Human MitoCarta2.0: 1158 mitochondrial genes

The MitoCarta2.0 human inventory is a collection of 1158 nuclear and mtDNA genes encoding proteins with strong support of mitochondrial localization. The table below provides a summary of evidence supporting mitochondrial localization as well as the protein distribution across 14 tissues. The genes are ordered by strength of mitochondrial evidence. More complete information is available for download in file Human.MitoCarta2.0.xls. See also MitoCarta2.0 home for a description of the project and MitoCarta2.0 documentation for information on the columns below.

GeneIDSymbolDescriptionSynonymsMaestro scoreFDREvidenceTissues
1537CYC1cytochrome c-1MC3DN6, UQCR4, P08574430%"literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
6390SDHB"succinate dehydrogenase complex, subunit B, iron sulfur (Ip)"CWS2, IP, PGL4, SDH, SDH1, SDH2, SDHIP, P21912430%"literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
10229COQ7"coenzyme Q7 homolog, ubiquinone (yeast)"CAT5, CLK-1, CLK1, Q99807430%"literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS++"all 14
6389SDHA"succinate dehydrogenase complex, subunit A, flavoprotein (Fp)"CMD1GG, FP, PGL5, SDH1, SDH2, SDHF, P31040420%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
7384UQCRC1ubiquinol-cytochrome c reductase core protein ID3S3191, QCR1, UQCR1, P31930420%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
84274COQ5"coenzyme Q5 homolog, methyltransferase (S. cerevisiae)"Q5HYK3420%"APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
5160PDHA1pyruvate dehydrogenase (lipoamide) alpha 1PDHA, PDHCE1A, PHE1A, P08559420%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
57017COQ9coenzyme Q9C16orf49, COQ10D5, O75208420%"APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++"all 14
6182MRPL12mitochondrial ribosomal protein L125c5-2, L12mt, MRP-L31/34, MRPL7, MRPL7/L12, RPML12, P52815420%"literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
513ATP5D"ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunit"P30049420%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+"all 14
9377COX5Acytochrome c oxidase subunit VaCOX, COX-VA, VA, P20674410%"literature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
122961ISCA2iron-sulfur cluster assembly 2HBLD1, ISA2, c14_5557, Q86U28410%"APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++"all 14
9512PMPCBpeptidase (mitochondrial processing) betaBeta-MPP, MPP11, MPPB, MPPP52, P-52, O75439410%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
7386UQCRFS1"ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1"RIP1, RIS1, RISP, UQCR5, P47985400%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS++"all 14
498ATP5A1"ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1, cardiac muscle"ATP5A, ATP5AL2, ATPM, HEL-S-123m, MC5DN4, MOM2, OMR, ORM, hATP1, P25705400%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
7385UQCRC2ubiquinol-cytochrome c reductase core protein IIMC3DN5, QCR2, UQCR2, P22695400%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
5162PDHBpyruvate dehydrogenase (lipoamide) betaPDHBD, PDHE1-B, PHE1B, P11177400%"literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
4967OGDHoxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)AKGDH, E1k, OGDC, Q02218400%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
6392SDHD"succinate dehydrogenase complex, subunit D, integral membrane protein"CBT1, CII-4, CWS3, PGL, PGL1, QPs3, SDH4, cybS, O14521400%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+"all 14
60488MRPS35mitochondrial ribosomal protein S35MDS023, MRP-S28, MRPS28, P82673390%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
27089UQCRQ"ubiquinol-cytochrome c reductase, complex III subunit VII, 9.5kDa"MC3DN4, QCR8, QP-C, QPC, UQCR7, O14949390%"literature, APEX_IMS, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
116540MRPL53mitochondrial ribosomal protein L53L53MT, Q96EL3390%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
1629DBTdihydrolipoamide branched chain transacylase E2BCATE2, BCKAD-E2, BCKADE2, E2, E2B, P11182390%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS++"all 14
5166PDK4"pyruvate dehydrogenase kinase, isozyme 4"Q16654380%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, testis
4191MDH2"malate dehydrogenase 2, NAD (mitochondrial)"M-MDH, MDH, MGC:3559, MOR1, P40926380%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
23107MRPS27mitochondrial ribosomal protein S27MRP-S27, S27mt, Q92552380%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
1431CScitrate synthaseO75390370%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
80273GRPEL1"GrpE-like 1, mitochondrial (E. coli)"HMGE, Q9HAV7370%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
1737DLATdihydrolipoamide S-acetyltransferaseDLTA, PDC-E2, PDCE2, P10515370%"literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
10128LRPPRCleucine-rich pentatricopeptide repeat containingCLONE-23970, GP130, LRP130, LSFC, P42704370%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++"all 14
8050PDHX"pyruvate dehydrogenase complex, component X"DLDBP, E3BP, OPDX, PDX1, proX, O00330370%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+"all 14
1743DLSTdihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)DLTS, P36957370%"literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+"all 14
85476GFM1"G elongation factor, mitochondrial 1"COXPD1, EFG, EFG1, EFGM, EGF1, GFM, hEFG1, Q96RP9370%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
25874MPC2mitochondrial pyruvate carrier 2BRP44, O95563370%"literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
4719NDUFS1"NADH dehydrogenase (ubiquinone) Fe-S protein 1, 75kDa (NADH-coenzyme Q reductase)"CI-75Kd, CI-75k, PRO1304, P28331360%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
26589MRPL46mitochondrial ribosomal protein L46C15orf4, LIECG2, P2ECSL, Q9H2W6360%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++"cerebrum, cerebellum, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
5250SLC25A3"solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 3"PHC, PTP, Q00325360%"literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
514ATP5E"ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunit"ATPE, MC5DN3, P56381360%"literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
51649MRPS23mitochondrial ribosomal protein S23HSPC329, MRP-S23, Q9Y3D9360%"literature, APEX_matrix, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
2271FHfumarate hydrataseHLRCC, LRCC, MCL, MCUL1, P07954350%"literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
23203PMPCApeptidase (mitochondrial processing) alphaAlpha-MPP, INPP5E, P-55, Q10713350%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS++"all 14
506ATP5B"ATP synthase, H+ transporting, mitochondrial F1 complex, beta polypeptide"ATPMB, ATPSB, HEL-S-271, P06576350%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++"all 14
135154C6orf57chromosome 6 open reading frame 57Q5VUM1350%"yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS"adipose, testis
29796UQCR10"ubiquinol-cytochrome c reductase, complex III subunit X"HSPC051, HSPC151, QCR9, UCCR7.2, UCRC, Q9UDW1350%"literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
81689ISCA1iron-sulfur cluster assembly 1HBLD2, ISA1, RP11-507D14.2, hIscA, Q9BUE6350%"APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
8803SUCLA2"succinate-CoA ligase, ADP-forming, beta subunit"A-BETA, MTDPS5, SCS-betaA, Q9P2R7340%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
51805COQ3coenzyme Q3 methyltransferaseDHHBMT, DHHBMTASE, UG0215E05, bA9819.1, Q9NZJ6340%"APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55699IARS2"isoleucyl-tRNA synthetase 2, mitochondrial"ILERS, Q9NSE4340%"APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++"all 14
64960MRPS15mitochondrial ribosomal protein S15MPR-S15, RPMS15, S15mt, P82914340%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++"all 14
3419IDH3Aisocitrate dehydrogenase 3 (NAD+) alphaP50213340%"APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
1353COX11cytochrome c oxidase assembly homolog 11 (yeast)COX11P, Q9Y6N1340%"literature, APEX_IMS, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS"cerebrum, cerebellum, spinalcord, skeletalmuscle, largeintestine, placenta
26519TIMM10translocase of inner mitochondrial membrane 10 homolog (yeast)TIM10, TIM10A, P62072340%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
2110ETFDHelectron-transferring-flavoprotein dehydrogenaseETFQO, MADD, Q16134340%"literature, APEX_matrix, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
64981MRPL34mitochondrial ribosomal protein L34L34mt, Q9BQ48340%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
51069MRPL2mitochondrial ribosomal protein L2MRP-L14, RPML14, Q5T653340%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"spinalcord, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
593BCKDHA"branched chain keto acid dehydrogenase E1, alpha polypeptide"BCKDE1A, MSU, MSUD1, OVD1A, P12694340%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++"cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
7388UQCRHubiquinol-cytochrome c reductase hinge proteinQCR6, UQCR8, P07919340%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
192286HIGD2A"HIG1 hypoxia inducible domain family, member 2A"RCF1b, Q9BW72340%"APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++"all 14
539ATP5O"ATP synthase, H+ transporting, mitochondrial F1 complex, O subunit"ATPO, OSCP, P48047340%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, MS/MS++"all 14
1892ECHS1"enoyl CoA hydratase, short chain, 1, mitochondrial"SCEH, P30084330%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
25875LETMD1LETM1 domain containing 11110019O13Rik, HCCR-1, HCCR-2, HCCR1, HCRR-2, Q6P1Q0330%"GFP, targetP signal+, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
1337COX6A1cytochrome c oxidase subunit VIa polypeptide 1COX6A, COX6AL, P12074330%"literature, targetP signal+, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"all 14
1355COX15cytochrome c oxidase assembly homolog 15 (yeast)CEMCOX2, Q7KZN9330%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS"cerebrum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
10939AFG3L2AFG3-like AAA ATPase 2SCA28, SPAX5, Q9Y4W6330%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
3030HADHA"hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit"ECHA, GBP, HADH, LCEH, LCHAD, MTPA, TP-ALPHA, P40939330%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++"all 14
2108ETFA"electron-transfer-flavoprotein, alpha polypeptide"EMA, GA2, MADD, P13804330%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++"all 14
374291NDUFS7"NADH dehydrogenase (ubiquinone) Fe-S protein 7, 20kDa (NADH-coenzyme Q reductase)"CI-20, CI-20KD, MY017, PSST, O75251330%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
1376CPT2carnitine palmitoyltransferase 2CPT1, CPTASE, IIAE4, P23786320%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression+, MS/MS++"all 14
594BCKDHB"branched chain keto acid dehydrogenase E1, beta polypeptide"E1B, dJ279A18.1, P21953320%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
3420IDH3Bisocitrate dehydrogenase 3 (NAD+) betaH-IDHB, RP46, O43837320%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
23395LARS2"leucyl-tRNA synthetase 2, mitochondrial"LEURS, PRLTS4, Q15031320%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++"all 14
35ACADS"acyl-CoA dehydrogenase, C-2 to C-3 short chain"ACAD3, SCAD, P16219320%"literature, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++"all 14
3954LETM1leucine zipper-EF-hand containing transmembrane protein 1O95202320%"literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++"all 14
521ATP5I"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit E"ATP5K, P56385320%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, coexpression++, MS/MS++"all 14
4976OPA1optic atrophy 1 (autosomal dominant)MGM1, NPG, NTG, largeG, O60313320%"literature, APEX_IMS, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++"all 14
549AUHAU RNA binding protein/enoyl-CoA hydrataseQ13825320%"literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
8802SUCLG1"succinate-CoA ligase, alpha subunit"GALPHA, MTDPS9, SUCLA1, P53597320%"yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
4729NDUFV2"NADH dehydrogenase (ubiquinone) flavoprotein 2, 24kDa"CI-24k, P19404320%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, induction, coexpression++, MS/MS++"all 14
51004COQ6coenzyme Q6 monooxygenaseCGI10, COQ10D6, Q9Y2Z9310%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+"cerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
84545MRPL43mitochondrial ribosomal protein L43bMRP36a, Q8N983310%"literature, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++"all 14
83451ABHD11abhydrolase domain containing 11WBSCR21, Q8NFV4310%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++"cerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
522ATP5J"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F6"ATP5, ATP5A, ATPM, CF6, F6, P18859310%"literature, APEX_IMS, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++"all 14
4714NDUFB8"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 8, 19kDa"ASHI, CI-ASHI, O95169310%"literature, APEX_IMS, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++"all 14
9361LONP1"lon peptidase 1, mitochondrial"LON, LONP, LonHS, PIM1, PRSS15, hLON, P36776310%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
1738DLDdihydrolipoamide dehydrogenaseDLDD, DLDH, E3, GCSL, LAD, PHE3, P09622310%"literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
9131AIFM1"apoptosis-inducing factor, mitochondrion-associated, 1"AIF, CMT2D, CMTX4, COWCK, COXPD6, NADMR, NAMSD, PDCD8, O95831310%"literature, APEX_IMS, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
79746ECHDC3enoyl CoA hydratase domain containing 3Q96DC8310%"targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"spinalcord, kidney, liver, heart, adipose, largeintestine, stomach, placenta, testis
139322APOOLapolipoprotein O-likeCXorf33, FAM121A, UNQ8193, Q6UXV4310%"literature, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
124995MRPL10mitochondrial ribosomal protein L10L10MT, MRP-L10, MRP-L8, MRPL8, RPML8, Q7Z7H8300%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++"all 14
92399MRRFmitochondrial ribosome recycling factorMRFF, MTRRF, RRF, Q96E11300%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
4728NDUFS8"NADH dehydrogenase (ubiquinone) Fe-S protein 8, 23kDa (NADH-coenzyme Q reductase)"CI-23k, CI23KD, TYKY, O00217300%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
34ACADM"acyl-CoA dehydrogenase, C-4 to C-12 straight chain"ACAD1, MCAD, MCADH, P11310300%"literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++"all 14
10989IMMT"inner membrane protein, mitochondrial"HMP, MINOS2, P87, P87/89, P89, PIG52, Q16891300%"literature, targetP signal, yeast mito homolog, mito protein domain+, coexpression++, MS/MS++"all 14
26520TIMM9translocase of inner mitochondrial membrane 9 homolog (yeast)TIM9, TIM9A, Q9Y5J7300%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS++"all 14
291SLC25A4"solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 4"1, AAC1, ANT, ANT 1, ANT1, MTDPS12, PEO2, PEO3, T1, P12235300%"literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS++"all 14
25813SAMM50SAMM50 sorting and assembly machinery componentOMP85, SAM50, TOB55, TRG-3, YNL026W, Q9Y512300%"literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, induction, coexpression++, MS/MS++"all 14
4723NDUFV1"NADH dehydrogenase (ubiquinone) flavoprotein 1, 51kDa"CI-51K, CI51KD, UQOR1, P49821300%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
4720NDUFS2"NADH dehydrogenase (ubiquinone) Fe-S protein 2, 49kDa (NADH-coenzyme Q reductase)"CI-49, O75306300%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
50ACO2"aconitase 2, mitochondrial"ACONM, ICRD, Q99798300%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
6832SUPV3L1"suppressor of var1, 3-like 1 (S. cerevisiae)"SUV3, Q8IYB8300%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
2235FECHferrochelataseEPP, FCE, P22830300%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
4528MTIF2mitochondrial translational initiation factor 2P46199300%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS"all 14
5245PHBprohibitinHEL-215, HEL-S-54e, PHB1, P35232290%"literature, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
26275HIBCH3-hydroxyisobutyryl-CoA hydrolaseHIBYLCOAH, Q6NVY1290%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++"all 14
51116MRPS2mitochondrial ribosomal protein S2MRP-S2, S2mt, Q9Y399290%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
3313HSPA9heat shock 70kDa protein 9 (mortalin)CSA, GRP-75, GRP75, HEL-S-124m, HSPA9B, MOT, MOT2, MTHSP75, PBP74, P38646290%"APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
6834SURF1surfeit 1Q15526290%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
10935PRDX3peroxiredoxin 3AOP-1, AOP1, HBC189, MER5, PRO1748, SP-22, prx-III, P30048290%"literature, APEX_IMS, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
27069GHITMgrowth hormone inducible transmembrane proteinDERP2, HSPC282, MICS1, PTD010, TMBIM5, Q9H3K2290%"literature, APEX_IMS, targetP signal+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS"all 14
60558GUF1GUF1 GTPase homolog (S. cerevisiae)EF-4, Q8N442290%"APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
26517TIMM13translocase of inner mitochondrial membrane 13 homolog (yeast)TIM13, TIM13B, TIMM13A, TIMM13B, ppv1, Q9Y5L4290%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS++"all 14
57128LYRM4LYR motif containing 4C6orf149, CGI-203, COXPD19, ISD11, RP11-428J1.4, Q9HD34290%"literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS++"all 14
54948MRPL16mitochondrial ribosomal protein L16L16mt, MRP-L16, Q9NX20280%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
64976MRPL40mitochondrial ribosomal protein L40MRP-L22, MRPL22, NLVCF, URIM, Q9NQ50280%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
3421IDH3Gisocitrate dehydrogenase 3 (NAD+) gammaH-IDHG, P51553280%"literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
6391SDHC"succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa"CYB560, CYBL, PGL3, QPS1, SDH3, Q99643280%"literature, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+"all 14
4711NDUFB5"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 5, 16kDa"CISGDH, SGDH, O43674280%"literature, APEX_IMS, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS+"all 14
54949SDHAF2succinate dehydrogenase complex assembly factor 2C11orf79, PGL2, SDH5, Q9NX18280%"GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
93058COQ10Acoenzyme Q10 homolog A (S. cerevisiae)Q96MF6280%"targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach
8209C21orf33chromosome 21 open reading frame 33ES1, GT335, HES1, KNPH, KNPI, P30042280%"APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++"all 14
25828TXN2thioredoxin 2MT-TRX, MTRX, TRX2, Q99757280%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+"all 14
55168MRPS18Amitochondrial ribosomal protein S18AHumanS18b, MRP-S18-3, MRPS18-3, S18bmt, Q9NVS2280%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"cerebrum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
4715NDUFB9"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 9, 22kDa"B22, CI-B22, LYRM3, UQOR22, Q9Y6M9280%"literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++"all 14
1345COX6Ccytochrome c oxidase subunit VIcP09669280%"literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++"all 14
23788MTCH2mitochondrial carrier 2MIMP, SLC25A50, Q9Y6C9280%"literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression+, MS/MS++"all 14
4700NDUFA6"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 6, 14kDa"B14, CI-B14, LYRM6, NADHB14, P56556280%"literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++"all 14
788SLC25A20"solute carrier family 25 (carnitine/acylcarnitine translocase), member 20"CAC, CACT, O43772280%"literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"all 14
65008MRPL1mitochondrial ribosomal protein L1BM022, L1MT, MRP-L1, Q9BYD6280%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++"cerebrum, cerebellum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
10469TIMM44translocase of inner mitochondrial membrane 44 homolog (yeast)TIM44, O43615280%"literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
440574MINOS1mitochondrial inner membrane organizing system 1C1orf151, MIO10, Q5TGZ0280%"literature, APEX_IMS, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++"all 14
10063COX17COX17 cytochrome c oxidase copper chaperoneQ14061280%"literature, APEX_IMS, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++"heart, adipose, smallintestine, placenta, testis
6648SOD2"superoxide dismutase 2, mitochondrial"IPOB, MNSOD, MVCD6, P04179280%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++"all 14
7416VDAC1voltage-dependent anion channel 1PORIN, VDAC-1, P21796280%"literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++"all 14
1340COX6B1cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous)COX6B, COXG, COXVIb1, P14854280%"literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++"all 14
8192CLPPcaseinolytic mitochondrial matrix peptidase proteolytic subunitPRLTS3, Q16740280%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
3033HADHhydroxyacyl-CoA dehydrogenaseHAD, HADH1, HADHSC, HCDH, HHF4, MSCHAD, SCHAD, Q16836280%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
33ACADL"acyl-CoA dehydrogenase, long chain"ACAD4, LCAD, P28330280%"literature, targetP signal+, mito protein domain+, induction, coexpression+, MS/MS++"all 14
38ACAT1acetyl-CoA acetyltransferase 1ACAT, MAT, T2, THIL, P24752280%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
115416MALSU1mitochondrial assembly of ribosomal large subunit 1C7orf30, mtRsfA, Q96EH3270%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS"cerebrum, cerebellum, liver, smallintestine, largeintestine, placenta
10845CLPXcaseinolytic mitochondrial matrix peptidase chaperone subunitO76031270%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
4724NDUFS4"NADH dehydrogenase (ubiquinone) Fe-S protein 4, 18kDa (NADH-coenzyme Q reductase)"AQDQ, CI-18, O43181270%"literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MS++"all 14
51073MRPL4mitochondrial ribosomal protein L4CGI-28, L4mt, Q9BYD3270%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++"cerebrum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
708C1QBP"complement component 1, q subcomponent binding protein"GC1QBP, HABP1, SF2p32, gC1Q-R, gC1qR, p32, Q07021270%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++"all 14
10531PITRM1pitrilysin metallopeptidase 1MP1, PreP, Q5JRX3270%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++"all 14
55245UQCC1ubiquinol-cytochrome c reductase complex assembly factor 1BFZB, C20orf44, CBP3, UQCC, Q9NVA1270%"literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, coexpression++, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
