SLC25A family
placenta
Dutdeoxyuridine ­triphosphatase5031412I06Rik, 5133400F09Rik, D2Bwg0749e, Dutp, dUTPase, Q8VCG1, gene:11007414literature, targetP signal+, Rickettsial homolog, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, spinalcord, liver, heart, adipose, largeintestine, stomach, placenta
Immp2lIMP2 ­inner ­mitochondrial ­membrane ­peptidase-like ­(S. ­cerevisiae)AI853880, IM, IMP2, Tg(HLA-A/H2-D)2Enge, Q8BPT6, gene:9375714literature, yeast mito homolog++, mito protein domain, coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases
cerebellum, brainstem, liver, skeletalmuscle, adipose, largeintestine, testis
Cox19cytochrome ­c ­oxidase ­assembly ­protein ­191810074D02Rik, 2810437L13Rik, Q8K0C8, gene:6803313yeast mito homolog, mito protein domain, induction, coexpression+, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
Metabolism > Metals and cofactors > Copper metabolism;
OXPHOS > OXPHOS assembly factors
liver, placenta
Aldh1l2aldehyde ­dehydrogenase ­1 ­family, ­member ­L2D330038I09Rik, mtFDH, Q8K009, gene:21618813literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismbrainstem, spinalcord, liver, skeletalmuscle, smallintestine, largeintestine, stomach, placenta
Chchd2coiled-coil-helix-coiled-coil-helix ­domain ­containing ­2AL033347, Etoh, Etohi6, Q9D1L0, gene:1400413APEX_IMS, targetP signal+, yeast mito homolog+, mito protein domain, coexpressionIMSMitochondrial dynamics and surveillance > Apoptosisnone
Pisdphosphatidylserine ­decarboxylase9030221M09Rik, Q8BSF4, gene:32095113targetP signal, yeast mito homolog++, mito protein domain, MS/MSMIMMetabolism > Lipid metabolism > Phospholipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Crotcarnitine ­O-octanoyltransferase1200003H03Rik, Q9DC50, gene:7411413yeast mito homolog+, mito protein domain, induction, coexpression, MS/MSunknownMetabolism > Lipid metabolism > Fatty acid oxidationkidney, liver
Noa1nitric ­oxide ­associated ­12610024G14Rik, AU022345, AtNOS1, mAt, mAtNOS1, Q9JJG9, gene:5641213literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
adipose, largeintestine
Ndufaf8NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­81810043H04Rik, A2AMZ4, gene:20850113targetP signal, induction, coexpression+, MS/MSIMSOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
adipose, stomach
Acaa1bacetyl-Coenzyme ­A ­acyltransferase ­1BQ8VCH0, gene:23567413targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Lipid metabolismkidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mtrf1lmitochondrial ­translational ­release ­factor ­1-like9130004K12Rik, Q8BJU9, gene:10885313literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Translation factorstestis
Atp23ATP23 ­metallopeptidase ­and ­ATP ­synthase ­assembly ­factor ­homolog1110068E08Rik, 2410012H02Rik, Xrcc6b, Xrcc6bp1, Q9CWQ3, gene:6887613yeast mito homolog++, mito protein domain+, coexpressionIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebellum
Yme1l1YME1-like ­1 ­(S. ­cerevisiae)Fts, FtsH1, Ftsh, O88967, gene:2737713literature, APEX_IMS, yeast mito homolog, Rickettsial homolog, mito protein domain+, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Hdhd5haloacid ­dehalogenase ­like ­hydrolase ­domain ­containing ­5A930002G03Rik, Cecr, Cecr5, Q91WM2, gene:21493213APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++Matrixnonecerebellum, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Aldh7a1aldehyde ­dehydrogenase ­family ­7, ­member ­A1Atq, Atq1, D18Wsu181, D18Wsu181e, Q9DBF1, gene:11069513literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolism;
Metabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Vitamin metabolism > Choline and betaine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Chchd7coiled-coil-helix-coiled-coil-helix ­domain ­containing ­71810049H20Rik, Q8K2Q5, gene:6643313yeast mito homolog, induction, coexpression, MS/MS+IMSMetabolism > Metals and cofactors > Copper metabolismcerebrum, smallintestine, placenta, testis
Pdprpyruvate ­dehydrogenase ­phosphatase ­regulatory ­subunit4930402E16Rik, AU018056, mKIAA1990, Q7TSQ8, gene:31951813APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismcerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Nlnneurolysin ­(metallopeptidase ­M3 ­family)4930472G13Rik, C79345, Q91YP2, gene:7580513literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ndufaf2NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­21810058I14Rik, C86051, Ndufa, Ndufa12l, mim, mimitin, Q59J78, gene:7559713literature, APEX_matrix, targetP signal, induction, coexpression, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
Fastkd2FAST ­kinase ­domains ­22810421I24Rik, Q922E6, gene:7561913literature, APEX_matrix, targetP signal+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Dcakddephospho-CoA ­kinase ­domain ­containing3010024O21Rik, 6720485C15Rik, AI849483, Q8BHC4, gene:6808713GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMembranenoneall 14
Sdr39u1short ­chain ­dehydrogenase/reductase ­family ­39U, ­member ­12310014G06Rik, Q5M8N4, gene:65479513targetP signal, mito protein domain, coexpression, MS/MS++unknownnonecerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Garsglycyl-tRNA ­synthetaseGENA202, Gars1, Gena2, Gena201, Nmf249, Sgr, Sgrp23, Q9CZD3, gene:35317213targetP signal+, yeast mito homolog, mito protein domain, inductionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Uqcr11ubiquinol-cytochrome ­c ­reductase, ­complex ­III ­subunit ­XI0710008D09Rik, AL022707, Uqc, Uqcr, Q9CPX8, gene:6659413literature, targetP signal, mito protein domain+, MS/MS++MIMOXPHOS > Complex III > CIII subunits;
OXPHOS > OXPHOS subunits
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, stomach, placenta, testis
Ears2glutamyl-tRNA ­synthetase ­2, ­mitochondrial3230401I01Rik, mKIAA1970, Q9CXJ1, gene:6741713literature, APEX_matrix, GFP, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesadipose, largeintestine, placenta
Cox6b2cytochrome ­c ­oxidase ­subunit ­6B21700067P11Rik, BC048670, COXV, COXVIB2, Q80ZN9, gene:33318213literature, yeast mito homolog+, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
testis
Timm10btranslocase ­of ­inner ­mitochondrial ­membrane ­10BFxc1, Tim10, Tim10b, Tim9, Tim9b, Q9WV96, gene:1435613literature, APEX_IMS, yeast mito homolog+, mito protein domain+, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, largeintestine, stomach, placenta, testis
Atpaf1ATP ­synthase ­mitochondrial ­F1 ­complex ­assembly ­factor ­16330547J17Rik, AI593252, ATP, ATP11, ATP11p, H3BLL2, gene:23064913literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MSMatrixOXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, brainstem, spinalcord, adipose, smallintestine, largeintestine, placenta, testis
Sfxn3sideroflexin ­3Q91V61, gene:9428013yeast mito homolog, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Serine metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Small molecule transport > Sideroflexins
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Abcd2ATP-binding ­cassette, ­sub-family ­D ­(ALD), ­member ­2A, ABC3, ABC39, AL, ALDL1, ALDR, ALDRP, Q61285, gene:2687413targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MembraneSmall molecule transport > ABC transportersadipose
Sqorsulfide ­quinone ­oxidoreductase0610039J17Rik, 4930557M22Rik, Sq, Sqrdl, Q9R112, gene:5901013literature, targetP signal+, mito protein domain, MS/MS++MIMMetabolism > Electron carriers > Q-linked reactions, other;
Metabolism > Sulfur metabolism
spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sirt5sirtuin ­50610012J09Rik, 1500032M05Rik, AV001953, Q8K2C6, gene:6834613literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebrum, brainstem, spinalcord, liver, heart, adipose, largeintestine, stomach
Nudt13nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­134933433B15Rik, Q8JZU0, gene:6772513GFP, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebellum, brainstem, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Acad11acyl-Coenzyme ­A ­dehydrogenase ­family, ­member ­115730439E10Rik, AI987948, Q80XL6, gene:10263213mito protein domain+, induction, coexpressionMIMMetabolism > Lipid metabolism > Fatty acid oxidationspinalcord, kidney, liver, adipose
Ppoxprotoporphyrinogen ­oxidasePpo, P51175, gene:1904413literature, APEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Heme synthesis and processingcerebrum, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
D2hgdhD-2-hydroxyglutarate ­dehydrogenaseAA408776, AA408778, AI325464, Q8CIM3, gene:9831413literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domainMatrixMetabolism > Carbohydrate metabolism > TCA-associatedadipose, largeintestine
Diablodiablo, ­IAP-binding ­mitochondrial ­protein0610041G12Rik, 1700006L01Rik, AU040403, Sm, Smac, Q9JIQ3, gene:6659313literature, APEX_IMS, targetP signal+, mito protein domain+, MS/MSIMSMitochondrial dynamics and surveillance > Apoptosiscerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a45solute ­carrier ­family ­25, ­member ­45AW491445, Q8CFJ7, gene:10737513yeast mito homolog, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A familyliver, adipose, smallintestine, stomach, placenta, testis
Ttc19tetratricopeptide ­repeat ­domain ­192010204O13Rik, 2810460C24Rik, AI505442, Q8CC21, gene:7279512literature, APEX_IMS, targetP signal+, mito protein domain, induction, MS/MS+MIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, spinalcord, adipose, largeintestine, stomach, testis
Agxtalanine-glyoxylate ­aminotransferaseAGT, Agt1, Agxt1, SPT, O35423, gene:1161112literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Serine metabolism;
Metabolism > Amino acid metabolism > Glyoxylate metabolism
liver
DglucyD-glutamate ­cyclase9030617O03Rik, Q8BH86, gene:21783012literature, APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolismall 14
Mtfmtmitochondrial ­methionyl-tRNA ­formyltransferase2310020P08Rik, Q9D799, gene:6960612literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > fMet processing;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism
none
mt-Co1cytochrome ­c ­oxidase ­subunit ­ICoxI, P00397, gene:1770812literature, APEX_IMS, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV subunits;
Metabolism > Metals and cofactors > Heme-containing proteins;
OXPHOS > OXPHOS subunits
all 14
Endogendonuclease ­GO08600, gene:1380412literature, APEX_IMS, yeast mito homolog, mito protein domain, coexpression++, MS/MSIMSMitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial dynamics and surveillance > Apoptosis
all 14
Fam162afamily ­with ­sequence ­similarity ­162, ­member ­A2310056P07Rik, HGTD-P, Q9D6U8, gene:7018612APEX_IMS, APEX_matrix, targetP signal, induction, coexpression, MS/MS++MIMnoneall 14
Atp5j2ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­F21110019H14Rik, Atp5mf, P56135, gene:5742312literature, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Gls2glutaminase ­2 ­(liver, ­mitochondrial)A330074B06Rik, AI195532, GA, GLS, L, Lga, Q571F8, gene:21645612targetP signal, mito protein domain+, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, smallintestine, largeintestine
Timmdc1translocase ­of ­inner ­mitochondrial ­membrane ­domain ­containing ­12810021C21Rik, 4930455C21Rik, AV135763, Q8BUY5, gene:7691612literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrps33mitochondrial ­ribosomal ­protein ­S33AI841153, CGI-13, CGI-139, Gda, Gdap3, MRP-, MRP-S33, PTD00, PTD003, Q9D2R8, gene:1454812literature, targetP signal, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tfamtranscription ­factor ­A, ­mitochondrialAI661103, Hmgt, Hmgts, mtTF, mtTFA, tsHM, tsHMG, P40630, gene:2178012literature, APEX_matrix, targetP signal, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtRNA metabolism > Transcription
all 14
EcsitECSIT ­signalling ­integratorSit, Sitpec, Q9QZH6, gene:2694012literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrs2MRS2 ­magnesium ­transporterGm902, HPT, Mr, Mrs2l, RPT, Q5NCE8, gene:38083612APEX_matrix, GFP, targetP signal, yeast mito homolog++, coexpressionMIMSmall molecule transport;
Signaling
cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, smallintestine, largeintestine, stomach, placenta, testis
Abcb6ATP-binding ­cassette, ­sub-family ­B ­(MDR/TAP), ­member ­61200005B17Rik, Q9DC29, gene:7410412literature, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMOMMetabolism > Metals and cofactors > Heme synthesis and processing;
Small molecule transport > ABC transporters
cerebrum, brainstem, liver, largeintestine, stomach, placenta, testis
Mtfr1lmitochondrial ­fission ­regulator ­1-like2410166I05Rik, AI480750, Fam54, Fam54b, Q9CWE0, gene:7682412mito protein domain+, induction, coexpression, MS/MSunknownnonecerebrum, cerebellum, brainstem, spinalcord, placenta, testis
Lap3leucine ­aminopeptidase ­32410015L10Rik, AA410100, LAP-3, Lap, Lapep, Pe, Pep, Pep-7, Pep-S, Pep7, Peps, Q9CPY7, gene:6698812APEX_matrix, targetP signal, Rickettsial homolog, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteasesall 14
Acsf2acyl-CoA ­synthetase ­family ­member ­2Q8VCW8, gene:26489512APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Gpt2glutamic ­pyruvate ­transaminase ­(alanine ­aminotransferase) ­24631422C05Rik, AL, ALT2, AU014768, AU041193, C87201, Q8BGT5, gene:10868212APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolismcerebrum, brainstem, liver, skeletalmuscle, adipose, stomach, placenta, testis
Grhprglyoxylate ­reductase/hydroxypyruvate ­reductase1110059D05Rik, 6430629L09Rik, Glxr, Q91Z53, gene:7623812APEX_matrix, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glyoxylate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
StomstomatinEpb7., Epb7.2, sto, P54116, gene:1383012yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSMembranenoneadipose, placenta, testis
Glod4glyoxalase ­domain ­containing ­41700082G03Rik, 2700085E05Rik, C81254, Q9CPV4, gene:6720112APEX_matrix, targetP signal, coexpression, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tomm6translocase ­of ­outer ­mitochondrial ­membrane ­61110002E23Rik, AI663970, Q9CQN3, gene:6611912GFP, mito protein domain+, coexpression, MS/MS+MOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrps36mitochondrial ­ribosomal ­protein ­S361110018B13Rik, S36mt, Q9CQX8, gene:6612812literature, APEX_matrix, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome;
Metabolism > Carbohydrate metabolism > TCA cycle
all 14
Tmem65transmembrane ­protein ­652610029O13Rik, 4930438D12Rik, Q4VAE3, gene:7486812literature, APEX_matrix, targetP signal, coexpression, MS/MS++MIMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Tomm70atranslocase ­of ­outer ­mitochondrial ­membrane ­70A2610044B22Rik, D16Ium2, D16Ium22, D16Ium22e, D16Wsu109, D16Wsu109e, Tom7, Tom70, Tomm7, Tomm70, mKIAA0719, Q9CZW5, gene:2818512literature, yeast mito homolog+, mito protein domain, induction, coexpressionMOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Fhitfragile ­histidine ­triad ­geneAW045638, Fra1, Fra14A2, O89106, gene:1419812targetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Osgepl1O-sialoglycoprotein ­endopeptidase-like ­12610001M19Rik, AA416452, Q6PEB4, gene:7208512APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Crls1cardiolipin ­synthase ­10610009I22Rik, 4930557M15Rik, 5730490M08Rik, Q80ZM8, gene:6658612literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cardiolipin synthesisnone