128308MRPL55mitochondrial ribosomal protein L55AAVG5835, L55nt, MRP-L55, PRO19675, Q7Z7F7270%"literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
79922MRM1mitochondrial rRNA methyltransferase 1 homolog (S. cerevisiae)Q6IN84270%"APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression"spinalcord, placenta, testis
51102MECRmitochondrial trans-2-enoyl-CoA reductaseCGI-63, FASN2B, NRBF1, Q9BV79270%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++"all 14
65080MRPL44mitochondrial ribosomal protein L44COXPD16, L44MT, MRP-L44, Q9H9J2270%"literature, APEX_matrix, targetP signal, yeast mito homolog++, induction, coexpression+, MS/MS++"cerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
84263HSDL2hydroxysteroid dehydrogenase like 2C9orf99, SDR13C1, Q6YN16270%"APEX_matrix, GFP, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS++"all 14
63931MRPS14mitochondrial ribosomal protein S14DJ262D12.2, HSMRPS14, MRP-S14, S14mt, O60783270%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
11194ABCB8"ATP-binding cassette, sub-family B (MDR/TAP), member 8"EST328128, M-ABC1, MABC1, Q9NUT2270%"literature, targetP signal+, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++"all 14
91647ATPAF2ATP synthase mitochondrial F1 complex assembly factor 2ATP12, ATP12p, MC5DN1, Q8N5M1270%"literature, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4704NDUFA9"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 9, 39kDa"CC6, CI-39k, CI39k, NDUFS2L, SDR22E1, Q16795270%"literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++"all 14
388753COA6cytochrome c oxidase assembly factor 6 homolog (S. cerevisiae)C1orf31, Q5JTJ3270%"APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS"cerebrum, cerebellum, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
5442POLRMTpolymerase (RNA) mitochondrial (DNA directed)APOLMT, MTRNAP, MTRPOL, h-mtRPOL, O00411270%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression++, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
23479ISCUiron-sulfur cluster assembly enzyme2310020H20Rik, HML, ISU2, NIFU, NIFUN, hnifU, Q9H1K1270%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++"all 14
84816RTN4IP1reticulon 4 interacting protein 1NIMP, Q8WWV3270%"literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++"all 14
55753OGDHLoxoglutarate dehydrogenase-likeQ9ULD0270%"APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++"all 14
509ATP5C1"ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1"ATP5C, ATP5CL1, P36542270%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++"all 14
10295BCKDKbranched chain ketoacid dehydrogenase kinaseBCKDKD, BDK, O14874270%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++"cerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
84340GFM2"G elongation factor, mitochondrial 2"EF-G2mt, EFG2, MRRF2, MST027, RRF2, RRF2mt, hEFG2, mEF-G 2, Q969S9270%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++"all 14
29078NDUFAF4"NADH dehydrogenase (ubiquinone) complex I, assembly factor 4"C6orf66, HRPAP20, My013, bA22L21.1, Q9P032270%"APEX_matrix, GFP, mito protein domain+, induction, coexpression++, MS/MS++"all 14
399512SLC25A35"solute carrier family 25, member 35"Q3KQZ1270%"APEX_matrix, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"cerebrum, cerebellum, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
8402SLC25A11"solute carrier family 25 (mitochondrial carrier; oxoglutarate carrier), member 11"OGC, SLC20A4, Q02978270%"literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"all 14
26521TIMM8Btranslocase of inner mitochondrial membrane 8 homolog B (yeast)DDP2, TIM8B, Q9Y5J9270%"literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
27349MCATmalonyl CoA:ACP acyltransferase (mitochondrial)FASN2C, MCT, MT, NET62, fabD, Q8IVS2260%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
200205IBA57"IBA57, iron-sulfur cluster assembly homolog (S. cerevisiae)"C1orf69, MMDS3, Q5T440260%"APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
11331PHB2prohibitin 2BAP, BCAP37, Bap37, PNAS-141, REA, p22, Q99623260%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
7818DAP3death associated protein 3DAP-3, MRP-S29, MRPS29, bMRP-10, P51398260%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++"all 14
56942CMC2C-x(9)-C motif containing 22310061C15Rik, C16orf61, Q9NRP2260%"APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+"cerebrum, cerebellum, spinalcord, liver, heart, adipose, largeintestine, stomach, placenta, testis
644096SDHAF1succinate dehydrogenase complex assembly factor 1LYRM8, A6NFY7260%"literature, targetP signal+, yeast mito homolog, mito protein domain+, induction, coexpression+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
51373MRPS17mitochondrial ribosomal protein S17HSPC011, MRP-S17, RPMS17, S17mt, Q9Y2R5260%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+"all 14
137872ADHFE1"alcohol dehydrogenase, iron containing, 1"ADH8, HOT, Q8IWW8260%"targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++"kidney, liver, heart, adipose, stomach, placenta
9054NFS1NFS1 cysteine desulfuraseIscS, NIFS, Q9Y697260%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++"all 14
79133NDUFAF5"NADH dehydrogenase (ubiquinone) complex I, assembly factor 5"C20orf7, bA526K24.2, dJ842G6.1, Q5TEU4260%"literature, APEX_matrix, GFP, targetP signal+, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS"cerebellum, brainstem, skeletalmuscle, largeintestine, stomach, placenta
63875MRPL17mitochondrial ribosomal protein L17L17mt, LIP2, MRP-L17, MRP-L26, RPL17L, RPML26, Q9NRX2260%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS"all 14
51204TACO1translational activator of mitochondrially encoded cytochrome c oxidase ICCDC44, Q9BSH4260%"literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, MS/MS++"all 14
55669MFN1mitofusin 1hfzo1, hfzo2, Q8IWA4260%"literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+"cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
160760PPTC7PTC7 protein phosphatase homolog (S. cerevisiae)TA-PP2C, TAPP2C, Q8NI37260%"APEX_matrix, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, largeintestine, placenta, testis
65003MRPL11mitochondrial ribosomal protein L11L11MT, MRP-L11, Q9Y3B7260%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+"all 14
4726NDUFS6"NADH dehydrogenase (ubiquinone) Fe-S protein 6, 13kDa (NADH-coenzyme Q reductase)"CI-13kA, CI-13kD-A, CI13KDA, O75380260%"literature, APEX_matrix, targetP signal, mito protein domain+, coexpression++, MS/MS++"all 14
1327COX4I1cytochrome c oxidase subunit IV isoform 1COX4, COX4-1, COXIV, P13073260%"literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, coexpression++, MS/MS++"all 14
28998MRPL13mitochondrial ribosomal protein L13L13, L13A, L13mt, RPL13, RPML13, Q9BYD1260%"literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
5019OXCT13-oxoacid CoA transferase 1OXCT, SCOT, P55809260%"literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression++, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
1329COX5Bcytochrome c oxidase subunit VbCOXVB, P10606260%"literature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
5164PDK2"pyruvate dehydrogenase kinase, isozyme 2"PDHK2, PDKII, Q15119260%"literature, APEX_matrix, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"all 14
211ALAS1"aminolevulinate, delta-, synthase 1"ALAS, ALAS3, ALASH, MIG4, P13196260%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS"liver, heart, adipose, largeintestine, placenta
9553MRPL33mitochondrial ribosomal protein L33C2orf1, L33mt, MRP-L33, RPL33L, O75394260%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, stomach, placenta, testis
25821MTO1mitochondrial tRNA translation optimization 1COXPD10, Q9Y2Z2260%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++"cerebellum, spinalcord, stomach, placenta
11019LIASlipoic acid synthetaseLAS, LIP1, LS, PDHLD, O43766260%"literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS"brainstem, skeletalmuscle, adipose, largeintestine, placenta
4712NDUFB6"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 6, 17kDa"B17, CI, O95139260%"literature, APEX_IMS, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++"all 14
4698NDUFA5"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 5"B13, CI-13KD-B, CI-13kB, NUFM, UQOR13, Q16718260%"literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++"all 14
10651MTX2metaxin 2O75431260%"literature, mito protein domain+, induction, coexpression++, MS/MS++"all 14
8801SUCLG2"succinate-CoA ligase, GDP-forming, beta subunit"GBETA, Q96I99260%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
2230FDX1ferredoxin 1ADX, FDX, LOH11CR1D, P10109260%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+"all 14
6576SLC25A1"solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1"CTP, D2L2AD, SEA, SLC20A3, P53007260%"literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
28957MRPS28mitochondrial ribosomal protein S28MRP-S28, MRP-S35, MRPS35, Q9Y2Q9260%"literature, targetP signal, mito protein domain+, coexpression++, MS/MS++"all 14
92609TIMM50translocase of inner mitochondrial membrane 50 homolog (S. cerevisiae)TIM50, TIM50L, Q3ZCQ8260%"literature, APEX_IMS, yeast mito homolog++, mito protein domain, coexpression++, MS/MS++"all 14
7417VDAC2voltage-dependent anion channel 2POR, P45880260%"literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"all 14
284439SLC25A42"solute carrier family 25, member 42"Q86VD7260%"literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++"all 14
54543TOMM7translocase of outer mitochondrial membrane 7 homolog (yeast)TOM7, Q9P0U1260%"literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
1891ECH1"enoyl CoA hydratase 1, peroxisomal"HPXEL, Q13011250%"APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, coexpression+, MS/MS++"all 14
5188PET112PET112 homolog (yeast)PET112L, O75879250%"literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS"cerebrum, skeletalmuscle, adipose, stomach, testis
617BCS1LBC1 (ubiquinol-cytochrome c reductase) synthesis-likeBCS, BCS1, BJS, FLNMS, GRACILE, Hs.6719, MC3DN1, PTD, h-BCS, Q9Y276250%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
26284ERAL1Era-like 12S mitochondrial rRNA chaperone 1ERA, ERAL1A, H-ERA, HERA-A, HERA-B, O75616250%"APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++"none
152100CMC1C-x(9)-C motif containing 1C3orf68, Q7Z7K0250%"APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
10573MRPL28mitochondrial ribosomal protein L28MAAT1, p15, Q13084250%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
10102TSFM"Ts translation elongation factor, mitochondrial"EFTS, EFTSMT, P43897250%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
51067YARS2"tyrosyl-tRNA synthetase 2, mitochondrial"MLASA2, MT-TYRRS, TYRRS, Q9Y2Z4250%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"brainstem, spinalcord, kidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
27247NFU1NFU1 iron-sulfur cluster scaffold homolog (S. cerevisiae)HIRIP, HIRIP5, MMDS1, NIFUC, Nfu, NifU, Q9UMS0250%"APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"all 14
2395FXNfrataxinCyaY, FA, FARR, FRDA, X25, Q16595250%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"all 14
219927MRPL21mitochondrial ribosomal protein L21L21mt, MRP-L21, Q7Z2W9250%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"all 14
8659ALDH4A1"aldehyde dehydrogenase 4 family, member A1"ALDH4, P5CD, P5CDh, P30038250%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++"all 14
84134TOMM40Ltranslocase of outer mitochondrial membrane 40 homolog (yeast)-likeRP11-297K8.10, TOMM40B, Q969M1250%"targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, testis
51103NDUFAF1"NADH dehydrogenase (ubiquinone) complex I, assembly factor 1"CGI65, CIA30, Q9Y375250%"literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression++, MS/MS++"cerebellum, brainstem, spinalcord, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
4716NDUFB10"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 10, 22kDa"PDSW, O96000250%"literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++"all 14
36ACADSB"acyl-CoA dehydrogenase, short/branched chain"2-MEBCAD, ACAD7, SBCAD, P45954250%"literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MS++"all 14
64965MRPS9mitochondrial ribosomal protein S9MRP-S9, RPMS9, S9mt, P82933250%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"all 14
56997ADCK3aarF domain containing kinase 3ARCA2, CABC1, COQ10D4, COQ8, SCAR9, Q8NI60250%"literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
37ACADVL"acyl-CoA dehydrogenase, very long chain"ACAD6, LCACD, VLCAD, P49748250%"literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MS++"all 14
51117COQ4coenzyme Q4CGI-92, Q9Y3A0250%"literature, targetP signal+, yeast mito homolog++, mito protein domain+, coexpression, MS/MS"cerebrum, cerebellum, brainstem, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
29088MRPL15mitochondrial ribosomal protein L15L15mt, MRP-L15, MRP-L7, RPML7, Q9P015250%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
4695NDUFA2"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 2, 8kDa"B8, CD14, CIB8, O43678250%"literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression++, MS/MS++"all 14
79590MRPL24mitochondrial ribosomal protein L24L24mt, MRP-L18, MRP-L24, Q96A35250%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
3329HSPD1heat shock 60kDa protein 1 (chaperonin)CPN60, GROEL, HLD4, HSP-60, HSP60, HSP65, HuCHA60, SPG13, P10809250%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++"all 14
4725NDUFS5"NADH dehydrogenase (ubiquinone) Fe-S protein 5, 15kDa (NADH-coenzyme Q reductase)"CI-15k, CI15K, O43920250%"literature, APEX_IMS, mito protein domain+, induction, coexpression++, MS/MS++"all 14
50808AK3adenylate kinase 3AK3L1, AK6, AKL3L, AKL3L1, FIX, Q9UIJ7250%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
54205CYCS"cytochrome c, somatic"CYC, HCS, THC4, P99999240%"literature, APEX_IMS, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS++"all 14
4285MIPEPmitochondrial intermediate peptidaseHMIP, MIP, Q99797240%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, MS/MS++"cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
90624LYRM7LYR motif containing 7C5orf31, MZM1L, Q5U5X0240%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
1384CRATcarnitine O-acetyltransferaseCAT1, P43155240%"literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++"all 14
5096PCCB"propionyl CoA carboxylase, beta polypeptide"P05166240%"literature, targetP signal+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++"all 14
51081MRPS7mitochondrial ribosomal protein S7MRP-S, MRP-S7, RP-S7, RPMS7, S7mt, bMRP27a, Q9Y2R9240%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS"all 14
11222MRPL3mitochondrial ribosomal protein L3COXPD9, MRL3, RPML3, P09001240%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
5625PRODHproline dehydrogenase (oxidase) 1HSPOX2, PIG6, POX, PRODH1, PRODH2, TP53I6, O43272240%"literature, targetP signal, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
56922MCCC1methylcrotonoyl-CoA carboxylase 1 (alpha)MCC-B, MCCA, Q96RQ3240%"literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
5095PCCA"propionyl CoA carboxylase, alpha polypeptide"P05165240%"literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
6183MRPS12mitochondrial ribosomal protein S12MPR-S12, MT-RPS12, RPMS12, RPS12, RPSM12, O15235240%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
81570CLPBClpB caseinolytic peptidase B homolog (E. coli)HSP78, SKD3, Q9H078240%"APEX_IMS, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
5163PDK1"pyruvate dehydrogenase kinase, isozyme 1"Q15118240%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain+, MS/MS++"all 14
740MRPL49mitochondrial ribosomal protein L49C11orf4, L49mt, MRP-L49, NOF, NOF1, Q13405240%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MS++"all 14
84233TMEM126Atransmembrane protein 126AOPA7, Q9H061240%"literature, mito protein domain+, induction, coexpression++, MS/MS++"all 14
1347COX7A2cytochrome c oxidase subunit VIIa polypeptide 2 (liver)COX7AL, COX7AL1, COXVIIAL, COXVIIa-L, VIIAL, P14406240%"literature, mito protein domain+, induction, coexpression++, MS/MS++"all 14
55268ECHDC2enoyl CoA hydratase domain containing 2Q86YB7240%"targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
3052HCCSholocytochrome c synthaseCCHL, MCOPS7, MLS, P53701240%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS"cerebrum, spinalcord, heart, adipose, smallintestine, largeintestine, placenta, testis
11112HIBADH3-hydroxyisobutyrate dehydrogenaseNS5ATP1, P31937240%"literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression+, MS/MS++"all 14
9801MRPL19mitochondrial ribosomal protein L19L19mt, MRP-L15, MRP-L19, MRPL15, RLX1, RP11-342K6.1, RPML15, P49406240%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
64979MRPL36mitochondrial ribosomal protein L36BRIP1, L36mt, MRP-L36, PRPL36, RPMJ, Q9P0J6240%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+"none
253512SLC25A30"solute carrier family 25, member 30"KMCP1, Q5SVS4240%"literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, liver, placenta, testis
622BDH1"3-hydroxybutyrate dehydrogenase, type 1"BDH, SDR9C1, Q02338230%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
10667FARS2"phenylalanyl-tRNA synthetase 2, mitochondrial"COXPD14, FARS1, HSPC320, PheRS, dJ520B18.2, O95363230%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"adipose, largeintestine, stomach, placenta, testis
22ABCB7"ATP-binding cassette, sub-family B (MDR/TAP), member 7"ABC7, ASAT, Atm1p, EST140535, O75027230%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+"all 14
4580MTX1metaxin 1MTX, MTXN, Q13505230%"literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++"all 14
4701NDUFA7"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 7, 14.5kDa"B14.5a, O95182230%"literature, APEX_matrix, mito protein domain+, coexpression++, MS/MS++"all 14
10440TIMM17Atranslocase of inner mitochondrial membrane 17 homolog A (yeast)TIM17, TIM17A, Q99595230%"literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS+"all 14
223ALDH9A1"aldehyde dehydrogenase 9 family, member A1"ALDH4, ALDH7, ALDH9, E3, TMABADH, P49189230%"APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, coexpression, MS/MS++"brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
51023MRPS18Cmitochondrial ribosomal protein S18CMRP-S18-1, MRPS18-1, Q9Y3D5230%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
92935MARS2"methionyl-tRNA synthetase 2, mitochondrial"MetRS, SPAX3, mtMetRS, Q96GW9230%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4329ALDH6A1"aldehyde dehydrogenase 6 family, member A1"MMSADHA, MMSDH, Q02252230%"literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++"all 14
2232FDXRferredoxin reductaseADXR, P22570230%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, coexpression, MS/MS++"spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
283459GATC"glutamyl-tRNA(Gln) amidotransferase, subunit C"15E1.2, O43716230%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS"cerebrum, cerebellum, spinalcord, kidney, largeintestine, testis
10131TRAP1TNF receptor-associated protein 1HSP 75, HSP75, HSP90L, TRAP-1, Q12931230%"APEX_matrix, GFP, targetP signal+, Rickettsial homolog, mito protein domain, coexpression++, MS/MS+"all 14
27034ACAD8"acyl-CoA dehydrogenase family, member 8"ACAD-8, ARC42, Q9UKU7220%"literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++"all 14
217ALDH2aldehyde dehydrogenase 2 family (mitochondrial)ALDH-E2, ALDHI, ALDM, P05091220%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, coexpression, MS/MS++"all 14
10105PPIFpeptidylprolyl isomerase FCYP3, CyP-M, Cyp-D, CypD, P30405220%"literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression, MS/MS++"all 14
29928TIMM22translocase of inner mitochondrial membrane 22 homolog (yeast)TEX4, TIM22, Q9Y584220%"literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS"all 14
3712IVDisovaleryl-CoA dehydrogenaseACAD2, P26440220%"literature, APEX_matrix, targetP signal, mito protein domain+, coexpression+, MS/MS++"all 14
79944L2HGDHL-2-hydroxyglutarate dehydrogenaseC14orf160, Q9H9P8220%"literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression, MS/MS++"cerebrum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, testis
23474ETHE1ethylmalonic encephalopathy 1HSCO, YF13H12, O95571220%"literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, induction, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
55052MRPL20mitochondrial ribosomal protein L20L20mt, MRP-L20, Q9BYC9220%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
8604SLC25A12"solute carrier family 25 (aspartate/glutamate carrier), member 12"AGC1, ARALAR, O75746220%"literature, yeast mito homolog+, mito protein domain+, induction, MS/MS++"all 14
292SLC25A5"solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 5"2F1, AAC2, ANT2, T2, T3, P05141220%"literature, yeast mito homolog+, mito protein domain+, induction, MS/MS++"all 14
54460MRPS21mitochondrial ribosomal protein S21MRP-S21, RPMS21, P82921220%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++"all 14
56993TOMM22translocase of outer mitochondrial membrane 22 homolog (yeast)1C9-2, MST065, MSTP065, TOM22, Q9NS69220%"literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++"all 14
10449ACAA2acetyl-CoA acyltransferase 2DSAEC, P42765220%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
51263MRPL30mitochondrial ribosomal protein L30L28MT, L30MT, MRP-L28, MRP-L30, MRPL28, MRPL28M, RPML28, Q8TCC3220%"literature, APEX_matrix, yeast mito homolog++, mito protein domain, coexpression++, MS/MS"all 14
9093DNAJA3"DnaJ (Hsp40) homolog, subfamily A, member 3"HCA57, TID1, hTID-1, Q96EY1220%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+"all 14
65993MRPS34mitochondrial ribosomal protein S34MRP-S12, MRP-S34, MRPS12, P82930220%"literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS++"all 14
4708NDUFB2"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 2, 8kDa"AGGG, CI-AGGG, O95178220%"literature, targetP signal, induction, coexpression++, MS/MS++"all 14
2109ETFB"electron-transfer-flavoprotein, beta polypeptide"MADD, P38117220%"literature, APEX_matrix, yeast mito homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
246269LACE1lactation elevated 1AFG1, Q8WV93220%"APEX_matrix, yeast mito homolog++, Rickettsial homolog, coexpression, MS/MS+"cerebrum, cerebellum, spinalcord, heart, adipose, smallintestine, largeintestine, stomach, placenta
93974ATPIF1ATPase inhibitory factor 1ATPI, ATPIP, IP, Q9UII2220%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
515ATP5F1"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit B1"PIG47, P24539220%"literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
1350COX7Ccytochrome c oxidase subunit VIIcP15954220%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
54927CHCHD3coiled-coil-helix-coiled-coil-helix domain containing 3MINOS3, PPP1R22, Q9NX63220%"literature, APEX_IMS, APEX_matrix, GFP, yeast mito homolog, induction, coexpression++, MS/MS++"all 14
80219COQ10Bcoenzyme Q10 homolog B (S. cerevisiae)Q9H8M1220%"GFP, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
197322ACSF3acyl-CoA synthetase family member 3Q4G176220%"APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++"all 14
26073POLDIP2"polymerase (DNA-directed), delta interacting protein 2"PDIP38, POLD4, Q9Y2S7220%"literature, APEX_matrix, targetP signal+, induction, coexpression++, MS/MS++"all 14
1468SLC25A10"solute carrier family 25 (mitochondrial carrier; dicarboxylate transporter), member 10"DIC, Q9UBX3210%"literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
10165SLC25A13"solute carrier family 25 (aspartate/glutamate carrier), member 13"ARALAR2, CITRIN, CTLN2, Q9UJS0210%"literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++"all 14
5165PDK3"pyruvate dehydrogenase kinase, isozyme 3"CMTX6, GS1-358P8.4, Q15120210%"literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
10873ME3"malic enzyme 3, NADP(+)-dependent, mitochondrial"NADP-ME, Q16798210%"literature, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
29093MRPL22mitochondrial ribosomal protein L22L22mt, MRP-L22, MRP-L25, RPML25, Q9NWU5210%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++"all 14
3418IDH2"isocitrate dehydrogenase 2 (NADP+), mitochondrial"D2HGA2, ICD-M, IDH, IDHM, IDP, IDPM, mNADP-IDH, P48735210%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
2639GCDHglutaryl-CoA dehydrogenaseACAD5, GCD, Q92947210%"literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++"all 14
57129MRPL47mitochondrial ribosomal protein L47L47mt, MRP-L47, NCM1, Q9HD33210%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression"all 14
27068PPA2pyrophosphatase (inorganic) 2SID6-306, Q9H2U2210%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
65005MRPL9mitochondrial ribosomal protein L9L9mt, Q9BYD2210%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS"all 14
400916CHCHD10coiled-coil-helix-coiled-coil-helix domain containing 10C22orf16, N27C7-4, Q8WYQ3210%"literature, targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression++"none
10352WARS2"tryptophanyl tRNA synthetase 2, mitochondrial"TrpRS, Q9UGM6210%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, kidney, skeletalmuscle, adipose, largeintestine, placenta, testis
60386SLC25A19"solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19"DNC, MCPHA, MUP1, THMD3, THMD4, TPC, Q9HC21210%"literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS"cerebellum, spinalcord, adipose, testis
84869CBR4carbonyl reductase 4SDR45C1, Q8N4T8210%"literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++"all 14
91689SMDT1single-pass membrane protein with aspartate-rich tail 1C22orf32, DDDD, EMRE, dJ186O1.1, Q9H4I9210%"literature, targetP signal, mito protein domain+, induction, coexpression+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
3029HAGHhydroxyacylglutathione hydrolaseGLO2, GLX2, GLXII, HAGH1, Q16775210%"literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
1346COX7A1cytochrome c oxidase subunit VIIa polypeptide 1 (muscle)COX7A, COX7AH, COX7AM, P24310210%"literature, targetP signal, mito protein domain+, induction, coexpression, MS/MS+"cerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
92170MTG1mitochondrial ribosome-associated GTPase 1GTP, GTPBP7, RP11-108K14.2, Q9BT17210%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS"largeintestine, testis
84987COX14cytochrome c oxidase assembly homolog 14 (S. cerevisiae)C12orf62, Q96I36210%"literature, GFP, mito protein domain+, induction, coexpression++, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, smallintestine, testis
55967NDUFA12"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 12"B17.2, DAP13, Q9UI09210%"literature, APEX_matrix, Rickettsial homolog, coexpression++, MS/MS++"all 14
51021MRPS16mitochondrial ribosomal protein S16COXPD2, MRP-S16, RPMS16, Q9Y3D3210%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS+"all 14
80298MTERFD3MTERF domain containing 3mTERF2, mTERFL, Q49AM1210%"literature, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, testis
144363LYRM5LYR motif containing 5Q6IPR1210%"mito protein domain+, induction, coexpression, MS/MS++"cerebrum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
2820GPD2glycerol-3-phosphate dehydrogenase 2 (mitochondrial)GDH2, GPDM, mGPDH, P43304210%"literature, APEX_IMS, yeast mito homolog++, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4705NDUFA10"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 10, 42kDa"CI-42KD, CI-42k, O95299210%"literature, targetP signal, mito protein domain, coexpression++, MS/MS++"all 14
4718NDUFC2"NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 2, 14.5kDa"B14.5b, CI-B14.5b, HLC-1, NADHDH2, O95298210%"literature, APEX_IMS, mito protein domain+, coexpression++, MS/MS++"all 14
81892SLIRPSRA stem-loop interacting RNA binding proteinC14orf156, DC50, PD04872, Q9GZT3210%"literature, APEX_matrix, GFP, targetP signal+, mito protein domain, induction, coexpression, MS/MS++"all 14
4513COX2cytochrome c oxidase subunit IICOII, MTCO2, P00403210%"literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS+"all 14
4508ATP6ATP synthase F0 subunit 6ATPase6, MTATP6, P00846210%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS+"all 14
29090TIMM21translocase of inner mitochondrial membrane 21 homolog (yeast)C18orf55, TIM21, Q9BVV7210%"APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
4702NDUFA8"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 8, 19kDa"CI-19KD, CI-PGIV, PGIV, P51970210%"literature, APEX_IMS, mito protein domain, induction, coexpression++, MS/MS++"all 14
2744GLSglutaminaseAAD20, GAC, GAM, GLS1, KGA, O94925200%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
54539NDUFB11"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 11, 17.3kDa"CI-ESSS, ESSS, NP17.3, Np15, P17.3, Q9NX14200%"literature, APEX_IMS, APEX_matrix, targetP signal+, coexpression++, MS/MS++"all 14
55526DHTKD1dehydrogenase E1 and transketolase domain containing 1AMOXAD, CMT2Q, Q96HY7200%"APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS"cerebrum, kidney, liver, adipose, placenta, testis
51011FAHD2Afumarylacetoacetate hydrolase domain containing 2AQ96GK7200%"APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++"all 14
84681HINT2histidine triad nucleotide binding protein 2HIT-17, Q9BX68200%"APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
7923HSD17B8hydroxysteroid (17-beta) dehydrogenase 8D6S2245E, FABG, FABGL, H2-KE6, HKE6, KE6, RING2, SDR30C1, dJ1033B10.9, Q92506200%"APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
64969MRPS5mitochondrial ribosomal protein S5MRP-S5, S5mt, P82675200%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"cerebrum, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
221545C6orf136chromosome 6 open reading frame 136Q5SQH8200%"targetP signal, induction, coexpression++, MS/MS+"all 14
283377SPRYD4SPRY domain containing 4Q8WW59200%"APEX_matrix, GFP, targetP signal+, mito protein domain, coexpression+, MS/MS++"all 14
387787LIPT2lipoyl(octanoyl) transferase 2 (putative)A6NK58200%"targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
1666DECR1"2,4-dienoyl CoA reductase 1, mitochondrial"DECR, NADPH, SDR18C1, Q16698200%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++"all 14
64949MRPS26mitochondrial ribosomal protein S26C20orf193, GI008, MRP-S13, MRP-S26, MRPS13, NY-BR-87, RPMS13, dJ534B8.3, Q9BYN8200%"literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MS+"all 14
10166SLC25A15solute carrier family 25 (mitochondrial carrier; ornithine transporter) member 15D13S327, HHH, ORC1, ORNT1, Q9Y619200%"literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++"spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta
4731NDUFV3"NADH dehydrogenase (ubiquinone) flavoprotein 3, 10kDa"CI-10k, CI-9KD, P56181200%"literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS++"all 14
670BPHLbiphenyl hydrolase-like (serine hydrolase)BPH-RP, MCNAA, VACVASE, Q86WA6200%"targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
30968STOML2stomatin (EPB72)-like 2SLP-2, Q9UJZ1200%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
22921MSRB2methionine sulfoxide reductase B2CBS-1, CBS1, MSRB, PILB, Q9Y3D2200%"APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
114294LACTB"lactamase, beta"G24, MRPL56, P83111200%"literature, APEX_IMS, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
114789SLC25A25"solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 25"MCSC, PCSCL, RP11-395P17.4, SCAMC-2, Q6KCM7200%"literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++"cerebrum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, placenta
10452TOMM40translocase of outer mitochondrial membrane 40 homolog (yeast)C19orf1, D19S1177E, PER-EC1, PEREC1, TOM40, O96008200%"literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++"cerebrum, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
203054ADCK5aarF domain containing kinase 5Q3MIX3200%"targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"cerebrum, largeintestine, testis
80724ACAD10"acyl-CoA dehydrogenase family, member 10"Q6JQN1200%"APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++"cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
23078VWA8von Willebrand factor A domain containing 8KIAA0564, A3KMH1200%"APEX_matrix, targetP signal, mito protein domain, coexpression+, MS/MS++"all 14
60492CCDC90Bcoiled-coil domain containing 90BMDS011, MDS025, Q9GZT6200%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain+, MS/MS"all 14
55735DNAJC11"DnaJ (Hsp40) homolog, subfamily C, member 11"dJ126A5.1, Q9NVH1200%"GFP, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
84266ALKBH7"alkB, alkylation repair homolog 7 (E. coli)"ABH7, SPATA11, UNQ6002, Q9BT30200%"APEX_matrix, targetP signal, mito protein domain, induction, coexpression++, MS/MS"cerebellum, brainstem, largeintestine, testis
2731GLDCglycine dehydrogenase (decarboxylating)GCE, GCSP, HYGN1, P23378200%"literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, kidney, liver, adipose, placenta
347411MPC1Lmitochondrial pyruvate carrier 1-likeP0DKB6200%"targetP signal, yeast mito homolog+, mito protein domain+, MS/MS++"testis
117145THEM4thioesterase superfamily member 4CTMP, Q5T1C6190%"literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, induction, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
6742SSBP1"single-stranded DNA binding protein 1, mitochondrial"Mt-SSB, SOSS-B1, SSBP, mtSSB, Q04837190%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"all 14
51264MRPL27mitochondrial ribosomal protein L27L27mt, Q9P0M9190%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"all 14
150274HSCBHscB mitochondrial iron-sulfur cluster co-chaperoneDNAJC20, HSC20, JAC1, dJ366L4.2, Q8IWL3190%"APEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
55173MRPS10mitochondrial ribosomal protein S10MRP-S10, PNAS-122, P82664190%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++"all 14
205AK4adenylate kinase 4AK 4, AK3, AK3L1, AK3L2, P27144190%"APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++"all 14
55210ATAD3A"ATPase family, AAA domain containing 3A"Q9NVI7190%"APEX_IMS, APEX_matrix, GFP, Rickettsial homolog, mito protein domain+, coexpression, MS/MS++"all 14
80142PTGES2prostaglandin E synthase 2C9orf15, GBF-1, GBF1, PGES2, mPGES-2, Q9H7Z7190%"literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+, MS/MS++"all 14
51253MRPL37mitochondrial ribosomal protein L37L37mt, MRP-L2, MRP-L37, MRPL2, RPML2, Q9BZE1190%"literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+, MS/MS++"kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
54988ACSM5acyl-CoA synthetase medium-chain family member 5Q6NUN0190%"literature, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"kidney, liver, adipose, smallintestine, largeintestine
10587TXNRD2thioredoxin reductase 2SELZ, TR, TR-BETA, TR3, TRXR2, Q9NNW7190%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55847CISD1CDGSH iron sulfur domain 1C10orf70, ZCD1, mitoNEET, Q9NZ45190%"literature, mito protein domain, induction, coexpression++, MS/MS++"all 14
64975MRPL41mitochondrial ribosomal protein L41BMRP, MRP-L27, MRPL27, RPML27, Q8IXM3190%"literature, APEX_matrix, yeast mito homolog++, mito protein domain, induction, MS/MS++"all 14
54996MARC2mitochondrial amidoxime reducing component 2MOSC2, RP11-270A6.1, Q969Z3190%"literature, targetP signal, mito protein domain+, induction, coexpression, MS/MS++"all 14
64968MRPS6mitochondrial ribosomal protein S6C21orf101, MRP-S6, RPMS6, S6mt, P82932190%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++"all 14
6150MRPL23mitochondrial ribosomal protein L23L23MRP, RPL23, RPL23L, Q16540190%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MS++"all 14
58472SQRDLsulfide quinone reductase-like (yeast)PRO1975, Q9Y6N5190%"literature, targetP signal, yeast mito homolog++, mito protein domain, MS/MS++"spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
6341SCO1SCO1 cytochrome c oxidase assembly proteinSCOD1, O75880190%"literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
25902MTHFD1Lmethylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-likeFTHFSDC1, MTC1THFS, dJ292B18.2, Q6UB35190%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
23464GCATglycine C-acetyltransferaseKBL, O75600190%"literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++"brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
10455ECI2enoyl-CoA delta isomerase 2ACBD2, DRS-1, DRS1, HCA88, PECI, dJ1013A10.3, O75521190%"literature, APEX_matrix, targetP signal+, mito protein domain, coexpression+, MS/MS++"all 14
7381UQCRBubiquinol-cytochrome c reductase binding proteinMC3DN3, QCR7, QP-C, QPC, UQBC, UQBP, UQCR6, UQPC, P14927190%"literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
131076CCDC58coiled-coil domain containing 58Q4VC31190%"APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
10632ATP5L"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit G"ATP5JG, O75964190%"literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
10476ATP5H"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit d"ATPQ, O75947190%"literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
64087MCCC2methylcrotonoyl-CoA carboxylase 2 (beta)MCCB, Q9HCC0190%"literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++"all 14
84693MCEEmethylmalonyl CoA epimeraseGLOD2, Q96PE7190%"targetP signal, induction, coexpression++, MS/MS++"all 14
4337MOCS1molybdenum cofactor synthesis 1MIG11, MOCOD, MOCODA, Q9NZB8190%"APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain+, MS/MS+"cerebrum, liver, adipose, smallintestine, largeintestine, stomach, placenta
4594MUTmethylmalonyl CoA mutaseMCM, P22033190%"literature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS++"all 14
92014SLC25A51"solute carrier family 25, member 51"CG7943, MCART1, Q9H1U9190%"GFP, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
6687SPG7spastic paraplegia 7 (pure and complicated autosomal recessive)CAR, CMAR, PGN, SPG5C, Q9UQ90190%"literature, targetP signal, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
518ATP5G3"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C3 (subunit 9)"P3, P48201190%"literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression++"none
84896ATAD1"ATPase family, AAA domain containing 1"AFDC1, THORASE, Q8NBU5190%"yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
92106OXNAD1oxidoreductase NAD-binding domain containing 1Q96HP4190%"APEX_matrix, GFP, mito protein domain, coexpression++, MS/MS++"cerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
26164MTG2mitochondrial ribosome-associated GTPase 2GTPBP5, ObgH1, dJ1005F21.2, Q9H4K7190%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression"largeintestine, placenta
55157DARS2"aspartyl-tRNA synthetase 2, mitochondrial"ASPRS, LBSL, MT-ASPRS, RP3-383J4.2, Q6PI48190%"APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
51258MRPL51mitochondrial ribosomal protein L51HSPC241, MRP64, bMRP64, Q4U2R6190%"literature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
5091PCpyruvate carboxylasePCB, P11498190%"literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
171425CLYBLcitrate lyase beta likeCLB, Q8N0X4190%"APEX_matrix, targetP signal+, induction, coexpression+, MS/MS++"all 14
50640PNPLA8patatin-like phospholipase domain containing 8IPLA2(GAMMA), IPLA2-2, IPLA2G, iPLA2gamma, Q9NP80190%"APEX_matrix, Rickettsial homolog, induction, coexpression++, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, testis
23417MLYCDmalonyl-CoA decarboxylaseMCD, O95822190%"literature, APEX_matrix, targetP signal+, mito protein domain, coexpression++, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
100996939PYURFPIGY upstream reading framePREY, Q96I23190%"targetP signal+, induction, coexpression++, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
10245TIMM17Btranslocase of inner mitochondrial membrane 17 homolog B (yeast)DXS9822, TIM17B, O60830190%"literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression, MS/MS+"all 14
64983MRPL32mitochondrial ribosomal protein L32L32mt, MRP-L32, bMRP-59b, Q9BYC8190%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
115286SLC25A26"solute carrier family 25 (S-adenosylmethionine carrier), member 26"SAMC, Q70HW3190%"literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS"cerebrum, cerebellum, adipose, largeintestine, placenta, testis
58510PRODH2proline dehydrogenase (oxidase) 2HSPOX1, Q9UF12190%"targetP signal, yeast mito homolog+, mito protein domain+, MS/MS+"kidney, liver
56954NIT2"nitrilase family, member 2"HEL-S-8a, Q9NQR4180%"Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
112812FDX1Lferredoxin 1-likeFDX2, Q6P4F2180%"APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
7284TUFM"Tu translation elongation factor, mitochondrial"COXPD4, EF-TuMT, EFTU, P43, P49411180%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++"all 14
4200ME2"malic enzyme 2, NAD(+)-dependent, mitochondrial"ODS1, P23368180%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
1339COX6A2cytochrome c oxidase subunit VIa polypeptide 2COX6AH, COXVIAH, Q02221180%"literature, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression"heart, skeletalmuscle
10463SLC30A9"solute carrier family 30 (zinc transporter), member 9"C4orf1, GAC63, HUEL, ZNT9, Q6PML9180%"APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
132001TAMM41"TAM41, mitochondrial translocator assembly and maintenance protein, homolog (S. cerevisiae)"C3orf31, RAM41, TAM41, Q96BW9180%"GFP, yeast mito homolog++, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
100287932TIMM23translocase of inner mitochondrial membrane 23 homolog (yeast)TIM23, O14925180%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++"all 14
55005RMND1required for meiotic nuclear division 1 homolog (S. cerevisiae)C6orf96, COXPD11, RMD1, bA351K16, bA351K16.3, Q9NWS8180%"literature, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
9927MFN2mitofusin 2CMT2A, CMT2A2, CPRP1, HSG, MARF, O95140180%"literature, mito protein domain+, induction, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
728489DNLZDNL-type zinc fingerC9orf151, HEP, HEP1, TIMM15, ZIM17, bA413M3.2, Q5SXM8180%"APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, heart, adipose, smallintestine, largeintestine, stomach, placenta
131474CHCHD4coiled-coil-helix-coiled-coil-helix domain containing 4MIA40, TIMM40, Q8N4Q1180%"literature, APEX_IMS, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4706NDUFAB1"NADH dehydrogenase (ubiquinone) 1, alpha/beta subcomplex, 1, 8kDa"ACP, FASN2A, SDAP, O14561180%"literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS+"all 14
116285ACSM1acyl-CoA synthetase medium-chain family member 1BUCS1, MACS1, Q08AH1180%"literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"spinalcord, kidney, liver, smallintestine
493753COA5cytochrome c oxidase assembly factor 56330578E17Rik, C2orf64, Pet191, Q86WW8180%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, MS/MS"adipose, placenta, testis
27235COQ2coenzyme Q2 4-hydroxybenzoate polyprenyltransferaseCL640, COQ10D1, MSA1, Q96H96180%"literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+"none
57107PDSS2"prenyl (decaprenyl) diphosphate synthase, subunit 2"C6orf210, COQ10D3, DLP1, bA59I9.3, hDLP1, Q86YH6180%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression+"smallintestine, largeintestine
1962EHHADH"enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase"ECHD, FRTS3, L-PBE, LBFP, LBP, PBFE, Q08426180%"yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta
4722NDUFS3"NADH dehydrogenase (ubiquinone) Fe-S protein 3, 30kDa (NADH-coenzyme Q reductase)"CI-30, O75489180%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++"all 14
23456ABCB10"ATP-binding cassette, sub-family B (MDR/TAP), member 10"EST20237, M-ABC2, MTABC2, Q9NRK6180%"literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+"cerebellum, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
64432MRPS25mitochondrial ribosomal protein S25MRP-S25, RPMS25, P82663180%"literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++"all 14
1160CKMT2"creatine kinase, mitochondrial 2 (sarcomeric)"SMTCK, P17540180%"literature, targetP signal, mito protein domain, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
28976ACAD9"acyl-CoA dehydrogenase family, member 9"NPD002, Q9H845180%"literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++"all 14
51241COX16COX16 cytochrome c oxidase assembly homolog (S. cerevisiae)C14orf112, Q9P0S2180%"APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, MS/MS+"kidney, liver, adipose, largeintestine, placenta, testis
125228FAM210A"family with sequence similarity 210, member A"C18orf19, HsT2329, Q96ND0180%"GFP, targetP signal, induction, coexpression++, MS/MS"all 14
55856ACOT13acyl-CoA thioesterase 13PNAS-27, THEM2, Q9NPJ3180%"mito protein domain, induction, coexpression, MS/MS++"all 14
2710GKglycerol kinaseGK1, GKD, P32189180%"literature, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, testis
1374CPT1Acarnitine palmitoyltransferase 1A (liver)CPT1, CPT1-L, L-CPT1, P50416180%"literature, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++"all 14
10901DHRS4dehydrogenase/reductase (SDR family) member 4CR, NRDR, PHCR, PSCD, SCAD-SRL, SDR-SRL, SDR25C1, SDR25C2, Q9BTZ2180%"targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
153768PRELID2PRELI domain containing 2Q8N945180%"yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS"largeintestine, stomach
79587CARS2"cysteinyl-tRNA synthetase 2, mitochondrial (putative)"Q9HA77180%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression++, MS/MS"cerebrum, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
2631GBASglioblastoma amplified sequenceNIPSNAP2, O75323180%"literature, APEX_matrix, targetP signal+, induction, coexpression, MS/MS++"all 14
125988C19orf70chromosome 19 open reading frame 70P117, QIL1, Q5XKP0170%"induction, coexpression++, MS/MS++"all 14
4713NDUFB7"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 7, 18kDa"B18, CI-B18, P17568170%"literature, APEX_IMS, APEX_matrix, induction, coexpression++, MS/MS++"all 14
51022GLRX2glutaredoxin 2CGI-133, GRX2, Q9NS18170%"literature, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, largeintestine, placenta, testis