Mocs1molybdenum ­cofactor ­synthesis ­13110045D15Rik, AI043170, AW536397, Q5RKZ7, gene:5673812APEX_matrix, targetP signal, mito protein domain+, MS/MS+MatrixMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteinscerebrum, liver, adipose, smallintestine, largeintestine, stomach, placenta
Aldh1l1aldehyde ­dehydrogenase ­1 ­family, ­member ­L11810048F20Rik, FDH, Fthfd, Neut2, Q8R0Y6, gene:10774712APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismcerebrum, liver, smallintestine, largeintestine, stomach, placenta, testis
Rfkriboflavin ­kinase0610038L10Rik, AF031381, KOI-4, fla, Q8CFV9, gene:5439112targetP signal, yeast mito homolog++, MS/MSMatrixMetabolism > Vitamin metabolism > Vitamin B2 metabolismbrainstem, spinalcord, kidney, adipose, smallintestine, largeintestine
Dhrs1dehydrogenase/reductase ­(SDR ­family) ­member ­11110029G07Rik, AW112170, D14Ertd484e, Q99L04, gene:5258512targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesiscerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Polgpolymerase ­(DNA ­directed), ­gammaAA409516, P, PolgA, Q3UG70, gene:1897512literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtDNA maintenance > mtDNA repair
cerebrum, cerebellum, spinalcord, liver, adipose, largeintestine, placenta, testis
Prelid3aPRELI ­domain ­containing ­3AA230074A19Rik, BC019561, Sl, Slmo1, Q8VE85, gene:22565511yeast mito homolog+, mito protein domain+, MS/MSIMSMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
cerebrum, cerebellum, spinalcord
Timm8a2translocase ­of ­inner ­mitochondrial ­membrane ­8A2Q4FZG7, gene:22326211literature, yeast mito homolog+, mito protein domain+, MS/MSIMSProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting
all 14
Slc25a14solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­brain), ­member ­14BMCP, BMCP1, UCP, UCP5, UCP5L, UCP5S, Q9Z2B2, gene:2052311literature, yeast mito homolog+, mito protein domain+, MS/MSMIMMetabolism > Sulfur metabolism;
Small molecule transport > SLC25A family
cerebrum, cerebellum, brainstem, placenta, testis
Rhot1ras ­homolog ­family ­member ­T12210403N23Rik, AA415293, AF244542, AI834919, Arh, Arht1, C430039G08Rik, Mi, Miro1, Q8BG51, gene:5904011literature, targetP signal, yeast mito homolog, mito protein domain+, MS/MS+MOMSignaling > Calcium homeostasis > EF hand proteins;
Mitochondrial dynamics and surveillance > Trafficking
all 14
Gpx1glutathione ­peroxidase ­1AI195024, AL033363, CGP, CGPx, GPx-, GPx-1, GSHPx, GSHPx-1, Gp, Gpx, P11352, gene:1477511literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Detoxification > Selenoproteins
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a46solute ­carrier ­family ­25, ­member ­461200007B05Rik, AI325987, Q9CQS4, gene:6745311yeast mito homolog+, mito protein domain+, inductionMOMSmall molecule transport > SLC25A family;
Mitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
cerebrum, spinalcord, adipose, placenta
mt-Nd5NADH ­dehydrogenase ­subunit ­5P03921, gene:1772111literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
mt-Nd4NADH ­dehydrogenase ­subunit ­4P03911, gene:1771911literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
mt-Nd2NADH ­dehydrogenase ­subunit ­2P03893, gene:1771711literature, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Prelid1PRELI ­domain ­containing ­12610524G07Rik, Preli, Q8R107, gene:6649411literature, APEX_IMS, GFP, targetP signal, yeast mito homolog++, mito protein domain+IMSMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
none
Tstd3thiosulfate ­sulfurtransferase ­(rhodanese)-like ­domain ­containing ­32610029I01Rik, Q9D0B5, gene:7703211targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, MS/MSunknownnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a32solute ­carrier ­family ­25, ­member ­322610043O12Rik, Mftc, Q8BMG8, gene:6990611literature, targetP signal, yeast mito homolog+, mito protein domain+MIMMetabolism > Vitamin metabolism > Vitamin B2 metabolism;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Small molecule transport > SLC25A family
adipose, placenta
Mcumitochondrial ­calcium ­uniporter2010012O16Rik, AV064928, C10orf42, Ccdc109, Ccdc109a, D130073L02Rik, Gm64, Q3UMR5, gene:21599911literature, GFP, targetP signal, mito protein domain+, MS/MS++MIMSignaling > Calcium homeostasis > Calcium cycle;
Small molecule transport > Calcium uniporter
cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Nipsnap1nipsnap ­homolog ­1O55125, gene:1808211APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
all 14
Pus1pseudouridine ­synthase ­1A730013B20Rik, MPU, MPUS1, mPus1p, Q9WU56, gene:5636111APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
none
Pdp2pyruvate ­dehyrogenase ­phosphatase ­catalytic ­subunit ­24833426J09Rik, Gm1705, mKIAA1348, Q504M2, gene:38205111APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpressionMatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolismadipose
Lypla1lysophospholipase ­1APT-1, Gm39587, LPL-I, P, Pla1a, P97823, gene:1877711Rickettsial homolog, mito protein domain, coexpression, MS/MS++unknownMetabolism > Lipid metabolism;
Signaling
all 14
Mthfd2lmethylenetetrahydrofolate ­dehydrogenase ­(NADP+ ­dependent) ­2-like1110019K23Rik, C630010D07Rik, D3YZG8, gene:66556311literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismspinalcord, placenta
Mtrf1mitochondrial ­translational ­release ­factor ­1A830062K05Rik, MtRF-1, Q8K126, gene:21125311literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Translation factorsadipose
Coq8bcoenzyme ­Q8B0610012P18Rik, Adck, Adck4, E9QLB8, gene:7688911APEX_matrix, GFP, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMMetabolism > Metals and cofactors > Coenzyme Q metabolismadipose, smallintestine, largeintestine, placenta
Hemk1HemK ­methyltransferase ­family ­member ­12310008M14Rik, AW049265, Q921L7, gene:6953611GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+MatrixMitochondrial central dogma > Translation > Translation factorsnone
Akr7a5aldo-keto ­reductase ­family ­7, ­member ­A5 ­(aflatoxin ­aldehyde ­reductase)0610025K21Rik, A, Afar, Afar1, Akr7a2, Q8CG76, gene:11019811APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism;
Metabolism > Detoxification > Xenobiotic metabolism
all 14
Cyp27a1cytochrome ­P450, ­family ­27, ­subfamily ­a, ­polypeptide ­11300013A03Rik, Cyp2, Cyp27, Q9DBG1, gene:10408611literature, targetP signal+, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme-containing proteins
kidney, liver, skeletalmuscle, adipose, smallintestine, placenta, testis
Oxct2a3-oxoacid ­CoA ­transferase ­2AOxct, Oxct2, Scot, Scot-, Scot-t1, Q9JJN4, gene:6405911targetP signal+, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolismtestis
Mrpl52mitochondrial ­ribosomal ­protein ­L521110047B07Rik, Q9D0Y8, gene:6883611literature, APEX_matrix, targetP signal+, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Fis1fission, ­mitochondrial ­12010003O14Rik, Ttc11, Q9CQ92, gene:6643711literature, yeast mito homolog++, mito protein domain+MOMMitochondrial dynamics and surveillance > Fissionall 14
AmtaminomethyltransferaseEG434437, GCVT, Q8CFA2, gene:43443711targetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Amino acid metabolism > Glycine cleavage system;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism
cerebrum, brainstem, spinalcord, kidney, liver, largeintestine, stomach, placenta
Exogendo/exonuclease ­(5'-3'), ­endonuclease ­G-likeAW557704, ENDO, ENG, ENGL-B, ENGL-a, Endogl1, Endogl2, Engl, Engla, Englb, Q8C163, gene:20819411APEX_IMS, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MIMMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA repair;
Mitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay
cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, placenta
Mpstmercaptopyruvate ­sulfurtransferaseMst, Q3UW66, gene:24622111APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MIMMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Sulfur metabolism
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pnpopyridoxine ­5'-phosphate ­oxidaseAI415282, Q91XF0, gene:10371111APEX_matrix, targetP signal, yeast mito homolog++, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Vitamin B6 metabolismbrainstem, liver
Mpv17l2MPV17 ­mitochondrial ­membrane ­protein-like ­2Fksg2, Fksg24, Q8VIK2, gene:23438411GFP, targetP signal, yeast mito homolog+, mito protein domain, coexpressionMIMMitochondrial central dogma > Translation > Mitochondrial ribosome assemblylargeintestine, placenta
Fundc2FUN14 ­domain ­containing ­24833415N24Rik, DC44, HCBP, HCBP6, Q9D6K8, gene:6739111mito protein domain+, MS/MS++MOMMitochondrial dynamics and surveillance > Organelle contact sites;
Signaling
cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mrpl18mitochondrial ­ribosomal ­protein ­L181010001C05Rik, C79879, HSPC0, HSPC071, MRP-, MRP-L18, Q9CQL5, gene:6768111literature, APEX_matrix, targetP signal, Rickettsial homolog, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Atp5g2ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­C2 ­(subunit ­9)1810041M08Rik, Atp5mc2, P56383, gene:6794211literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
none
Mettl5methyltransferase ­like ­52810410A08Rik, Q8K1A0, gene:7542211Rickettsial homolog, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modificationsnone
Slc25a38solute ­carrier ­family ­25, ­member ­38AV019094, BC010801, a, appoptosin, Q91XD8, gene:20863811yeast mito homolog++, mito protein domain+, coexpressionMIMMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism;
Small molecule transport > SLC25A family
none
Slc25a36solute ­carrier ­family ­25, ­member ­36C330005L02Rik, Q922G0, gene:19228711GFP, yeast mito homolog+, mito protein domain+, coexpressionMIMMetabolism > Nucleotide metabolism > Nucleotide import;
Small molecule transport > SLC25A family
brainstem, spinalcord, placenta, testis
Trmt2bTRM2 ­tRNA ­methyltransferase ­2B4732479N06Rik, Q8BQJ6, gene:21520111GFP, targetP signal, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
none
Abat4-aminobutyrate ­aminotransferase9630038C02Rik, AI255750, GABA, Gabaat, Gabat, Gm9851, I54, Laibat, X61497, P61922, gene:26886011literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism;
Metabolism > Metals and cofactors > Fe-S-containing proteins
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Aldh5a1aldhehyde ­dehydrogenase ­family ­5, ­subfamily ­A16330403E24Rik, Ahd-1, Ahd1, D630032B01Rik, SS, SSADH, Ssdh1, Q8BWF0, gene:21457911APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolismall 14
Got2glutamatic-oxaloacetic ­transaminase ­2, ­mitochondrialAL022787, FABP, FABP-pm, Got-2, Kyat, Kyat4, mA, mAspAT, P05202, gene:1471911literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle;
Metabolism > Amino acid metabolism > Glutamate metabolism;
Metabolism > Amino acid metabolism > Glyoxylate metabolism;
Metabolism > Amino acid metabolism > Kynurenine metabolism;
Metabolism > Sulfur metabolism
all 14
Ckmt1creatine ­kinase, ­mitochondrial ­1, ­ubiquitousMt-CK, ScCKmit, U-MtCK, UbCKmi, UbCKmit, mi-C, mi-CK, mia-CK, P30275, gene:1271611literature, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Nucleotide metabolism > Creatine metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Gtpbp3GTP ­binding ­protein ­32410009F13Rik, AI607903, Gtpb, Q923K4, gene:7035911literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism
largeintestine
Sirt3sirtuin ­32310003L23Rik, AI848213, Si, Sir2l3, Q8R104, gene:6438411literature, APEX_matrix, mito protein domain, induction, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism;
Signaling
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
C330018D20RikRIKEN ­cDNA ­C330018D20 ­geneAU018666, Q9CWB7, gene:7742211targetP signal, coexpression+, MS/MSMatrixnonecerebrum, cerebellum, spinalcord, liver, heart, skeletalmuscle, adipose, placenta, testis
Parlpresenilin ­associated, ­rhomboid-likeD16Ertd607, D16Ertd607e, P, PRO2, PRO2207, PS, PSARL1, PSENIP2, Psarl, Q5XJY4, gene:38103811literature, targetP signal, yeast mito homolog++, mito protein domain, MS/MSMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Bloc1s1biogenesis ­of ­lysosomal ­organelles ­complex-1, ­subunit ­1AI839753, BL, BLOS1, Gcn5, Gcn5l1, O55102, gene:1453310mito protein domain, coexpression++, MS/MSunknownSignalingplacenta, testis
Cox8ccytochrome ­c ­oxidase ­subunit ­8C1700007F21Rik, COX8-, COX8-3, COXV, COXVIII-3, A6H666, gene:7548310literature, targetP signal, mito protein domain+, MS/MSMIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
testis
AclyATP ­citrate ­lyaseA730098H14Rik, AW538652, Q91V92, gene:10411210APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Carbohydrate metabolism > TCA-associatedcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Sfxn5sideroflexin ­5C230001H08Rik, Q925N0, gene:9428210literature, yeast mito homolog, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > TCA-associated;
Small molecule transport > Sideroflexins
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine
Slc25a40solute ­carrier ­family ­25, ­member ­40B230315F11Rik, Q8BGP6, gene:31965310literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Slc25a27solute ­carrier ­family ­25, ­member ­273632410G24Rik, 9430092A03Rik, D530043E16Rik, Ucp, Ucp4, Q9D6D0, gene:7401110literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A familycerebrum, cerebellum, brainstem, spinalcord
Slc25a23solute ­carrier ­family ­25 ­(mitochondrial ­carrier; ­phosphate ­carrier), ­member ­232310067G05Rik, SCaMC, SCaMC-3, Q6GQS1, gene:6697210literature, yeast mito homolog+, mito protein domain+, MS/MSMIMMetabolism > Nucleotide metabolism > Nucleotide import;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > SLC25A family
cerebrum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta
Ucp3uncoupling ­protein ­3 ­(mitochondrial, ­proton ­carrier)AI645527, Slc2, Slc25a9, UCP-, UCP-3, P56501, gene:2222910literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A familyspinalcord, heart, skeletalmuscle, adipose
Htra2HtrA ­serine ­peptidase ­2AI481710, Htr, O, Omi, Pr, Prss25, mnd, mnd2, Q9JIY5, gene:6470410literature, APEX_IMS, targetP signal, Rickettsial homolog, mito protein domain, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Apoptosis
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Nadk2NAD ­kinase ­2, ­mitochondrialMNA, MNADK, Nadk, Nadkd1, Q8C5H8, gene:6864610APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
mt-Cytbcytochrome ­bP00158, gene:1771110literature, yeast mito homolog++, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex III > CIII subunits;
Metabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Electron carriers > Cytochromes;
OXPHOS > OXPHOS subunits
all 14
Chchd5coiled-coil-helix-coiled-coil-helix ­domain ­containing ­51110027L01Rik, AW045710, Q9CQP3, gene:6617010APEX_IMS, yeast mito homolog++, coexpression, MS/MSIMSnoneadipose, placenta, testis
Mrps31mitochondrial ­ribosomal ­protein ­S311500002D03Rik, AA960481, Imoge, Imogen38, Imogen44, Q61733, gene:5731210literature, APEX_matrix, targetP signal, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Ndufa1NADH:ubiquinone ­oxidoreductase ­subunit ­A11810049F12Rik, MWFE, O35683, gene:5440510literature, coexpression+, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Hoga14-hydroxy-2-oxoglutarate ­aldolase ­10610010D20Rik, Dhd, Dhdpsl, N, Npl2, Q9DCU9, gene:6743210GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Amino acid metabolism > Glyoxylate metabolismkidney, liver, adipose, largeintestine, placenta, testis
Aldh3a2aldehyde ­dehydrogenase ­family ­3, ­subfamily ­A2AI194803, Ahd, Ahd-, Ahd-3, Ahd-3r, Ahd3, Ahd3-r, Ald, Aldh, Aldh4, Aldh4-r, FAL, FALDH, P47740, gene:1167110targetP signal+, yeast mito homolog, mito protein domain, coexpressionMembraneMetabolism > Detoxification > ROS and glutathione metabolismspinalcord, kidney, liver, smallintestine, largeintestine, stomach, placenta, testis
Pam16presequence ­translocase-asssociated ­motor ­16 ­homolog ­(S. ­cerevisiae)2010110I09Rik, AV006767, CGI-13, CGI-136, Mag, Magmas, Tim1, Tim16, Timm16, Q9CQV1, gene:6644910literature, APEX_matrix, targetP signal, yeast mito homolog, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motorall 14
Tomm5translocase ­of ­outer ­mitochondrial ­membrane ­51110019J04Rik, Tom5, B1AXP6, gene:6851210literature, mito protein domain+, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOMcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ndufb4NADH:ubiquinone ­oxidoreductase ­subunit ­B40610006N12Rik, 1300010H20Rik, Q9CQC7, gene:6819410literature, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Fam136afamily ­with ­sequence ­similarity ­136, ­member ­A2010309E21Rik, AW124904, Hyccin, Q9CR98, gene:6648810APEX_IMS, mito protein domain+, MS/MS++IMSnoneall 14
Mpv17lMpv17 ­transgene, ­kidney ­disease ­mutant-likeM-, M-LP, Q99MS3, gene:9373410yeast mito homolog+, mito protein domain, MS/MS++MIMSmall molecule transportcerebrum, cerebellum, brainstem, spinalcord, kidney, liver
Gykl1glycerol ­kinase-like ­1AI449806, Gk-r, Gk-rs1, Q8C635, gene:1462510yeast mito homolog+, mito protein domain, MS/MS++Membranenonecerebrum, cerebellum, brainstem, spinalcord, kidney, heart, smallintestine, testis
Cpt1bcarnitine ­palmitoyltransferase ­1b, ­muscleCpt, Cpt1, Cpt1-m, Cpti, Cpti-m, M-CP, M-cpti, Q924X2, gene:1289510literature, yeast mito homolog+, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle
cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Akr1b10aldo-keto ­reductase ­family ­1, ­member ­B10 ­(aldose ­reductase)2310005E10Rik, Akr1b16, G5E895, gene:6786110induction, coexpression, MS/MS++unknownMetabolism > Vitamin metabolism > Vitamin A metabolism;
Metabolism > Detoxification > Xenobiotic metabolism
cerebrum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc25a2solute ­carrier ­family ­25 ­(mitochondrial ­carrier, ­ornithine ­transporter) ­member ­2Or, Ornt2, Q99ML6, gene:8388510literature, yeast mito homolog++, mito protein domain+MIMMetabolism > Amino acid metabolism > Urea cycle;
Small molecule transport > SLC25A family
testis
Slc25a53solute ­carrier ­family ­25, ­member ­532310046F18Rik, 2810402A17Rik, AI448995, AI841128, Mcar, Mcart6, A2AF28, gene:6706210yeast mito homolog++, mito protein domain+MIMSmall molecule transport > SLC25A familytestis
Opa3optic ­atrophy ­3D630048P19Rik, Gm1425, Gm472, Q505D7, gene:40318710literature, targetP signal, coexpression, MS/MS++MOMnoneall 14
Fahd1fumarylacetoacetate ­hydrolase ­domain ­containing ­11110025H10Rik, AV002085, Q8R0F8, gene:6863610literature, APEX_matrix, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associatedall 14
Pxmp4peroxisomal ­membrane ­protein ­43010018P03Rik, Pmp24, Q9JJW0, gene:5903810targetP signal, mito protein domain+, coexpressionunknownnonekidney, liver, adipose
Nif3l1Ngg1 ­interacting ­factor ­3-like ­1 ­(S. ­pombe)1110030G24Rik, Q9EQ80, gene:6510210APEX_matrix, targetP signal, yeast mito homolog, coexpression, MS/MS+Matrixnonecerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
Grsf1G-rich ­RNA ­sequence ­binding ­factor ­1BB232551, C80280, D5Wsu31, D5Wsu31e, Q8C5Q4, gene:23141310APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
adipose, smallintestine, largeintestine, stomach, placenta, testis
Macrod1mono-ADP ­ribosylhydrolase ­1AI604841, AW743046, D930010J01Rik, Lrp16, Q922B1, gene:10722710APEX_matrix, targetP signal, coexpression, MS/MS++MatrixSignalingcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cisd3CDGSH ­iron ­sulfur ­domain ­3Mel-13, Mel1, Mel13, B1AR13, gene:21714910APEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
all 14
Nmnat3nicotinamide ­nucleotide ­adenylyltransferase ­34933408N02Rik, PN, PNAT3, Q99JR6, gene:7408010literature, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Nudt8nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­82310039H17Rik, Q9CR24, gene:6638710APEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Coenzyme A metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Catcatalase2210418N07, Ca, Cas, Cas-1, Cas1, Cs-, Cs-1, P24270, gene:1235910yeast mito homolog++, mito protein domain, coexpressionIMSMetabolism > Detoxification > ROS and glutathione metabolismspinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dnajc19DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C191810055D05Rik, AA959924, Tim14, Q9CQV7, gene:6771310literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motorall 14
Elac2elaC ­ribonuclease ­Z ­21110017O07Rik, D11Wsu80, D11Wsu80e, Hpc2, Q80Y81, gene:6862610APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processingcerebellum, skeletalmuscle, adipose, largeintestine, stomach
Sugctsuccinyl-CoA ­glutarate-CoA ­transferase5033411D12Rik, D17907, Q7TNE1, gene:19213610APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Amino acid metabolismkidney, liver, testis
Hint3histidine ­triad ­nucleotide ­binding ­protein ­30610010I17Rik, AV009015, HIN, HINT-3, HINT-4, HINT4, Q9CPS6, gene:6684710Rickettsial homolog, mito protein domain, induction, coexpression+unknownnonebrainstem, heart, skeletalmuscle
Karslysyl-tRNA ­synthetaseAA589550, AL024334, AL033315, AL033367, D8Ertd698, D8Ertd698e, D8Wsu108, D8Wsu108e, Kars1, L, LysRS, mKIAA0070, Q99MN1, gene:8530510literature, GFP, targetP signal+, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Dnajc28DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C28BC020175, ORF28, Q8VCE1, gene:24673810targetP signal, Rickettsial homolog, mito protein domain, coexpression+unknownnonestomach
Cyb5bcytochrome ­b5 ­type ­B1810044O22Rik, AU015618, Cyb5m, Q9CQX2, gene:6642710literature, mito protein domain, coexpression, MS/MS++MOMMetabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > Amidoxime reducing complex;
Metabolism > Electron carriers > Cytochromes
all 14
Nudt2nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­22310051L06Rik, AA939917, AP, APAH1, P56380, gene:6640110mito protein domain, coexpression, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingall 14
Phyhphytanoyl-CoA ­hydroxylaseAI256161, AI265699, L, Lnap1, PAHX, O35386, gene:1692210targetP signal, induction, MS/MS++MatrixMetabolism > Lipid metabolismkidney, liver, smallintestine
Guk1guanylate ­kinase ­1AA409738, AL033299, AL033300, AV026611, Gmk, Guk-1, Q64520, gene:149239APEX_matrix, targetP signal, Rickettsial homolog, induction, coexpression, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach
Nudt19nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­19D7R, D7Rp, D7Rp2, D7Rp2-r, D7Rp2-s, D7Rp2e, RP, RP2-r, RP2-s, P11930, gene:1109599APEX_matrix, targetP signal+, mito protein domain, inductionMatrixMetabolism > Metals and cofactors > Coenzyme A metabolismkidney, liver, largeintestine, placenta
mt-Co3cytochrome ­c ­oxidase ­subunit ­IIIP00416, gene:177109literature, yeast mito homolog++, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits
all 14
Mrpl42mitochondrial ­ribosomal ­protein ­L422700009F22Rik, 2900055D03Rik, D10Ertd322, D10Ertd322e, HSPC2, HSPC204, L31mt, L42mt, MRP-, MRP-L31, MRP-L42, MRP-S32, PTD00, PTD007, Rpm, Rpml31, S32mt, Q9CPV3, gene:672709APEX_matrix, GFP, mito protein domain+, induction, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeliver, adipose, largeintestine, testis
Dhrs7bdehydrogenase/reductase ­(SDR ­family) ­member ­7BBC003479, C79874, C80074, PexRAP, Q99J47, gene:2168209Rickettsial homolog, mito protein domain, induction, coexpressionMembranenonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Nt5m5',3'-nucleotidase, ­mitochondrial2010013E09Rik, AI846937, dNT-, dNT-2, Q8VCE6, gene:1038509literature, targetP signal, mito protein domain, induction, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, testis
Mthfsl5, ­10-methenyltetrahydrofolate ­synthetase-likeGm2382, L7N466, gene:1000397079targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismcerebrum, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta
Mthfs5, ­10-methenyltetrahydrofolate ­synthetase1110034I12Rik, 2310020H23Rik, AI119695, Q9D110, gene:1078859targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismcerebrum, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta
Nme4NME/NM23 ­nucleoside ­diphosphate ­kinase ­42610027N22Rik, 2810024O08Rik, 5730493H09Rik, NM23-M, NM23-M4, Nm23M4, Q9WV84, gene:565209APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMIMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingadipose, largeintestine, placenta, testis
Oma1OMA1 ­zinc ­metallopeptidase2010001O09Rik, MPRP-1, ZMPOMA1, Q9D8H7, gene:670139APEX_IMS, GFP, targetP signal, yeast mito homolog++, coexpressionMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Fission
skeletalmuscle, adipose, largeintestine
Acsl6acyl-CoA ­synthetase ­long-chain ­family ­member ­6A330035H04Rik, AW050338, Fac, Facl6, L, LACS, Lacsl, mKIAA0837, Q91WC3, gene:2167399yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, testis
Rpusd3RNA ­pseudouridylate ­synthase ­domain ­containing ­3AI527266, Q14AI6, gene:1011229APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
largeintestine
Acss1acyl-CoA ­synthetase ­short-chain ­family ­member ­11110032O15Rik, AI788978, Ac, Acas2, Acas2l, AceC, AceCS2, Q99NB1, gene:687389literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidationcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dguokdeoxyguanosine ­kinasedGK, dGK1, dGK2, dGK3, Q9QX60, gene:273699literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pars2prolyl-tRNA ­synthetase ­(mitochondrial)(putative)BC027073, Q8CFI5, gene:2305779APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasessmallintestine, largeintestine, stomach
Htatip2HIV-1 ­Tat ­interactive ­protein ­2AW111545, Cc3, TIP, Tip30, Q9Z2G9, gene:534159yeast mito homolog, mito protein domain+, MS/MSMembranenonecerebrum, cerebellum, brainstem, liver, adipose, placenta, testis
Qrsl1glutaminyl-tRNA ­synthase ­(glutamine-hydrolyzing)-like ­12700038P16Rik, C80053, Ga, GatA, Q9CZN8, gene:765639literature, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasesbrainstem, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
NaxdNAD(P)HX ­dehydratase0710008K08Rik, 2810407E01Rik, Car, Carkd, Q9CZ42, gene:692259GFP, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolismall 14
Chchd6coiled-coil-helix-coiled-coil-helix ­domain ­containing ­60710001P09Rik, 1700021B03Rik, Mico, Micos25, Q91VN4, gene:660989literature, APEX_IMS, APEX_matrix, yeast mito homolog, coexpression, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complexcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pcbd2pterin ­4 ­alpha ­carbinolamine ­dehydratase/dimerization ­cofactor ­of ­hepatocyte ­nuclear ­factor ­1 ­alpha ­(TCF1) ­22700061N24Rik, Dcoh, Dcoh2, Dcohm, Q9CZL5, gene:725629targetP signal+, yeast mito homolog, induction, MS/MSunknownMetabolism > Metals and cofactors > Tetrahydobiopterin synthesiscerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Agmatagmatine ­ureohydrolase ­(agmatinase)5033405N08Rik, A2AS89, gene:759869literature, targetP signal+, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolismliver, smallintestine
Micu2mitochondrial ­calcium ­uptake ­21110008L20Rik, 4833427E09Rik, AU041871, Efha, Efha1, Smhs2, Q8CD10, gene:685149literature, APEX_IMS, GFP, targetP signal+, mito protein domain, MS/MS+MIMSignaling > Calcium homeostasis > Calcium cycle;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > Calcium uniporter
smallintestine, largeintestine, placenta, testis
Akr1b7aldo-keto ­reductase ­family ­1, ­member ­B7A, AR, Avdp, MV, MVDP, P21300, gene:119979induction, coexpression, MS/MS++unknownMetabolism > Lipid metabolism > Phospholipid metabolismcerebrum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Scp2sterol ­carrier ­protein ­2, ­liverAA409774, AA409893, C76618, C79031, NSL-TP, SC, SCP, SCP-2, SCP-X, SCPX, ns, ns-LTP, P32020, gene:202809targetP signal, Rickettsial homolog, mito protein domain+MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesisbrainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, placenta, testis
Rab24RAB24, ­member ­RAS ­oncogene ­family6530406O07Rik, P35290, gene:193369yeast mito homolog, mito protein domain, induction, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Autophagy
cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, stomach, testis
Mcubmitochondrial ­calcium ­uniporter ­dominant ­negative ­beta ­subunit9030408N13Rik, Ccdc109b, Q810S1, gene:668159literature, targetP signal+, mito protein domain+MIMSignaling > Calcium homeostasis > Calcium cycle;
Small molecule transport > Calcium uniporter
placenta
Lyplal1lysophospholipase-like ­1BC027340, Q96, Q96AVO, Q3UFF7, gene:2267918targetP signal, mito protein domain, MS/MS++unknownMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, placenta, testis
Spata19spermatogenesis ­associated ­191700001L23Rik, AV047838, spergen-1, Q9DAQ9, gene:754698mito protein domain+, MS/MS++unknownnonetestis
mt-Atp8ATP ­synthase ­F0 ­subunit ­8P03930, gene:177068literature, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
all 14
Ldhal6blactate ­dehydrogenase ­A-like ­6B4933402O15Rik, AI326310, LD, LDHL, Ldhal, Q8BVP2, gene:1065578targetP signal, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Carbohydrate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Aldh1a7aldehyde ­dehydrogenase ­family ­1, ­subfamily ­A7AI987940, Ahd2-l, Ahd2-like, Aldh, Aldh-pb, Aldh1a4, Aldhpb, O35945, gene:263588yeast mito homolog+, mito protein domain, coexpression, MS/MSunknownnonecerebrum, cerebellum, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Kyat3kynurenine ­aminotransferase ­3Ccbl, Ccbl2, KA, KATIII, Kat, Kat3, Q71RI9, gene:2299058APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Kynurenine metabolism;