10884MRPS30mitochondrial ribosomal protein S30MRP-S30, PAP, PDCD9, S30mt, Q9NP92170%"literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++"cerebrum, cerebellum, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
9997SCO2SCO2 cytochrome c oxidase assembly proteinCEMCOX1, MYP6, SCO1L, O43819170%"literature, APEX_IMS, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS"all 14
3028HSD17B10hydroxysteroid (17-beta) dehydrogenase 1017b-HSD10, ABAD, CAMR, DUPXp11.22, ERAB, HADH2, HCD2, MHBD, MRPP2, MRX17, MRX31, MRXS10, SCHAD, SDR5C1, Q99714170%"literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"all 14
79731NARS2"asparaginyl-tRNA synthetase 2, mitochondrial (putative)"SLM5, asnRS, Q96I59170%"GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression"spinalcord, adipose, largeintestine, stomach, placenta
285367RPUSD3RNA pseudouridylate synthase domain containing 3Q6P087170%"APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression"largeintestine
6821SUOXsulfite oxidaseP51687170%"APEX_IMS, targetP signal, mito protein domain+, coexpression, MS/MS++"cerebrum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
1757SARDHsarcosine dehydrogenaseBPR-2, DMGDHL1, SAR, SARD, SDH, Q9UL12170%"literature, targetP signal+, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
10247HRSP12heat-responsive protein 12P14.5, PSP, UK114, P52758170%"APEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
1351COX8Acytochrome c oxidase subunit VIIIA (ubiquitous)COX, COX8, COX8-2, COX8L, VIII, VIII-L, P10176170%"literature, targetP signal, mito protein domain+, coexpression+, MS/MS"stomach, placenta, testis
6697SPR"sepiapterin reductase (7,8-dihydrobiopterin:NADP+ oxidoreductase)"SDR38C1, P35270170%"Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach
4358MPV17MpV17 mitochondrial inner membrane proteinMTDPS6, SYM1, P39210170%"literature, yeast mito homolog+, mito protein domain, coexpression, MS/MS++"all 14
284273ZADH2zinc binding alcohol dehydrogenase domain containing 2Q8N4Q0170%"mito protein domain, induction, coexpression+, MS/MS++"all 14
29074MRPL18mitochondrial ribosomal protein L18L18mt, MRP-L18, Q9H0U6170%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS"all 14
219ALDH1B1"aldehyde dehydrogenase 1 family, member B1"ALDH5, ALDHX, P30837170%"literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, MS/MS++"all 14
118487CHCHD1coiled-coil-helix-coiled-coil-helix domain containing 1C10orf34, C2360, MRP-S37, Q96BP2170%"GFP, targetP signal, yeast mito homolog+, mito protein domain, coexpression+, MS/MS"cerebrum, cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
83733SLC25A18"solute carrier family 25 (glutamate carrier), member 18"GC2, Q9H1K4170%"literature, yeast mito homolog+, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
83447SLC25A31"solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 31"AAC4, ANT4, SFEC35kDa, Q9H0C2170%"literature, yeast mito homolog+, mito protein domain+, MS/MS++"all 14
79751SLC25A22"solute carrier family 25 (mitochondrial carrier: glutamate), member 22"EIEE3, GC1, NET44, Q9H936170%"literature, yeast mito homolog+, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
7419VDAC3voltage-dependent anion channel 3HD-VDAC3, VDAC-3, Q9Y277170%"literature, yeast mito homolog+, mito protein domain+, MS/MS++"all 14
51660MPC1mitochondrial pyruvate carrier 1BRP44L, MPYCD, dJ68L15.3, Q9Y5U8170%"GFP, yeast mito homolog+, mito protein domain+, MS/MS++"all 14
29957SLC25A24"solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 24"APC1, SCAMC-1, Q6NUK1170%"literature, APEX_IMS, yeast mito homolog+, mito protein domain+, MS/MS++"adipose, smallintestine, largeintestine, stomach, placenta, testis
1678TIMM8Atranslocase of inner mitochondrial membrane 8 homolog A (yeast)DDP, DDP1, DFN1, MTS, TIM8, O60220170%"literature, yeast mito homolog+, mito protein domain+, MS/MS++"all 14
51095TRNT1"tRNA nucleotidyl transferase, CCA-adding, 1"CCA1, MtCCA, Q96Q11170%"literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, MS/MS"spinalcord, adipose, placenta, testis
3416IDEinsulin-degrading enzymeINSULYSIN, P14735170%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
373156GSTK1glutathione S-transferase kappa 1GST, GST 13-13, GST13, GST13-13, GSTK1-1, hGSTK1, Q9Y2Q3170%"literature, mito protein domain+, coexpression+, MS/MS++"all 14
57176VARS2"valyl-tRNA synthetase 2, mitochondrial"G7a, VARS2L, VARSL, Q5ST30170%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
3336HSPE1heat shock 10kDa protein 1CPN10, EPF, GROES, HSP10, P61604170%"literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++"all 14
116541MRPL54mitochondrial ribosomal protein L54L54mt, MRP-L54, Q6P161170%"literature, APEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
64978MRPL38mitochondrial ribosomal protein L38L38MT, MRP-L3, MRP-L38, RPML3, Q96DV4170%"APEX_matrix, targetP signal, mito protein domain, coexpression++, MS/MS+"cerebrum, spinalcord, heart, smallintestine, largeintestine, stomach, placenta, testis
3396ICT1immature colon carcinoma transcript 1DS-1, DS1, MRP-L58, Q14197170%"APEX_matrix, GFP, targetP signal+, mito protein domain, induction, coexpression, MS/MS"all 14
23787MTCH1mitochondrial carrier 1CGI-64, PIG60, PSAP, SLC25A49, Q9NZJ7170%"literature, yeast mito homolog+, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
51499TRIAP1TP53 regulated inhibitor of apoptosis 1MDM35, P53CSV, WF-1, O43715170%"literature, yeast mito homolog++, mito protein domain, induction, MS/MS++"adipose, stomach, placenta
55037PTCD3pentatricopeptide repeat domain 3MRP-S39, Q96EY7170%"literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++"all 14
1352COX10cytochrome c oxidase assembly homolog 10 (yeast)Q12887170%"literature, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++"none
8165AKAP1A kinase (PRKA) anchor protein 1AKAP, AKAP121, AKAP149, AKAP84, D-AKAP1, PPP1R43, PRKA1, SAKAP84, TDRD17, Q92667170%"literature, mito protein domain, induction, coexpression++, MS/MS+"cerebellum, skeletalmuscle, testis
55178RNMTL1RNA methyltransferase like 1Q9HC36170%"APEX_matrix, GFP, targetP signal+, mito protein domain+, induction, coexpression"none
204AK2adenylate kinase 2ADK2, AK 2, P54819170%"literature, APEX_IMS, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++"all 14
54968TMEM70transmembrane protein 70MC5DN2, Q9BUB7170%"literature, APEX_matrix, mito protein domain+, coexpression++, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
84273NOA1nitric oxide associated 1C4orf14, MTG3, hAtNOS1, hNOA1, mAtNOS1, Q8NC60170%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression"adipose, largeintestine
63933MCUR1mitochondrial calcium uniporter regulator 1C6orf79, CCDC90A, Q96AQ8170%"APEX_matrix, yeast mito homolog+, mito protein domain+, induction, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
51522TMEM14Ctransmembrane protein 14CC6orf53, MSTP073, NET26, bA421M1.6, Q9P0S9170%"literature, mito protein domain+, induction, coexpression, MS/MS+"all 14
4717NDUFC1"NADH dehydrogenase (ubiquinone) 1, subcomplex unknown, 1, 6kDa"KFYI, O43677170%"literature, targetP signal+, mito protein domain+, coexpression++"none
51318MRPL35mitochondrial ribosomal protein L35L35mt, MRP-L35, Q9NZE8170%"literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression++"largeintestine, testis
4696NDUFA3"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 3, 9kDa"B9, CI-B9, O95167170%"literature, induction, coexpression++, MS/MS++"all 14
23590PDSS1"prenyl (decaprenyl) diphosphate synthase, subunit 1"COQ1, COQ10D2, DPS, RP13-16H11.3, SPS, TPRT, TPT, TPT 1, hDPS1, Q5T2R2170%"APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression"skeletalmuscle, largeintestine, placenta, testis
8034SLC25A16"solute carrier family 25 (mitochondrial carrier; Graves disease autoantigen), member 16"D10S105E, GDA, GDC, HGT.1, ML7, hML7, P16260160%"literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS"cerebrum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
154791C7orf55chromosome 7 open reading frame 55FMC1160%"literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
6296ACSM3acyl-CoA synthetase medium-chain family member 3SA, SAH, Q53FZ2160%"literature, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++"kidney, liver, adipose, smallintestine, largeintestine, stomach
137682NDUFAF6"NADH dehydrogenase (ubiquinone) complex I, assembly factor 6"C8orf38, Q330K2160%"literature, targetP signal, mito protein domain, induction, coexpression++, MS/MS"adipose, smallintestine, largeintestine, placenta, testis
7350UCP1"uncoupling protein 1 (mitochondrial, proton carrier)"SLC25A7, UCP, P25874160%"literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS"adipose
94081SFXN1sideroflexin 1Q9H9B4160%"literature, mito protein domain+, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
51218GLRX5glutaredoxin 5C14orf87, FLB4739, GRX5, PR01238, PRO1238, Q86SX6160%"literature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"all 14
138428PTRH1peptidyl-tRNA hydrolase 1 homolog (S. cerevisiae)C9orf115, PTH1, Q86Y79160%"APEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, largeintestine, placenta
64963MRPS11mitochondrial ribosomal protein S11HCC-2, P82912160%"literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"all 14
63929XPNPEP3"X-prolyl aminopeptidase (aminopeptidase P) 3, putative"APP3, NPHPL1, Q9NQH7160%"literature, APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"cerebrum, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
54704PDP1pyruvate dehyrogenase phosphatase catalytic subunit 1PDH, PDP, PDPC, PPM2C, Q9P0J1160%"literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, MS/MS++"cerebrum, cerebellum, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
1632ECI1enoyl-CoA delta isomerase 1DCI, P42126160%"literature, APEX_matrix, targetP signal, mito protein domain, coexpression+, MS/MS++"all 14
283130SLC25A45"solute carrier family 25, member 45"Q8N413160%"yeast mito homolog+, mito protein domain+, MS/MS++"liver, adipose, smallintestine, stomach, placenta, testis
89874SLC25A21"solute carrier family 25 (mitochondrial oxoadipate carrier), member 21"ODC, ODC1, Q9BQT8160%"literature, yeast mito homolog+, mito protein domain+, MS/MS++"spinalcord, kidney, liver, testis
123096SLC25A29"solute carrier family 25 (mitochondrial carnitine/acylcarnitine carrier), member 29"AL157871.2, C14orf69, CACL, ORNT3, Q8N8R3160%"literature, yeast mito homolog+, mito protein domain+, MS/MS++"placenta, testis
57001ACN9ACN9 homolog (S. cerevisiae)Q9NRP4160%"targetP signal, yeast mito homolog++, coexpression+, MS/MS"adipose, testis
51629SLC25A39"solute carrier family 25, member 39"CGI69, Q9BZJ4160%"literature, yeast mito homolog+, mito protein domain+, induction, coexpression"none
51012SLMO2slowmo homolog 2 (Drosophila)C20orf45, PRELID3B, dJ543J19.5, Q9Y3B1160%"GFP, yeast mito homolog+, mito protein domain+, induction, coexpression"none
4709NDUFB3"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 3, 12kDa"B12, CI-B12, O43676160%"literature, APEX_IMS, APEX_matrix, mito protein domain+, coexpression+, MS/MS++"all 14
25996REXO2RNA exonuclease 2REX2, RFN, SFN, Q9Y3B8160%"APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MS+"all 14
2628GATMglycine amidinotransferase (L-arginine:glycine amidinotransferase)AGAT, AT, CCDS3, P50440160%"literature, targetP signal, mito protein domain+, MS/MS++"spinalcord, kidney, liver, stomach, placenta, testis
26515TIMM10Btranslocase of inner mitochondrial membrane 10 homolog B (yeast)FXC1, TIM10B, Tim9b, Q9Y5J6160%"literature, APEX_IMS, yeast mito homolog+, mito protein domain+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, largeintestine, stomach, placenta, testis
54938SARS2"seryl-tRNA synthetase 2, mitochondrial"SARS, SARSM, SERS, SYS, SerRS, SerRSmt, mtSerRS, Q9NP81160%"literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55349CHDHcholine dehydrogenaseQ8NE62160%"APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++"spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
78988MRPL57mitochondrial ribosomal protein L57MRP63, bMRP63, Q9BQC6160%"literature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS+"cerebrum, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
414919C8orf82chromosome 8 open reading frame 82Q6P1X6160%"APEX_matrix, targetP signal, coexpression+, MS/MS++"all 14
124454EARS2"glutamyl-tRNA synthetase 2, mitochondrial"COXPD12, MSE1, Q5JPH6160%"literature, APEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression"adipose, largeintestine, placenta
9380GRHPRglyoxylate reductase/hydroxypyruvate reductaseGLXR, GLYD, PH2, Q9UBQ7160%"APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
123263MTFMTmitochondrial methionyl-tRNA formyltransferaseCOXPD15, FMT1, Q96DP5160%"literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression"none
79810PTCD2pentatricopeptide repeat domain 2Q8WV60160%"literature, mito protein domain+, induction, coexpression, MS/MS"smallintestine, largeintestine, placenta
55862ECHDC1enoyl CoA hydratase domain containing 1HEL-S-76, MMCD, dJ351K20.2, Q9NTX5160%"yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"brainstem, spinalcord, liver, adipose, largeintestine, placenta, testis
23438HARS2"histidyl-tRNA synthetase 2, mitochondrial"HARSL, HARSR, HO3, PRLTS2, P49590160%"literature, APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"cerebellum, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
51079NDUFA13"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 13"B16.6, CDA016, GRIM-19, GRIM19, Q9P0J0160%"literature, APEX_IMS, mito protein domain, coexpression++, MS/MS++"all 14
4697NDUFA4"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 4, 9kDa"CI-9k, CI-MLRQ, MLRQ, O00483160%"literature, mito protein domain, coexpression++, MS/MS++"all 14
128240APOA1BPapolipoprotein A-I binding proteinAIBP, YJEFN1, Q8NCW5160%"APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++"all 14
8834TMEM11transmembrane protein 11C17orf35, PM1, PMI, P17152150%"GFP, targetP signal, mito protein domain+, induction, coexpression, MS/MS"all 14
83642SELOselenoprotein OQ9BVL4150%"targetP signal+, yeast mito homolog, mito protein domain+, coexpression"spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
162417NAGSN-acetylglutamate synthaseAGAS, ARGA, Q8N159150%"literature, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS"liver
3295HSD17B4hydroxysteroid (17-beta) dehydrogenase 4DBP, MFE-2, MPF-2, PRLTS1, SDR8C1, P51659150%"Rickettsial homolog, mito protein domain+, induction, coexpression"kidney, liver, adipose, largeintestine, stomach, testis
55471NDUFAF7"NADH dehydrogenase (ubiquinone) complex I, assembly factor 7"C2orf56, MidA, Q7L592150%"APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MS"cerebrum, brainstem, spinalcord, kidney, adipose, largeintestine, stomach, placenta, testis
4942OATornithine aminotransferaseGACR, HOGA, OATASE, OKT, P04181150%"literature, APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++"all 14
54534MRPL50mitochondrial ribosomal protein L50MRP-L50, Q8N5N7150%"literature, APEX_matrix, targetP signal, mito protein domain+, coexpression+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
1349COX7Bcytochrome c oxidase subunit VIIbAPLCC, P24311150%"literature, targetP signal, mito protein domain+, induction, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
57038RARS2"arginyl-tRNA synthetase 2, mitochondrial"ArgRS, DALRD2, PCH6, PRO1992, RARSL, dJ382I10.6, Q5T160150%"literature, APEX_matrix, GFP, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
339229OXLD1oxidoreductase-like domain containing 1C17orf90, Q5BKU9150%"targetP signal, yeast mito homolog, mito protein domain+, coexpression+"adipose, largeintestine, stomach
51110LACTB2"lactamase, beta 2"Q53H82150%"targetP signal, yeast mito homolog+, mito protein domain, induction, MS/MS+"kidney, liver, largeintestine, stomach
126328NDUFA11"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 11, 14.7kDa"B14.7, CI-B14.7, Q86Y39150%"literature, APEX_IMS, mito protein domain+, induction, MS/MS++"all 14
54998AURKAIP1aurora kinase A interacting protein 1AIP, AKIP, MRP-S38, Q9NWT8150%"GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpression+"none
79145CHCHD7coiled-coil-helix-coiled-coil-helix domain containing 7COX23, Q9BUK0150%"yeast mito homolog, induction, coexpression, MS/MS+"cerebrum, smallintestine, placenta, testis
6472SHMT2serine hydroxymethyltransferase 2 (mitochondrial)GLYA, HEL-S-51e, SHMT, P34897150%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
10797MTHFD2"methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2, methenyltetrahydrofolate cyclohydrolase"NMDMC, P13995150%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS"spinalcord, placenta, testis
51115RMDN1regulator of microtubule dynamics 1FAM82B, RMD-1, RMD1, Q96DB5150%"APEX_IMS, targetP signal+, induction, coexpression, MS/MS"all 14
1373CPS1"carbamoyl-phosphate synthase 1, mitochondrial"CPSASE1, PHN, P31327150%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++"cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
64928MRPL14mitochondrial ribosomal protein L14L14mt, L32mt, MRP-L14, MRP-L32, MRPL32, RMPL32, RPML32, Q6P1L8150%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS"all 14
51250C6orf203chromosome 6 open reading frame 203PRED31, RP11-59I9.1, Q9P0P8150%"GFP, induction, coexpression++, MS/MS+"all 14
112724RDH13retinol dehydrogenase 13 (all-trans/9-cis)SDR7C3, Q8NBN7150%"yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
79979TRMT2BtRNA methyltransferase 2 homolog B (S. cerevisiae)CXorf34, dJ341D10.3, Q96GJ1150%"GFP, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression"none
64951MRPS24mitochondrial ribosomal protein S24MRP-S24, S24mt, bMRP-47, bMRP47, Q96EL2150%"literature, APEX_matrix, induction, coexpression++, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
28958COA3cytochrome c oxidase assembly factor 3CCDC56, MITRAC12, Q9Y2R0150%"APEX_IMS, APEX_matrix, mito protein domain+, coexpression, MS/MS++"all 14
2936GSRglutathione reductaseHEL-75, P00390150%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++"spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
2021ENDOGendonuclease GQ14249150%"literature, APEX_IMS, mito protein domain, coexpression++, MS/MS"all 14
587BCAT2"branched chain amino-acid transaminase 2, mitochondrial"BCAM, BCATM, BCT2, PP18, O15382150%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
79736TEFM"transcription elongation factor, mitochondrial"C17orf42, Q96QE5150%"APEX_matrix, targetP signal, induction, coexpression++, MS/MS"liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
80221ACSF2acyl-CoA synthetase family member 2ACSMW, AVYV493, Q96CM8150%"APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
55687TRMUtRNA 5-methylaminomethyl-2-thiouridylate methyltransferaseMTO2, MTU1, TRMT, TRMT1, TRNT1, O75648150%"literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression"adipose, largeintestine, placenta
56945MRPS22mitochondrial ribosomal protein S22C3orf5, COXPD5, GIBT, MRP-S22, RPMS22, P82650150%"literature, APEX_matrix, mito protein domain+, induction, coexpression, MS/MS"all 14
51056LAP3leucine aminopeptidase 3HEL-S-106, LAP, LAPEP, PEPS, P28838150%"APEX_matrix, targetP signal+, Rickettsial homolog, coexpression, MS/MS++"all 14
2746GLUD1glutamate dehydrogenase 1GDH, GDH1, GLUD, P00367140%"literature, APEX_matrix, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
3155HMGCL3-hydroxymethyl-3-methylglutaryl-CoA lyaseHL, P35914140%"literature, APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++"all 14
2272FHITfragile histidine triadAP3Aase, FRA3B, P49789140%"yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
51650MRPS33mitochondrial ribosomal protein S33MRP-S33, PTD003, S33mt, Q9Y291140%"literature, targetP signal, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
80224NUBPLnucleotide binding protein-likeC14orf127, IND1, huInd1, Q8TB37140%"literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+"spinalcord, adipose, largeintestine, stomach, placenta, testis
57226LYRM2LYR motif containing 2DJ122O8.2, Q9NU23140%"APEX_matrix, GFP, targetP signal+, mito protein domain+, coexpression, MS/MS"heart, adipose, largeintestine, placenta
255027MPV17LMPV17 mitochondrial membrane protein-likeM-LPH, MLPH1, MLPH2, MPV17L1, Q2QL34140%"targetP signal, yeast mito homolog+, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver
90480GADD45GIP1"growth arrest and DNA-damage-inducible, gamma interacting protein 1"CKBBP2, CKbetaBP2, CRIF1, MRP-L59, PLINP, PLINP-1, PRG6, Plinp1, Q8TAE8140%"APEX_matrix, GFP, targetP signal, coexpression+, MS/MS++"all 14
7019TFAM"transcription factor A, mitochondrial"MTTF1, MTTFA, TCF6, TCF6L1, TCF6L2, TCF6L3, Q00059140%"literature, APEX_matrix, targetP signal, mito protein domain, induction, MS/MS++"all 14
5832ALDH18A1"aldehyde dehydrogenase 18 family, member A1"ARCL3A, GSAS, P5CS, PYCS, P54886140%"literature, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
80222TARS2"threonyl-tRNA synthetase 2, mitochondrial (putative)"TARSL1, thrRS, Q9BW92140%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
56267CCBL2cysteine conjugate-beta lyase 2KAT3, KATIII, RP4-531M19.2, Q6YP21140%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++"spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
54995OXSM"3-oxoacyl-ACP synthase, mitochondrial"FASN2D, KASI, KS, Q9NWU1140%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++"liver, heart, adipose, smallintestine, largeintestine, placenta, testis
9238TBRG4transforming growth factor beta regulator 4CPR2, FASTKD4, Q969Z0140%"literature, APEX_matrix, targetP signal+, coexpression, MS/MS++"all 14
157378TMEM65transmembrane protein 65Q6PI78140%"literature, APEX_matrix, targetP signal+, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
140823ROMO1reactive oxygen species modulator 1C20orf52, MTGM, MTGMP, bA353C18.2, P60602140%"literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
25824PRDX5peroxiredoxin 5ACR1, AOEB166, B166, HEL-S-55, PLP, PMP20, PRDX6, PRXV, prx-V, P30044140%"literature, APEX_matrix, targetP signal, mito protein domain, induction, MS/MS++"all 14
29103DNAJC15"DnaJ (Hsp40) homolog, subfamily C, member 15"DNAJD1, HSD18, MCJ, Q9Y5T4140%"GFP, mito protein domain, induction, coexpression, MS/MS+"cerebrum, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
79568C2orf47chromosome 2 open reading frame 47Q8WWC4140%"GFP, targetP signal, induction, coexpression, MS/MS+"all 14
25994HIGD1A"HIG1 hypoxia inducible domain family, member 1A"HIG1, RCF1a, Q9Y241140%"literature, APEX_IMS, mito protein domain+, induction, MS/MS++"all 14
283951C16orf91chromosome 16 open reading frame 91CCSMST1, gs103, Q4G0I0140%"APEX_IMS, targetP signal+, induction, coexpression, MS/MS"brainstem, spinalcord, adipose, largeintestine, placenta, testis
89941RHOT2ras homolog family member T2ARHT2, C16orf39, MIRO-2, MIRO2, RASL, Q8IXI1140%"literature, mito protein domain+, induction, coexpression"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
9673SLC25A44"solute carrier family 25, member 44"RP11-54H19.3, Q96H78140%"yeast mito homolog+, mito protein domain+, induction, MS/MS"placenta
51179HAO2hydroxyacid oxidase 2 (long chain)GIG16, HAOX2, Q9NYQ3140%"yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS"kidney, largeintestine, testis
5018OXA1Loxidase (cytochrome c) assembly 1-likeOXA1, Q15070140%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression"cerebrum, brainstem, spinalcord, kidney, heart, adipose, smallintestine, largeintestine, placenta, testis
91137SLC25A46"solute carrier family 25, member 46"Q96AG3140%"yeast mito homolog++, mito protein domain+, induction"cerebrum, spinalcord, adipose, placenta
57665RDH14retinol dehydrogenase 14 (all-trans/9-cis/11-cis)PAN2, SDR7C4, Q9HBH5140%"yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, smallintestine, largeintestine, stomach, placenta, testis
9556C14orf2chromosome 14 open reading frame 2MP68, PLPM, P56378140%"induction, coexpression++, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
80347COASYCoA synthaseDPCK, NBP, PPAT, UKR1, pOV-2, Q13057140%"APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
284106CISD3CDGSH iron sulfur domain 3Miner2, P0C7P0140%"APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++"all 14
11238CA5B"carbonic anhydrase VB, mitochondrial"CA-VB, Q9Y2D0140%"literature, targetP signal, mito protein domain, coexpression, MS/MS++"cerebellum, spinalcord, kidney, adipose, stomach, placenta, testis
2954GSTZ1glutathione S-transferase zeta 1GSTZ1-1, MAAI, MAI, O43708140%"APEX_matrix, mito protein domain, coexpression, MS/MS++"all 14
125965COX6B2cytochrome c oxidase subunit VIb polypeptide 2 (testis)COXVIB2, CT59, Q6YFQ2140%"literature, yeast mito homolog+, mito protein domain+, MS/MS+"testis
51031GLOD4glyoxalase domain containing 4C17orf25, HC71, Q9HC38140%"APEX_matrix, targetP signal+, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
30ACAA1acetyl-CoA acyltransferase 1ACAA, PTHIO, THIO, P09110140%"yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression"kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
54677CROTcarnitine O-octanoyltransferaseCOT, Q9UKG9140%"yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS"kidney, liver
64146PDFpeptide deformylase (mitochondrial)Q9HBH1140%"APEX_matrix, Rickettsial homolog, mito protein domain+, coexpression, MS/MS"cerebrum, heart, skeletalmuscle, adipose, largeintestine, placenta, testis
90639COX19cytochrome c oxidase assembly homolog 19 (S. cerevisiae)Q49B96130%"yeast mito homolog, mito protein domain, induction, coexpression+, MS/MS"liver, placenta
275AMTaminomethyltransferaseGCE, GCST, GCVT, NKH, P48728130%"targetP signal+, mito protein domain, MS/MS++"cerebrum, brainstem, spinalcord, kidney, liver, largeintestine, stomach, placenta
57486NLNneurolysin (metallopeptidase M3 family)AGTBP, EP24.16, MEP, MOP, Q9BYT8130%"literature, APEX_matrix, targetP signal+, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55066PDPRpyruvate dehydrogenase phosphatase regulatory subunitPDP3, Q8NCN5130%"APEX_matrix, targetP signal+, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
51027BOLA1bolA family member 1Q9Y3E2130%"GFP, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebrum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
212ALAS2"aminolevulinate, delta-, synthase 2"ALAS-E, ALASE, ANH1, ASB, XLDPP, XLEPP, XLSA, P22557130%"literature, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression"none
134266GRPEL2"GrpE-like 2, mitochondrial (E. coli)"Mt-GrpE#2, Q8TAA5130%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain+"placenta
501ALDH7A1"aldehyde dehydrogenase 7 family, member A1"ATQ1, EPD, PDE, P49419130%"literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
27440CECR5"cat eye syndrome chromosome region, candidate 5"Q9BXW7130%"APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++"cerebellum, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
83943IMMP2LIMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae)IMMP2L-IT1, IMP2, IMP2-LIKE, Q96T52130%"literature, yeast mito homolog++, mito protein domain, coexpression, MS/MS"cerebellum, brainstem, liver, skeletalmuscle, adipose, largeintestine, testis
2671GFER"growth factor, augmenter of liver regeneration"ALR, ERV1, HERV1, HPO, HPO1, HPO2, HSS, P55789130%"literature, GFP, yeast mito homolog++, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
84701COX4I2cytochrome c oxidase subunit IV isoform 2 (lung)COX4, COX4-2, COX4B, COX4L2, COXIV-2, dJ857M17.2, Q96KJ9130%"literature, targetP signal, yeast mito homolog++, mito protein domain+"cerebrum, spinalcord, heart, adipose, largeintestine, stomach, placenta
54148MRPL39mitochondrial ribosomal protein L39C21orf92, L39mt, MRP-L5, MRPL5, PRED22, PRED66, RPML5, Q9NYK5130%"literature, APEX_matrix, targetP signal, Rickettsial homolog, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
51166AADATaminoadipate aminotransferaseKAT2, KATII, Q8N5Z0130%"targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"kidney, liver
65991FUNDC2FUN14 domain containing 2DC44, HCBP6, HCC3, PD03104, Q9BWH2130%"mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
10434LYPLA1lysophospholipase IAPT-1, APT1, LPL-I, LPL1, hAPT1, O75608130%"Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
5161PDHA2pyruvate dehydrogenase (lipoamide) alpha 2PDHAL, P29803130%"targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+"none
84705GTPBP3GTP binding protein 3 (mitochondrial)GTPBG3, MSS1, MTGP1, THDF1, Q969Y2130%"literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain"largeintestine
54516MTRF1Lmitochondrial translational release factor 1-likeHMRF1L, MRF1L, mtRF1a, Q9UGC7130%"literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain"testis
441024MTHFD2Lmethylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2-likeQ9H903130%"literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain"spinalcord, placenta
10730YME1L1YME1-like 1 ATPaseFTSH, MEG4, PAMP, YME1L, Q96TA2130%"literature, APEX_IMS, Rickettsial homolog, mito protein domain+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
10965ACOT2acyl-CoA thioesterase 2CTE-IA, CTE1A, MTE1, PTE2, PTE2A, ZAP128, P49753130%"literature, mito protein domain, induction, coexpression, MS/MS++"all 14
84334APOPT1"apoptogenic 1, mitochondrial"APOP1, C14orf153, Q96IL0130%"literature, targetP signal, mito protein domain+, coexpression+"largeintestine, placenta
326625MMABmethylmalonic aciduria (cobalamin deficiency) cblB typeATR, cblB, cob, Q96EY8130%"APEX_matrix, GFP, targetP signal, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
5498PPOXprotoporphyrinogen oxidasePPO, V290M, VP, P50336130%"literature, APEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MS"cerebrum, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
5825ABCD3"ATP-binding cassette, sub-family D (ALD), member 3"ABC43, PMP70, PXMP1, ZWS2, P28288130%"GFP, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression"kidney, liver, adipose, placenta, testis
23410SIRT3sirtuin 3SIR2L3, Q9NTG7130%"literature, APEX_matrix, mito protein domain, induction, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
197257LDHDlactate dehydrogenase DDLD, Q86WU2130%"literature, yeast mito homolog+, mito protein domain, MS/MS++"kidney, liver, heart, adipose, stomach, placenta, testis
84311MRPL45mitochondrial ribosomal protein L45L45mt, MRP-L45, B4DEF8130%"literature, APEX_matrix, mito protein domain, induction, coexpression, MS/MS+"cerebrum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
91574C12orf65chromosome 12 open reading frame 65COXPD7, SPG55, Q9H3J6130%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta
196294IMMP1LIMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae)IMP1, IMP1-LIKE, Q96LU5130%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"testis
5428POLG"polymerase (DNA directed), gamma"MDP1, MIRAS, MTDPS4A, MTDPS4B, PEO, POLG1, POLGA, SANDO, SCAE, P54098130%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MS"cerebrum, cerebellum, spinalcord, liver, adipose, largeintestine, placenta, testis
64756ATPAF1ATP synthase mitochondrial F1 complex assembly factor 1ATP11, ATP11p, Q5TC12130%"literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS"cerebrum, brainstem, spinalcord, adipose, smallintestine, largeintestine, placenta, testis
2647BLOC1S1"biogenesis of lysosomal organelles complex-1, subunit 1"BLOS1, GCN5L1, MICoA, RT14, P78537130%"mito protein domain, coexpression++, MS/MS"placenta, testis
160428ALDH1L2"aldehyde dehydrogenase 1 family, member L2"mtFDH, Q3SY69130%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS"brainstem, spinalcord, liver, skeletalmuscle, smallintestine, largeintestine, stomach, placenta
285521COX18COX18 cytochrome C oxidase assembly factorCOX18HS, Q8N8Q8130%"literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression"none
1371CPOXcoproporphyrinogen oxidaseCPO, CPX, HCP, P36551130%"literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
23530NNTnicotinamide nucleotide transhydrogenaseGCCD4, Q13423130%"literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+"cerebrum, spinalcord, skeletalmuscle, adipose, placenta
284184C17orf89chromosome 17 open reading frame 89A1L188130%"targetP signal, induction, coexpression+, MS/MS"adipose, stomach
91419XRCC6BP1XRCC6 binding protein 1KUB3, Q9Y6H3130%"yeast mito homolog++, mito protein domain+, coexpression"cerebellum
79877DCAKDdephospho-CoA kinase domain containingQ8WVC6130%"GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS"all 14
9551ATP5J2"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit F2"ATP5JL, P56134130%"literature, coexpression++, MS/MS++"all 14
6566SLC16A1"solute carrier family 16 (monocarboxylate transporter), member 1"HHF7, MCT, MCT1, P53985130%"yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS"smallintestine, largeintestine, placenta
81855SFXN3sideroflexin 3BA108L7.2, SFX3, Q9BWM7130%"mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
83752LONP2"lon peptidase 2, peroxisomal"LONP, LONPL, Q86WA8130%"yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression"kidney, liver, adipose
10157AASSaminoadipate-semialdehyde synthaseLKR/SDH, LKRSDH, LORSDH, Q9UDR5130%"APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
56616DIABLO"diablo, IAP-binding mitochondrial protein"DFNA64, SMAC, Q9NR28130%"literature, APEX_IMS, targetP signal+, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
341947COX8Ccytochrome c oxidase subunit VIIICCOX8-3, Q7Z4L0130%"literature, targetP signal+, mito protein domain+, MS/MS"testis
5827PXMP2"peroxisomal membrane protein 2, 22kDa"PMP22, Q9NR77130%"GFP, targetP signal, yeast mito homolog+, mito protein domain, induction"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
64902AGXT2alanine--glyoxylate aminotransferase 2AGT2, DAIBAT, Q9BYV1130%"literature, yeast mito homolog++, mito protein domain, MS/MS+"kidney, liver
27165GLS2"glutaminase 2 (liver, mitochondrial)"GA, GLS, LGA, hLGA, Q9UI32130%"targetP signal, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, smallintestine, largeintestine
79135APOOapolipoprotein OFAM121B, Q9BUR5130%"literature, APEX_IMS, mito protein domain+, MS/MS++"all 14
84129ACAD11"acyl-CoA dehydrogenase family, member 11"ACAD-11, Q709F0130%"mito protein domain+, induction, coexpression"spinalcord, kidney, liver, adipose
401207C5orf63chromosome 5 open reading frame 63YDR286C, A6NC05130%"targetP signal+, coexpression+, MS/MS"cerebrum, cerebellum, spinalcord, liver, heart, skeletalmuscle, adipose, placenta, testis
112817HOGA14-hydroxy-2-oxoglutarate aldolase 1C10orf65, DHDPS2, DHDPSL, HP3, NPL2, Q86XE5130%"GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS"kidney, liver, adipose, largeintestine, placenta, testis
54902TTC19tetratricopeptide repeat domain 192010204O13Rik, MC3DN2, Q6DKK2130%"literature, APEX_IMS, targetP signal+, mito protein domain, induction, MS/MS+"cerebrum, cerebellum, spinalcord, adipose, largeintestine, stomach, testis
51335NGRN"neugrin, neurite outgrowth associated"DSC92, Q9NPE2120%"APEX_matrix, yeast mito homolog++, mito protein domain+, coexpression"none
285343TCAIM"T cell activation inhibitor, mitochondrial"C3orf23, TOAG-1, TOAG1, Q8N3R3120%"literature, APEX_matrix, targetP signal, mito protein domain+, coexpression++"none
2653GCSHglycine cleavage system protein H (aminomethyl carrier)GCE, NKH, P23434120%"literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, MS/MS"spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
23408SIRT5sirtuin 5SIR2L5, Q9NXA8120%"literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"cerebrum, brainstem, spinalcord, liver, heart, adipose, largeintestine, stomach
84706GPT2glutamic pyruvate transaminase (alanine aminotransferase) 2ALT2, Q8TD30120%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, brainstem, liver, skeletalmuscle, adipose, stomach, placenta, testis
100188893TOMM6translocase of outer mitochondrial membrane 6 homolog (yeast)OBTP, Q96B49120%"GFP, mito protein domain+, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
26355FAM162A"family with sequence similarity 162, member A"C3orf28, E2IG5, HGTD-P, Q96A26120%"APEX_IMS, APEX_matrix, targetP signal, induction, coexpression, MS/MS++"all 14
10058ABCB6"ATP-binding cassette, sub-family B (MDR/TAP), member 6"ABC, ABC14, DUH3, LAN, MCOPCB7, MTABC3, PRP, umat, Q9NP58120%"literature, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, brainstem, liver, largeintestine, stomach, placenta, testis
28992MACROD1MACRO domain containing 1LRP16, Q9BQ69120%"APEX_matrix, targetP signal+, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
7263TSTthiosulfate sulfurtransferase (rhodanese)RDS, Q16762120%"literature, APEX_matrix, Rickettsial homolog, mito protein domain, coexpression, MS/MS++"all 14
4512COX1cytochrome c oxidase subunit ICOI, MTCO1, P00395120%"literature, APEX_IMS, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS"all 14
56181MTFR1Lmitochondrial fission regulator 1-likeFAM54B, MST116, MSTP116, Q9H019120%"mito protein domain+, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, placenta, testis
56948SDR39U1"short chain dehydrogenase/reductase family 39U, member 1"C14orf124, HCDI, Q9NRG7120%"mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
29958DMGDHdimethylglycine dehydrogenaseDMGDHD, ME2GLYDH, Q9UI17120%"literature, targetP signal, mito protein domain, MS/MS++"spinalcord, kidney, liver, smallintestine, stomach, placenta
10650SLMO1slowmo homolog 1 (Drosophila)C18orf43, HFL-EDDG1, PRELID3A, Q96N28120%"yeast mito homolog+, mito protein domain+, MS/MS"cerebrum, cerebellum, spinalcord
9016SLC25A14"solute carrier family 25 (mitochondrial carrier, brain), member 14"BMCP1, UCP5, O95258120%"literature, yeast mito homolog+, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, placenta, testis
10478SLC25A17"solute carrier family 25 (mitochondrial carrier; peroxisomal membrane protein, 34kDa), member 17"PMP34, O43808120%"yeast mito homolog++, mito protein domain+, coexpression"none
84269CHCHD5coiled-coil-helix-coiled-coil-helix domain containing 5C2orf9, MIC14, Q9BSY4120%"APEX_IMS, yeast mito homolog++, mito protein domain, coexpression, MS/MS"adipose, placenta, testis
9868TOMM70Atranslocase of outer mitochondrial membrane 70 homolog A (S. cerevisiae)O94826120%"literature, yeast mito homolog+, mito protein domain, induction, coexpression"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
4817NIT1nitrilase 1Q86X76120%"APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
81889FAHD1fumarylacetoacetate hydrolase domain containing 1C16orf36, YISKL, Q6P587120%"literature, APEX_matrix, mito protein domain, coexpression, MS/MS++"all 14
90550MCUmitochondrial calcium uniporterC10orf42, CCDC109A, Q8NE86120%"literature, GFP, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
1593CYP27A1"cytochrome P450, family 27, subfamily A, polypeptide 1"CP27, CTX, CYP27, Q02318120%"literature, targetP signal+, mito protein domain, MS/MS++"kidney, liver, skeletalmuscle, adipose, smallintestine, placenta, testis
4540ND5"NADH dehydrogenase, subunit 5 (complex I)"MTND5, P03915120%"literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain+, MS/MS+"all 14
4538ND4"NADH dehydrogenase, subunit 4 (complex I)"MTND4, P03905120%"literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain+, MS/MS+"all 14
4536ND2MTND2MTND2, P03891120%"literature, Rickettsial homolog, mito protein domain+, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4190MDH1"malate dehydrogenase 1, NAD (soluble)"HEL-S-32, MDH-s, MDHA, MGC:1375, MOR2, P40925120%"Rickettsial homolog, mito protein domain, induction, coexpression+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
9812KIAA0141KIAA0141DELE, Q14154120%"targetP signal+, mito protein domain, induction, coexpression"none
79675FASTKD1FAST kinase domains 1Q53R41120%"APEX_matrix, induction, coexpression++"liver, largeintestine
10240MRPS31mitochondrial ribosomal protein S31IMOGN38, MRP-S31, S31mt, Q92665110%"literature, APEX_matrix, targetP signal, induction, coexpression, MS/MS"all 14
10840ALDH1L1"aldehyde dehydrogenase 1 family, member L1"10-FTHFDH, 10-fTHF, FDH, FTHFD, O75891110%"APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS"cerebrum, liver, smallintestine, largeintestine, stomach, placenta, testis
26024PTCD1pentatricopeptide repeat domain 1O75127110%"targetP signal+, mito protein domain+, coexpression"cerebellum, largeintestine, placenta
3032HADHB"hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit"ECHB, MTPB, TP-BETA, P55084110%"literature, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++"all 14
54802TRIT1tRNA isopentenyltransferase 1IPT, MOD5, Q9H3H1110%"literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression"cerebellum
54675CRLS1cardiolipin synthase 1C20orf155, CLS, CLS1, GCD10, dJ967N21.6, Q9UJA2110%"literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression"none
132158GLYCTKglycerate kinaseHBEBP2, HBEBP4, HBeAgBP4A, Q8IVS8110%"targetP signal+, coexpression, MS/MS+"kidney, liver, placenta
81034SLC25A32"solute carrier family 25 (mitochondrial folate carrier), member 32"MFT, MFTC, Q9H2D1110%"literature, targetP signal, yeast mito homolog+, mito protein domain+"adipose, placenta
57505AARS2"alanyl-tRNA synthetase 2, mitochondrial"AARSL, COXPD8, MT-ALARS, MTALARS, Q5JTZ9110%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
9941EXOG"endo/exonuclease (5'-3'), endonuclease G-like"ENDOGL1, ENDOGL2, ENGL, ENGL-a, ENGL-b, ENGLA, ENGLB, Q9Y2C4110%"APEX_IMS, targetP signal, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, placenta
51142CHCHD2coiled-coil-helix-coiled-coil-helix domain containing 2C7orf17, Q9Y6H1110%"APEX_IMS, targetP signal, yeast mito homolog+, mito protein domain, coexpression"none
8564KMOkynurenine 3-monooxygenase (kynurenine 3-hydroxylase)dJ317G22.1, O15229110%"yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++"kidney, liver
94097SFXN5sideroflexin 5BBG-TCC, Q8TD22110%"literature, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine
60528ELAC2elaC ribonuclease Z 2COXPD17, ELC2, HPC2, Q9BQ52110%"APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, MS/MS"cerebellum, skeletalmuscle, adipose, largeintestine, stomach
2876GPX1glutathione peroxidase 1GPXD, GSHPX1, P07203110%"literature, APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
1375CPT1Bcarnitine palmitoyltransferase 1B (muscle)CPT1-M, CPT1M, CPTI, CPTI-M, M-CPT1, MCCPT1, MCPT1, Q92523110%"literature, yeast mito homolog+, mito protein domain, MS/MS++"cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4199ME1"malic enzyme 1, NADP(+)-dependent, cytosolic"HUMNDME, MES, P48163110%"yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression"spinalcord, liver, adipose, placenta, testis
51024FIS1fission 1 (mitochondrial outer membrane) homolog (S. cerevisiae)TTC11, Q9Y3D6110%"literature, yeast mito homolog++, mito protein domain+"all 14
27166PRELID1PRELI domain containing 1PRELI, PX19, SBBI12, Q9Y255110%"literature, APEX_IMS, GFP, targetP signal, yeast mito homolog++, mito protein domain+"none
9481SLC25A27"solute carrier family 25, member 27"UCP4, O95847110%"literature, yeast mito homolog+, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord
79085SLC25A23"solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 23"APC2, MCSC2, SCaMC-3, Q9BV35110%"literature, yeast mito homolog+, mito protein domain+, MS/MS"cerebrum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta
7352UCP3"uncoupling protein 3 (mitochondrial, proton carrier)"SLC25A9, P55916110%"literature, yeast mito homolog+, mito protein domain+, MS/MS"spinalcord, heart, skeletalmuscle, adipose
55972SLC25A40"solute carrier family 25, member 40"MCFP, Q8TBP6110%"literature, yeast mito homolog+, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
51409HEMK1HemK methyltransferase family member 1HEMK, MTQ1, Q9Y5R4110%"GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+"none
55186SLC25A36"solute carrier family 25 (pyrimidine nucleotide carrier ), member 36"PNC2, Q96CQ1110%"GFP, yeast mito homolog+, mito protein domain+, coexpression"brainstem, spinalcord, placenta, testis
115209OMA1OMA1 zinc metallopeptidase2010001O09Rik, DAB1, MPRP-1, YKR087C, ZMPOMA1, peptidase, Q96E52110%"APEX_IMS, GFP, targetP signal+, yeast mito homolog++, coexpression"skeletalmuscle, adipose, largeintestine
137994LETM2leucine zipper-EF-hand containing transmembrane protein 2Q2VYF4110%"targetP signal, yeast mito homolog+, mito protein domain+"none
115817DHRS1dehydrogenase/reductase (SDR family) member 1SDR19C1, Q96LJ7110%"Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
2040STOMstomatinBND7, EPB7, EPB72, P27105110%"yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS"adipose, placenta, testis
29081METTL5methyltransferase like 5HSPC133, Q9NRN9100%"Rickettsial homolog, mito protein domain+, induction, coexpression"none
4482MSRAmethionine sulfoxide reductase APMSR, Q9UJ68100%"mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
349565NMNAT3nicotinamide nucleotide adenylyltransferase 3PNAT-3, PNAT3, Q96T66100%"literature, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
254552NUDT8nudix (nucleoside diphosphate linked moiety X)-type motif 8Q8WV74100%"APEX_matrix, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
54977SLC25A38"solute carrier family 25, member 38"Q96DW6100%"yeast mito homolog++, mito protein domain+, coexpression"none
84769MPV17L2MPV17 mitochondrial membrane protein-like 2FKSG24, Q567V2100%"GFP, targetP signal, yeast mito homolog+, mito protein domain, coexpression"largeintestine, placenta
47ACLYATP citrate lyaseACL, ATPCL, CLATP, P53396100%"APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
225ABCD2"ATP-binding cassette, sub-family D (ALD), member 2"ABC39, ALDL1, ALDR, ALDRP, hALDR, Q9UBJ2100%"targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS+"adipose
80308FLAD1flavin adenine dinucleotide synthetase 1FAD1, FADS, RP11-307C12.7, Q8NFF5100%"APEX_matrix, targetP signal, mito protein domain, induction, coexpression"spinalcord, adipose, stomach
51601LIPT1lipoyltransferase 1Q9Y234100%"GFP, yeast mito homolog++, mito protein domain, coexpression"adipose, placenta
80017C14orf159chromosome 14 open reading frame 159Q7Z3D6100%"literature, APEX_matrix, targetP signal, coexpression, MS/MS++"all 14
5106PCK2phosphoenolpyruvate carboxykinase 2 (mitochondrial)PEPCK, PEPCK-M, PEPCK2, Q16822100%"literature, targetP signal, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