Metabolism > Metals and cofactors > NAD biosynthesis and metabolism
spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Oxsm3-oxoacyl-ACP ­synthase, ­mitochondrial4933425A18Rik, C80494, Q9D404, gene:711478literature, APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisliver, heart, adipose, smallintestine, largeintestine, placenta, testis
mt-Nd3NADH ­dehydrogenase ­subunit ­3P03899, gene:177188literature, Rickettsial homolog, mito protein domain+, MS/MSMIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Adck1aarF ­domain ­containing ­kinase ­12610005A10Rik, Q9D0L4, gene:721138yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSunknownnonecerebrum, spinalcord, kidney, heart, skeletalmuscle, adipose, stomach, placenta
Slc25a33solute ­carrier ­family ­25, ­member ­335730438N18Rik, Pn, Pnc1, Q3TZX3, gene:705568literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Small molecule transport > SLC25A family
brainstem, spinalcord, placenta, testis
Mgst1microsomal ­glutathione ­S-transferase ­11500002K10Rik, Gst, Q91VS7, gene:566158mito protein domain, coexpression, MS/MS++MembraneMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism
cerebrum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Unguracil ­DNA ­glycosylaseUNG1, UNG2, P97931, gene:222568literature, targetP signal, yeast mito homolog, mito protein domain, inductionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Nsun4NOL1/NOP2/Sun ­domain ­family, ­member ­42310010O12Rik, 2810405F18Rik, AI507900, Shtap, Q9CZ57, gene:721818APEX_matrix, targetP signal, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
placenta
Tmem205transmembrane ­protein ­205Q91XE8, gene:2350438yeast mito homolog, mito protein domain+, coexpressionMembranenoneliver, adipose
Dbidiazepam ­binding ­inhibitorACBD1, Ac, Acbp, E, EP, endoz, endozepine, P31786, gene:131678targetP signal, mito protein domain, induction, coexpressionunknownMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
CoasyCoenzyme ­A ­synthase1300003G02Rik, Dpc, Dpck, P, Ppat, Ukr, Ukr1, Q9DBL7, gene:717438APEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Coenzyme A metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Stard7START ­domain ­containing ­7AI852671, AL022671, AW544915, Q8R1R3, gene:991388APEX_IMS, targetP signal, mito protein domain, induction, coexpression+IMSMetabolism > Lipid metabolism > Phospholipid metabolism;
Small molecule transport
none
Letm2leucine ­zipper-EF-hand ­containing ­transmembrane ­protein ­26030453H13, D030041N04Rik, Q7TNU7, gene:2700358targetP signal, yeast mito homolog+, mito protein domain+MIMnonenone
Ptcd1pentatricopeptide ­repeat ­domain ­11110069M14Rik, Q8C2E4, gene:717998targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granulescerebellum, largeintestine, placenta
Mtfp1mitochondrial ­fission ­process ­11700020C11Rik, 2610507A21Rik, AV005788, Mtp1, Mtp18, Q9CRB8, gene:679008literature, induction, coexpression, MS/MS+MembraneMitochondrial dynamics and surveillance > Fissionall 14
Coa4cytochrome ­c ­oxidase ­assembly ­factor ­45330414O08Rik, AI115477, AW047259, Chchd8, E2ig2, Q8BT51, gene:681858yeast mito homolog++, mito protein domain, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
placenta
Ephx2epoxide ­hydrolase ­2, ­cytoplasmicCEH, Eph, Eph2, SEH, s, sE, sEP, P34914, gene:138508Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Lipid metabolism
kidney, liver, heart, skeletalmuscle, adipose, smallintestine, stomach
Nrd1nardilysin, ­N-arginine ­dibasic ­convertase, ­NRD ­convertase ­12600011I06Rik, AI875733, NRD, NRD-C, Nrdc, Q8BHG1, gene:2305988targetP signal, Rickettsial homolog, mito protein domain+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones;
Protein import, sorting and homeostasis > Protein import and sorting
testis
Acacbacetyl-Coenzyme ­A ­carboxylase ­betaAI597064, AW743042, Acc, Acc2, Accb, E9Q4Z2, gene:1007058yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+MOMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Vitamin metabolism > Biotin utilizing proteins
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Mavsmitochondrial ­antiviral ­signaling ­proteinD430028G21Rik, IP, IPS-1, Visa, cardif, Q8VCF0, gene:2286078literature, induction, coexpression+, MS/MSMOMSignaling > Immune responsebrainstem, skeletalmuscle, adipose, placenta, testis
Tmem143transmembrane ­protein ­1432310076O21Rik, AI481604, Q8VD26, gene:702098targetP signal, coexpression+, MS/MSMIMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
Mtpapmitochondrial ­poly(A) ­polymerase0610027A18Rik, AW551379, Pa, Papd1, Tent, Tent6, Q9D0D3, gene:674408literature, APEX_matrix, targetP signal+, mito protein domain, inductionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
cerebrum, cerebellum, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sdslserine ­dehydratase-like4432411H13Rik, AI504310, SDH1, SDS, SDS-RS1, TDH, Q8R238, gene:2576358yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Amino acid metabolism > Serine metabolismnone
Cmpk2cytidine ­monophosphate ­(UMP-CMP) ­kinase ­2, ­mitochondrial1200004E04Rik, TDK, TDKI, Tyk, Tyki, Q3U5Q7, gene:221698literature, targetP signal+, Rickettsial homolog, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingspinalcord, smallintestine
Glyctkglycerate ­kinase6230410P16Rik, C430006L12, Q8QZY2, gene:2355828targetP signal, coexpression, MS/MS+MatrixMetabolism > Carbohydrate metabolismkidney, liver, placenta
Rpusd4RNA ­pseudouridylate ­synthase ­domain ­containing ­42410001E19Rik, Q9CWX4, gene:719898APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
placenta
Smim20small ­integral ­membrane ­protein ­201110067B18Rik, 1810013D10Rik, MITRAC7, N28078, D3Z7Q2, gene:662787literature,targetP signal, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, placenta, testis
Mterf4mitochondrial ­transcription ­termination ­factor ­41810059A23Rik, 4933412H03Rik, Mterfd, Mterfd2, Q8BVN4, gene:698217APEX_matrix, targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblynone
Top1mtDNA ­topoisomerase ­1, ­mitochondrial2900052H09Rik, Q8R4U6, gene:729607literature, APEX_matrix, targetP signal+, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtRNA metabolism > Transcription
none
Arg2arginase ­type ­IIAII, AU022422, O08691, gene:118477literature, APEX_matrix, targetP signal+, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolismkidney, adipose, smallintestine, largeintestine, placenta
Ptrh2peptidyl-tRNA ­hydrolase ­2A230072I16Rik, Bit, Bit1, CGI-147, PTH 2, Q8R2Y8, gene:2170577literature, yeast mito homolog, mito protein domain, MS/MS++MOMnoneall 14
Lyrm1LYR ­motif ­containing ­11110065L10Rik, 2310004B22Rik, 4930404J24Rik, Q9CQB7, gene:739197GFP, yeast mito homolog, mito protein domain+, MS/MSunknownnonebrainstem, testis
Aars2alanyl-tRNA ­synthetase ­2, ­mitochondrialAarsl, AlaRS, Gm89, Q14CH7, gene:2248057literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetasescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Acsl1acyl-CoA ­synthetase ­long-chain ­family ­member ­1Ac, Acas, Acas1, Acs, FACS, Fac, Facl2, LACS 1, LACS1, P41216, gene:140817yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMOMMetabolism > Lipid metabolism > Fatty acid oxidationall 14
Dnajc30DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C301300007M11Rik, Wbscr, Wbscr18, P59041, gene:661147APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, MS/MSMIMnonecerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach
Tmlhetrimethyllysine ­hydroxylase, ­epsilonBbox, Bbox2, D430017M14Rik, TML, TMLD, TMLH, Q91ZE0, gene:1922897literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Carnitine synthesis and transportkidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
BaxBCL2-associated ­X ­proteinQ07813, gene:120287literature, mito protein domain, coexpression, MS/MS++MOMMitochondrial dynamics and surveillance > Apoptosiscerebrum, cerebellum, brainstem, adipose, largeintestine, placenta, testis
Cryzl2crystallin ­zeta ­like ­2Q3UNZ8, gene:2265277targetP signal, mito protein domain, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Dnm1ldynamin ­1-like6330417M19Rik, AI450666, Dlp1, Dnm, Dnmlp1, Dr, Drp1, pyt, python, Q8K1M6, gene:740067literature, yeast mito homolog+, mito protein domain, inductionMOMMitochondrial dynamics and surveillance > Fissioncerebrum, cerebellum, brainstem, spinalcord
Pxmp2peroxisomal ­membrane ­protein ­222kD, 22kDa, PMP, PMP22, P42925, gene:193017GFP, yeast mito homolog+, mito protein domain, inductionMIMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
Cox20cytochrome ­c ­oxidase ­assembly ­protein ­202310005N03Rik, Fam3, Fam36a, Q9D7J4, gene:663597literature, APEX_IMS, GFP, yeast mito homolog++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
Tmem177transmembrane ­protein ­1772300008B03Rik, Q8BPE4, gene:663437targetP signal, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, adipose, stomach, placenta, testis
Tk2thymidine ­kinase ­2, ­mitochondrialAU024611, mt-TK, Q8BN51, gene:578137literature, targetP signal+, mito protein domain, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, adipose
Fundc1FUN14 ­domain ­containing ­11500005J14Rik, 1810033P05Rik, Q9DB70, gene:720187yeast mito homolog, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, testis
Pgs1phosphatidylglycerophosphate ­synthase ­12610019F11Rik, 4933424M23Rik, SAF, Q8BHF7, gene:744517targetP signal, yeast mito homolog++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
cerebrum, spinalcord, placenta
Fasnfatty ­acid ­synthaseA630082H08Rik, F, FAS, P19096, gene:141047yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionIMSMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
Cbr2carbonyl ­reductase ­2ML, MLCR, P08074, gene:124097targetP signal, Rickettsial homolog, mito protein domain, MS/MS+MatrixMetabolismcerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Chpt1choline ­phosphotransferase ­1Q8C025, gene:2128627targetP signal, mito protein domain, induction, coexpression+MIMMetabolism > Lipid metabolism > Phospholipid metabolismnone
Atp5g1ATP ­synthase, ­H+ ­transporting, ­mitochondrial ­F0 ­complex, ­subunit ­C1 ­(subunit ­9)Atp5mc1, Q9CR84, gene:119517literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
none
Fam210bfamily ­with ­sequence ­similarity ­210, ­member ­B2010011I20Rik, AI430961, AV108736, Q9D8B6, gene:670177targetP signal, yeast mito homolog, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Iron homeostasiscerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Sfxn2sideroflexin ­2C79732, F630107H02Rik, Q925N2, gene:942797yeast mito homolog, mito protein domain+, coexpressionMIMSmall molecule transport > Sideroflexinskidney, liver, adipose, largeintestine, stomach, placenta, testis
Mmadhcmethylmalonic ­aciduria ­(cobalamin ­deficiency) ­cblD ­type, ­with ­homocystinuria2010311D03Rik, AI314967, CblD, Q99LS1, gene:1091297APEX_matrix, targetP signal, induction, coexpressionMatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolismnone
Otcornithine ­transcarbamylaseAI265390, Sf, spf, P11725, gene:184167literature, targetP signal, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolism > Urea cyclecerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
Txnrd1thioredoxin ­reductase ­1T, TR, TR1, Trx, TrxR1, Q9JMH6, gene:504937GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSunknownMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Detoxification > Selenoproteins
skeletalmuscle, smallintestine, placenta, testis
Arf5ADP-ribosylation ­factor ­5P84084, gene:118447targetP signal, mito protein domain, coexpression, MS/MSunknownnonecerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Fpgsfolylpolyglutamyl ­synthetaseAA408187, P48760, gene:142876APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homologMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolismnone
Trmt10ctRNA ­methyltransferase ­10C, ­mitochondrial ­RNase ­P ­subunit1300018J16Rik, D16Ertd454, D16Ertd454e, Rg9mtd, Rg9mtd1, Rnmtd1, Q3UFY8, gene:525756literature, APEX_matrix, GFP, targetP signal+, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
largeintestine, placenta
Them7thioesterase ­superfamily ­member ­70610012H03Rik, Q9DCP4, gene:740886targetP signal, mito protein domain, MS/MS+Matrixnonekidney
Lactb2lactamase, ­beta ­2Cgi-8, Cgi-83, E430032H21Rik, Q99KR3, gene:2124426mito protein domain, induction, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decaykidney, liver, largeintestine, stomach
Smim26small ­integral ­membrane ­protein ­26Gm561, Q3V460, gene:2287156induction, coexpression, MS/MSMembranenonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, placenta, testis
Pgam5phosphoglycerate ­mutase ­family ­member ­52610528A17Rik, Q8BX10, gene:725426APEX_IMS, mito protein domain, coexpression, MS/MS++MOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
Ptpmt1protein ­tyrosine ­phosphatase, ­mitochondrial ­11110001D10Rik, 2810004N20Rik, PLIP, Q66GT5, gene:664616literature, APEX_matrix, mito protein domain, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
all 14
Hebp1heme ­binding ­protein ­1Hebp, p22HBP, Q9R257, gene:151996APEX_IMS, mito protein domain, coexpression, MS/MS++IMSnonecerebrum, cerebellum, liver, adipose, placenta
Abcd1ATP-binding ­cassette, ­sub-family ­D ­(ALD), ­member ­1A, ALDP, Ald, Aldgh, P48410, gene:116666targetP signal, Rickettsial homolog, mito protein domain, inductionMembraneSmall molecule transport > ABC transportersadipose
Hsdl1hydroxysteroid ­dehydrogenase ­like ­12700067E09Rik, Q8BTX9, gene:725526GFP, Rickettsial homolog, mito protein domain, MS/MS++unknownnonecerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cbr3carbonyl ­reductase ­31110001J05Rik, C81353, Q8K354, gene:1098576targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Detoxification > Xenobiotic metabolismcerebrum, spinalcord, adipose, smallintestine, largeintestine, stomach
Prdx6peroxiredoxin ­61-Cys Prx, 1-cys, 1-cysPrx, 9430088D19Rik, AA690119, Aop2, Brp-, Brp-12, CP-, CP-3, GP, GPx, Ltw, Ltw-, Ltw-4, Ltw4, Lvtw, Lvtw-4, N, NSGPx, ORF06, Prdx5, a, aiPLA2, O08709, gene:117586yeast mito homolog+, Rickettsial homolog, mito protein domainunknownMetabolism > Lipid metabolism > Phospholipid metabolism;
Metabolism > Detoxification > ROS and glutathione metabolism
cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
Dnajc4DnaJ ­heat ­shock ­protein ­family ­(Hsp40) ­member ­C4Hsp, Hspf2, Mcg18, Q9D844, gene:574316GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMembraneProtein import, sorting and homeostasis > Protein homeostasislargeintestine
CebpzosCCAAT/enhancer ­binding ­protein ­(C/EBP), ­zeta, ­opposite ­strand1110001A16Rik, Q8BTE5, gene:685546coexpression+, MS/MS+unknownnonecerebrum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, placenta, testis