133686NADK2"NAD kinase 2, mitochondrial"C5orf33, MNADK, NADKD1, Q4G0N4100%"APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
3099HK2hexokinase 2HKII, HXK2, P52789100%"literature, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4357MPSTmercaptopyruvate sulfurtransferaseMST, TST2, P25325100%"APEX_matrix, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
25961NUDT13nudix (nucleoside diphosphate linked moiety X)-type motif 13Q86X67100%"GFP, targetP signal, mito protein domain, induction, coexpression, MS/MS"cerebellum, brainstem, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
31ACACAacetyl-CoA carboxylase alphaACAC, ACACAD, ACC, ACC1, ACCA, Q13085100%"targetP signal, Rickettsial homolog, mito protein domain, coexpression"brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
7915ALDH5A1"aldehyde dehydrogenase 5 family, member A1"SSADH, SSDH, P51649100%"APEX_matrix, targetP signal, mito protein domain, MS/MS++"all 14
548596CKMT1A"creatine kinase, mitochondrial 1A"CKMT1100%"literature, targetP signal, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
3158HMGCS23-hydroxy-3-methylglutaryl-CoA synthase 2 (mitochondrial)P54868100%"literature, targetP signal, mito protein domain, MS/MS++"cerebellum, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
18ABAT4-aminobutyrate aminotransferaseGABA-AT, GABAT, NPD009, P80404100%"literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
23761PISDphosphatidylserine decarboxylaseDJ858B16, PSD, PSDC, PSSC, dJ858B16.2, Q9UG56100%"yeast mito homolog++, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
84908FAM136A"family with sequence similarity 136, member A"Q96C01100%"APEX_IMS, mito protein domain+, MS/MS++"all 14
4710NDUFB4"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 4, 15kDa"B15, CI-B15, O95168100%"literature, mito protein domain+, MS/MS++"all 14
401505TOMM5translocase of outer mitochondrial membrane 5 homolog (yeast)C9orf105, RP11-263I4.1, Tom5, bA613M10.3, Q8N4H5100%"literature, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
10975UQCR11"ubiquinol-cytochrome c reductase, complex III subunit XI"0710008D09Rik, QCR10, UQCR, O14957100%"literature, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, stomach, placenta, testis
27429HTRA2HtrA serine peptidase 2OMI, PARK13, PRSS25, O43464100%"literature, APEX_IMS, targetP signal, Rickettsial homolog, mito protein domain, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
2821GPIglucose-6-phosphate isomeraseAMF, GNPI, NLK, PGI, PHI, SA-36, SA36, P06744100%"yeast mito homolog++, induction, coexpression"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
4694NDUFA1"NADH dehydrogenase (ubiquinone) 1 alpha subcomplex, 1, 7.5kDa"CI-MWFE, MWFE, ZNF183, O15239101%"literature, coexpression+, MS/MS++"all 14
4519CYTBcytochrome bMTCYB, P00156101%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain"all 14
2987GUK1guanylate kinase 1GMK, Q16774101%"APEX_matrix, targetP signal, Rickettsial homolog, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach
728294D2HGDHD-2-hydroxyglutarate dehydrogenaseD2HGD, Q8N465101%"literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain"adipose, largeintestine
80207OPA3"optic atrophy 3 (autosomal recessive, with chorea and spastic paraplegia)"MGA3, Q9H6K4101%"literature, targetP signal, coexpression, MS/MS++"all 14
57016AKR1B10"aldo-keto reductase family 1, member B10 (aldose reductase)"AKR1B11, AKR1B12, ALDRLn, ARL-1, ARL1, HIS, HSI, O60218101%"induction, coexpression, MS/MS++"cerebrum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
5264PHYHphytanoyl-CoA 2-hydroxylaseLN1, LNAP1, PAHX, PHYH1, RD, O14832101%"targetP signal, induction, MS/MS++"kidney, liver, smallintestine
91942NDUFAF2"NADH dehydrogenase (ubiquinone) complex I, assembly factor 2"B17.2L, MMTN, NDUFA12L, mimitin, Q8N183101%"literature, APEX_matrix, induction, coexpression, MS/MS++"all 14
51295ECSITECSIT signalling integratorSITPEC, Q9BQ95101%"literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+"brainstem, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55486PARL"presenilin associated, rhomboid-like"PSARL, PSARL1, PSENIP2, RHBDS1, Q9H300101%"literature, yeast mito homolog++, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
28977MRPL42mitochondrial ribosomal protein L42L31MT, L42MT, MRP-L31, MRP-L42, MRP-S32, MRPL31, MRPS32, PTD007, RPML31, S32MT, Q9Y6G3101%"APEX_matrix, GFP, mito protein domain+, induction, MS/MS"liver, adipose, largeintestine, testis
3338DNAJC4"DnaJ (Hsp40) homolog, subfamily C, member 4"DANJC4, HSPF2, MCG18, Q9NNZ3101%"GFP, targetP signal+, Rickettsial homolog, mito protein domain, coexpression"largeintestine
51025PAM16presequence translocase-associated motor 16 homolog (S. cerevisiae)MAGMAS, TIM16, TIMM16, Q9Y3D7101%"literature, APEX_matrix, yeast mito homolog, MS/MS++"all 14
224ALDH3A2"aldehyde dehydrogenase 3 family, member A2"ALDH10, FALDH, SLS, P51648101%"targetP signal+, mito protein domain, coexpression"spinalcord, kidney, liver, smallintestine, largeintestine, stomach, placenta, testis
23305ACSL6acyl-CoA synthetase long-chain family member 6ACS2, FACL6, LACS 6, LACS2, LACS5, Q9UKU0101%"Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, testis
219743TYSND1trypsin domain containing 1NET41, Q2T9J0101%"targetP signal, Rickettsial homolog, mito protein domain, coexpression"liver
57380MRS2MRS2 magnesium transporterHPT, MRS2L, Q9HD2391%"APEX_matrix, GFP, targetP signal, yeast mito homolog++, coexpression"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, smallintestine, largeintestine, stomach, placenta, testis
55347ABHD10abhydrolase domain containing 10Q9NUJ191%"literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
135114HINT3histidine triad nucleotide binding protein 3HINT4, Q9NQE991%"Rickettsial homolog, mito protein domain, induction, coexpression+"brainstem, heart, skeletalmuscle
11264PXMP4"peroxisomal membrane protein 4, 24kDa"PMP24, Q9Y6I891%"targetP signal, mito protein domain+, coexpression"kidney, liver, adipose
64172OSGEPL1O-sialoglycoprotein endopeptidase-like 1Qri7, Q9H4B091%"APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression"none
318NUDT2nudix (nucleoside diphosphate linked moiety X)-type motif 2APAH1, P5058391%"mito protein domain, coexpression, MS/MS++"all 14
80777CYB5Bcytochrome b5 type B (outer mitochondrial membrane)CYB5-M, CYPB5M, OMB5, RP11-140H17.1, O4316991%"literature, mito protein domain, coexpression, MS/MS++"all 14
2926GRSF1G-rich RNA sequence binding factor 1Q1284991%"APEX_matrix, mito protein domain, induction, coexpression, MS/MS"adipose, smallintestine, largeintestine, stomach, placenta, testis
84277DNAJC30"DnaJ (Hsp40) homolog, subfamily C, member 30"WBSCR18, Q96LL991%"APEX_matrix, GFP, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, largeintestine, stomach
28973MRPS18Bmitochondrial ribosomal protein S18BC6orf14, HSPC183, HumanS18a, MRP-S18-2, MRPS18-2, PTD017, S18amt, Q9Y67691%"literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, placenta, testis
847CATcatalaseP0404091%"yeast mito homolog++, mito protein domain, coexpression"spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
84532ACSS1acyl-CoA synthetase short-chain family member 1ACAS2L, ACECS1, AceCS2L, Q9NUB191%"literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
23597ACOT9acyl-CoA thioesterase 9ACATE2, MT-ACT48, MTACT48, Q9Y30591%"literature, targetP signal, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
1716DGUOKdeoxyguanosine kinaseMTDPS3, dGK, Q1685491%"literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55312RFKriboflavin kinaseRIFK, Q969G691%"targetP signal, yeast mito homolog++, MS/MS"brainstem, spinalcord, kidney, adipose, smallintestine, largeintestine
56910STARD7StAR-related lipid transfer (START) domain containing 7GTT1, Q9NQZ591%"APEX_IMS, targetP signal, mito protein domain, induction, coexpression+"none
56994CHPT1choline phosphotransferase 1CPT, CPT1, Q8WUD691%"targetP signal, mito protein domain, induction, coexpression+"none
219938SPATA19spermatogenesis associated 19CT132, SPAS1, spergen1, Q7Z5L491%"mito protein domain+, MS/MS++"testis
51300TIMMDC1translocase of inner mitochondrial membrane domain containing 1C3orf1, Q9NPL891%"literature, APEX_IMS, APEX_matrix, mito protein domain+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4509ATP8ATP synthase F0 subunit 8ATPase8, MTATP8, P0392891%"literature, mito protein domain+, MS/MS++"all 14
10553HTATIP2"HIV-1 Tat interactive protein 2, 30kDa"CC3, SDR44U1, TIP30, Q9BUP391%"yeast mito homolog, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, liver, adipose, placenta, testis
8574AKR7A2"aldo-keto reductase family 7, member A2 (aflatoxin aldehyde reductase)"AFAR, AFAR1, AFB1-AR1, AKR7, O4348891%"APEX_matrix, targetP signal, coexpression, MS/MS++"all 14
1854DUTdeoxyuridine triphosphatasedUTPase, P3331691%"literature, targetP signal, Rickettsial homolog, MS/MS++"cerebrum, spinalcord, liver, heart, adipose, largeintestine, stomach, placenta
9703KIAA0100KIAA0100BCOX, BCOX1, CT101, Q1466791%"mito protein domain+, induction, coexpression"cerebrum, placenta
4514COX3cytochrome c oxidase IIICOIII, MTCO3, P0041491%"literature, yeast mito homolog++, Rickettsial homolog, mito protein domain"all 14
25979DHRS7Bdehydrogenase/reductase (SDR family) member 7BSDR32C1, Q6IAN091%"Rickettsial homolog, mito protein domain, induction, coexpression"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
9617MTRF1mitochondrial translational release factor 1MRF1, MTTRF1, RF1, O7557091%"literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain"adipose
55260TMEM143transmembrane protein 143Q96AN591%"targetP signal, coexpression+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta
56953NT5M"5',3'-nucleotidase, mitochondrial"dNT-2, dNT2, mdN, Q9NPB191%"literature, targetP signal, mito protein domain, induction, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, testis
55288RHOT1ras homolog family member T1ARHT1, MIRO-1, MIRO1, Q8IXI291%"literature, mito protein domain+, MS/MS+"all 14
10588MTHFS"5,10-methenyltetrahydrofolate synthetase (5-formyltetrahydrofolate cyclo-ligase)"HsT19268, P4991491%"targetP signal, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta
4833NME4NME/NM23 nucleoside diphosphate kinase 4NDPK-D, NM23H4, nm23-H4, O0074691%"APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, MS/MS"adipose, largeintestine, placenta, testis
90580C19orf52chromosome 19 open reading frame 52Q9BSF491%"targetP signal+, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, largeintestine, placenta, testis
55163PNPOpyridoxamine 5'-phosphate oxidaseHEL-S-302, PDXPO, Q9NVS991%"APEX_matrix, yeast mito homolog++, coexpression, MS/MS"brainstem, liver
3417IDH1"isocitrate dehydrogenase 1 (NADP+), soluble"HEL-216, HEL-S-26, IDCD, IDH, IDP, IDPC, PICD, O7587491%"yeast mito homolog++, Rickettsial homolog, mito protein domain"brainstem, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
221154MICU2mitochondrial calcium uptake 21110008L20Rik, EFHA1, Q8IYU891%"literature, APEX_IMS, GFP, targetP signal+, mito protein domain, MS/MS+"smallintestine, largeintestine, placenta, testis
84105PCBD2pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2DCOH2, DCOHM, PHS2, Q9H0N591%"targetP signal+, induction, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
55278QRSL1glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1GatA, Q9H0R691%"literature, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS"brainstem, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
57143ADCK1aarF domain containing kinase 1Q86TW291%"yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, spinalcord, kidney, heart, skeletalmuscle, adipose, stomach, placenta
9588PRDX6peroxiredoxin 61-Cys, AOP2, HEL-S-128m, NSGPx, PRX, aiPLA2, p29, P3004191%"yeast mito homolog++, Rickettsial homolog, mito protein domain"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, placenta, testis
7086TKTtransketolaseHEL107, TK, TKT1, P2940191%"Rickettsial homolog, mito protein domain+, induction"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, stomach, placenta, testis
8508NIPSNAP1nipsnap homolog 1 (C. elegans)Q9BPW891%"APEX_matrix, targetP signal, coexpression, MS/MS++"all 14
2617GARSglycyl-tRNA synthetaseCMT2D, DSMAV, GlyRS, HMN5, SMAD1, P4125091%"targetP signal, yeast mito homolog, mito protein domain, induction"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
123876ACSM2Aacyl-CoA synthetase medium-chain family member 2AA-923A4.1, ACSM2, Q08AH391%"targetP signal, mito protein domain, MS/MS+"kidney, liver, heart
84275SLC25A33"solute carrier family 25 (pyrimidine nucleotide carrier), member 33"BMSC-MCP, PNC1, Q9BSK291%"literature, yeast mito homolog+, mito protein domain+"brainstem, spinalcord, placenta, testis
207063DHRSXdehydrogenase/reductase (SDR family) X-linkedCXorf11, DHRS5X, DHRS5Y, DHRSXY, DHRSY, SDR46C1, Q8N5I481%"targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain"none
201229LYRM9LYR motif containing 9C17orf108, A8MSI881%"targetP signal, mito protein domain+, MS/MS"cerebellum, heart, adipose, testis
53917RAB24"RAB24, member RAS oncogene family"Q969Q582%"mito protein domain, induction, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, stomach, testis
25973PARS2"prolyl-tRNA synthetase 2, mitochondrial (putative)"MT-PRORS, Q7L3T882%"APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain"smallintestine, largeintestine, stomach
122704MRPL52mitochondrial ribosomal protein L52Q86TS982%"literature, APEX_matrix, targetP signal, coexpression, MS/MS"cerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
80324PUS1pseudouridylate synthase 1MLASA1, Q9Y60682%"APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression"none
55739CARKDcarbohydrate kinase domain containingLP3298, Q8IW4582%"GFP, targetP signal, mito protein domain, MS/MS++"all 14
2806GOT2"glutamic-oxaloacetic transaminase 2, mitochondrial"KAT4, KATIV, mitAAT, P0050582%"literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain, MS/MS++"all 14
4537ND3"NADH dehydrogenase, subunit 3 (complex I)"MTND3, P0389781%"literature, Rickettsial homolog, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
84680ACCS1-aminocyclopropane-1-carboxylate synthase homolog (Arabidopsis)(non-functional)ACS, PHACS, Q96QU681%"yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression"none
51651PTRH2peptidyl-tRNA hydrolase 2BIT1, PTH2, Q9Y3E582%"literature, yeast mito homolog, mito protein domain, MS/MS++"all 14
9489PGS1phosphatidylglycerophosphate synthase 1Q32NB882%"targetP signal, yeast mito homolog++, mito protein domain"cerebrum, spinalcord, placenta
55074OXR1oxidation resistance 1TLDC3, Q8N57382%"literature, yeast mito homolog+, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem
127018LYPLAL1lysophospholipase-like 1Q5VWZ282%"mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, placenta, testis
54943DNAJC28"DnaJ (Hsp40) homolog, subfamily C, member 28"C21orf55, C21orf78, Q9NX3682%"Rickettsial homolog, mito protein domain, coexpression+"stomach
9446GSTO1glutathione S-transferase omega 1GSTO 1-1, GSTTLp28, HEL-S-21, P28, SPG-R, P7841782%"Rickettsial homolog, mito protein domain, induction"smallintestine, stomach, placenta
2356FPGSfolylpolyglutamate synthaseQ0593282%"APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain"none
374882TMEM205transmembrane protein 205UNQ501, Q6UW6882%"yeast mito homolog, mito protein domain+, coexpression"liver, adipose
401612SLC25A53"solute carrier family 25, member 53"MCART6, Q5H9E482%"yeast mito homolog+, mito protein domain+"testis
150209AIFM3"apoptosis-inducing factor, mitochondrion-associated, 3"AIFL, Q96NN982%"literature, yeast mito homolog, Rickettsial homolog, mito protein domain+"none
4257MGST1microsomal glutathione S-transferase 1GST12, MGST, MGST-I, P1062082%"mito protein domain, coexpression, MS/MS++"cerebrum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
154664ABCA13"ATP-binding cassette, sub-family A (ABC1), member 13"Q86UQ482%"yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, brainstem, spinalcord, kidney, liver, adipose
51537MTFP1mitochondrial fission process 1MTP18, Q9UDX582%"literature, induction, coexpression, MS/MS+"all 14
10381TUBB3"tubulin, beta 3 class III"CDCBM, CDCBM1, CFEOM3, CFEOM3A, FEOM3, TUBB4, beta-4, Q1350982%"Rickettsial homolog, mito protein domain+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, stomach, placenta, testis
51287COA4cytochrome c oxidase assembly factor 4 homolog (S. cerevisiae)CHCHD8, CMC3, E2IG2, Q9NYJ182%"yeast mito homolog++, mito protein domain, MS/MS"placenta
60491NIF3L1NIF3 NGG1 interacting factor 3-like 1 (S. cerevisiae)ALS2CR1, CALS-7, Q9GZT882%"APEX_matrix, targetP signal, yeast mito homolog, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
126789PUSL1pseudouridylate synthase-like 1Q8N0Z882%"APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain"cerebrum, spinalcord, largeintestine, placenta
113675SDSLserine dehydratase-likeSDH 2, SDS-RS1, TDH, Q96GA782%"yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression"none
581BAXBCL2-associated X proteinBCL2L4, Q0781282%"literature, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, adipose, largeintestine, placenta, testis
57506MAVSmitochondrial antiviral signaling proteinCARDIF, IPS-1, IPS1, VISA, Q7Z43482%"literature, induction, coexpression+, MS/MS"brainstem, skeletalmuscle, adipose, placenta, testis
64745METTL17methyltransferase like 17METT11D1, Q9H7H082%"GFP, yeast mito homolog++, mito protein domain+"none
32ACACBacetyl-CoA carboxylase betaACC2, ACCB, HACC275, O0076372%"Rickettsial homolog, mito protein domain, coexpression+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
384ARG2arginase 2P7854072%"literature, APEX_matrix, targetP signal+, mito protein domain, MS/MS"kidney, adipose, smallintestine, largeintestine, placenta
55149MTPAPmitochondrial poly(A) polymerasePAPD1, SPAX4, Q9NVV472%"literature, APEX_matrix, targetP signal+, mito protein domain, induction"cerebrum, cerebellum, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
79714CCDC51coiled-coil domain containing 51Q96ER972%"APEX_matrix, targetP signal, MS/MS++"all 14
79783SUGCTsuccinylCoA:glutarate-CoA transferaseC7orf10, DERP13, ORF19, Q9HAC772%"APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS+"kidney, liver, testis
10059DNM1Ldynamin 1-likeDLP1, DRP1, DVLP, DYMPLE, EMPF, HDYNIV, O0042972%"literature, yeast mito homolog+, mito protein domain, induction"cerebrum, cerebellum, brainstem, spinalcord
4898NRD1nardilysin (N-arginine dibasic convertase)hNRD1, hNRD2, O4384772%"targetP signal, Rickettsial homolog, mito protein domain+"testis
55863TMEM126Btransmembrane protein 126BQ8IUX172%"targetP signal, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
387338NSUN4"NOP2/Sun domain family, member 4"RP4-603I14.2, SHTAP, Q96CB972%"APEX_matrix, targetP signal, mito protein domain, induction, coexpression"placenta
79611ACSS3acyl-CoA synthetase short-chain family member 3Q9H6R372%"Rickettsial homolog, mito protein domain, MS/MS"kidney, liver, adipose, placenta, testis
116151FAM210B"family with sequence similarity 210, member B"5A3, C20orf108, dJ1167H4.1, Q96KR672%"targetP signal, yeast mito homolog, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
79863RBFAribosome binding factor A (putative)C18orf22, HsT169, Q8N0V372%"APEX_matrix, targetP signal+, Rickettsial homolog, coexpression"none
493856CISD2CDGSH iron sulfur domain 2ERIS, Miner1, NAF-1, WFS2, ZCD2, Q8N5K172%"literature, mito protein domain, induction, coexpression"testis
254042METAP1Dmethionyl aminopeptidase type 1D (mitochondrial)MAP 1D, MAP1D, MetAP 1D, Metap1l, Q6UB2872%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression"none
10768AHCYL1adenosylhomocysteinase-like 1DCAL, IRBIT, PRO0233, XPVKONA, O4386572%"targetP signal, mito protein domain+, induction"brainstem, spinalcord, smallintestine, stomach
25934NIPSNAP3Anipsnap homolog 3A (C. elegans)NIPSNAP4, TASSC, Q9UFN072%"APEX_matrix, targetP signal+, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
64757MARC1mitochondrial amidoxime reducing component 1MOSC1, Q5VT6672%"mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
139341FUNDC1FUN14 domain containing 1Q8IVP572%"yeast mito homolog, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, skeletalmuscle, adipose, largeintestine, stomach, testis
2180ACSL1acyl-CoA synthetase long-chain family member 1ACS1, FACL1, FACL2, LACS, LACS1, LACS2, P3312172%"Rickettsial homolog, mito protein domain, coexpression"all 14
116228COX20COX20 cytochrome C oxidase assembly factorFAM36A, Q5RI1572%"literature, APEX_IMS, GFP, yeast mito homolog++, MS/MS"all 14
83693HSDL1hydroxysteroid dehydrogenase like 1SDR12C3, Q3SXM572%"GFP, Rickettsial homolog, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, stomach, placenta, testis
874CBR3carbonyl reductase 3HEL-S-25, SDR21C2, hCBR3, O7582872%"targetP signal, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, spinalcord, adipose, smallintestine, largeintestine, stomach
130916MTERFD2MTERF domain containing 2MTERF4, Q7Z6M472%"APEX_matrix, targetP signal, mito protein domain+, coexpression"none
390916NUDT19nudix (nucleoside diphosphate linked moiety X)-type motif 19RP2, A8MXV472%"APEX_matrix, targetP signal, mito protein domain, induction"kidney, liver, largeintestine, placenta
50865HEBP1heme binding protein 1HBP, HEBP, Q9NRV972%"APEX_IMS, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, liver, adipose, placenta
192111PGAM5phosphoglycerate mutase family member 5BXLBV68, Q96HS172%"APEX_IMS, mito protein domain, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, placenta, testis
114971PTPMT1"protein tyrosine phosphatase, mitochondrial 1"DUSP23, MOSP, PLIP, Q8WUK072%"literature, APEX_matrix, mito protein domain, coexpression, MS/MS++"all 14
1841DTYMKdeoxythymidylate kinase (thymidylate kinase)CDC8, PP3731, TMPK, TYMK, P2391972%"Rickettsial homolog, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
3735KARSlysyl-tRNA synthetaseCMTRIB, DFNB89, KARS1, KARS2, KRS, Q1504672%"literature, GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
6770STARsteroidogenic acute regulatory proteinSTARD1, P4967572%"literature, targetP signal, mito protein domain, coexpression, MS/MS"testis
131118DNAJC19"DnaJ (Hsp40) homolog, subfamily C, member 19"PAM18, TIM14, TIMM14, Q96DA672%"literature, APEX_matrix, mito protein domain, MS/MS++"all 14
3145HMBShydroxymethylbilane synthasePBG-D, PBGD, PORC, UPS, P0839772%"targetP signal, Rickettsial homolog, induction, coexpression"none
5009OTCornithine carbamoyltransferaseOCTD, P0048072%"literature, targetP signal, mito protein domain, MS/MS+"cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
9167COX7A2Lcytochrome c oxidase subunit VIIa polypeptide 2 likeCOX7AR, COX7RP, EB1, SIG81, O1454872%"literature, APEX_IMS, APEX_matrix, mito protein domain+, MS/MS+"all 14
51001MTERFD1MTERF domain containing 1mTERF3, Q96E2972%"literature, APEX_matrix, GFP, targetP signal, mito protein domain+, coexpression"none
118980SFXN2sideroflexin 2Q96NB272%"mito protein domain+, coexpression"kidney, liver, adipose, largeintestine, stomach, placenta, testis