Foxred1FAD-dependent ­oxidoreductase ­domain ­containing ­1BC024806, TEG-23, Tex23, Q3TQB2, gene:2351696literature, targetP signal, mito protein domain, coexpression+MIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
adipose, largeintestine, placenta, testis
Eri3exoribonuclease ­3P, PI, PINT1, Prnpip1, Q8C460, gene:1405466targetP signal+, mito protein domain, MS/MSMatrixnonecerebrum, cerebellum
Dhx30DEAH ­(Asp-Glu-Ala-His) ­box ­polypeptide ­302810477H02Rik, C130058C04Rik, Ddx30, HELG, Ret-CoR, hel, Q99PU8, gene:728316literature, targetP signal+, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Bcl2l13BCL2-like ­13 ­(apoptosis ­facilitator)BCL-R, BCL-RAMBO, E430016C20Rik, Mi, Mil, Mil-1, Mil1, P59017, gene:940446literature, mito protein domain, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy;
Mitochondrial dynamics and surveillance > Apoptosis
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Acp6acid ­phosphatase ­6, ­lysophosphatidic5730559A09Rik, AC, ACPL1, AU022842, mPA, mPACPL1, Q8BP40, gene:666596literature, APEX_IMS, targetP signal, mito protein domain, MS/MS++IMSMetabolism > Lipid metabolism > Phospholipid metabolismcerebrum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cox7a2lcytochrome ­c ­oxidase ­subunit ­7A2 ­likeCOX, COX7AR, COX7RP, EB1, SIG, SIG-, SIG-81, SIG81, Silg81, Q61387, gene:204636literature, APEX_IMS, APEX_matrix, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits;
OXPHOS > OXPHOS subunits;
OXPHOS > OXPHOS assembly factors;
OXPHOS > Respirasome assembly
all 14
Tstd1thiosulfate ­sulfurtransferase ­(rhodanese)-like ­domain ­containing ­1AV065366, EG226654, Gm4848, KAT, E9PY03, gene:2266546targetP signal, yeast mito homolog, mito protein domain, MS/MSunknownMetabolism > Sulfur metabolismkidney, smallintestine, largeintestine
Qdprquinoid ­dihydropteridine ­reductase2610008L04Rik, D5Ertd371e, Dhpr, PKU2, Q8BVI4, gene:1103916APEX_matrix, targetP signal, mito protein domain, inductionMatrixMetabolism > Metals and cofactors > Tetrahydobiopterin synthesis;
Metabolism > Vitamin metabolism > Folate and 1-C metabolism
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, stomach, placenta, testis
Acsm2acyl-CoA ­synthetase ­medium-chain ­family ­member ­2AI315615, BC031140, Q8K0L3, gene:2337996yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS+MatrixMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Detoxification > Xenobiotic metabolism
kidney, liver, heart
Adck2aarF ­domain ­containing ­kinase ­2AA408112, BB006057, Q6NSR3, gene:578696GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMIMnonenone
Osbpl1aoxysterol ­binding ­protein-like ­1AG430090F17Rik, Gm753, ORP-1, Osbpl1b, Q91XL9, gene:642916Rickettsial homolog, mito protein domain, induction, MS/MSunknownMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
cerebrum, liver, largeintestine, placenta
Trmt1tRNA ­methyltransferase ­16720406L13Rik, 6720477L24, D8Ertd812, D8Ertd812e, Q3TX08, gene:2125286targetP signal+, yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Mtif3mitochondrial ­translational ­initiation ­factor ­32810012L14Rik, AI414549, Q9CZD5, gene:763666literature, APEX_matrix, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > Translation factorslargeintestine
Pet100PET100 ­homolog2900053A13Rik, P0DJE0, gene:1005038906literature, yeast mito homolog++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, spinalcord, kidney, liver, heart, smallintestine, largeintestine, placenta
Mtfr1mitochondrial ­fission ­regulator ­11300002C08Rik, 1700080D04Rik, 2810026O10Rik, 4930579E05Rik, Chppr, Fam54, Fam54a2, Q99MB2, gene:674726literature, targetP signal, mito protein domain+, coexpressionMembraneMitochondrial dynamics and surveillance > Fissionnone
Tfb1mtranscription ­factor ­B1, ­mitochondrialAI429207, mtTFB1, Q8JZM0, gene:2244816literature, APEX_matrix, Rickettsial homolog, mito protein domain, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
brainstem, largeintestine, placenta, testis
Fth1ferritin ­heavy ­polypeptide ­1FHC, Fth, H-fer, HFt, MFH, P09528, gene:143196mito protein domain, MS/MS++unknownMetabolism > Metals and cofactors > Iron homeostasiscerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta
Tspotranslocator ­proteinBz, Bzrp, IBP, P, PBR, Ts, Tspo1, P50637, gene:122576literature, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesisspinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Glyatglycine-N-acyltransferaseA330009E03Rik, ACGNAT, AI195249, AI315345, CAT, GAT, Q91XE0, gene:1071466literature, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Amino acid metabolism > Glycine metabolism;
Metabolism > Detoxification > Xenobiotic metabolism
spinalcord, kidney, liver, placenta
Rbfaribosome ­binding ­factor ­A1110032A13Rik, AI595940, Q6P3B9, gene:687316APEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblynone
Rnaseh1ribonuclease ­H1E9QLN8, gene:198196literature, APEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
none
Tmem186transmembrane ­protein ­1862810440M13Rik, 4432406C05Rik, AI648175, AW210586, Q9CR76, gene:666905targetP signal, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pex11bperoxisomal ­biogenesis ­factor ­11 ­betaPEX11beta, Pex11pbeta, Q9Z210, gene:186325targetP signal, coexpression, MS/MSMembranenonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
Nudt5nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­5Q9JKX6, gene:538935yeast mito homolog++, mito protein domain, coexpressionunknownMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingnone
Sod1superoxide ­dismutase ­1, ­solubleB430204E11Rik, Cu/Zn-, Cu/Zn-SOD, CuZn, CuZnSOD, I, Ip, Ipo-1, Ipo1, SO, SODC, Sod, Sod-1, P08228, gene:206555literature, yeast mito homolog, mito protein domain, induction, coexpressionIMSMetabolism > Detoxification > ROS and glutathione metabolismall 14
Starsteroidogenic ­acute ­regulatory ­proteinAV363654, D8Ertd419, D8Ertd419e, stARD1, P51557, gene:208455literature, targetP signal, mito protein domain, coexpression, MS/MSMOM , IMSMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesistestis
Gtpbp10GTP-binding ­protein ­10 ­(putative)4930545J22Rik, BC034507, Q8K013, gene:2077045APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblylargeintestine, placenta
Acss3acyl-CoA ­synthetase ­short-chain ­family ­member ­38430416H19Rik, Gm874, Q14DH7, gene:3806605targetP signal, yeast mito homolog, mito protein domain, MS/MSMatrixMetabolism > Lipid metabolismkidney, liver, adipose, placenta, testis
Ccdc51coiled-coil ­domain ­containing ­515730568A12Rik, AI551049, Mit, Mitok, Q3URS9, gene:666585APEX_matrix, targetP signal, MS/MS++MIMSmall molecule transportall 14
Acot9acyl-CoA ­thioesterase ­90610041P13Rik, Acat, Acate2, C76421, MT-ACT4, MT-ACT48, MTE-2, U8, p4, p48, Q9R0X4, gene:563605literature, targetP signal, MS/MS++MIMMetabolism > Lipid metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Ndufaf3NADH:ubiquinone ­oxidoreductase ­complex ­assembly ­factor ­34733401H18Rik, Q9JKL4, gene:667065literature, targetP signal, mito protein domain, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
Flad1flavin ­adenine ­dinucleotide ­synthetase ­1A930017E24Rik, Pp5, Pp591, Q8R123, gene:3199455APEX_matrix, mito protein domain, induction, coexpressionMatrixMetabolism > Vitamin metabolism > Vitamin B2 metabolismspinalcord, adipose, stomach
Acacaacetyl-Coenzyme ­A ­carboxylase ­alphaA530025K05Rik, Ac, Acac, Acc, Acc1, Gm738, Q5SWU9, gene:1074765yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis;
Metabolism > Vitamin metabolism > Biotin utilizing proteins
brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
Kmokynurenine ­3-monooxygenase ­(kynurenine ­3-hydroxylase)AI046660, Q91WN4, gene:982565yeast mito homolog, mito protein domain, MS/MS++MOMMetabolism > Amino acid metabolism > Kynurenine metabolism;
Metabolism > Metals and cofactors > NAD biosynthesis and metabolism
kidney, liver
Mterf3mitochondrial ­transcription ­termination ­factor ­32410017I18Rik, Mterfd, Mterfd1, Q8R3J4, gene:664105literature, APEX_matrix, GFP, targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assemblynone
Oxr1oxidation ­resistance ­12210416C20Rik, C7, C7B, Q4KMM3, gene:1707195literature, yeast mito homolog+, mito protein domain, MS/MSMOMMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem
Nudt9nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­91190002C07Rik, ADPR-PPase, AI462474, Q8BVU5, gene:741675APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, placenta, testis
Thnsl1threonine ­synthase-like ­1 ­(bacterial)AW413632, Q8BH55, gene:2089675APEX_matrix, mito protein domain, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, testis
Pycr2pyrroline-5-carboxylate ­reductase ­family, ­member ­21810018M05Rik, P5c, P5cr2, Q922Q4, gene:690515APEX_matrix, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Hint1histidine ­triad ­nucleotide ­binding ­protein ­1AA673479, Hint, Ip, Ipk1, PKCI, PKCI-1, PRKC, PRKCNH1, P70349, gene:152545Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, spinalcord, kidney, smallintestine, placenta, testis
Slc25a34solute ­carrier ­family ­25, ­member ­34Gm1369, A2ADF7, gene:3840715yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
Slc25a48solute ­carrier ­family ­25, ­member ­48AU042651, E230025K15, Q8BW66, gene:3282585yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
Slc25a28solute ­carrier ­family ­25, ­member ­28Mfr, Mfrn2, Mrs3, Mrs3/4, Q8R0Z5, gene:2466965literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Metals and cofactors > Iron homeostasis;
Small molecule transport > SLC25A family
none
Slc25a43solute ­carrier ­family ­25, ­member ­43Gm8, A2A3V2, gene:1947445yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
Slc25a47solute ­carrier ­family ­25, ­member ­47AI132487, AI876593, HDMCP, Q6IS41, gene:1049105literature, yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
Slc25a41solute ­carrier ­family ­25, ­member ­414933406J04Rik, AI507137, Q8BVN7, gene:1037755yeast mito homolog+, mito protein domain+MIMMetabolism > Nucleotide metabolism > Nucleotide import;
Small molecule transport > SLC25A family
none
Slc25a54solute ­carrier ­family ­25, ­member ­544930443G12Rik, SCaMC-1, SCaMC-1like, B1AUS6, gene:746865yeast mito homolog+, mito protein domain+MembraneSmall molecule transport > SLC25A familynone
Slc25a37solute ­carrier ­family ­25, ­member ­371700020E22Rik, 4930513O14Rik, 4930526G11Rik, AI848481, C330015G08Rik, Fra, Mf, Mfr, Mfrn, Mfrn1, Ms, Mscp, frascati, mito, mitoferrin, Q920G8, gene:677125literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Metals and cofactors > Iron homeostasis;
Small molecule transport > SLC25A family
none
Ucp2uncoupling ­protein ­2 ­(mitochondrial, ­proton ­carrier)Slc25a8, UCP 2, UCPH, P70406, gene:222285literature, yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A familynone
YbeyybeY ­metallopeptidase1110068N23Rik, A130042E20Rik, C21orf57, ORF57, ORF66, Q8CAV0, gene:2161195APEX_matrix, targetP signal, Rickettsial homolog, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
largeintestine, placenta, testis
Ogg18-oxoguanine ­DNA-glycosylase ­1Mmh, O08760, gene:182945literature, targetP signal+, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Gm4952predicted ­gene ­4952EG240549, Q5FW57, gene:2405495mito protein domain, MS/MS++unknownMetabolismkidney, liver
Fabp1fatty ­acid ­binding ­protein ­1, ­liverFa, Fabpl, L-F, L-FABP, P12710, gene:140805mito protein domain, MS/MS++unknownMetabolism > Metals and cofactors > Heme synthesis and processing;
Metabolism > Lipid metabolism
liver, smallintestine
Mettl15methyltransferase ­like ­150610027B03Rik, AI303697, AW049952, Mett5d1, Q9DCL4, gene:768945APEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modificationslargeintestine, placenta
Metap1dmethionyl ­aminopeptidase ­type ­1D ­(mitochondrial)2310066F24Rik, 3110033D18Rik, AV117938, MAP 1D, Map1d, MetAP 1D, Meta, Metapl1, Q9CPW9, gene:665595literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > fMet processing;
Protein import, sorting and homeostasis > Protein homeostasis > Proteases
none
Ldhblactate ­dehydrogenase ­BAI790582, H-Ld, H-Ldh, LDH-B, LDH-H, Ldh-, Ldh-2, Ldh2, P16125, gene:168325Rickettsial homolog, mito protein domain, inductionunknownMetabolism > Amino acid metabolism > Glyoxylate metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Lyrm9LYR ­motif ­containing ­91810012P15Rik, Q3UN90, gene:662745mito protein domain+, MS/MSunknownnonecerebellum, heart, adipose, testis
Mtarc1mitochondrial ­amidoxime ­reducing ­component ­11300013F15Rik, Mar, Marc1, Mos, Mosc1, Q9CW42, gene:661125mito protein domain+, MS/MSMOMMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins;
Metabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > Amidoxime reducing complex
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Recql4RecQ ­protein-like ­4RecQ4, Q75NR7, gene:794565targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Plpbppyridoxal ­phosphate ­binding ­protein1700024N20Rik, 2200002F22Rik, P, Prosc, Q9Z2Y8, gene:1148635APEX_matrix, targetP signal, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin B6 metabolismall 14
Mul1mitochondrial ­ubiquitin ­ligase ­activator ­of ­NFKB ­10610009K11Rik, AV000801, Gide, Q8VCM5, gene:683505literature, mito protein domain+, inductionMOMProtein import, sorting and homeostasis > Protein homeostasis;
Mitochondrial dynamics and surveillance > Fission;
Signaling
skeletalmuscle, largeintestine
Nudt6nudix ­(nucleoside ­diphosphate ­linked ­moiety ­X)-type ­motif ­6Asfgf2b, Q8CH40, gene:2292285APEX_matrix, targetP signal, mito protein domain, coexpressionMatrixnonenone
Pink1PTEN ­induced ­putative ­kinase ­11190006F07Rik, AU042772, AW557854, BRPK, br, mFLJ00387, Q99MQ3, gene:689435literature, targetP signal, mito protein domain, coexpressionMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy;
Signaling
none
Vps13dvacuolar ­protein ­sorting ­13DB1ART2, gene:2308955manual, yeast mito homolog, mito protein domain, induction, coexpressionMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle
Dmac2distal ­membrane ­arm ­assembly ­complex ­22310004L02Rik, At, Atp5sl, C030044E10Rik, Q9D7K5, gene:663494APEX_matrix, GFP, targetP signal, induction, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, stomach
Micu1mitochondrial ­calcium ­uptake ­1C730016L05Rik, Calc, Cba, Cbara1, Q8VCX5, gene:2160014literature, APEX_IMS, GFP, targetP signal, mito protein domain, MS/MS+MIMSignaling > Calcium homeostasis > Calcium cycle;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > Calcium uniporter
cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Nt5dc35'-nucleotidase ­domain ­containing ­3AU040402, AW540062, C630002B14Rik, G, TU12B1-TY, Q3UHB1, gene:1034664APEX_matrix, targetP signal, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, stomach, placenta, testis
Nipsnap3anipsnap ­homolog ­3A1700054F22Rik, AI429120, G3X8S9, gene:733984APEX_matrix, targetP signal, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Top3atopoisomerase ­(DNA) ­III ­alphaO70157, gene:219754APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replicationtestis
Amacralpha-methylacyl-CoA ­racemaseMac, Macr1, O09174, gene:171174literature, mito protein domain, coexpression, MS/MSMatrixMetabolism > Lipid metabolism > Fatty acid oxidationkidney, liver, adipose, smallintestine, testis
Trmt5TRM5 ­tRNA ­methyltransferase ­52610027O18Rik, mKIAA1393, Q9D0C4, gene:763574literature,targetP signal, yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Micu3mitochondrial ­calcium ­uptake ­family, ­member ­32900075B16Rik, Efha, Efha2, Q9CTY5, gene:785064manual, targetP signal, mito protein domain, MS/MSMIMSignaling > Calcium homeostasis > Calcium cycle;
Signaling > Calcium homeostasis > EF hand proteins;
Small molecule transport > Calcium uniporter
cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, stomach
Pnkdparoxysmal ­nonkinesiogenic ­dyskinesia2210013N15Rik, 2810403H05Rik, AI854243, Brp, Brp17, MNCb-5687, MR-1, Tahccp2, Q69ZP3, gene:566954literature,targetP signal, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Car5acarbonic ­anhydrase ­5a, ­mitochondrialCAV, Ca, Ca5a, Car5, P23589, gene:123524literature, targetP signal, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Urea cycleliver
Nthl1nth ­(endonuclease ­III)-like ­1 ­(E.coli)Nth, Nth1, Octs3, O35980, gene:182074literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainunknownMetabolism > Metals and cofactors > Fe-S-containing proteinsnone
Arl2ADP-ribosylation ­factor-like ­22610009M23Rik, AI115441, AW553335, Q9D0J4, gene:563274literature, mito protein domain, coexpression, MS/MS+IMSMitochondrial dynamics and surveillance > Fusioncerebrum, brainstem, spinalcord, adipose, largeintestine
Synj2bpsynaptojanin ­2 ­binding ­proteinA, AA409442, ARIP2, ActRIP4, D12Wsu118, D12Wsu118e, OMP, OMP25, Q9D6K5, gene:240714APEX_IMS, mito protein domain, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Organelle contact sitescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Mettl8methyltransferase ­like ­8BC004636, T, Tip, A2AUU0, gene:2280194APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtRNA metabolismnone
Mterf1bmitochondrial ­transcription ­termination ­factor ­1bGm9897, B9EJ57, gene:2085954literature, APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtRNA metabolism > Transcription
none
Rsad1radical ­S-adenosyl ­methionine ­domain ­containing ­1B430319G23, BC056485, Q5SUV1, gene:2379264APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Metals and cofactors > Fe-S-containing proteinsnone
Fdpsfarnesyl ­diphosphate ­synthetase6030492I17Rik, AI256750, Fdp, Fdpsl1, mKIAA1293, Q920E5, gene:1101964Rickettsial homolog, mito protein domain, MS/MS+MIMMetabolism > Lipid metabolism > Cholesterol-associatedliver, adipose, smallintestine, largeintestine, placenta
Ociad1OCIA ­domain ­containing ­16030432N09Rik, A, AI481327, AW557942, Asrij, B230209J16Rik, BB021357, Emi, Emi2, Im, Imi2, OCIA, TPA0, TPA018, Q9CRD0, gene:680954APEX_IMS, GFP, MS/MS++MOMnoneall 14
FastkFas-activated ­serine/threonine ­kinase0610011K02Rik, 610011K02Rik, Q8C725, gene:665874GFP, targetP signal, induction, coexpressionMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
none
Acsm4acyl-CoA ­synthetase ­medium-chain ­family ­member ­4O-M, O-MACS, OM, OMACS, Q80W40, gene:2338014manual, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMetabolism > Lipid metabolism > Fatty acid oxidationnone
Nme6NME/NM23 ­nucleoside ­diphosphate ­kinase ­6nm23-M, nm23-M6, O88425, gene:543694literature, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processinglargeintestine
Ahcyl1S-adenosylhomocysteine ­hydrolase-like ­11110034F20Rik, AA409031, AA414901, Ahcy-, Ahcy-rs3, DC, DCAL, IR, Irbit, Q80SW1, gene:2297094mito protein domain+, inductionMOMMitochondrial dynamics and surveillance > Organelle contact sitesbrainstem, spinalcord, smallintestine, stomach
Smim8small ­integral ­membrane ­protein ­81810030N24Rik, 2810406B13Rik, Q9CQQ0, gene:662914manual, induction, coexpression, MS/MSMOMnonecerebrum, cerebellum, brainstem, spinalcord, kidney, adipose, placenta, testis
Idi1isopentenyl-diphosphate ­delta ­isomerase4832416K17Rik, IPPI1, P58044, gene:3195544targetP signal, mito protein domain, MS/MS+MatrixMetabolism > Lipid metabolism > Cholesterol-associatedcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mtx3metaxin ­34930470O13Rik, AA409304, AI853833, AU067765, EG624619, Gm1194, Gm6514, D3YTP3, gene:3827934manual, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Intramitochondrial membrane interactionscerebrum, cerebellum, brainstem, spinalcord
Tmem126btransmembrane ­protein ­126B1110001A23Rik, Q9D1R1, gene:684724mito protein domain+, MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Bnip3BCL2/adenovirus ­E1B ­interacting ­protein ­3N, Nip3, O55003, gene:121764literature, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Apoptosiscerebrum, cerebellum, brainstem, heart, skeletalmuscle, adipose
Fkbp8FK506 ­binding ­protein ­838kD, 38kDa, FKBP-38, FKBP-8, FKBPR38, Fkbp3, Fkbp38, mFKBP38, O35465, gene:142324literature, yeast mito homolog, mito protein domain, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Organelle contact sites;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
cerebrum, brainstem, spinalcord, largeintestine, placenta, testis
Mcrip2MAPK ­regulated ­corepressor ­interacting ­protein ­29530058B02Rik, Fam19, Fam195a, Q9CQB2, gene:682413induction, coexpression+unknownSignalingnone
Bola3bolA-like ­3 ­(E. ­coli)1810056O20Rik, Q8CEI1, gene:786533targetP signal, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis;
Metabolism > Metals and cofactors > Fe-S-containing proteins
cerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pnpt1polyribonucleotide ­nucleotidyltransferase ­11200003F12Rik, Old35, P, PNPase, Pnptl1, Q8K1R3, gene:717013literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrix, IMSMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decayall 14
Pde12phosphodiesterase ­122'-PDE, E430028B21Rik, Q3TIU4, gene:2119483APEX_matrix, targetP signal+, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
brainstem, smallintestine, largeintestine, testis
Usp30ubiquitin ­specific ­peptidase ­306330590F17Rik, AI851327, D5Ertd483, D5Ertd483e, Q3UN04, gene:1007563literature,targetP signal+, mito protein domainMOMProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
adipose, placenta, testis
Tfb2mtranscription ­factor ­B2, ­mitochondrialHkp, Hkp1, Q3TL26, gene:152783literature, APEX_matrix, targetP signal+, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtRNA metabolism > Transcription
placenta
Mrps18bmitochondrial ­ribosomal ­protein ­S18B2400002C15Rik, MRP-S18-2, S18mt-b, Q99N84, gene:669733literature, APEX_matrix, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosomecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
Maobmonoamine ­oxidase ­B6330414K01Rik, MAO, MAO-B, Q8BW75, gene:1097313literature, mito protein domain, MS/MS++MOMMetabolism > Amino acid metabolism > Catechol metabolism;
Metabolism > Detoxification > Xenobiotic metabolism
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Prxl2aperoxiredoxin ­like ­2A5730469M10Rik, AU040822, Ad, Adrx, Fam21, Fam213a, Pamm, Q9CYH2, gene:705643GFP, mito protein domain, MS/MS++MembraneMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, placenta, testis
Mgst3microsomal ­glutathione ­S-transferase ­32010012L10Rik, 2010306B17Rik, 2700004G04Rik, AA516734, GST, GST-III, Q9CPU4, gene:664473APEX_IMS, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Eicosanoid metabolismall 14
Dhodhdihydroorotate ­dehydrogenase2810417D19Rik, AI834883, O35435, gene:567493literature, mito protein domain, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing;
Metabolism > Electron carriers > Q-linked reactions, other
cerebrum, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mrpl48mitochondrial ­ribosomal ­protein ­L481810030E20Rik, 2610028L11Rik, CGI-11, CGI-118, D4Ertd786, D4Ertd786e, L48mt, MRP-L48, Q8JZS9, gene:524433literature, APEX_matrix, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosomeall 14
Gdap1ganglioside-induced ­differentiation-associated-protein ­1O88741, gene:145453APEX_IMS, mito protein domain, MS/MS++MOMnonecerebrum, cerebellum, brainstem, spinalcord
Bak1BCL2-antagonist/killer ­1Ba, Bak, N-B, N-BAK1, N-Bak, O08734, gene:120183literature, mito protein domain, MS/MS++MOMMitochondrial dynamics and surveillance > Apoptosisbrainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
mt-Nd1NADH ­dehydrogenase ­subunit ­1P03888, gene:177163literature, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
all 14
Ociad2OCIA ­domain ­containing ­21810027I20Rik, Q9D8W7, gene:4339043MS/MS++unknownSignalingall 14
Taztafazzin5031411C02Rik, 9130012G04Rik, AW107266, AW552613, G4.5, I7HJS2, gene:668263literature,yeast mito homolog++, mito protein domainIMSMetabolism > Lipid metabolism > Cardiolipin synthesisnone
Dcxrdicarbonyl ­L-xylulose ­reductase0610038K04Rik, 1810027P18Rik, XR, Q91X52, gene:678803APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMetabolism > Carbohydrate metabolismcerebrum, cerebellum, spinalcord, heart, adipose, largeintestine, stomach, placenta, testis
Pmaip1phorbol-12-myristate-13-acetate-induced ­protein ­1N, Noxa, Q9JM54, gene:588013literature, targetP signal, mito protein domain+MOMMitochondrial dynamics and surveillance > Apoptosisnone
Nipsnap3bnipsnap ­homolog ­3B2700063N13Rik, Nipsnap3a, Q9CQE1, gene:665363GFP, targetP signal, MS/MS+Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Mmaamethylmalonic ­aciduria ­(cobalamin ­deficiency) ­type ­A2810018E08Rik, AI840684, Q8C7H1, gene:1091363manual, targetP signal, coexpression+MatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolismcerebrum, cerebellum, brainstem, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Cyp11a1cytochrome ­P450, ­family ­11, ­subfamily ­a, ­polypeptide ­1Cyp1, Cyp11a, Cypxia1, D9Ertd411, D9Ertd411e, P450s, P450scc, Sc, Scc, csc, cscc, Q9QZ82, gene:130703literature, mito protein domain, MS/MS+MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme-containing proteins
adipose, placenta, testis
Aifm2apoptosis-inducing ­factor, ­mitochondrion-associated ­25430437E11Rik, Am, Amid, D730001I10Rik, FSP1, PR, PRG3, Q8BUE4, gene:713613literature, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMembraneMetabolism > Detoxification > ROS and glutathione metabolism;
Mitochondrial dynamics and surveillance > Apoptosis
none
Marchf5membrane ­associated ­ring-CH-type ­finger ­51810015H18Rik, 2310008I22Rik, 2700055A20Rik, 5730499H23Rik, E130202O05Rik, MARC, MARCH-V, MI, MITOL, March5, Marchv, Rnf1, Rnf153, Q3KNM2, gene:691043literature, mito protein domain, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Prdx2peroxiredoxin ­2AL022839, Band-8, NkefB, P, PRP, PrxII, T, TDX1, TP, TPx, TPx-B, TR, TSA, Tdpx, Tdpx1, Torin, Q61171, gene:216723GFP, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, stomach, placenta, testis
Sfxn4sideroflexin ­4Q925N1, gene:942813literature, yeast mito homolog, mito protein domain+MIMSmall molecule transport > Sideroflexinscerebellum, spinalcord
Ifi27interferon, ­alpha-inducible ­protein ­271110013J02Rik, 2900026P10Rik, D12Ertd647, D12Ertd647e, ISG12a, Ifi2, Ifi27l1, Q8C6G0, gene:526683literature, targetP signal, induction, coexpressionMembraneSignaling > Immune response;
Mitochondrial dynamics and surveillance > Apoptosis
none
Abca9ATP-binding ­cassette, ­sub-family ­A ­(ABC1), ­member ­9D630040K07Rik, Q8K449, gene:2172623GFP, targetP signal, Rickettsial homolog, mito protein domainMembraneSmall molecule transport > ABC transporterscerebrum, placenta
Ddx28DEAD ­box ­helicase ­282410004K13Rik, AI449652, Mddx28, Q9CWT6, gene:719863literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
spinalcord, adipose
Acot7acyl-CoA ­thioesterase ­72410041A17Rik, AU01471, Ach1, Act, Bac, Bach, CTE-IIa, Cte-II, Lach1, Q91V12, gene:700252targetP signal, mito protein domain, inductionMatrixMetabolism > Lipid metabolismbrainstem, spinalcord, adipose, largeintestine
Msrb3methionine ­sulfoxide ­reductase ­B3D430026P16Rik, I-8-23, MsrB2, Q8BU85, gene:3201832yeast mito homolog+, mito protein domainunknownMetabolism > Detoxification > ROS and glutathione metabolismnone
2300009A05RikRIKEN ­cDNA ­2300009A05 ­geneQ0VG49, gene:694782APEX_matrix, targetP signal, MS/MSMatrixnonebrainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, testis
Agpat51-acylglycerol-3-phosphate ­O-acyltransferase ­5 ­(lysophosphatidic ­acid ­acyltransferase, ­epsilon)1110013A05Rik, D8Ertd319, D8Ertd319e, Q9D1E8, gene:521232literature, mito protein domain, induction, MS/MSMOMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, placenta, testis
Acod1aconitate ­decarboxylase ­1AI323667, CAD, Ir, Irg1, P54987, gene:163652literature,yeast mito homolog, mito protein domain+MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolism;
Signaling > Immune response
none
Fbxl4F-box ­and ­leucine-rich ­repeat ­protein ­4AI836810, FBL, FBL4, FBL5, Q8BH70, gene:2695142literature, mito protein domain, coexpressionIMSnoneadipose
Ftmtferritin ­mitochondrial4930447C24Rik, FerH, Fth3, MtF, Q9D5H4, gene:676342literature, targetP signal, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Iron homeostasistestis
Gpamglycerol-3-phosphate ­acyltransferase, ­mitochondrialGPA, GPAT, GPAT-1, GPAT1, P90, Q61586, gene:147322literature, mito protein domain, coexpressionMembraneMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Qtrt1queuine ­tRNA-ribosyltransferase ­catalytic ­subunit ­12610028E17Rik, Tgt, Q9JMA2, gene:605072APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Hpdl4-hydroxyphenylpyruvate ­dioxygenase-likeA830048M07Rik, BC034099, Glox, Gloxd1, Q8K248, gene:2426422manual, targetP signal, inductionunknownnonenone
Isoc2aisochorismatase ­domain ­containing ­2aIs, Isoc2, P85094, gene:6649942APEX_matrix, MS/MS++Matrixnoneall 14
Cyp11b1cytochrome ­P450, ­family ­11, ­subfamily ­b, ­polypeptide ­1AA389061, CPN1, Cyp11, Cyp11b, Cyp11b-, Cyp11b-1, FHI, Q3TG86, gene:1101152literature, targetP signal, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesisnone
Cyp11b2cytochrome ­P450, ­family ­11, ­subfamily ­b, ­polypeptide ­2ALDOS, Cpn2, Cyp11, Cyp11b, Cyp11b-, Cyp11b-2, P15539, gene:130722literature, targetP signal, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis;
Metabolism > Metals and cofactors > Heme-containing proteins
none
Pet117PET117 ­homologGm20571, P0DJF2, gene:1000486442literature, yeast mito homolog, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, liver, adipose, largeintestine, stomach, placenta
Dhrs2dehydrogenase/reductase ­member ­25430405K24Rik, Hep27, Q149L0, gene:714122literature,targetP signal, Rickettsial homolog, mito protein domainMatrixMetabolism > Detoxification > Xenobiotic metabolismnone