2194FASNfatty acid synthaseFAS, OA-519, SDR27X1, P4932772%"Rickettsial homolog, mito protein domain, coexpression"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, stomach, placenta, testis
65018PINK1PTEN induced putative kinase 1BRPK, PARK6, Q9BXM762%"literature, targetP signal+, mito protein domain, coexpression"none
80775TMEM177transmembrane protein 177Q53S5862%"targetP signal, coexpression, MS/MS"cerebrum, adipose, stomach, placenta, testis
7296TXNRD1thioredoxin reductase 1GRIM-12, TR, TR1, TRXR1, TXNR, Q1688162%"GFP, Rickettsial homolog, mito protein domain, coexpression, MS/MS"skeletalmuscle, smallintestine, placenta, testis
79896THNSL1threonine synthase-like 1 (S. cerevisiae)TSH1, Q8IYQ762%"APEX_matrix, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, testis
2542SLC37A4"solute carrier family 37 (glucose-6-phosphate transporter), member 4"G6PT1, G6PT2, G6PT3, GSD1b, GSD1c, GSD1d, TRG-19, TRG19, O4382662%"targetP signal, Rickettsial homolog, mito protein domain, coexpression"liver
3422IDI1isopentenyl-diphosphate delta isomerase 1IPP1, IPPI1, Q1390763%"targetP signal, mito protein domain, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
2224FDPSfarnesyl diphosphate synthaseFPPS, FPS, P1432463%"targetP signal, mito protein domain, MS/MS+"liver, adipose, smallintestine, largeintestine, placenta
7156TOP3Atopoisomerase (DNA) III alphaTOP3, Q1347263%"APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain"testis
94033FTMTferritin mitochondrialMTF, Q8N4E763%"literature, targetP signal+, mito protein domain, MS/MS"testis
92483LDHAL6Blactate dehydrogenase A-like 6BLDH6B, LDHAL6, LDHL, Q9BYZ263%"targetP signal, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
6311ATXN2ataxin 2ASL13, ATX2, SCA2, TNRC13, Q9970063%"targetP signal, mito protein domain, coexpression"liver, largeintestine
9650MTFR1mitochondrial fission regulator 1CHPPR, FAM54A2, Q1539063%"literature, targetP signal, mito protein domain+, coexpression"none
23576DDAH1dimethylarginine dimethylaminohydrolase 1DDAH, HEL-S-16, O9476063%"targetP signal, mito protein domain+, coexpression"placenta, testis
23786BCL2L13BCL2-like 13 (apoptosis facilitator)BCL-RAMBO, Bcl2-L-13, MIL1, Q9BXK563%"literature, mito protein domain, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
54931TRMT10CtRNA methyltransferase 10 homolog C (S. cerevisiae)HNYA, MRPP1, RG9MTD1, Q7L0Y363%"literature, APEX_matrix, GFP, targetP signal+, mito protein domain, coexpression"largeintestine, placenta
11332ACOT7acyl-CoA thioesterase 7ACH1, ACT, BACH, CTE-II, LACH, LACH1, RP1-120G22.10, hBACH, O0015463%"targetP signal+, mito protein domain, induction"brainstem, spinalcord, adipose, largeintestine
51106TFB1M"transcription factor B1, mitochondrial"CGI75, RP11-477D19.2, mtTFB, mtTFB1, Q8WVM063%"literature, APEX_matrix, Rickettsial homolog, mito protein domain, MS/MS+"brainstem, largeintestine, placenta, testis
381ARF5ADP-ribosylation factor 5P8408563%"targetP signal, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55013CCDC109Bcoiled-coil domain containing 109BMCUb, Q9NWR863%"literature, targetP signal, mito protein domain+"placenta
56652C10orf2chromosome 10 open reading frame 2ATXN8, IOSCA, MTDPS7, PEO, PEO1, PEOA3, SANDO, SCA8, TWINL, Q96RR163%"literature, APEX_matrix, targetP signal, induction, coexpression"none
27249MMADHC"methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuria"C2orf25, CL25022, cblD, Q9H3L063%"APEX_matrix, targetP signal, induction, coexpression"none
221120ALKBH3"alkB, alkylation repair homolog 3 (E. coli)"ABH3, DEPC-1, DEPC1, PCA1, Q96Q8363%"targetP signal, mito protein domain, induction, coexpression"none
29920PYCR2"pyrroline-5-carboxylate reductase family, member 2"P5CR2, Q96C3663%"APEX_matrix, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
6222RPS18ribosomal protein S18D6S218E, HKE3, KE-3, KE3, S18, P6226963%"yeast mito homolog, Rickettsial homolog, mito protein domain"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
100131187TSTD1thiosulfate sulfurtransferase (rhodanese)-like domain containing 1KAT, Q8NFU363%"Rickettsial homolog, mito protein domain, MS/MS"kidney, smallintestine, largeintestine
51109RDH11retinol dehydrogenase 11 (all-trans/9-cis/11-cis)ARSDR1, CGI82, HCBP12, MDT1, PSDR1, RALR1, SCALD, SDR7C1, Q8TC1263%"yeast mito homolog+, Rickettsial homolog, mito protein domain"testis
27129HSPB7"heat shock 27kDa protein family, member 7 (cardiovascular)"cvHSP, Q9UBY963%"targetP signal+, mito protein domain, induction"none
57149LYRM1LYR motif containing 1A211C6.1, O4332563%"GFP, mito protein domain+, MS/MS"brainstem, testis
114876OSBPL1Aoxysterol binding protein-like 1AORP-1, ORP1, OSBPL1B, Q9BXW663%"Rickettsial homolog, mito protein domain, induction, MS/MS"cerebrum, liver, largeintestine, placenta
9401RECQL4RecQ protein-like 4RECQ4, O9476163%"targetP signal, Rickettsial homolog, mito protein domain, coexpression"none
100131801PET100PET100 homolog (S. cerevisiae)C19orf79, P0DJ0763%"literature, yeast mito homolog++, MS/MS"cerebrum, spinalcord, kidney, liver, heart, smallintestine, largeintestine, placenta
54332GDAP1ganglioside induced differentiation associated protein 1CMT4, CMT4A, CMTRIA, Q8TB3663%"APEX_IMS, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord
3098HK1hexokinase 1HK1-ta, HK1-tb, HK1-tc, HKD, HKI, HMSNR, HXK1, P1936763%"literature, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
219402MTIF3mitochondrial translational initiation factor 3IF3mt, Q9H2K063%"literature, APEX_matrix, Rickettsial homolog, mito protein domain, coexpression"largeintestine
7374UNGuracil-DNA glycosylaseDGU, HIGM4, HIGM5, UDG, UNG1, UNG15, UNG2, P1305163%"literature, targetP signal, yeast mito homolog, mito protein domain, induction"none
10249GLYATglycine-N-acyltransferaseACGNAT, CAT, GAT, Q6IB7763%"literature, mito protein domain, coexpression, MS/MS+"spinalcord, kidney, liver, placenta
6470SHMT1serine hydroxymethyltransferase 1 (soluble)CSHMT, SHMT, P3489663%"Rickettsial homolog, mito protein domain, induction, coexpression"none
79763ISOC2isochorismatase domain containing 2Q96AB363%"APEX_matrix, targetP signal, MS/MS++"all 14
5805PTS6-pyruvoyltetrahydropterin synthasePTPS, Q0339363%"targetP signal, Rickettsial homolog, coexpression"none
23398PPWD1peptidylprolyl isomerase domain and WD repeat containing 1Q96BP363%"targetP signal, yeast mito homolog++, mito protein domain"none
162515SLC16A11"solute carrier family 16, member 11"MCT11, Q8NCK763%"yeast mito homolog+, Rickettsial homolog, mito protein domain"none
516ATP5G1"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C1 (subunit 9)"ATP5A, ATP5G, P0549663%"literature, yeast mito homolog+, Rickettsial homolog, mito protein domain"none
5860QDPRquinoid dihydropteridine reductaseDHPR, PKU2, SDR33C1, P0941763%"APEX_matrix, targetP signal, mito protein domain, induction"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, stomach, placenta, testis
23457ABCB9"ATP-binding cassette, sub-family B (MDR/TAP), member 9"EST122234, TAPL, Q9NP7863%"yeast mito homolog+, Rickettsial homolog, mito protein domain"cerebrum, cerebellum, stomach, placenta, testis
9194SLC16A7"solute carrier family 16 (monocarboxylate transporter), member 7"MCT2, O6066963%"yeast mito homolog+, Rickettsial homolog, mito protein domain"stomach, testis
85865GTPBP10GTP-binding protein 10 (putative)ObgH2, A4D1E963%"APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain"largeintestine, placenta
79934ADCK4aarF domain containing kinase 4NPHS9, Q96D5363%"APEX_matrix, GFP, yeast mito homolog+, Rickettsial homolog, mito protein domain"adipose, smallintestine, largeintestine, placenta
6897TARSthreonyl-tRNA synthetaseThrRS, P2663963%"Rickettsial homolog, mito protein domain, coexpression"smallintestine
2495FTH1"ferritin, heavy polypeptide 1"FHC, FTH, FTHL6, HFE5, PIG15, PLIF, P0279463%"mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, smallintestine, largeintestine, stomach, placenta
706TSPOtranslocator protein (18kDa)BPBS, BZRP, DBI, IBP, MBR, PBR, PBS, PKBS, PTBR, mDRC, pk18, P3053663%"literature, mito protein domain, MS/MS++"spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55621TRMT1tRNA methyltransferase 1 homolog (S. cerevisiae)TRM1, Q9NXH963%"targetP signal+, mito protein domain, coexpression"none
5687PSMA6"proteasome (prosome, macropain) subunit, alpha type, 6"IOTA, PROS27, p27K, P6090063%"yeast mito homolog, mito protein domain, induction"cerebrum, cerebellum, brainstem, spinalcord
90956ADCK2aarF domain containing kinase 2AARF, Q7Z69563%"GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain"none
8310ACOX3"acyl-CoA oxidase 3, pristanoyl"O1525463%"mito protein domain+, induction"kidney, liver, adipose, testis
11021RAB35"RAB35, member RAS oncogene family"H-ray, RAB1C, RAY, Q1528663%"mito protein domain, induction, MS/MS"all 14
100130890TSTD3thiosulfate sulfurtransferase (rhodanese)-like domain containing 3RP1-199J3.3, H0UI3763%"mito protein domain, induction, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
92259MRPS36mitochondrial ribosomal protein S36MRP-S36, P8290964%"literature, APEX_matrix, MS/MS++"all 14
57546PDP2pyruvate dehyrogenase phosphatase catalytic subunit 2PPM2C2, Q9P2J964%"APEX_matrix, yeast mito homolog+, mito protein domain, coexpression"adipose
55326AGPAT51-acylglycerol-3-phosphate O-acyltransferase 51AGPAT5, LPAATE, Q9NUQ254%"literature, Rickettsial homolog, mito protein domain, induction, MS/MS"cerebellum, brainstem, spinalcord, adipose, smallintestine, largeintestine, placenta, testis
84331FAM195A"family with sequence similarity 195, member A"C16orf14, c349E10.1, Q9BUT954%"induction, coexpression+"none
284723SLC25A34"solute carrier family 25, member 34"RP11-169K16.2, Q6PIV754%"yeast mito homolog+, mito protein domain+"none
284427SLC25A41"solute carrier family 25, member 41"APC4, Q8N5S154%"yeast mito homolog+, mito protein domain+"none
203427SLC25A43"solute carrier family 25, member 43"Q8WUT954%"yeast mito homolog+, mito protein domain+"none
153328SLC25A48"solute carrier family 25, member 48"Q6ZT8954%"yeast mito homolog+, mito protein domain+"none
81894SLC25A28"solute carrier family 25 (mitochondrial iron transporter), member 28"MFRN2, MRS3/4, MRS4L, Q96A4654%"literature, yeast mito homolog+, mito protein domain+"none
7351UCP2"uncoupling protein 2 (mitochondrial, proton carrier)"BMIQ4, SLC25A8, UCPH, P5585154%"literature, yeast mito homolog+, mito protein domain+"none
51312SLC25A37"solute carrier family 25 (mitochondrial iron transporter), member 37"MFRN, MFRN1, MSC, MSCP, PRO1278, PRO1584, PRO2217, Q9NYZ254%"literature, yeast mito homolog+, mito protein domain+"none
283600SLC25A47"solute carrier family 25, member 47"C14orf68, HDMCP, Q6Q0C154%"literature, yeast mito homolog+, mito protein domain+"none
11252PACSIN2protein kinase C and casein kinase substrate in neurons 2SDPII, Q9UNF054%"Rickettsial homolog, mito protein domain, induction, coexpression"cerebrum, brainstem, spinalcord
48ACO1"aconitase 1, soluble"ACONS, HEL60, IREB1, IREBP, IREBP1, IRP1, P2139954%"Rickettsial homolog, mito protein domain, coexpression"liver, smallintestine, placenta, testis
4292MLH1mutL homolog 1COCA2, FCC2, HNPCC, HNPCC2, hMLH1, P4069254%"yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression"none
4522MTHFD1"methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1, methenyltetrahydrofolate cyclohydrolase, formyltetrahydrofolate synthetase"MTHFC, MTHFD, P1158654%"literature, Rickettsial homolog, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
60678EEFSEC"eukaryotic elongation factor, selenocysteine-tRNA-specific"EFSEC, SELB, P5777254%"yeast mito homolog+, Rickettsial homolog, mito protein domain"none
2053EPHX2"epoxide hydrolase 2, cytoplasmic"CEH, SEH, P3491354%"Rickettsial homolog, mito protein domain, coexpression"kidney, liver, heart, skeletalmuscle, adipose, smallintestine, stomach
1718DHCR2424-dehydrocholesterol reductaseDCE, Nbla03646, SELADIN1, seladin-1, Q1539254%"yeast mito homolog++, mito protein domain, coexpression"none
11164NUDT5nudix (nucleoside diphosphate linked moiety X)-type motif 5YSA1, YSA1H, YSAH1, hYSAH1, Q9UKK954%"yeast mito homolog++, mito protein domain, coexpression"none
10367MICU1mitochondrial calcium uptake 1CALC, CBARA1, EFHA3, Q9BPX654%"literature, APEX_IMS, GFP, targetP signal, mito protein domain, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
6647SOD1"superoxide dismutase 1, soluble"ALS, ALS1, HEL-S-44, IPOA, SOD, hSod1, homodimer, P0044154%"literature, mito protein domain, induction, coexpression"all 14
253190SERHL2serine hydrolase-like 2dJ222E13.1, Q9H4I854%"Rickettsial homolog, mito protein domain, MS/MS"kidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
124997WDR81WD repeat domain 81CAMRQ2, Q562E754%"targetP signal+, mito protein domain"placenta
388962BOLA3bolA family member 3MMDS2, Q53S3354%"targetP signal, mito protein domain, MS/MS"cerebrum, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
25915NDUFAF3"NADH dehydrogenase (ubiquinone) complex I, assembly factor 3"2P1, C3orf60, E3-3, Q9BU6154%"literature, targetP signal, mito protein domain, MS/MS"all 14
132299OCIAD2OCIA domain containing 2Q56VL354%MS/MS++all 14
55316RSAD1radical S-adenosyl methionine domain containing 1Q9HA9254%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression"none
57552NCEH1neutral cholesterol ester hydrolase 1AADACL1, NCEH, Q6PIU254%"targetP signal, mito protein domain, induction"cerebellum, spinalcord
84303CHCHD6coiled-coil-helix-coiled-coil-helix domain containing 6CHCM1, PPP1R23, Q9BRQ654%"literature, APEX_IMS, APEX_matrix, coexpression, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
7167TPI1triosephosphate isomerase 1HEL-S-49, TIM, TPI, TPID, P6017454%"yeast mito homolog++, induction"all 14
22868FASTKD2FAST kinase domains 2KIAA0971, Q9NYY854%"literature, APEX_matrix, induction, coexpression, MS/MS"skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
8799PEX11Bperoxisomal biogenesis factor 11 betaPEX11-BETA, PEX14B, O9601154%"targetP signal, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, placenta, testis
25880TMEM186transmembrane protein 186C16orf51, Q96B7754%"targetP signal, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
84033OBSCN"obscurin, cytoskeletal calmodulin and titin-interacting RhoGEF"ARHGEF30, UNC89, Q5VST954%"mito protein domain, induction, coexpression"cerebrum, cerebellum, kidney, skeletalmuscle, smallintestine, stomach, testis
1528CYB5Acytochrome b5 type A (microsomal)CYB5, MCB5, P0016754%"mito protein domain, coexpression, MS/MS"cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
80119PIF1PIF1 5'-to-3' DNA helicaseC15orf20, PIF, Q9H61154%"literature, targetP signal+, yeast mito homolog, mito protein domain"none
2168FABP1"fatty acid binding protein 1, liver"FABPL, L-FABP, P0714854%"mito protein domain, MS/MS++"liver, smallintestine
215ABCD1"ATP-binding cassette, sub-family D (ALD), member 1"ABC42, ALD, ALDP, AMN, P3389754%"Rickettsial homolog, mito protein domain, induction"adipose
2597GAPDHglyceraldehyde-3-phosphate dehydrogenaseG3PD, GAPD, HEL-S-162eP, P0440654%"targetP signal, yeast mito homolog, Rickettsial homolog"all 14
11212PROSCproline synthetase co-transcribed homolog (bacterial)O9490354%"APEX_matrix, coexpression, MS/MS++"all 14
9399STOML1stomatin (EPB72)-like 1SLP-1, STORP, hUNC-24, Q9UBI454%"targetP signal, Rickettsial homolog, mito protein domain+"none
1622DBI"diazepam binding inhibitor (GABA receptor modulator, acyl-CoA binding protein)"ACBD1, ACBP, CCK-RP, EP, P0710855%"mito protein domain, induction, coexpression"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
5297PI4KA"phosphatidylinositol 4-kinase, catalytic, alpha"PI4K-ALPHA, PIK4CA, pi4K230, P4235655%"yeast mito homolog, mito protein domain, induction"cerebrum, cerebellum, brainstem, spinalcord, placenta, testis
87178PNPT1polyribonucleotide nucleotidyltransferase 1COXPD13, DFNB70, OLD35, PNPASE, old-35, Q8TCS855%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain"all 14
51643TMBIM4transmembrane BAX inhibitor motif containing 4GAAP, LFG4, S1R, ZPRO, Q9HC2455%"Rickettsial homolog, mito protein domain, induction, coexpression"none
116447TOP1MT"topoisomerase (DNA) I, mitochondrial"Q969P655%"literature, APEX_matrix, targetP signal, mito protein domain, coexpression"none
123207C15orf40chromosome 15 open reading frame 40Q8WUR755%"targetP signal, Rickettsial homolog, coexpression"none
246243RNASEH1ribonuclease H1H1RNA, RNH1, O6093055%"literature, APEX_matrix, targetP signal, Rickettsial homolog, coexpression"none
10350ABCA9"ATP-binding cassette, sub-family A (ABC1), member 9"EST640918, Q8IUA755%"GFP, yeast mito homolog, Rickettsial homolog, mito protein domain"cerebrum, placenta
6342SCP2sterol carrier protein 2NLTP, NSL-TP, SCP-2, SCP-CHI, SCP-X, SCPX, P2230755%"Rickettsial homolog, mito protein domain+"brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, placenta, testis
51559NT5DC35'-nucleotidase domain containing 3TU12B1-TY, TU12B1TY, Q86UY855%"APEX_matrix, targetP signal, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, stomach, placenta, testis
5775PTPN4"protein tyrosine phosphatase, non-receptor type 4 (megakaryocyte)"MEG, PTPMEG, PTPMEG1, P2907455%"targetP signal, mito protein domain, coexpression"none
100272147CMC4C-x(9)-C motif containing 4C6.1B, MTCP1, MTCP1B, MTCP1NB, p8, p8MTCP1, P5627755%"yeast mito homolog++, mito protein domain+"none
51ACOX1"acyl-CoA oxidase 1, palmitoyl"ACOX, PALMCOX, SCOX, Q1506755%"mito protein domain+, coexpression"kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, placenta, testis
3945LDHBlactate dehydrogenase BHEL-S-281, LDH-B, LDH-H, LDHBD, TRG-5, P0719555%"Rickettsial homolog, mito protein domain, induction"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
54059YBEYybeY metallopeptidase (putative)C21orf57, P5855755%"APEX_matrix, targetP signal, Rickettsial homolog, MS/MS"largeintestine, placenta, testis
3094HINT1histidine triad nucleotide binding protein 1HINT, NMAN, PKCI-1, PRKCNH1, P4977355%"Rickettsial homolog, mito protein domain, coexpression"cerebrum, cerebellum, brainstem, spinalcord, kidney, smallintestine, placenta, testis
5313PKLR"pyruvate kinase, liver and RBC"PK1, PKL, PKR, PKRL, RPK, P3061355%"yeast mito homolog++, mito protein domain"cerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
79594MUL1mitochondrial E3 ubiquitin protein ligase 1C1orf166, GIDE, MAPL, MULAN, RNF218, RP11-401M16.2, Q969V555%"literature, mito protein domain+, induction"skeletalmuscle, largeintestine
7084TK2"thymidine kinase 2, mitochondrial"MTDPS2, MTTK, O0014255%"literature, targetP signal, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, adipose
79814AGMATagmatine ureohydrolase (agmatinase)Q9BSE546%"literature, targetP signal, mito protein domain, MS/MS+"liver, smallintestine
129607CMPK2"cytidine monophosphate (UMP-CMP) kinase 2, mitochondrial"TMPK2, TYKi, UMP-CMPK2, Q5EBM046%"literature, targetP signal+, MS/MS"spinalcord, smallintestine
637BIDBH3 interacting domain death agonistFP497, P5595746%"literature, targetP signal+, mito protein domain, coexpression"none
55333SYNJ2BPsynaptojanin 2 binding proteinARIP2, OMP25, P5710546%"APEX_IMS, mito protein domain, coexpression, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
402ARL2ADP-ribosylation factor-like 2ARFL2, P3640446%"literature, mito protein domain, coexpression, MS/MS+"cerebrum, brainstem, spinalcord, adipose, largeintestine
56947MFFmitochondrial fission factorC2orf33, GL004, Q9GZY846%"literature, induction, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, placenta, testis
51181DCXRdicarbonyl/L-xylulose reductaseDCR, HCR2, HCRII, KIDCR, P34H, SDR20C1, XR, Q7Z4W146%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain"cerebrum, cerebellum, spinalcord, heart, adipose, largeintestine, stomach, placenta, testis
53343NUDT9nudix (nucleoside diphosphate linked moiety X)-type motif 9NUDT10, Q9BW9146%"APEX_matrix, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, placenta, testis
23600AMACRalpha-methylacyl-CoA racemaseAMACRD, CBAS4, RACE, RM, Q9UHK646%"literature, mito protein domain, coexpression, MS/MS"kidney, liver, adipose, smallintestine, testis
11162NUDT6nudix (nucleoside diphosphate linked moiety X)-type motif 6ASFGF2, FGF-AS, FGF2AS, GFG-1, GFG1, P5337046%"APEX_matrix, targetP signal, mito protein domain, coexpression"none
55101ATP5SLATP5S-likeQ9NW8147%"APEX_matrix, GFP, targetP signal, induction, MS/MS"cerebrum, cerebellum, brainstem, stomach
29960FTSJ2FtsJ RNA methyltransferase homolog 2 (E. coli)FJH1, HEL97, MRM2, Q9UI4347%"literature, Rickettsial homolog, mito protein domain, coexpression"cerebrum
578BAK1BCL2-antagonist/killer 1BAK, BAK-LIKE, BCL2L7, CDN1, Q1661147%"literature, mito protein domain, MS/MS++"brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
51642MRPL48mitochondrial ribosomal protein L48HSPC290, L48MT, MRP-L48, Q96GC547%"literature, APEX_matrix, mito protein domain, MS/MS++"all 14
51205ACP6"acid phosphatase 6, lysophosphatidic"ACPL1, LPAP, PACPL1, Q9NPH047%"literature, APEX_IMS, mito protein domain, MS/MS++"cerebrum, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
4259MGST3microsomal glutathione S-transferase 3GST-III, O1488047%"APEX_IMS, mito protein domain, MS/MS++"all 14
4129MAOBmonoamine oxidase BP2733847%"literature, mito protein domain, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
1723DHODHdihydroorotate dehydrogenase (quinone)DHOdehase, POADS, URA1, Q0212747%"literature, mito protein domain, MS/MS++"cerebrum, spinalcord, kidney, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
189AGXTalanine-glyoxylate aminotransferaseAGT, AGT1, AGXT1, PH1, SPAT, SPT, TLH6, P2154947%"literature, yeast mito homolog, mito protein domain, MS/MS"liver
1727CYB5R3cytochrome b5 reductase 3B5R, DIA1, P0038747%"literature, mito protein domain, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
55794DDX28DEAD (Asp-Glu-Ala-Asp) box polypeptide 28MDDX28, Q9NUL747%"literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain"spinalcord, adipose
664BNIP3BCL2/adenovirus E1B 19kDa interacting protein 3NIP3, Q1298347%"literature, mito protein domain+, MS/MS"cerebrum, cerebellum, brainstem, heart, skeletalmuscle, adipose
8225GTPBP6GTP binding protein 6 (putative)PGPL, O4382448%"APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain"none
4595MUTYHmutY homologCYP2C, MYH, Q9UIF748%"GFP, targetP signal+, Rickettsial homolog, mito protein domain"none
1583CYP11A1"cytochrome P450, family 11, subfamily A, polypeptide 1"CYP11A, CYPXIA1, P450SCC, P0510848%"literature, mito protein domain, MS/MS+"adipose, placenta, testis
54940OCIAD1OCIA domain containing 1ASRIJ, OCIA, TPA018, Q9NX4048%"APEX_IMS, GFP, MS/MS++"all 14
79828METTL8methyltransferase like 8TIP, Q9H82548%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain"none
84881RPUSD4RNA pseudouridylate synthase domain containing 4Q96CM349%"APEX_matrix, GFP, Rickettsial homolog, mito protein domain, coexpression"placenta
10201NME6NME/NM23 nucleoside diphosphate kinase 6IPIA-ALPHA, NDK 6, NM23-H6, O75414310%"literature, APEX_matrix, GFP, Rickettsial homolog, mito protein domain, coexpression"largeintestine