Cdk5rap1CDK5 ­regulatory ­subunit ­associated ­protein ­12310066P17Rik, Q8BTW8, gene:669712literature,targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Snd1staphylococcal ­nuclease ­and ­tudor ­domain ­containing ­1AL033314, Tudo, Tudor-SN, Q78PY7, gene:564632GFP, yeast mito homolog, mito protein domainunknownnonecerebrum, cerebellum, brainstem, liver, smallintestine, placenta, testis
Cyb5r3cytochrome ­b5 ­reductase ­30610016L08Rik, 2500002N19Rik, B5R, C85115, Di, Dia, Dia-1, Dia1, WU:Cyb5r3, Q9DCN2, gene:1097542literature, mito protein domain, MS/MS+MOMMetabolism > Detoxification > Xenobiotic metabolism;
Metabolism > Detoxification > Amidoxime reducing complex;
Metabolism > Lipid metabolism
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Maoamonoamine ­oxidase ­A1110061B18Rik, AA407771, MA, Q64133, gene:171612literature, mito protein domain, MS/MS+MOMMetabolism > Amino acid metabolism > Catechol metabolism;
Metabolism > Detoxification > Xenobiotic metabolism
all 14
Mffmitochondrial ­fission ­factor5230400G24Rik, AI314724, Q6PCP5, gene:757342literature, induction, MS/MSMOMMitochondrial dynamics and surveillance > Fissioncerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, placenta, testis
Nlrx1NLR ­family ­member ­X1BC034204, NOD9, Q3TL44, gene:2701512APEX_matrix, targetP signal, MS/MSMatrixSignaling > Immune responseall 14
Fam185afamily ­with ­sequence ­similarity ­185, ­member ­A4631428I10, AI847670, Q7TPD2, gene:3300502APEX_matrix, targetP signal, coexpressionMatrixnonenone
Mief1mitochondrial ­elongation ­factor ­1A230016E22, AI452372, Smc, Smcr7l, Q8BGV8, gene:2395552literature, mito protein domain, induction, coexpressionMOM , MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly;
Mitochondrial dynamics and surveillance > Fission
none
Coa7cytochrome ­c ­oxidase ­assembly ­factor ­72010305A19Rik, AI451324, D4Ertd796, D4Ertd796e, Sel, Selrc1, Q921H9, gene:698932literature, APEX_IMS, mito protein domain, coexpression, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Acot11acyl-CoA ­thioesterase ­111110020M10Rik, 2010309H15Rik, AW060409, BFIT, BFIT1, The, Thea, Them1, mKIAA0707, Q8VHQ9, gene:3299102literature,targetP signal, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Fatty acid oxidationnone
Pusl1pseudouridylate ­synthase-like ­12810021I11Rik, AI853843, D18346, A2ADA5, gene:4338131APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translationcerebrum, spinalcord, largeintestine, placenta
Polqpolymerase ­(DNA ­directed), ­thetaA430110D14Rik, Q8CGS6, gene:777821literature,targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenancebrainstem, testis
Dmac2ldistal ­membrane ­arm ­assembly ­complex ­2 ­like1110015E18Rik, ATPW, At, Atp5s, Q9CRA7, gene:680551literature, APEX_matrix, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Rmdn3regulator ­of ­microtubule ­dynamics ­31200015F23Rik, AI131757, Fam82, Fam82a2, Ptpip51, RMD-3, Rmd3, Q3UJU9, gene:678091literature, APEX_IMS, GFP, MS/MS++MOMMitochondrial dynamics and surveillance > Organelle contact sitescerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
Atp5mdATP ­synthase ­membrane ­subunit ­DAPIT2010301L15Rik, Usmg, Usmg5, Q78IK2, gene:664771GFP, MS/MS++MIMOXPHOS > Complex V > CV subunits;
OXPHOS > OXPHOS subunits;
Mitochondrial dynamics and surveillance > Cristae formation
all 14
Tomm20translocase ­of ­outer ­mitochondrial ­membrane ­201810060K07Rik, BB284719, Gm19268, MAS20, MOM19, TOM2, TOM20, mKIAA0016, Q9DCC8, gene:679521literature, yeast mito homolog+MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM;
Mitochondrial dynamics and surveillance
cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Bnip3lBCL2/adenovirus ­E1B ­interacting ­protein ­3-likeC86132, D14Ertd719, D14Ertd719e, N, Nip3L, Nix, Q9Z2F7, gene:121771literature, mito protein domain+, coexpressionMOMMitochondrial dynamics and surveillance > Apoptosisnone
Aifm3apoptosis-inducing ­factor, ­mitochondrion-associated ­32810401C16Rik, AI840249, Aifl, Q3TY86, gene:721681literature, Rickettsial homolog, mito protein domain+MIMMetabolism > Metals and cofactors > Fe-S-containing proteins;
Mitochondrial dynamics and surveillance > Apoptosis
none
Timm29translocase ­of ­inner ­mitochondrial ­membrane ­291810026J23Rik, TIM29, Q8BGX2, gene:697731coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathwaycerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, largeintestine, placenta, testis
Ppm1kprotein ­phosphatase ­1K ­(PP2C ­domain ­containing)2900063A19Rik, A930026L03Rik, PP2, PP2C-kappa, PP2Cm, Q8BXN7, gene:2433821literature, targetP signal, mito protein domainMatrixMetabolism > Amino acid metabolism > BCAA metabolism;
Metabolism > Amino acid metabolism > BCAA dehydrogenase complex
cerebellum, liver, heart, adipose
Sirt4sirtuin ­44930596O17Rik, Q8R216, gene:753871literature, targetP signal, mito protein domainMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismlargeintestine
Park7Parkinson ­disease ­(autosomal ­recessive, ­early ­onset) ­7DJ-1, Dj1, Q99LX0, gene:573201literature, mito protein domain, coexpressionMOMProtein import, sorting and homeostasis > Protein homeostasis;
Mitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
all 14
Mterf1amitochondrial ­transcription ­termination ­factor ­1a4931431L11Rik, 9230106K09Rik, Mter, Mterf, Mterf1, mTERF1b, Q8CHZ9, gene:5457251literature, APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid;
Mitochondrial central dogma > mtRNA metabolism > Transcription;
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
none
mt-Nd4lNADH ­dehydrogenase ­subunit ­4LP03903, gene:177201literature, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
heart, skeletalmuscle
AA467197expressed ­sequence ­AA467197NME, Nmes1, mir-147, Q810Q5, gene:4334701GFP, mito protein domain, MS/MS+Membranenonesmallintestine, largeintestine, stomach, placenta, testis
Uqcc2ubiquinol-cytochrome ­c ­reductase ­complex ­assembly ­factor ­22900010M23Rik, Cbp, Cbp6, M19, Mnf, Mnf1, Q9CQY6, gene:672671APEX_matrix, GFP, coexpression, MS/MSMIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors
all 14
Nme3NME/NM23 ­nucleoside ­diphosphate ­kinase ­31810009F08Rik, AI413736, DR-nm, DR-nm23, Ndk, Ndk3, Nm23-DR, Nm23-M, Nm23-M3, Q9WV85, gene:790591GFP, yeast mito homolog, Rickettsial homolog, mito protein domainMOMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingcerebrum, cerebellum, brainstem, kidney, adipose, placenta, testis
Gtpbp6GTP ­binding ­protein ­6 ­(putative)AV119224, Pg, Pgbpll, p, pgpl, Q3U6U5, gene:1079991APEX_matrix, targetP signal+, mito protein domainMatrixnonenone
Them5thioesterase ­superfamily ­member ­51110007B02Rik, 1110038F21Rik, Q9CQJ0, gene:661981literature,targetP signal+, mito protein domainMatrixMetabolism > Lipid metabolismnone
Prkacaprotein ­kinase, ­cAMP ­dependent, ­catalytic, ­alphaC, P, PKCD, Pk, Pkaca, P05132, gene:187471literature,mito protein domain, coexpressionMIMSignaling > cAMP-PKA signalingcerebrum, brainstem, spinalcord, adipose, testis
Miga2mitoguardin ­25730472N09Rik, AA408683, AI790341, C9orf54, Fam73, Fam73b, R7476, R74766, Q8BK03, gene:1089580literature,coexpressionMOMMitochondrial dynamics and surveillance > Fusion;
Mitochondrial dynamics and surveillance > Organelle contact sites
cerebrum, cerebellum, brainstem, spinalcord, liver, testis
Mgarpmitochondria ­localized ­glutamic ­acid ­rich ­protein4930583H14Rik, AI195347, CESP-1, HUMMR, Osap, Qsap, Q8VI64, gene:677490literature, APEX_IMS, targetP signal, yeast mito homolog, coexpressionMembraneMitochondrial dynamics and surveillance > Traffickingnone
Mcl1myeloid ­cell ­leukemia ­sequence ­1AW556805, Mcl-, Mcl-1, P97287, gene:172100manual, targetP signal, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisadipose, largeintestine, placenta, testis
Myg1melanocyte ­proliferating ­gene ­10610023A07Rik, 2810433J21Rik, 5830429P19Rik, AI325965, Gamm, Gamm1, Q9JK81, gene:603150literature, targetP signal, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications;
Mitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications
none
Etfbkmtelectron ­transfer ­flavoprotein ­beta ­subunit ­lysine ­methyltransferase4833442J19Rik, AI256744, ETFB-KMT, Mettl2, Mettl20, Q80ZM3, gene:3202040literature,mito protein domain+MatrixMetabolism > Electron carriers > Q-linked reactions, othernone
MutyhmutY ­DNA ­glycosylase5730495A01Rik, Mutyha, Mutyhalpha, Mutyhb, Mutyhbet, Mutyhbeta, Mutyhc, Myh, Q99P21, gene:706030GFP, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenancenone
Fastkd5FAST ­kinase ­domains ­5C78212, mKIAA1792, Q7TMV3, gene:3806010APEX_matrix, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
skeletalmuscle, largeintestine, placenta
Paicsphosphoribosylaminoimidazole ­carboxylase, ­phosphoribosylaminoribosylaminoimidazole, ­succinocarboxamide ­synthetase2610511I09Rik, A, ADE2H, ADE2H1, AIRC, PAIS, Q9DCL9, gene:670540APEX_matrix, Rickettsial homolog, coexpressionMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingnone
Cpt1ccarnitine ­palmitoyltransferase ­1c6530437J22Rik, 9630004I06Rik, CPT I-C, CPT IC, CPT1-B, CPTI-B, Q8BGD5, gene:780700literature, yeast mito homolog+, mito protein domainMOMMetabolism > Lipid metabolism > Fatty acid oxidation;
Metabolism > Metals and cofactors > Carnitine synthesis and transport;
Metabolism > Metals and cofactors > Carnitine shuttle
none
Rcc1lreculator ­of ­chromosome ­condensation ­1 ­like5730496C04Rik, AU019812, Wbscr, Wbscr16, Q9CYF5, gene:942540literature, APEX_matrix, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modificationsplacenta
Antkmtadenine ­nucleotide ­translocase ­lysine ­methyltransferaseANT-KMT, Fam17, Fam173a, Q501J2, gene:2149170literature,coexpression, MS/MSMIMMetabolism > Nucleotide metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, placenta
Uqcc3ubiquinol-cytochrome ­c ­reductase ­complex ­assembly ­factor ­3AI4624, AI462493, Cbp, Cbp4, Q8K2T4, gene:1071970literature,coexpression, MS/MSMIMOXPHOS > Complex III > CIII assembly factors;
OXPHOS > OXPHOS assembly factors
liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
Prdx4peroxiredoxin ­4AOE3, AOE372, Pr, Prx-iv, Prx4, TRANK, O08807, gene:533810APEX_IMS, Rickettsial homolog, mito protein domainIMSMetabolism > Detoxification > ROS and glutathione metabolismcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pycr1pyrroline-5-carboxylate ­reductase ­1P5CR 1, P5CR1, Q922W5, gene:2090270literature, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Proline metabolismcerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
Cryzcrystallin, ­zetaSEZ, Sez9, P47199, gene:129720APEX_matrix, mito protein domain, MS/MSMatrixnonespinalcord, kidney, liver, adipose, placenta, testis
Angel2angel ­homolog ­22610307I21Rik, 5730410O10Rik, AI845692, D1Ertd396, D1Ertd396e, D1Ertd654, D1Ertd654e, Q8K1C0, gene:52477-0APEX_matrix, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mt-mRNA modificationsadipose, smallintestine, placenta, testis
Mgme1mitochondrial ­genome ­maintenance ­exonuclease ­18430406I07Rik, AI426476, Q9CXC3, gene:74528-0literature, APEX_matrix, GFP, targetP signalMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay
largeintestine, placenta
Agpat41-acylglycerol-3-phosphate ­O-acyltransferase ­4 ­(lysophosphatidic ­acid ­acyltransferase, ­delta)1500003P24Rik, Q8K4X7, gene:68262-0literature,mito protein domain, inductionMOMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
testis
Comtd1catechol-O-methyltransferase ­domain ­containing ­11810030M08Rik, MT773, Q8BIG7, gene:69156-0GFP, MS/MS++Membranenoneall 14
Neu4sialidase ­49330166I04, Q8BZL1, gene:241159-0GFP, targetP signal+MOMMetabolism > Carbohydrate metabolismnone
Cyp27b1cytochrome ­P450, ­family ­27, ­subfamily ­b, ­polypeptide ­1Cp2, Cp2b, Cyp, Cyp1, Cyp27, Cyp27b, Cyp4, Cyp40, P450c, P450c1, Pd, Pddr, Vd, Vdd, Vdd1, Vddr, VddrI, Vdr, O35084, gene:13115-0literature, targetP signal, mito protein domainMIMMetabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Vitamin metabolism > Vitamin D metabolism
none
NoctnocturninAU043840, Ccr, Ccr4, Ccrn4l, O35710, gene:12457-0literature,targetP signal, mito protein domainMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolismnone
Hdhd3haloacid ­dehalogenase-like ­hydrolase ­domain ­containing ­32810435D12Rik, Q9CYW4, gene:72748-0APEX_matrix, MS/MS++Matrixnonecerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
Slc8b1solute ­carrier ­family ­8 ­(sodium/lithium/calcium ­exchanger), ­member ­B1AF261233, NC, NCKX, NCKX6, NCLX, Slc2, Slc24a6, Q925Q3, gene:170756-0literature,mito protein domain, inductionMIMSignaling > Calcium homeostasis > Calcium cycle;
Small molecule transport
placenta
mt-Nd6NADH ­dehydrogenase ­subunit ­6P03925, gene:17722-1literature, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex I > CI subunits;
OXPHOS > OXPHOS subunits
none
Dmac1distal ­membrane ­arm ­assembly ­complex ­11700027K24Rik, 3110001D03Rik, Tmem261, Q9CQ00, gene:66928-1literature,MS/MSMIMOXPHOS > Complex I > CI assembly factors;
OXPHOS > OXPHOS assembly factors
cerebrum, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Bco2beta-carotene ­oxygenase ­2B-dio, B-diox-II, Bcdo, Bcdo2, Bcmo, Bcmo2, CMO, CMO2, Q99NF1, gene:170752-1literature,mito protein domain, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin A metabolismsmallintestine
Tdrkhtudor ­and ­KH ­domain ­containing ­protein2700091C21Rik, Tdrd, Tdrd2, Q80VL1, gene:72634-1GFP, mito protein domain, MS/MSMembranenonecerebrum, cerebellum, brainstem, spinalcord, adipose, testis
Gpx4glutathione ­peroxidase ­4GPx-4, GSHPx-4, PHG, PHGPx, mtPHG, mtPHGPx, sn, snGPx, Q91XR9, gene:625249-1literature, yeast mito homolog, mito protein domainMIMMetabolism > Detoxification > ROS and glutathione metabolism;
Metabolism > Detoxification > Selenoproteins
all 14
Comtcatechol-O-methyltransferaseComt1, D16Wsu103, D16Wsu103e, D330014B15Rik, O88587, gene:12846-1GFP, induction, coexpressionMembraneMetabolism > Amino acid metabolism > Catechol metabolismliver
Mtfr2mitochondrial ­fission ­regulator ­22610016C23Rik, 4933412C16Rik, Dufd1, Fam5, Fam54a, Q8VED8, gene:71804-1manual, mito protein domain+MembraneMitochondrial dynamics and surveillance > Fissionnone
BikBCL2-interacting ­killerBiklk, Bl, Blk, Nb, Nbk, O70337, gene:12124-1manual, mito protein domain+MOMMitochondrial dynamics and surveillance > Apoptosisnone
Lig3ligase ­III, ­DNA, ­ATP-dependentD11Wsu78, D11Wsu78e, Q80ZH7, gene:16882-1literature,yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA repair
none
Cry1cryptochrome ­1 ­(photolyase-like)AU020726, AU021000, Ph, Phll1, P97784, gene:12952-1literature, yeast mito homolog, mito protein domain, coexpressionunknownnonenone
Trub2TruB ­pseudouridine ­(psi) ­synthase ­family ­member ­2G430055L02Rik, Q91WG3, gene:227682-1APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
none
Tomm20ltranslocase ­of ­outer ­mitochondrial ­membrane ­20-like4930553D19Rik, Q9D4V6, gene:75266-1manual, yeast mito homolog+MOMProtein import, sorting and homeostasis > Protein import and sortingnone
Ccdc127coiled-coil ­domain ­containing ­1270610011N22Rik, 5430420E17Rik, A430066A18, AI256405, AW050060, C130002N06, Q3TC33, gene:67433-1APEX_IMS, MS/MSMembranenonecerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
YrdcyrdC ­domain ­containing ­(E.coli)AV303379, BC023823, IRIP, ITIP, Q3U5F4, gene:230734-1manual, targetP signal, Rickettsial homologMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Preplprolyl ­endopeptidase-like2810457N15Rik, 9530014L06Rik, D030028O16Rik, mKIAA0436, Q8C167, gene:213760-1APEX_matrix, targetP signal, Rickettsial homologMatrixnonespinalcord, largeintestine
Myo19myosin ­XIX1110055A02Rik, Myohd, Myohd1, Q5SV80, gene:66196-2literature,yeast mito homolog, mito protein domainMOMMitochondrial dynamics and surveillance > Traffickingadipose
Thg1ltRNA-histidine ­guanylyltransferase ­1-like ­(S. ­cerevisiae)Q9CY52, gene:66628-2literature, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Pif1PIF1 ­5'-to-3' ­DNA ­helicase4631410M14, AI4494, AI449441, Q80SX8, gene:208084-2literature, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenancenone
Rab5ifRAB5 ­interacting ­factor1110008F13Rik, AI316789, RCAF1, RIP5, Q9CQT9, gene:67388-2GFP, induction, coexpressionMIMOXPHOS > OXPHOS assembly factors;
OXPHOS > Respirasome assembly
none
Cep89centrosomal ­protein ­892610507L03Rik, Ccdc123, Q9CZX2, gene:72140-2literature, targetP signalIMSOXPHOS > Complex IV > CIV assembly factors;
OXPHOS > OXPHOS assembly factors
none
Acot10acyl-CoA ­thioesterase ­10Acat, Acate3, MT-ACT4, MT-ACT48, p4, p48, Q32MW3, gene:64833-2literature, targetP signalMatrixMetabolism > Lipid metabolismnone
Efhd1EF ­hand ­domain ­containing ­14931430I01Rik, AI452351, PP30, PP3051, mito, mitocalcin, Q9D4J1, gene:98363-2literature, mito protein domain, inductionMIMSignaling > Calcium homeostasis > EF hand proteinsnone
BidBH3 ­interacting ­domain ­death ­agonist2700049M22Rik, AI875481, AU022477, P70444, gene:12122-2literature, mito protein domain, coexpressionMOMMitochondrial dynamics and surveillance > Apoptosisnone
AtpsckmtATP ­synthase ­C ­subunit ­lysine ­N-methyltransferaseA930016P21Rik, AA987072, Fam173, Fam173b, mFam173b, Q9D1Z3, gene:68073-2literature,coexpressionMIMOXPHOS > Complex V > CV assembly factors;
OXPHOS > OXPHOS assembly factors
placenta
Cyp24a1cytochrome ­P450, ­family ­24, ­subfamily ­a, ­polypeptide ­124-OH, 24-OHase, CP2, CP24, Cyp2, Cyp24, Q64441, gene:13081-2literature, targetP signal, mito protein domainMIMMetabolism > Metals and cofactors > Heme-containing proteins;
Metabolism > Vitamin metabolism > Vitamin D metabolism
none
Sptlc2serine ­palmitoyltransferase, ­long ­chain ­base ­subunit ­2LCB, LCB2, LCB2a, Sp, Spt2, P97363, gene:20773-2GFP, Rickettsial homolog, mito protein domainMembraneMetabolism > Lipid metabolism > Phospholipid metabolismnone
Apex1apurinic/apyrimidinic ­endonuclease ­1APE, Apex, HA, HAP1, Ref-, Ref-1, P28352, gene:11792-2literature,Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
E130311K13RikRIKEN ­cDNA ­E130311K13 ­geneQ8BN57, gene:329659-2APEX_matrix, MS/MSMatrixnoneadipose, testis
Agkacylglycerol ­kinase2610037M15Rik, 6720408I04Rik, AI465370, MuL, Mulk, Q9ESW4, gene:69923-3literature, APEX_IMS, mito protein domainMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathway;
Metabolism > Lipid metabolism > Phospholipid metabolism
cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
Dus2dihydrouridine ­synthase ­22310016K04Rik, Dus, Dus2l, Q9D7B1, gene:66369-3GFP, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Pank2pantothenate ­kinase ­24933409I19Rik, AI642621, Q3U4S0, gene:74450-3literature, targetP signal, mito protein domainIMSMetabolism > Metals and cofactors > Coenzyme A metabolismnone
Polg2polymerase ­(DNA ­directed), ­gamma ­2, ­accessory ­subunitmtPolB, p55, polG-beta, Q9QZM2, gene:50776-3literature, APEX_matrix, targetP signal, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid
none
Gpat2glycerol-3-phosphate ­acyltransferase ­2, ­mitochondrialA530057A03Rik, Gm116, Gpa, xGPAT1, Q14DK4, gene:215456-3manual, mito protein domainMOMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Metabolism > Lipid metabolism > Phospholipid metabolism
testis
Tomm34translocase ­of ­outer ­mitochondrial ­membrane ­342610100K07Rik, TOM3, TOM34, Q9CYG7, gene:67145-3literature, mito protein domainMOMProtein import, sorting and homeostasis > Protein import and sorting > TOMtestis
Plscr3phospholipid ­scramblase ­32210403O21Rik, 2610037N06Rik, ESTM3, X83310, Q9JIZ9, gene:70310-3literature,yeast mito homolog, mito protein domainMIMMetabolism > Lipid metabolism > Cardiolipin synthesisnone
Fkbp10FK506 ­binding ­protein ­1065kD, AI325255, FKBP-10, FKBP-65, FKBP65, Fkbp, Fkbp-, Fkbp-rs1, Fkbp1, Fkbp1-rs, Fkbp6, Fkbprp, Q61576, gene:14230-3APEX_IMS, mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Chaperonesnone
Exd2exonuclease ­3'-5' ­domain ­containing ­24930539P14Rik, C85658, Exdl, Exdl2, Q8VEG4, gene:97827-3literature,mito protein domainMatrixMitochondrial central dogma > Translationcerebrum, cerebellum, testis
Bcl2l1BCL2-like ­1Bcl, Bcl(X, Bcl(X)L, Bcl-XL, Bcl2l, BclX, bcl-, bcl-x, bcl2-L-1, Q64373, gene:12048-3literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosiscerebrum, cerebellum, placenta
Golph3golgi ­phosphoprotein ­34733401N08Rik, 5730410D03Rik, AW413496, Q9CRA5, gene:66629-4literature, targetP signal, inductionIMSnonenone
Nt5dc25'-nucleotidase ­domain ­containing ­22510015F01Rik, Q91X76, gene:70021-4APEX_matrix, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processingspinalcord, largeintestine, placenta
Armc10armadillo ­repeat ­containing ­102810037C14Rik, Svh, Q9D0L7, gene:67211-4GFP, MS/MSMOMMitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Trafficking
cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
Alkbh1alkB ­homolog ­1, ­histone ­H2A ­dioxygenase2700073G19Rik, Abh, Alk, Alkbh, al, alkB, hABH, P0CB42, gene:211064-4literature, APEX_matrix, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
none
Akap10A ­kinase ­(PRKA) ­anchor ­protein ­101500031L16Rik, B130049N18Rik, D-AK, D-AKAP-2, D-AKAP2, PRKA10, O88845, gene:56697-4literature, mito protein domainMOMSignaling > cAMP-PKA signalingnone
Serac1serine ­active ­site ­containing ­14930511N22Rik, D17Ertd141, D17Ertd141e, Q3U213, gene:321007-4literature, APEX_IMS, targetP signalMOMMetabolism > Lipid metabolism > Phospholipid metabolismcerebrum, cerebellum, skeletalmuscle, stomach, testis
Septin4septin ­4A, ARTS, Bh5, Pnu, Pnutl2, Sep, Sept4, P28661, gene:18952-4literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisbrainstem, spinalcord
Fastkd3FAST ­kinase ­domains ­32310010B21Rik, AW048587, Q8BSN9, gene:69577-5APEX_matrix, targetP signalMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing;
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
none
Bcl2l11BCL2-like ­11 ­(apoptosis ­facilitator)1500006F24Rik, Bi, Bim, Bo, Bod, bcl2-L-11, O54918, gene:12125-5manual, targetP signalMOMMitochondrial dynamics and surveillance > Apoptosisnone
Nbr1NBR1, ­autophagy ­cargo ­receptormKIAA0049, P97432, gene:17966-5APEX_IMS, coexpressionIMSMitochondrial dynamics and surveillance > Autophagycerebellum, liver
Rpiaribose ­5-phosphate ­isomerase ­ARPI, P47968, gene:19895-5APEX_matrix, targetP signalMatrixMetabolism > Carbohydrate metabolismplacenta
BokBCL2-related ­ovarian ­killermat, matador, mtd, O35425, gene:51800-5manual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Miga1mitoguardin ­1A930038D06, AI852168, C030011O14Rik, Fam7, Fam73a, Mit, Mita1, Q4QQM5, gene:215708-5literatureMOMMitochondrial dynamics and surveillance > Fusioncerebrum, cerebellum, brainstem, spinalcord, smallintestine, testis
Prorpprotein ­only ­RNase ­P ­catalytic ­subunit1110008L16Rik, Mr, Mrpp3, mKIAA0391, Q8JZY4, gene:66132-5APEX_matrixMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules;
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing
spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Stx17syntaxin ­174833418L03Rik, 6330411F21Rik, 9030425C21Rik, AW048351, Q9D0I4, gene:67727-6APEX_IMS, coexpressionMOMMitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Organelle contact sites;
Mitochondrial dynamics and surveillance > Autophagy
testis
Primpolprimase ­and ­polymerase ­(DNA-directed)BC065112, Ccdc111, Q6P1E7, gene:408022-6literature,mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Dna2DNA ­replication ­helicase/nuclease ­2Dn, Dna2l, E130315B21Rik, Q6ZQJ5, gene:327762-6literature, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication;
Metabolism > Metals and cofactors > Fe-S-containing proteins
none
Adcy10adenylate ­cyclase ­104930431D04Rik, 4931412F17, Sa, Sacy, s, sAC, Q8C0T9, gene:271639-6literature,mito protein domainMembraneSignaling > cAMP-PKA signalingnone
Prss35protease, ­serine ­356030424L22Rik, P3D9, Q8C0F9, gene:244954-6GFP, mito protein domainunknownProtein import, sorting and homeostasis > Protein homeostasisnone
Mief2mitochondrial ­elongation ­factor ­2AI482195, Gm11, Smc, Smcr7, Q5NCS9, gene:237781-6literature,mito protein domainMOMMitochondrial dynamics and surveillance > Fissionnone
Nsun3NOL1/NOP2/Sun ­domain ­family ­member ­36720484A09Rik, AU022521, Q8CCT7, gene:106338-6APEX_matrix, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Pabpc5poly(A) ­binding ­protein, ­cytoplasmic ­5C820015E17, Q8C7D3, gene:93728-6literature, mito protein domainMatrixnonenone
Styxl1serine/threonine/tyrosine ­interacting-like ­11700011C14Rik, Dusp, Dusp24, Mkstyx, Q9DAR2, gene:76571-6literature,mito protein domainMatrixMitochondrial dynamics and surveillance > Apoptosisnone
Sphk2sphingosine ­kinase ­2C76851, Sk2, Spk2, Q9JIA7, gene:56632-6literature,mito protein domainMIMMetabolism > Lipid metabolism > Phospholipid metabolism;
Mitochondrial dynamics and surveillance > Apoptosis
none
Prknparkin ­RBR ­E3 ­ubiquitin ­protein ­ligaseP, Pa, Park2, Q9WVS6, gene:50873-6manual, mito protein domainMOMMitochondrial dynamics and surveillance > Mitophagy;
Mitochondrial dynamics and surveillance > Autophagy
none
Nsun2NOL1/NOP2/Sun ­domain ­family ­member ­2D13Wsu123e, Mi, Misu, Q1HFZ0, gene:28114-6literature,mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modificationsnone
Pick1protein ­interacting ­with ­C ­kinase ­1Prk, Prkcabp, Q8C1W2, gene:18693-6literature, mito protein domainunknownnonenone
Dmpkdystrophia ­myotonica-protein ­kinaseDM, DMK, Dm15, MDPK, MT-PK, P54265, gene:13400-6literature, mito protein domainMOMnonenone
Casp9caspase ­9AI115399, APAF-3, AW493809, CASP-9, Casp, Caspase-9, ICE-, ICE-LAP6, Mch6, Q8C3Q9, gene:12371-6literature,mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Apoptosis
none
Casp8caspase ­8CASP-8, Casp, FLI, FLICE, MAC, MACH, Mch5, O89110, gene:12370-6literature, mito protein domainMOMProtein import, sorting and homeostasis > Protein homeostasis;
Mitochondrial dynamics and surveillance > Apoptosis
none
Casp3caspase ­3A830040C14Rik, AC-, AC-3, CASP-3, CC3, CPP, CPP-32, CPP32, Casp, Caspase-3, Lice, SCA-1, Ya, Yama, mld, mldy, P70677, gene:12367-6literature,mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases;
Mitochondrial dynamics and surveillance > Apoptosis
none
Bcl2l2BCL2-like ­2AW048834, Bcl-, Bcl-w, Gtrg, Gtrgal2, Gtro, Gtrosa41, bcl, bclw, c98, P70345, gene:12050-6literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Bcl2l10Bcl2-like ­10AA420380, AU023065, B, Boo, C85687, D, Diva, Q9Z0F3, gene:12049-6manual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Bcl2a1dB ­cell ­leukemia/lymphoma ­2 ­related ­protein ­A1dA1-, A1-d, O55179, gene:12047-6manual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Bcl2B ­cell ­leukemia/lymphoma ­2AW986256, Bcl-, Bcl-2, C430015F12Rik, D630044D05Rik, D830018M01Rik, P10417, gene:12043-6literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
BadBCL2-associated ­agonist ­of ­cell ­deathAI325008, Bbc2, Q61337, gene:12015-6literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosisnone
Pde2aphosphodiesterase ­2A, ­cGMP-stimulatedCGS-PDE, cGSPDE, Q3TYK5, gene:207728-6literature,targetP signalMIMSignaling > cAMP-PKA signalingcerebrum, cerebellum, brainstem, largeintestine
Spata20spermatogenesis ­associated ­20Tis, Tisp78, Q80YT5, gene:217116-6APEX_matrixMatrixnonetestis
Plgrktplasminogen ­receptor, ­C-terminal ­lysine ­transmembrane ­protein1110007H22Rik, 5033414D02Rik, AI852040, Plg-, Plg-R(KT), Plg-RKT, Q9D3P8, gene:67759-7GFPMembranenonecerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
Pld6phospholipase ­D ­family, ­member ­64933433K01Rik, Gm10, Zuc, mZuc, mit, mitoPLD, Q5SWZ9, gene:194908-8literatureMOMMetabolism > Lipid metabolism > Cardiolipin synthesis;
Mitochondrial dynamics and surveillance > Fusion
none
Bbc3BCL2 ­binding ­component ­3PU, PUMA, PUMA/JFY1, Q99ML1, gene:170770-8manualMOMMitochondrial dynamics and surveillance > Apoptosisnone
CstadCSA-conditional, ­T ­cell ­activation-dependent ­protein9530039B02Rik, Q9D245, gene:78617-8literatureMOMSignaling > Immune responsenone
1700066M21RikRIKEN ­cDNA ­1700066M21 ­geneAI428479, Q9D9H8, gene:73467-8APEX_matrixMatrixnonenone
Spire1spire ­type ­actin ­nucleation ­factor ­16030430B19Rik, AI415299, AU022898, AW550622, Sp, Spir-1, D3YTL8, gene:68166-8literatureMOMMitochondrial dynamics and surveillance > Fission;
Mitochondrial dynamics and surveillance > Organelle contact sites
none
Armcx1armadillo ­repeat ­containing, ­X-linked ­13010033I09Rik, ALEX1, Q9CX83, gene:78248-10literatureMOMMitochondrial dynamics and surveillance > Traffickingnone
Armcx2armadillo ­repeat ­containing, ­X-linked ­23230401N03Rik, AI043003, ALEX2, Q6A058, gene:67416-10literatureMembranenonenone
Armcx6armadillo ­repeat ­containing, ­X-linked ­6AW060994, Q8K3A6, gene:278097-11literatureMembranenonenone
Nat8lN-acetyltransferase ­8-like1110038O08Rik, Sh, Shati, Q3UGX3, gene:269642-11literatureMembraneMetabolism > Amino acid metabolism > Glutamate metabolismnone
SphkapSPHK1 ­interactor, ­AKAP ­domain ­containing4930544G21Rik, A930009L15Rik, AI852220, S, SKIP, mKIAA1678, Q6NSW3, gene:77629-11manualMIMSignaling > cAMP-PKA signalingnone
Mettl4methyltransferase ­like ­42410198H06Rik, A730091E08Rik, AV296509, HsT66, HsT661, Q3U034, gene:76781-11literatureMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA modificationsnone
Armcx3armadillo ­repeat ­containing, ­X-linked ­31200004E24Rik, AI450003, ALEX3, Q8BHS6, gene:71703-11literatureMOMMitochondrial dynamics and surveillance > Traffickingnone
Snap29synaptosomal-associated ­protein ­291300018G05Rik, AI891940, AU020222, BB131856, Gs32, Q9ERB0, gene:67474-11APEX_IMSIMSMitochondrial dynamics and surveillance > Autophagynone
Polbpolymerase ­(DNA ­directed), ­betaA430088C08Rik, Q8K409, gene:18970-11literatureMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repairnone
Htd2hydroxyacyl-thioester ­dehydratase ­type ­2, gene:109729085literatureMatrixMetabolism > Lipid metabolism > Type II fatty acid synthesisnone
Pigbos1Pigb ­opposite ­strand ­12310009A05Rik, 5031420N21Rik, A0A5F8MPY0, gene:66364literatureMOMMitochondrial dynamics and surveillance > Organelle contact sitesnone