23770FKBP8"FK506 binding protein 8, 38kDa"FKBP38, FKBPr38, Q14318310%"literature, mito protein domain, coexpression, MS/MS"cerebrum, brainstem, spinalcord, largeintestine, placenta, testis
79671NLRX1NLR family member X1CLR11.3, DLNB26, NOD26, NOD5, NOD9, Q86UT6310%"APEX_matrix, targetP signal, MS/MS"all 14
55572FOXRED1FAD-dependent oxidoreductase domain containing 1H17, Q96CU9310%"literature, mito protein domain, coexpression+"adipose, largeintestine, placenta, testis
64216TFB2M"transcription factor B2, mitochondrial"Hkp1, mtTFB2, Q9H5Q4310%"literature, APEX_matrix, targetP signal+, mito protein domain"placenta
152926PPM1K"protein phosphatase, Mg2+/Mn2+ dependent, 1K"BDP, MSUDMV, PP2Ckappa, PP2Cm, PTMP, UG0882E07, Q8N3J5310%"literature, targetP signal+, mito protein domain"cerebellum, liver, heart, adipose
517ATP5G2"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit C2 (subunit 9)"ATP5A, Q06055310%"literature, yeast mito homolog+, Rickettsial homolog, mito protein domain"none
4535ND1"NADH dehydrogenase, subunit 1 (complex I)"MTND1, P03886311%"literature, Rickettsial homolog, mito protein domain, MS/MS"all 14
253827MSRB3methionine sulfoxide reductase B3DFNB74, Q8IXL7311%"literature, yeast mito homolog+, mito protein domain"none
55335NIPSNAP3Bnipsnap homolog 3B (C. elegans)NIPSNAP3, Q9BS92311%"GFP, targetP signal, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
4913NTHL1nth endonuclease III-like 1 (E. coli)NTH1, OCTS3, P78549312%"literature, yeast mito homolog, Rickettsial homolog, mito protein domain"none
54708MARCH5membrane-associated ring finger (C3HC4) 5MARCH-V, MITOL, RNF153, Q9NX47312%"literature, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
119559SFXN4sideroflexin 4BCRM1, COXPD18, Q6P4A7312%"literature, mito protein domain+"cerebellum, spinalcord
293SLC25A6"solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 6"2, 3, AAC3, ANT, ANT 2, ANT 3, ANT3, ANT3Y, P12236312%"literature, yeast mito homolog+, mito protein domain+"none
4968OGG18-oxoguanine DNA glycosylaseHMMH, HOGG1, MUTM, OGH1, O15527312%"literature, targetP signal, yeast mito homolog, mito protein domain"none
81890QTRT1queuine tRNA-ribosyltransferase 1FP3235, TGT, TGUT, Q9BXR0313%"APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression"none
84883AIFM2"apoptosis-inducing factor, mitochondrion-associated, 2"AMID, PRG3, RP11-367H5.2, Q9BRQ8313%"literature, Rickettsial homolog, mito protein domain, coexpression"none
7001PRDX2peroxiredoxin 2HEL-S-2a, NKEF-B, NKEFB, PRP, PRX2, PRXII, PTX1, TDPX1, TPX1, TSA, P32119213%"GFP, Rickettsial homolog, mito protein domain, coexpression"cerebrum, cerebellum, brainstem, spinalcord, adipose, smallintestine, stomach, placenta, testis
26235FBXL4F-box and leucine-rich repeat protein 4FBL4, FBL5, MTDPS13, Q9UKA2214%"literature, mito protein domain, coexpression"adipose
57678GPAM"glycerol-3-phosphate acyltransferase, mitochondrial"GPAT, GPAT1, Q9HCL2215%"literature, mito protein domain, coexpression"cerebellum, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
84833USMG5up-regulated during skeletal muscle growth 5 homolog (mouse)DAPIT, HCVFTP2, bA792D24.4, Q96IX5215%"GFP, MS/MS++"all 14
84293FAM213A"family with sequence similarity 213, member A"C10orf58, PAMM, Q9BRX8215%"GFP, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, placenta, testis
55177RMDN3regulator of microtubule dynamics 3FAM82A2, FAM82C, RMD-3, RMD3, ptpip51, Q96TC7215%"literature, APEX_IMS, GFP, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, largeintestine, stomach, placenta, testis
27109ATP5S"ATP synthase, H+ transporting, mitochondrial Fo complex, subunit s (factor B)"ATPW, FB, HSU79253, Q99766215%"literature, APEX_matrix, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
100303755PET117PET117 homolog (S. cerevisiae)CSRP2BP, Q6UWS5215%"literature, yeast mito homolog, MS/MS"cerebrum, cerebellum, liver, adipose, largeintestine, stomach, placenta
4128MAOAmonoamine oxidase AMAO-A, P21397215%"literature, mito protein domain, MS/MS+"all 14
145853C15orf61chromosome 15 open reading frame 61A6NNL5215%"APEX_matrix, targetP signal, MS/MS"brainstem, spinalcord, skeletalmuscle, adipose, largeintestine, stomach, testis
3429IFI27"interferon, alpha-inducible protein 27"FAM14D, ISG12, ISG12A, P27, P40305215%"literature, induction, coexpression"none
25974MMACHC"methylmalonic aciduria (cobalamin deficiency) cblC type, with homocystinuria"RP11-291L19.3, cblC, Q9Y4U1215%"GFP, coexpression++"none
6210RPS15Aribosomal protein S15aS15a, P62244215%"GFP, Rickettsial homolog, mito protein domain"cerebrum, liver, smallintestine, placenta, testis
5831PYCR1pyrroline-5-carboxylate reductase 1ARCL2B, ARCL3B, P5C, P5CR, PIG45, PP222, PRO3, PYCR, P32322215%"literature, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, largeintestine, stomach, placenta, testis
1429CRYZ"crystallin, zeta (quinone reductase)"Q08257215%"APEX_matrix, mito protein domain, MS/MS"spinalcord, kidney, liver, adipose, placenta, testis
3852KRT5keratin 5CK5, DDD, DDD1, EBS2, K5, KRT5A, P13647216%"GFP, targetP signal, MS/MS+"all 14
4736RPL10Aribosomal protein L10aCsa-19, L10A, NEDD6, P62906216%"GFP, Rickettsial homolog, mito protein domain"cerebrum, cerebellum, liver, smallintestine, placenta, testis
55217TMLHE"trimethyllysine hydroxylase, epsilon"AUTSX6, BBOX2, TMLD, TMLH, TMLHED, XAP130, Q9NVH6216%"literature, APEX_matrix, mito protein domain, MS/MS"kidney, adipose, smallintestine, largeintestine, stomach, placenta, testis
9804TOMM20translocase of outer mitochondrial membrane 20 homolog (yeast)MAS20, MOM19, TOM20, Q15388216%"literature, yeast mito homolog+"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
6208RPS14ribosomal protein S14EMTB, S14, P62263216%"GFP, Rickettsial homolog, mito protein domain, MS/MS"cerebrum, cerebellum, kidney, liver, smallintestine, largeintestine, placenta, testis
65260COA7cytochrome c oxidase assembly factor 7 (putative)C1orf163, RESA1, SELRC1, Q96BR5217%"literature, APEX_IMS, mito protein domain, coexpression, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
54471MIEF1mitochondrial elongation factor 1HSU79252, MID51, SMCR7L, dJ1104E15.3, Q9NQG6119%"literature, mito protein domain, induction, coexpression"none
84419C15orf48chromosome 15 open reading frame 48FOAP-11, NMES1, Q9C002119%"GFP, mito protein domain, MS/MS+"smallintestine, largeintestine, stomach, placenta, testis
51097SCCPDHsaccharopine dehydrogenase (putative)NET11, RP11-439E19.2, Q8NBX0119%"GFP, mito protein domain, MS/MS+"cerebrum, cerebellum, brainstem, spinalcord, heart, skeletalmuscle, adipose, stomach, placenta, testis
665BNIP3LBCL2/adenovirus E1B 19kDa interacting protein 3-likeBNIP3a, NIX, O60238119%"literature, mito protein domain+, coexpression"none
60493FASTKD5FAST kinase domains 5dJ1187M17.5, Q7L8L6121%"APEX_matrix, targetP signal, coexpression"skeletalmuscle, largeintestine, placenta
11315PARK7parkinson protein 7DJ-1, DJ1, HEL-S-67p, Q99497121%"literature, mito protein domain, coexpression"all 14
5917RARSarginyl-tRNA synthetaseArgRS, DALRD1, P54136121%"GFP, Rickettsial homolog, mito protein domain, coexpression"none
23095KIF1Bkinesin family member 1BCMT2, CMT2A, CMT2A1, HMSNII, KLP, NBLST1, O60333121%"literature, mito protein domain, coexpression"cerebellum, brainstem, spinalcord, largeintestine, placenta
55744COA1cytochrome c oxidase assembly factor 1 homolog (S. cerevisiae)C7orf44, MITRAC15, Q9GZY4122%"APEX_IMS, targetP signal, mito protein domain+"none
4539ND4L"NADH dehydrogenase, subunit 4L (complex I)"MTND4L, P03901122%"literature, Rickettsial homolog, mito protein domain"heart, skeletalmuscle
84300UQCC2ubiquinol-cytochrome c reductase complex assembly factor 2C6orf125, Cbp6, M19, MNF1, bA6B20.2, Q9BRT2122%"APEX_matrix, GFP, coexpression, MS/MS"all 14
23409SIRT4sirtuin 4SIR2L4, Q9Y6E7122%"literature, targetP signal, mito protein domain"largeintestine
201626PDE12phosphodiesterase 122'-PDE, Q6L8Q7122%"APEX_matrix, targetP signal, mito protein domain"brainstem, smallintestine, largeintestine, testis
4832NME3NME/NM23 nucleoside diphosphate kinase 3DR-nm23, NDPK-C, NDPKC, NM23-H3, NM23H3, c371H6.2, Q13232122%"GFP, Rickettsial homolog, mito protein domain"cerebrum, cerebellum, brainstem, kidney, adipose, placenta, testis
22907DHX30DEAH (Asp-Glu-Ala-His) box helicase 30DDX30, RETCOR, Q7L2E3122%"literature, mito protein domain"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, largeintestine, stomach, placenta, testis
10922FASTKFas-activated serine/threonine kinaseFAST, Q14296122%"GFP, induction, coexpression"none
196074METTL15methyltransferase like 15METT5D1, A6NJ78122%"APEX_matrix, Rickettsial homolog, coexpression"largeintestine, placenta
80025PANK2pantothenate kinase 2C20orf48, HARP, HSS, NBIA1, PKAN, Q9BZ23122%"literature, targetP signal+, mito protein domain"none
1591CYP24A1"cytochrome P450, family 24, subfamily A, polypeptide 1"CP24, CYP24, HCAI, P450-CC24, Q07973122%"literature, targetP signal+, mito protein domain"none
763CA5A"carbonic anhydrase VA, mitochondrial"CA5, CAV, CAVA, P35218123%"literature, mito protein domain, MS/MS"liver
64943NT5DC25'-nucleotidase domain containing 2Q9H857123%"APEX_matrix, targetP signal, MS/MS"spinalcord, largeintestine, placenta
98ACYP2"acylphosphatase 2, muscle type"ACYM, ACYP, P14621123%"GFP, induction, MS/MS"brainstem, spinalcord, adipose
83858ATAD3B"ATPase family, AAA domain containing 3B"AAA-TOB3, TOB3, Q5T9A4123%"APEX_IMS, APEX_matrix, GFP, Rickettsial homolog, mito protein domain+"none
26995TRUB2TruB pseudouridine (psi) synthase family member 2CLONE24922, RP11-339B21.1, O95900123%"APEX_matrix, Rickettsial homolog, mito protein domain"none
118881COMTD1catechol-O-methyltransferase domain containing 1Q86VU5026%"GFP, MS/MS++"all 14
126129CPT1Ccarnitine palmitoyltransferase 1CCATL1, CPT1-B, CPT1P, CPTI-B, CPTIC, Q8TCG5026%"literature, yeast mito homolog+, mito protein domain"none
285315C3orf33chromosome 3 open reading frame 33AC3-33, Q6P1S2027%"APEX_matrix, targetP signal, MS/MS"adipose, testis
27044SND1staphylococcal nuclease and tudor domain containing 1TDRD11, p100, Q7KZF4028%"GFP, yeast mito homolog, mito protein domain"cerebrum, cerebellum, brainstem, liver, smallintestine, placenta, testis
90806ANGEL2angel homolog 2 (Drosophila)KIAA0759L, Q5VTE6030%"APEX_matrix, mito protein domain, MS/MS"adipose, smallintestine, placenta, testis
10574CCT7"chaperonin containing TCP1, subunit 7 (eta)"CCTETA, CCTH, NIP7-1, TCP1ETA, Q99832030%"GFP, Rickettsial homolog, mito protein domain"cerebrum, spinalcord, adipose, smallintestine, placenta, testis
10549PRDX4peroxiredoxin 4AOE37-2, HEL-S-97n, PRX-4, Q13162030%"APEX_IMS, Rickettsial homolog, mito protein domain"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
5034P4HB"prolyl 4-hydroxylase, beta polypeptide"DSI, ERBA2L, GIT, P4Hbeta, PDI, PDIA1, PHDB, PO4DB, PO4HB, PROHB, P07237030%"APEX_IMS, Rickettsial homolog, mito protein domain"cerebrum, brainstem, spinalcord, kidney, liver, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
27301APEX2APEX nuclease (apurinic/apyrimidinic endonuclease) 2APE2, APEXL2, XTH2, Q9UBZ4030%"literature, targetP signal, Rickettsial homolog, mito protein domain"none
10606PAICS"phosphoribosylaminoimidazole carboxylase, phosphoribosylaminoimidazole succinocarboxamide synthetase"ADE2, ADE2H1, AIRC, PAIS, P22234032%"APEX_matrix, Rickettsial homolog, coexpression"none
84709MGARPmitochondria-localized glutamic acid-rich proteinC4orf49, CESP-1, HUMMR, OSAP, Q8TDB4032%"literature, APEX_IMS, targetP signal, coexpression"none
81932HDHD3haloacid dehalogenase-like hydrolase domain containing 32810435D12Rik, C9orf158, Q9BSH5032%"APEX_matrix, MS/MS++"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, adipose, smallintestine, largeintestine, stomach, placenta, testis
118672PSTKphosphoseryl-tRNA kinaseC10orf89, Q8IV42032%"GFP, induction, coexpression+"none
1585CYP11B2"cytochrome P450, family 11, subfamily B, polypeptide 2"ALDOS, CPN2, CYP11B, CYP11BL, CYPXIB2, P-450C18, P450C18, P450aldo, P19099032%"literature, targetP signal, mito protein domain, coexpression"none
471ATIC5-aminoimidazole-4-carboxamide ribonucleotide formyltransferase/IMP cyclohydrolaseAICAR, AICARFT, HEL-S-70p, IMPCHASE, PURH, P31939034%"GFP, mito protein domain, MS/MS"adipose, testis
81554WBSCR16Williams-Beuren syndrome chromosome region 16Q96I51034%"literature, APEX_matrix, targetP signal, coexpression"placenta
222234FAM185A"family with sequence similarity 185, member A"Q8N0U4034%"APEX_matrix, targetP signal, coexpression"none
5366PMAIP1phorbol-12-myristate-13-acetate-induced protein 1APR, NOXA, Q13794034%"literature, mito protein domain+"none
51060TXNDC12thioredoxin domain containing 12 (endoplasmic reticulum)AG1, AGR1, ERP16, ERP18, ERP19, PDIA16, TLP19, hAG-1, hTLP19, O95881036%"APEX_IMS, Rickettsial homolog, mito protein domain"testis
10061ABCF2"ATP-binding cassette, sub-family F (GCN20), member 2"ABC28, EST133090, HUSSY18, Q9UG63038%"literature, Rickettsial homolog, mito protein domain"cerebrum
11022TDRKHtudor and KH domain containingTDRD2, Q9Y2W6039%"GFP, mito protein domain, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, adipose, testis
78986DUSP26dual specificity phosphatase 26 (putative)DUSP24, LDP-4, MKP8, NATA1, SKRP3, Q9BV47042%"GFP, targetP signal, mito protein domain"none
55676SLC30A6"solute carrier family 30 (zinc transporter), member 6"MST103, MSTP103, ZNT6, Q6NXT4042%"GFP, targetP signal, mito protein domain"none
1594CYP27B1"cytochrome P450, family 27, subfamily B, polypeptide 1"CP2B, CYP1, CYP1alpha, CYP27B, P450c1, PDDR, VDD1, VDDR, VDDRI, VDR, O15528042%"literature, targetP signal, mito protein domain"none
11232POLG2"polymerase (DNA directed), gamma 2, accessory subunit"HP55, MTPOLB, PEOA4, POLB, POLG-BETA, POLGB, Q9UHN1042%"literature, APEX_matrix, targetP signal, mito protein domain"none
7978MTERFmitochondrial transcription termination factorQ99551-143%"literature, APEX_matrix, mito protein domain+"none
2879GPX4glutathione peroxidase 4GPx-4, GSHPx-4, MCSP, PHGPx, snGPx, snPHGPx, P36969-143%"literature, mito protein domain"all 14
6583SLC22A4"solute carrier family 22 (organic cation/zwitterion transporter), member 4"OCTN1, Q9H015-144%"literature, mito protein domain, induction"none
1312COMTcatechol-O-methyltransferaseHEL-S-98n, P21964-144%"GFP, induction, coexpression"liver
60314C12orf10chromosome 12 open reading frame 10Gamm1, MST024, MSTP024, MYG, MYG1, Q86UA3-145%"literature, mito protein domain, coexpression"none
64847SPATA20spermatogenesis associated 20SSP411, Tisp78, Q8TB22-145%"APEX_matrix, targetP signal"testis
2787GNG5"guanine nucleotide binding protein (G protein), gamma 5"P63218-145%"GFP, MS/MS"adipose, placenta, testis
133957CCDC127coiled-coil domain containing 127Q96BQ5-145%"APEX_IMS, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
1407CRY1cryptochrome circadian clock 1PHLL1, Q16526-146%"literature, mito protein domain, coexpression"none
2182ACSL4acyl-CoA synthetase long-chain family member 4ACS4, FACL4, LACS4, MRX63, MRX68, O60488-147%"GFP, Rickettsial homolog, mito protein domain"spinalcord, kidney, placenta
92667MGME1mitochondrial genome maintenance exonuclease 1C20orf72, DDK1, MTDPS11, bA504H3.4, Q9BQP7-250%"literature, APEX_matrix, GFP, targetP signal"largeintestine, placenta
5414SEPT4septin 4ARTS, BRADEION, CE5B3, H5, MART, PNUTL2, SEP4, hCDCREL-2, O43236-251%"literature, mito protein domain"brainstem, spinalcord
9694EMC2ER membrane protein complex subunit 2KIAA0103, TTC35, Q15006-251%"GFP, mito protein domain, induction"none
80303EFHD1"EF-hand domain family, member D1"MST133, MSTP133, SWS2, Q9BUP0-251%"literature, mito protein domain, induction"none
55969C20orf24chromosome 20 open reading frame 24RIP5, Q9BUV8-252%"GFP, induction, coexpression"none
9517SPTLC2"serine palmitoyltransferase, long chain base subunit 2"HSN1C, LCB2, LCB2A, NSAN1C, SPT2, hLCB2a, O15270-252%"GFP, Rickettsial homolog, mito protein domain"none
10551AGR2anterior gradient 2AG2, GOB-4, HAG-2, HEL-S-116, PDIA17, XAG-2, O95994-253%"GFP, MS/MS"skeletalmuscle, smallintestine, largeintestine, stomach
30833NT5C"5', 3'-nucleotidase, cytosolic"DNT, DNT1, HEL74, P5N2, PN-I, PN-II, UMPH2, cdN, dNT-1, Q8TCD5-253%"GFP, mito protein domain"cerebrum, cerebellum, brainstem, spinalcord, smallintestine, largeintestine, placenta, testis
8031NCOA4nuclear receptor coactivator 4ARA70, ELE1, PTC3, RFG, Q13772-253%"GFP, targetP signal"none
129807NEU4sialidase 4Q8WWR8-253%"GFP, targetP signal"none
55750AGKacylglycerol kinaseCATC5, CTRCT38, MTDPS10, MULK, Q53H12-255%"literature, APEX_IMS, mito protein domain"cerebrum, cerebellum, brainstem, spinalcord, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta, testis
54920DUS2dihydrouridine synthase 2DUS2L, SMM1, URLC8, Q9NX74-357%"GFP, Rickettsial homolog, mito protein domain"none
10953TOMM34translocase of outer mitochondrial membrane 34HTOM34P, TOM34, URCC3, Q15785-362%"literature, mito protein domain"testis
9692KIAA0391KIAA0391MRPP3, PRORP, O15091-363%APEX_matrixspinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
84260TCHP"trichoplein, keratin filament binding"TpMs, Q9BT92-363%literaturespinalcord, largeintestine, stomach
1159CKMT1B"creatine kinase, mitochondrial 1B"CKMT, CKMT1, UMTCK-363%"literature, APEX_IMS, targetP signal, mito protein domain"none
4707NDUFB1"NADH dehydrogenase (ubiquinone) 1 beta subcomplex, 1, 7kDa"CI-MNLL, CI-SGDH, MNLL, O75438-363%"literature, mito protein domain+"none
100526740ATP5J2-PTCD1ATP5J2-PTCD1 readthroughB4DJ38-363%"APEX_matrix, mito protein domain+"none
841CASP8"caspase 8, apoptosis-related cysteine peptidase"ALPS2B, CAP4, Casp-8, FLICE, MACH, MCH5, Q14790-363%"literature, mito protein domain"none
598BCL2L1BCL2-like 1BCL-XL/S, BCL2L, BCLX, BCLXL, BCLXS, Bcl-X, PPP1R52, bcl-xL, bcl-xS, Q07817-364%"literature, mito protein domain"cerebrum, cerebellum, placenta
6165RPL35Aribosomal protein L35aDBA5, L35A, P18077-467%"GFP, targetP signal"liver, adipose, smallintestine, placenta, testis
83787ARMC10armadillo repeat containing 10PNAS-112, PNAS112, SVH, Q8N2F6-467%"GFP, MS/MS"cerebrum, cerebellum, brainstem, spinalcord, liver, adipose, largeintestine, stomach, placenta, testis
995CDC25Ccell division cycle 25CCDC25, PPP1R60, P30307-468%"APEX_IMS, mito protein domain"none
51700CYB5R2cytochrome b5 reductase 2B5R.2, Q6BCY4-469%"GFP, mito protein domain"none
10981RAB32"RAB32, member RAS oncogene family"Q13637-469%"literature, mito protein domain"none
54974THG1LtRNA-histidine guanylyltransferase 1-like (S. cerevisiae)ICF45, IHG-1, Q9NWX6-470%"literature, targetP signal, coexpression"none
26056RAB11FIP5RAB11 family interacting protein 5 (class I)GAF1, RIP11, pp75, Q9BXF6-470%"literature, targetP signal, coexpression"none
64083GOLPH3golgi phosphoprotein 3 (coat-protein)GOPP1, GPP34, MIDAS, Q9H4A6-470%"literature, induction"none
9581PREPLprolyl endopeptidase-likeQ4J6C6-470%"APEX_matrix, Rickettsial homolog"spinalcord, largeintestine
84902CEP89centrosomal protein 89kDaCCDC123, CEP123, Q96ST8-470%"literature, targetP signal"none
79072FASTKD3FAST kinase domains 3Q14CZ7-470%"APEX_matrix, targetP signal"none
4925NUCB2nucleobindin 2HEL-S-109, NEFA, P80303-471%"APEX_IMS, mito protein domain"cerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta
10312TCIRG1"T-cell, immune regulator 1, ATPase, H+ transporting, lysosomal V0 subunit A3"ATP6N1C, ATP6V0A3, Atp6i, OC-116kDa, OC116, OPTB1, RP11-802E16.3, Stv1, TIRC7, Vph1, a3, Q13488-572%"GFP, MS/MS"liver, largeintestine, stomach, placenta
4077NBR1neighbor of BRCA1 gene 11A1-3B, M17S2, Q14596-573%"APEX_IMS, coexpression"cerebellum, liver
60681FKBP10"FK506 binding protein 10, 65 kDa"FKBP65, OI11, OI6, PPIASE, hFKBP65, Q96AY3-573%"APEX_IMS, mito protein domain"none
5955RCN2"reticulocalbin 2, EF-hand calcium binding domain"E6BP, ERC-55, ERC55, TCBP49, Q14257-573%"APEX_IMS, mito protein domain"none
133383SETD9SET domain containing 9C5orf35, Q8NE22-574%"APEX_matrix, targetP signal"none
22934RPIAribose 5-phosphate isomerase ARPI, P49247-575%APEX_matrixplacenta
3915LAMC1"laminin, gamma 1 (formerly LAMB2)"LAMB2, P11047-676%APEX_IMSadipose, stomach, placenta
9463PICK1protein interacting with PRKCA 1PICK, PRKCABP, Q9NRD5-676%"literature, mito protein domain"none
8846ALKBH1"alkB, alkylation repair homolog 1 (E. coli)"ABH, ABH1, ALKBH, alkB, hABH, Q13686-676%"literature, APEX_matrix, mito protein domain"none
63899NSUN3"NOP2/Sun domain family, member 3"MST077, Q9H649-676%"APEX_matrix, mito protein domain"none
599BCL2L2BCL2-like 2BCL-W, BCL2-L-2, BCLW, PPP1R51, Q92843-676%"literature, mito protein domain"none
596BCL2B-cell CLL/lymphoma 2Bcl-2, PPP1R50, P10415-676%"literature, mito protein domain"none
572BADBCL2-associated agonist of cell deathBBC2, BCL2L8, Q92934-676%"literature, mito protein domain"none
57144PAK7p21 protein (Cdc42/Rac)-activated kinase 7PAK5, Q9P286-676%"literature, mito protein domain"none
4541ND6"NADH dehydrogenase, subunit 6 (complex I)"MTND6, P03923-676%"literature, mito protein domain"none
1763DNA2DNA replication helicase/nuclease 2DNA2L, PEOA6, hDNA2, P51530-676%"literature, mito protein domain"none
1760DMPKdystrophia myotonica-protein kinaseDM, DM1, DM1PK, DMK, MDPK, MT-PK, Q09013-676%"literature, mito protein domain"none
167681PRSS35"protease, serine, 35"C6orf158, dJ223E3.1, Q8N3Z0-676%"GFP, mito protein domain"none
140886PABPC5"poly(A) binding protein, cytoplasmic 5"PABP5, Q96DU9-676%"literature, mito protein domain"none
11216AKAP10A kinase (PRKA) anchor protein 10AKAP-10, D-AKAP-2, D-AKAP2, PRKA10, O43572-676%"literature, mito protein domain"none
84947SERAC1serine active site containing 1Q96JX3-682%"literature, APEX_IMS"cerebrum, cerebellum, skeletalmuscle, stomach, testis
57205ATP10D"ATPase, class V, type 10D"ATPVD, Q9P241-682%GFPcerebrum, cerebellum, brainstem, spinalcord, kidney, liver, heart, adipose, smallintestine, largeintestine, stomach, placenta
55014STX17syntaxin 17P56962-682%"APEX_IMS, coexpression"testis
55006TRMT61BtRNA methyltransferase 61 homolog B (S. cerevisiae)Q9BVS5-682%"APEX_matrix, mito protein domain"none
55848PLGRKT"plasminogen receptor, C-terminal lysine transmembrane protein"C9orf46, MDS030, PLG-RKT, Plg-R(KT), Q9HBL7-783%GFPcerebrum, cerebellum, brainstem, spinalcord, skeletalmuscle, adipose, smallintestine, largeintestine, stomach, placenta, testis
6164RPL34ribosomal protein L34L34, P49207-783%"GFP, targetP signal"none
79048SECISBP2SECIS binding protein 2SBP2, Q96T21-783%"literature, coexpression"none
4515MTCP1mature T-cell proliferation 1P13MTCP1, p8MTCP1, P56278-884%literaturenone
205327C2orf69chromosome 2 open reading frame 69Q8N8R5-884%APEX_matrixnone
11067C10orf10chromosome 10 open reading frame 10DEPP, FIG, Q9NTK1-884%literaturenone
56624ASAH2N-acylsphingosine amidohydrolase (non-lysosomal ceramidase) 2BCDase, HNAC1, LCDase, N-CDase, NCDase, Q9NR71-886%literaturesmallintestine, placenta
25932CLIC4chloride intracellular channel 4CLIC4L, H1, MTCLIC, huH1, p64H1, Q9Y696-988%literaturestomach, placenta
9342SNAP29"synaptosomal-associated protein, 29kDa"CEDNIK, SNAP-29, O95721-1088%APEX_IMSnone
60487TRMT11tRNA methyltransferase 11 homolog (S. cerevisiae)C6orf75, MDS024, TRM11, TRMT11-1, Q7Z4G4-1088%APEX_matrixnone
387715ARMS2age-related maculopathy susceptibility 2ARMD8, P0C7Q2-1092%literaturenone